Dystonia, athetosis, and epilepsia partialis continua in a patient with late‐onset Rasmussen's encephalitis
Identifieur interne : 004491 ( Main/Exploration ); précédent : 004490; suivant : 004492Dystonia, athetosis, and epilepsia partialis continua in a patient with late‐onset Rasmussen's encephalitis
Auteurs : Steven Frucht [États-Unis]Source :
- Movement Disorders [ 0885-3185 ] ; 2002-05.
Descripteurs français
- Pascal (Inist)
English descriptors
- KwdEn :
- Adult, Age of onset, Athetosis, Athetosis (complications), Athetosis (drug therapy), Biopsy, Needle, Brain (pathology), Case study, Continuous, Diagnosis, Dystonia, Dystonia (complications), Dystonia (drug therapy), Electroencephalography, Encephalitis (complications), Encephalitis (drug therapy), Encephalitis (pathology), Epilepsies, Partial (complications), Epilepsies, Partial (drug therapy), Epilepsy, Female, Humans, Immunoglobulins, Intravenous (therapeutic use), Magnetic Resonance Imaging, Partial, Rasmussen syndrome, Treatment Outcome, Young adult.
- MESH :
- chemical , therapeutic use : Immunoglobulins, Intravenous.
- complications : Athetosis, Dystonia, Encephalitis, Epilepsies, Partial.
- drug therapy : Athetosis, Dystonia, Encephalitis, Epilepsies, Partial.
- pathology : Brain, Encephalitis.
- Adult, Biopsy, Needle, Electroencephalography, Female, Humans, Magnetic Resonance Imaging, Treatment Outcome.
Abstract
Rasmussen's encephalitis is a rare autoimmune disorder characterized by intractable epilepsy and progressive hemispheric dysfunction. The disorder usually affects children, although cases have been reported with symptom onset in late adolescence or adulthood. Myoclonus is common in Rasmussen patients, usually occurring as part of epilepsia partialis continua (EPC); however, other hyperkinetic movements are rare. This report documents a 19‐year‐old woman with Rasmussen's encephalitis whose clinical presentation was dominated by foot dystonia, arm athetosis, and EPC. Intravenous immunoglobulin improved both hyperkinetic movements and EPC, but benefit was transient. The clinical significance and implications of these findings are discussed. © 2002 Movement Disorder Society
Url:
DOI: 10.1002/mds.10131
Affiliations:
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Le document en format XML
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<term>Athetosis (complications)</term>
<term>Athetosis (drug therapy)</term>
<term>Biopsy, Needle</term>
<term>Brain (pathology)</term>
<term>Case study</term>
<term>Continuous</term>
<term>Diagnosis</term>
<term>Dystonia</term>
<term>Dystonia (complications)</term>
<term>Dystonia (drug therapy)</term>
<term>Electroencephalography</term>
<term>Encephalitis (complications)</term>
<term>Encephalitis (drug therapy)</term>
<term>Encephalitis (pathology)</term>
<term>Epilepsies, Partial (complications)</term>
<term>Epilepsies, Partial (drug therapy)</term>
<term>Epilepsy</term>
<term>Female</term>
<term>Humans</term>
<term>Immunoglobulins, Intravenous (therapeutic use)</term>
<term>Magnetic Resonance Imaging</term>
<term>Partial</term>
<term>Rasmussen syndrome</term>
<term>Treatment Outcome</term>
<term>Young adult</term>
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<term>Encephalitis</term>
<term>Epilepsies, Partial</term>
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<term>Dystonia</term>
<term>Encephalitis</term>
<term>Epilepsies, Partial</term>
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<term>Encephalitis</term>
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<term>Biopsy, Needle</term>
<term>Electroencephalography</term>
<term>Female</term>
<term>Humans</term>
<term>Magnetic Resonance Imaging</term>
<term>Treatment Outcome</term>
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<term>Athétose</term>
<term>Continu</term>
<term>Diagnostic</term>
<term>Dystonie</term>
<term>Epilepsie</term>
<term>Etude cas</term>
<term>Femelle</term>
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<front><div type="abstract" xml:lang="en">Rasmussen's encephalitis is a rare autoimmune disorder characterized by intractable epilepsy and progressive hemispheric dysfunction. The disorder usually affects children, although cases have been reported with symptom onset in late adolescence or adulthood. Myoclonus is common in Rasmussen patients, usually occurring as part of epilepsia partialis continua (EPC); however, other hyperkinetic movements are rare. This report documents a 19‐year‐old woman with Rasmussen's encephalitis whose clinical presentation was dominated by foot dystonia, arm athetosis, and EPC. Intravenous immunoglobulin improved both hyperkinetic movements and EPC, but benefit was transient. The clinical significance and implications of these findings are discussed. © 2002 Movement Disorder Society</div>
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