Dystonia, athetosis, and epilepsia partialis continua in a patient with late‐onset Rasmussen's encephalitis
Identifieur interne : 002D82 ( Istex/Checkpoint ); précédent : 002D81; suivant : 002D83Dystonia, athetosis, and epilepsia partialis continua in a patient with late‐onset Rasmussen's encephalitis
Auteurs : Steven Frucht [États-Unis]Source :
- Movement Disorders [ 0885-3185 ] ; 2002-05.
Abstract
Rasmussen's encephalitis is a rare autoimmune disorder characterized by intractable epilepsy and progressive hemispheric dysfunction. The disorder usually affects children, although cases have been reported with symptom onset in late adolescence or adulthood. Myoclonus is common in Rasmussen patients, usually occurring as part of epilepsia partialis continua (EPC); however, other hyperkinetic movements are rare. This report documents a 19‐year‐old woman with Rasmussen's encephalitis whose clinical presentation was dominated by foot dystonia, arm athetosis, and EPC. Intravenous immunoglobulin improved both hyperkinetic movements and EPC, but benefit was transient. The clinical significance and implications of these findings are discussed. © 2002 Movement Disorder Society
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DOI: 10.1002/mds.10131
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<record><TEI wicri:istexFullTextTei="biblStruct"><teiHeader><fileDesc><titleStmt><title xml:lang="en">Dystonia, athetosis, and epilepsia partialis continua in a patient with late‐onset Rasmussen's encephalitis</title><author><name sortKey="Frucht, Steven" sort="Frucht, Steven" uniqKey="Frucht S" first="Steven" last="Frucht">Steven Frucht</name></author></titleStmt><publicationStmt><idno type="wicri:source">ISTEX</idno><idno type="RBID">ISTEX:F30843A60F52A97874DEA2BF1955BCE1CB24F6FC</idno><date when="2002" year="2002">2002</date><idno type="doi">10.1002/mds.10131</idno><idno type="url">https://api.istex.fr/document/F30843A60F52A97874DEA2BF1955BCE1CB24F6FC/fulltext/pdf</idno><idno type="wicri:Area/Istex/Corpus">000E71</idno><idno type="wicri:Area/Istex/Curation">000E71</idno><idno type="wicri:Area/Istex/Checkpoint">002D82</idno></publicationStmt><sourceDesc><biblStruct><analytic><title level="a" type="main" xml:lang="en">Dystonia, athetosis, and epilepsia partialis continua in a patient with late‐onset Rasmussen's encephalitis</title><author><name sortKey="Frucht, Steven" sort="Frucht, Steven" uniqKey="Frucht S" first="Steven" last="Frucht">Steven Frucht</name><affiliation wicri:level="2"><country xml:lang="fr">États-Unis</country><wicri:regionArea>Columbia‐Presbyterian Medical Center, The Neurological Institute, New York, New York</wicri:regionArea><placeName><region type="state">État de New York</region></placeName></affiliation></author></analytic><monogr></monogr><series><title level="j">Movement Disorders</title><title level="j" type="sub">Official Journal of the Movement Disorder Society</title><title level="j" type="abbrev">Mov. Disord.</title><idno type="ISSN">0885-3185</idno><idno type="eISSN">1531-8257</idno><imprint><publisher>Wiley Subscription Services, Inc., A Wiley Company</publisher><pubPlace>New York</pubPlace><date type="published" when="2002-05">2002-05</date><biblScope unit="vol">17</biblScope><biblScope unit="issue">3</biblScope><biblScope unit="page" from="609">609</biblScope><biblScope unit="page" to="612">612</biblScope></imprint><idno type="ISSN">0885-3185</idno></series><idno type="istex">F30843A60F52A97874DEA2BF1955BCE1CB24F6FC</idno><idno type="DOI">10.1002/mds.10131</idno><idno type="ArticleID">MDS10131</idno></biblStruct></sourceDesc><seriesStmt><idno type="ISSN">0885-3185</idno></seriesStmt></fileDesc><profileDesc><textClass></textClass><langUsage><language ident="en">en</language></langUsage></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">Rasmussen's encephalitis is a rare autoimmune disorder characterized by intractable epilepsy and progressive hemispheric dysfunction. The disorder usually affects children, although cases have been reported with symptom onset in late adolescence or adulthood. Myoclonus is common in Rasmussen patients, usually occurring as part of epilepsia partialis continua (EPC); however, other hyperkinetic movements are rare. This report documents a 19‐year‐old woman with Rasmussen's encephalitis whose clinical presentation was dominated by foot dystonia, arm athetosis, and EPC. Intravenous immunoglobulin improved both hyperkinetic movements and EPC, but benefit was transient. The clinical significance and implications of these findings are discussed. © 2002 Movement Disorder Society</div></front></TEI><affiliations><list><country><li>États-Unis</li></country><region><li>État de New York</li></region></list><tree><country name="États-Unis"><region name="État de New York"><name sortKey="Frucht, Steven" sort="Frucht, Steven" uniqKey="Frucht S" first="Steven" last="Frucht">Steven Frucht</name></region></country></tree></affiliations></record>Pour manipuler ce document sous Unix (Dilib)
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