MovDisordV3, PascalFrancis, Curation, bibRecord, 001A62

Regression of Symptoms After Selective Iron Chelation Therapy in a Case of Neurodegeneration with Brain Iron Accumulation

Identifieur interne : 001A62 ( PascalFrancis/Curation ); précédent : 001A61; suivant : 001A63

Regression of Symptoms After Selective Iron Chelation Therapy in a Case of Neurodegeneration with Brain Iron Accumulation

Auteurs : Gian Luca Fomi [Italie] ; Manuela Balocco [Italie] ; Laura Cremonesi [Italie] ; Giovanni Abbruzzese [Italie] ; Roberto Carlo Parodi [Italie] ; Roberta Marchese [Italie]

Source :

Movement disorders [ 0885-3185 ] ; 2008.

RBID : Pascal:08-0251877

Descripteurs français

Pascal (Inist)
- Pathologie du système nerveux, Fer, Traitement, Encéphale, Défériprone.
Wicri :
- topic : Fer.

English descriptors

KwdEn :
- Deferiprone, Encephalon, Iron, Nervous system diseases, Treatment.

Abstract

We report the results of iron chelating treatment with deferiprone in a 61-year-old woman with signs and symptoms of neurodegeneration with brain iron accumulation (NBIA). After 6 months of therapy the patient's gait had improved and a reduction in the incidence of choreic dyskinesias was observed. Her gait returned to normal after an additional 2 months of therapy, at which time there was a further reduction in involuntary movements and a partial resolution of the blepharospasm.

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A44				`@0 0000 @1 © 2008 INIST-CNRS. All rights reserved.`
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C01	`01`		`ENG`	`@0 We report the results of iron chelating treatment with deferiprone in a 61-year-old woman with signs and symptoms of neurodegeneration with brain iron accumulation (NBIA). After 6 months of therapy the patient's gait had improved and a reduction in the incidence of choreic dyskinesias was observed. Her gait returned to normal after an additional 2 months of therapy, at which time there was a further reduction in involuntary movements and a partial resolution of the blepharospasm.`
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C03	`01`	`X`	`SPA`	`@0 Sistema nervioso patología @5 01`
C03	`02`	`X`	`FRE`	`@0 Fer @2 NC @5 09`
C03	`02`	`X`	`ENG`	`@0 Iron @2 NC @5 09`
C03	`02`	`X`	`SPA`	`@0 Hierro @2 NC @5 09`
C03	`03`	`X`	`FRE`	`@0 Traitement @5 10`
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C03	`04`	`X`	`FRE`	`@0 Encéphale @5 11`
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C03	`04`	`X`	`SPA`	`@0 Encéfalo @5 11`
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C03	`05`	`X`	`SPA`	`@0 Deferiprona @2 NK @2 FR @5 12`
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C07	`01`	`X`	`ENG`	`@0 Central nervous system @5 37`
C07	`01`	`X`	`SPA`	`@0 Sistema nervioso central @5 37`
N21				`@1 162`
N44	`01`			`@1 OTO`
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Le document en format XML

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<author><name sortKey="Luca Fomi, Gian" sort="Luca Fomi, Gian" uniqKey="Luca Fomi G" first="Gian" last="Luca Fomi">Gian Luca Fomi</name>
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	Movement Disorders (revue)
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Movement Disorders (revue)

Regression of Symptoms After Selective Iron Chelation Therapy in a Case of Neurodegeneration with Brain Iron Accumulation

Regression of Symptoms After Selective Iron Chelation Therapy in a Case of Neurodegeneration with Brain Iron Accumulation

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Descripteurs français

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Abstract

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