MovDisordV3, PascalFrancis, Curation, bibRecord, 000595

Dystonia, athetosis, and epilepsia partialis continua in a patient with late-onset Rasmussen's encephalitis

Identifieur interne : 000595 ( PascalFrancis/Curation ); précédent : 000594; suivant : 000596

Dystonia, athetosis, and epilepsia partialis continua in a patient with late-onset Rasmussen's encephalitis

Auteurs : Steven Frucht [États-Unis]

Source :

Movement disorders [ 0885-3185 ] ; 2002.

RBID : Pascal:02-0369782

Descripteurs français

Pascal (Inist)
- Rasmussen syndrome, Dystonie, Athétose, Epilepsie, Partiel, Continu, Age apparition, Etude cas, Diagnostic, Adulte jeune, Femelle.

English descriptors

KwdEn :
- Age of onset, Athetosis, Case study, Continuous, Diagnosis, Dystonia, Epilepsy, Female, Partial, Rasmussen syndrome, Young adult.

Abstract

Rasmussen's encephalitis is a rare autoimmune disorder characterized by intractable epilepsy and progressive hemispheric dysfunction. The disorder usually affects children, although cases have been reported with symptom onset in late adolescence or adulthood. Myoclonus is common in Rasmussen patients, usually occurring as part of epilepsia partialis continua (EPC); however, other hyperkinetic movements are rare. This report documents a 19-year-old woman with Rasmussen's encephalitis whose clinical presentation was dominated by foot dystonia, arm athetosis, and EPC. Intravenous immunoglobulin improved both hyperkinetic movements and EPC, but benefit was transient. The clinical significance and implications of these findings are discussed.

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A06				`@2 3`
A08	`01`	`1`	`ENG`	`@1 Dystonia, athetosis, and epilepsia partialis continua in a patient with late-onset Rasmussen's encephalitis`
A11	`01`	`1`		`@1 FRUCHT (Steven)`
A14	`01`			`@1 Columbia-Presbyterian Medical Center, The Neurological Institute @2 New York, New York @3 USA @Z 1 aut.`
A20				`@1 609-612`
A21				`@1 2002`
A23	`01`			`@0 ENG`
A43	`01`			`@1 INIST @2 20953 @5 354000108224770320`
A44				`@0 0000 @1 © 2002 INIST-CNRS. All rights reserved.`
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C01	`01`		`ENG`	@0 Rasmussen's encephalitis is a rare autoimmune disorder characterized by intractable epilepsy and progressive hemispheric dysfunction. The disorder usually affects children, although cases have been reported with symptom onset in late adolescence or adulthood. Myoclonus is common in Rasmussen patients, usually occurring as part of epilepsia partialis continua (EPC); however, other hyperkinetic movements are rare. This report documents a 19-year-old woman with Rasmussen's encephalitis whose clinical presentation was dominated by foot dystonia, arm athetosis, and EPC. Intravenous immunoglobulin improved both hyperkinetic movements and EPC, but benefit was transient. The clinical significance and implications of these findings are discussed.
C02	`01`	`X`		`@0 002B17A02`
C03	`01`	`X`	`FRE`	`@0 Rasmussen syndrome @2 NM @5 01`
C03	`01`	`X`	`ENG`	`@0 Rasmussen syndrome @2 NM @5 01`
C03	`01`	`X`	`SPA`	`@0 Rasmussen síndrome @2 NM @5 01`
C03	`02`	`X`	`FRE`	`@0 Dystonie @5 04`
C03	`02`	`X`	`ENG`	`@0 Dystonia @5 04`
C03	`02`	`X`	`SPA`	`@0 Distonía @5 04`
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C03	`03`	`X`	`ENG`	`@0 Athetosis @5 07`
C03	`03`	`X`	`SPA`	`@0 Atetosis @5 07`
C03	`04`	`X`	`FRE`	`@0 Epilepsie @5 10`
C03	`04`	`X`	`ENG`	`@0 Epilepsy @5 10`
C03	`04`	`X`	`SPA`	`@0 Epilepsia @5 10`
C03	`05`	`X`	`FRE`	`@0 Partiel @5 11`
C03	`05`	`X`	`ENG`	`@0 Partial @5 11`
C03	`05`	`X`	`SPA`	`@0 Parcial @5 11`
C03	`06`	`X`	`FRE`	`@0 Continu @5 12`
C03	`06`	`X`	`ENG`	`@0 Continuous @5 12`
C03	`06`	`X`	`SPA`	`@0 Contínuo @5 12`
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C03	`09`	`X`	`FRE`	`@0 Diagnostic @5 18`
C03	`09`	`X`	`ENG`	`@0 Diagnosis @5 18`
C03	`09`	`X`	`SPA`	`@0 Diagnóstico @5 18`
C03	`10`	`X`	`FRE`	`@0 Adulte jeune @5 20`
C03	`10`	`X`	`ENG`	`@0 Young adult @5 20`
C03	`10`	`X`	`SPA`	`@0 Adulto joven @5 20`
C03	`11`	`X`	`FRE`	`@0 Femelle @5 21`
C03	`11`	`X`	`ENG`	`@0 Female @5 21`
C03	`11`	`X`	`SPA`	`@0 Hembra @5 21`
C07	`01`	`X`	`FRE`	`@0 Homme`
C07	`01`	`X`	`ENG`	`@0 Human`
C07	`01`	`X`	`SPA`	`@0 Hombre`
C07	`02`	`X`	`FRE`	`@0 Système nerveux pathologie @5 37`
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C07	`03`	`X`	`FRE`	`@0 Système nerveux central pathologie @5 38`
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C07	`03`	`X`	`SPA`	`@0 Sistema nervosio central patología @5 38`
C07	`04`	`X`	`FRE`	`@0 Encéphale pathologie @5 39`
C07	`04`	`X`	`ENG`	`@0 Cerebral disorder @5 39`
C07	`04`	`X`	`SPA`	`@0 Encéfalo patología @5 39`
C07	`05`	`X`	`FRE`	`@0 Encéphalite @5 40`
C07	`05`	`X`	`ENG`	`@0 Encephalitis @5 40`
C07	`05`	`X`	`SPA`	`@0 Encefalitis @5 40`
C07	`06`	`X`	`FRE`	`@0 Muscle strié pathologie @5 45`
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C07	`07`	`X`	`FRE`	`@0 Extrapyramidal syndrome @5 46`
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C07	`07`	`X`	`SPA`	`@0 Extrapiramidal síndrome @5 46`
C07	`08`	`X`	`FRE`	`@0 Trouble neurologique @5 47`
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C07	`08`	`X`	`SPA`	`@0 Trastorno neurológico @5 47`
C07	`09`	`X`	`FRE`	`@0 Mouvement involontaire @5 48`
C07	`09`	`X`	`ENG`	`@0 Involuntary movement @5 48`
C07	`09`	`X`	`SPA`	`@0 Movimiento involuntario @5 48`
N21				`@1 203`
N82				`@1 PSI`

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Pascal:02-0369782

Le document en format XML

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<front><div type="abstract" xml:lang="en">Rasmussen's encephalitis is a rare autoimmune disorder characterized by intractable epilepsy and progressive hemispheric dysfunction. The disorder usually affects children, although cases have been reported with symptom onset in late adolescence or adulthood. Myoclonus is common in Rasmussen patients, usually occurring as part of epilepsia partialis continua (EPC); however, other hyperkinetic movements are rare. This report documents a 19-year-old woman with Rasmussen's encephalitis whose clinical presentation was dominated by foot dystonia, arm athetosis, and EPC. Intravenous immunoglobulin improved both hyperkinetic movements and EPC, but benefit was transient. The clinical significance and implications of these findings are discussed.</div>
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   |type=    RBID
   |clé=     Pascal:02-0369782
   |texte=   Dystonia, athetosis, and epilepsia partialis continua in a patient with late-onset Rasmussen's encephalitis
}}

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	Movement Disorders (revue)
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Movement Disorders (revue)

Dystonia, athetosis, and epilepsia partialis continua in a patient with late-onset Rasmussen's encephalitis

Dystonia, athetosis, and epilepsia partialis continua in a patient with late-onset Rasmussen's encephalitis

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