Movement Disorders (revue)

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Extraocular Muscle Dystonia Due to Acquired (non-Wilsonian) Hepatocerebral Degeneration

Identifieur interne : 001A61 ( PascalFrancis/Curation ); précédent : 001A60; suivant : 001A62

Extraocular Muscle Dystonia Due to Acquired (non-Wilsonian) Hepatocerebral Degeneration

Auteurs : Joseph Ferrara [États-Unis] ; Deepak Gupta [États-Unis] ; Emily Foster [États-Unis] ; Katherine Garman [États-Unis] ; Mark Stacy [États-Unis]

Source :

RBID : Pascal:08-0251876

Descripteurs français

English descriptors

Abstract

We present a video report of a patient with advanced non-Wilsonian cirrhotic liver disease who developed extraocular muscle dystonia (oculogyric crisis) and severe orofaciolingual dyskinesias. Acquired hepatocerebral degeneration causes choreic movements, especially of cranial muscles, but dystonic ocular spasm is an infrequent manifestation of this disorder. This case illustrates that AHD should be considered in the differential diagnosis of extraocular muscle dystonia.
pA  
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A03   1    @0 Mov. disord.
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A08 01  1  ENG  @1 Extraocular Muscle Dystonia Due to Acquired (non-Wilsonian) Hepatocerebral Degeneration
A11 01  1    @1 FERRARA (Joseph)
A11 02  1    @1 GUPTA (Deepak)
A11 03  1    @1 FOSTER (Emily)
A11 04  1    @1 GARMAN (Katherine)
A11 05  1    @1 STACY (Mark)
A14 01      @1 Department of Medicine, Division of Neurology, Duke University Medical Center @2 Durham, North Carolina @3 USA @Z 1 aut. @Z 2 aut. @Z 3 aut. @Z 4 aut. @Z 5 aut.
A20       @1 875-878
A21       @1 2008
A23 01      @0 ENG
A43 01      @1 INIST @2 20953 @5 354000195888140150
A44       @0 0000 @1 © 2008 INIST-CNRS. All rights reserved.
A45       @0 46 ref.
A47 01  1    @0 08-0251876
A60       @1 P @3 CC
A61       @0 A
A64 01  1    @0 Movement disorders
A66 01      @0 USA
C01 01    ENG  @0 We present a video report of a patient with advanced non-Wilsonian cirrhotic liver disease who developed extraocular muscle dystonia (oculogyric crisis) and severe orofaciolingual dyskinesias. Acquired hepatocerebral degeneration causes choreic movements, especially of cranial muscles, but dystonic ocular spasm is an infrequent manifestation of this disorder. This case illustrates that AHD should be considered in the differential diagnosis of extraocular muscle dystonia.
C02 01  X    @0 002B17
C02 02  X    @0 002B17H
C03 01  X  FRE  @0 Dystonie @5 01
C03 01  X  ENG  @0 Dystonia @5 01
C03 01  X  SPA  @0 Distonía @5 01
C03 02  X  FRE  @0 Dégénérescence @5 02
C03 02  X  ENG  @0 Degeneration @5 02
C03 02  X  SPA  @0 Degeneración @5 02
C03 03  X  FRE  @0 Pathologie du système nerveux @5 03
C03 03  X  ENG  @0 Nervous system diseases @5 03
C03 03  X  SPA  @0 Sistema nervioso patología @5 03
C03 04  X  FRE  @0 Muscle oculaire @5 09
C03 04  X  ENG  @0 Eye muscle @5 09
C03 04  X  SPA  @0 Músculo ocular @5 09
C03 05  X  FRE  @0 Crise oculogyre @2 NM @5 10
C03 05  X  ENG  @0 Oculogyric crisis @2 NM @5 10
C03 05  X  SPA  @0 Crisis oculógira @2 NM @5 10
C07 01  X  FRE  @0 Syndrome extrapyramidal @5 37
C07 01  X  ENG  @0 Extrapyramidal syndrome @5 37
C07 01  X  SPA  @0 Extrapiramidal síndrome @5 37
C07 02  X  FRE  @0 Mouvement involontaire @5 38
C07 02  X  ENG  @0 Involuntary movement @5 38
C07 02  X  SPA  @0 Movimiento involuntario @5 38
C07 03  X  FRE  @0 Pathologie du muscle strié @5 39
C07 03  X  ENG  @0 Striated muscle disease @5 39
C07 03  X  SPA  @0 Músculo estriado patología @5 39
C07 04  X  FRE  @0 Trouble neurologique @5 41
C07 04  X  ENG  @0 Neurological disorder @5 41
C07 04  X  SPA  @0 Trastorno neurológico @5 41
C07 05  X  FRE  @0 Pathologie de l'encéphale @5 42
C07 05  X  ENG  @0 Cerebral disorder @5 42
C07 05  X  SPA  @0 Encéfalo patología @5 42
C07 06  X  FRE  @0 Pathologie du système nerveux central @5 43
C07 06  X  ENG  @0 Central nervous system disease @5 43
C07 06  X  SPA  @0 Sistema nervosio central patología @5 43
N21       @1 162
N44 01      @1 OTO
N82       @1 OTO

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Pascal:08-0251876

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