Movement Disorders (revue)

Attention, ce site est en cours de développement !
Attention, site généré par des moyens informatiques à partir de corpus bruts.
Les informations ne sont donc pas validées.

Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease

Identifieur interne : 002629 ( PascalFrancis/Corpus ); précédent : 002628; suivant : 002630

Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease

Auteurs : Mark A. Hellmann ; Eldad Melamed

Source :

RBID : Pascal:02-0584388

Descripteurs français

English descriptors

Abstract

A variety of movement disorders may occur during the course of prion disease. We describe a unique patient who had focal upper limb dystonia as the presenting symptom of familial codon 200 mutation-positive Creutzfeldt-Jakob disease.

Notice en format standard (ISO 2709)

Pour connaître la documentation sur le format Inist Standard.

pA  
A01 01  1    @0 0885-3185
A03   1    @0 Mov. disord.
A05       @2 17
A06       @2 5
A08 01  1  ENG  @1 Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease
A11 01  1    @1 HELLMANN (Mark A.)
A11 02  1    @1 MELAMED (Eldad)
A14 01      @1 Department of Neurology, Rabin Medical Centre, Beilinson Campus and Tel Aviv University School of Medicine @2 Petah Tiqva @3 ISR @Z 1 aut. @Z 2 aut.
A20       @1 1097-1098
A21       @1 2002
A23 01      @0 ENG
A43 01      @1 INIST @2 20953 @5 354000105152380370
A44       @0 0000 @1 © 2002 INIST-CNRS. All rights reserved.
A45       @0 7 ref.
A47 01  1    @0 02-0584388
A60       @1 P
A61       @0 A
A64 01  1    @0 Movement disorders
A66 01      @0 USA
C01 01    ENG  @0 A variety of movement disorders may occur during the course of prion disease. We describe a unique patient who had focal upper limb dystonia as the presenting symptom of familial codon 200 mutation-positive Creutzfeldt-Jakob disease.
C02 01  X    @0 002B17G
C02 02  X    @0 235
C03 01  X  FRE  @0 Encéphalopathie spongiforme Creutzfeldt Jakob @5 01
C03 01  X  ENG  @0 Creutzfeldt Jakob disease @5 01
C03 01  X  SPA  @0 Encefalopatía espongiforme Creutzfeldt Jakob @5 01
C03 02  X  FRE  @0 Dystonie @5 04
C03 02  X  ENG  @0 Dystonia @5 04
C03 02  X  SPA  @0 Distonía @5 04
C03 03  X  FRE  @0 Lésion focale @5 07
C03 03  X  ENG  @0 Focal lesion @5 07
C03 03  X  SPA  @0 Lesión focal @5 07
C03 04  X  FRE  @0 Etude cas @5 16
C03 04  X  ENG  @0 Case study @5 16
C03 04  X  SPA  @0 Estudio caso @5 16
C03 05  X  FRE  @0 Signe inaugural @5 17
C03 05  X  ENG  @0 Inaugural sign @5 17
C03 05  X  SPA  @0 Signo inaugural @5 17
C03 06  X  FRE  @0 Homme @5 20
C03 06  X  ENG  @0 Human @5 20
C03 06  X  SPA  @0 Hombre @5 20
C03 07  X  FRE  @0 Prion @5 25
C03 07  X  ENG  @0 Prion @5 25
C03 07  X  SPA  @0 Prión @5 25
C07 01  X  FRE  @0 Infection
C07 01  X  ENG  @0 Infection
C07 01  X  SPA  @0 Infección
C07 02  X  FRE  @0 Système nerveux pathologie @5 37
C07 02  X  ENG  @0 Nervous system diseases @5 37
C07 02  X  SPA  @0 Sistema nervioso patología @5 37
C07 03  X  FRE  @0 Système nerveux central pathologie @5 38
C07 03  X  ENG  @0 Central nervous system disease @5 38
C07 03  X  SPA  @0 Sistema nervosio central patología @5 38
C07 04  X  FRE  @0 Encéphale pathologie @5 39
C07 04  X  ENG  @0 Cerebral disorder @5 39
C07 04  X  SPA  @0 Encéfalo patología @5 39
C07 05  X  FRE  @0 Maladie dégénérative @5 40
C07 05  X  ENG  @0 Degenerative disease @5 40
C07 05  X  SPA  @0 Enfermedad degenerativa @5 40
C07 06  X  FRE  @0 Muscle strié pathologie @5 45
C07 06  X  ENG  @0 Striated muscle disease @5 45
C07 06  X  SPA  @0 Músculo estriado patología @5 45
C07 07  X  FRE  @0 Trouble neurologique @5 47
C07 07  X  ENG  @0 Neurological disorder @5 47
C07 07  X  SPA  @0 Trastorno neurológico @5 47
C07 08  X  FRE  @0 Mouvement involontaire @5 48
C07 08  X  ENG  @0 Involuntary movement @5 48
C07 08  X  SPA  @0 Movimiento involuntario @5 48
C07 09  X  FRE  @0 Extrapyramidal syndrome @5 49
C07 09  X  ENG  @0 Extrapyramidal syndrome @5 49
C07 09  X  SPA  @0 Extrapiramidal síndrome @5 49
N21       @1 343
N82       @1 PSI

Format Inist (serveur)

NO : PASCAL 02-0584388 INIST
ET : Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease
AU : HELLMANN (Mark A.); MELAMED (Eldad)
AF : Department of Neurology, Rabin Medical Centre, Beilinson Campus and Tel Aviv University School of Medicine/Petah Tiqva/Israël (1 aut., 2 aut.)
DT : Publication en série; Niveau analytique
SO : Movement disorders; ISSN 0885-3185; Etats-Unis; Da. 2002; Vol. 17; No. 5; Pp. 1097-1098; Bibl. 7 ref.
LA : Anglais
EA : A variety of movement disorders may occur during the course of prion disease. We describe a unique patient who had focal upper limb dystonia as the presenting symptom of familial codon 200 mutation-positive Creutzfeldt-Jakob disease.
CC : 002B17G; 235
FD : Encéphalopathie spongiforme Creutzfeldt Jakob; Dystonie; Lésion focale; Etude cas; Signe inaugural; Homme; Prion
FG : Infection; Système nerveux pathologie; Système nerveux central pathologie; Encéphale pathologie; Maladie dégénérative; Muscle strié pathologie; Trouble neurologique; Mouvement involontaire; Extrapyramidal syndrome
ED : Creutzfeldt Jakob disease; Dystonia; Focal lesion; Case study; Inaugural sign; Human; Prion
EG : Infection; Nervous system diseases; Central nervous system disease; Cerebral disorder; Degenerative disease; Striated muscle disease; Neurological disorder; Involuntary movement; Extrapyramidal syndrome
SD : Encefalopatía espongiforme Creutzfeldt Jakob; Distonía; Lesión focal; Estudio caso; Signo inaugural; Hombre; Prión
LO : INIST-20953.354000105152380370
ID : 02-0584388

Links to Exploration step

Pascal:02-0584388

Le document en format XML

<record>
<TEI>
<teiHeader>
<fileDesc>
<titleStmt>
<title xml:lang="en" level="a">Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease</title>
<author>
<name sortKey="Hellmann, Mark A" sort="Hellmann, Mark A" uniqKey="Hellmann M" first="Mark A." last="Hellmann">Mark A. Hellmann</name>
<affiliation>
<inist:fA14 i1="01">
<s1>Department of Neurology, Rabin Medical Centre, Beilinson Campus and Tel Aviv University School of Medicine</s1>
<s2>Petah Tiqva</s2>
<s3>ISR</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
</inist:fA14>
</affiliation>
</author>
<author>
<name sortKey="Melamed, Eldad" sort="Melamed, Eldad" uniqKey="Melamed E" first="Eldad" last="Melamed">Eldad Melamed</name>
<affiliation>
<inist:fA14 i1="01">
<s1>Department of Neurology, Rabin Medical Centre, Beilinson Campus and Tel Aviv University School of Medicine</s1>
<s2>Petah Tiqva</s2>
<s3>ISR</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
</inist:fA14>
</affiliation>
</author>
</titleStmt>
<publicationStmt>
<idno type="wicri:source">INIST</idno>
<idno type="inist">02-0584388</idno>
<date when="2002">2002</date>
<idno type="stanalyst">PASCAL 02-0584388 INIST</idno>
<idno type="RBID">Pascal:02-0584388</idno>
<idno type="wicri:Area/PascalFrancis/Corpus">002629</idno>
</publicationStmt>
<sourceDesc>
<biblStruct>
<analytic>
<title xml:lang="en" level="a">Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease</title>
<author>
<name sortKey="Hellmann, Mark A" sort="Hellmann, Mark A" uniqKey="Hellmann M" first="Mark A." last="Hellmann">Mark A. Hellmann</name>
<affiliation>
<inist:fA14 i1="01">
<s1>Department of Neurology, Rabin Medical Centre, Beilinson Campus and Tel Aviv University School of Medicine</s1>
<s2>Petah Tiqva</s2>
<s3>ISR</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
</inist:fA14>
</affiliation>
</author>
<author>
<name sortKey="Melamed, Eldad" sort="Melamed, Eldad" uniqKey="Melamed E" first="Eldad" last="Melamed">Eldad Melamed</name>
<affiliation>
<inist:fA14 i1="01">
<s1>Department of Neurology, Rabin Medical Centre, Beilinson Campus and Tel Aviv University School of Medicine</s1>
<s2>Petah Tiqva</s2>
<s3>ISR</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
</inist:fA14>
</affiliation>
</author>
</analytic>
<series>
<title level="j" type="main">Movement disorders</title>
<title level="j" type="abbreviated">Mov. disord.</title>
<idno type="ISSN">0885-3185</idno>
<imprint>
<date when="2002">2002</date>
</imprint>
</series>
</biblStruct>
</sourceDesc>
<seriesStmt>
<title level="j" type="main">Movement disorders</title>
<title level="j" type="abbreviated">Mov. disord.</title>
<idno type="ISSN">0885-3185</idno>
</seriesStmt>
</fileDesc>
<profileDesc>
<textClass>
<keywords scheme="KwdEn" xml:lang="en">
<term>Case study</term>
<term>Creutzfeldt Jakob disease</term>
<term>Dystonia</term>
<term>Focal lesion</term>
<term>Human</term>
<term>Inaugural sign</term>
<term>Prion</term>
</keywords>
<keywords scheme="Pascal" xml:lang="fr">
<term>Encéphalopathie spongiforme Creutzfeldt Jakob</term>
<term>Dystonie</term>
<term>Lésion focale</term>
<term>Etude cas</term>
<term>Signe inaugural</term>
<term>Homme</term>
<term>Prion</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front>
<div type="abstract" xml:lang="en">A variety of movement disorders may occur during the course of prion disease. We describe a unique patient who had focal upper limb dystonia as the presenting symptom of familial codon 200 mutation-positive Creutzfeldt-Jakob disease.</div>
</front>
</TEI>
<inist>
<standard h6="B">
<pA>
<fA01 i1="01" i2="1">
<s0>0885-3185</s0>
</fA01>
<fA03 i2="1">
<s0>Mov. disord.</s0>
</fA03>
<fA05>
<s2>17</s2>
</fA05>
<fA06>
<s2>5</s2>
</fA06>
<fA08 i1="01" i2="1" l="ENG">
<s1>Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease</s1>
</fA08>
<fA11 i1="01" i2="1">
<s1>HELLMANN (Mark A.)</s1>
</fA11>
<fA11 i1="02" i2="1">
<s1>MELAMED (Eldad)</s1>
</fA11>
<fA14 i1="01">
<s1>Department of Neurology, Rabin Medical Centre, Beilinson Campus and Tel Aviv University School of Medicine</s1>
<s2>Petah Tiqva</s2>
<s3>ISR</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
</fA14>
<fA20>
<s1>1097-1098</s1>
</fA20>
<fA21>
<s1>2002</s1>
</fA21>
<fA23 i1="01">
<s0>ENG</s0>
</fA23>
<fA43 i1="01">
<s1>INIST</s1>
<s2>20953</s2>
<s5>354000105152380370</s5>
</fA43>
<fA44>
<s0>0000</s0>
<s1>© 2002 INIST-CNRS. All rights reserved.</s1>
</fA44>
<fA45>
<s0>7 ref.</s0>
</fA45>
<fA47 i1="01" i2="1">
<s0>02-0584388</s0>
</fA47>
<fA60>
<s1>P</s1>
</fA60>
<fA61>
<s0>A</s0>
</fA61>
<fA64 i1="01" i2="1">
<s0>Movement disorders</s0>
</fA64>
<fA66 i1="01">
<s0>USA</s0>
</fA66>
<fC01 i1="01" l="ENG">
<s0>A variety of movement disorders may occur during the course of prion disease. We describe a unique patient who had focal upper limb dystonia as the presenting symptom of familial codon 200 mutation-positive Creutzfeldt-Jakob disease.</s0>
</fC01>
<fC02 i1="01" i2="X">
<s0>002B17G</s0>
</fC02>
<fC02 i1="02" i2="X">
<s0>235</s0>
</fC02>
<fC03 i1="01" i2="X" l="FRE">
<s0>Encéphalopathie spongiforme Creutzfeldt Jakob</s0>
<s5>01</s5>
</fC03>
<fC03 i1="01" i2="X" l="ENG">
<s0>Creutzfeldt Jakob disease</s0>
<s5>01</s5>
</fC03>
<fC03 i1="01" i2="X" l="SPA">
<s0>Encefalopatía espongiforme Creutzfeldt Jakob</s0>
<s5>01</s5>
</fC03>
<fC03 i1="02" i2="X" l="FRE">
<s0>Dystonie</s0>
<s5>04</s5>
</fC03>
<fC03 i1="02" i2="X" l="ENG">
<s0>Dystonia</s0>
<s5>04</s5>
</fC03>
<fC03 i1="02" i2="X" l="SPA">
<s0>Distonía</s0>
<s5>04</s5>
</fC03>
<fC03 i1="03" i2="X" l="FRE">
<s0>Lésion focale</s0>
<s5>07</s5>
</fC03>
<fC03 i1="03" i2="X" l="ENG">
<s0>Focal lesion</s0>
<s5>07</s5>
</fC03>
<fC03 i1="03" i2="X" l="SPA">
<s0>Lesión focal</s0>
<s5>07</s5>
</fC03>
<fC03 i1="04" i2="X" l="FRE">
<s0>Etude cas</s0>
<s5>16</s5>
</fC03>
<fC03 i1="04" i2="X" l="ENG">
<s0>Case study</s0>
<s5>16</s5>
</fC03>
<fC03 i1="04" i2="X" l="SPA">
<s0>Estudio caso</s0>
<s5>16</s5>
</fC03>
<fC03 i1="05" i2="X" l="FRE">
<s0>Signe inaugural</s0>
<s5>17</s5>
</fC03>
<fC03 i1="05" i2="X" l="ENG">
<s0>Inaugural sign</s0>
<s5>17</s5>
</fC03>
<fC03 i1="05" i2="X" l="SPA">
<s0>Signo inaugural</s0>
<s5>17</s5>
</fC03>
<fC03 i1="06" i2="X" l="FRE">
<s0>Homme</s0>
<s5>20</s5>
</fC03>
<fC03 i1="06" i2="X" l="ENG">
<s0>Human</s0>
<s5>20</s5>
</fC03>
<fC03 i1="06" i2="X" l="SPA">
<s0>Hombre</s0>
<s5>20</s5>
</fC03>
<fC03 i1="07" i2="X" l="FRE">
<s0>Prion</s0>
<s5>25</s5>
</fC03>
<fC03 i1="07" i2="X" l="ENG">
<s0>Prion</s0>
<s5>25</s5>
</fC03>
<fC03 i1="07" i2="X" l="SPA">
<s0>Prión</s0>
<s5>25</s5>
</fC03>
<fC07 i1="01" i2="X" l="FRE">
<s0>Infection</s0>
</fC07>
<fC07 i1="01" i2="X" l="ENG">
<s0>Infection</s0>
</fC07>
<fC07 i1="01" i2="X" l="SPA">
<s0>Infección</s0>
</fC07>
<fC07 i1="02" i2="X" l="FRE">
<s0>Système nerveux pathologie</s0>
<s5>37</s5>
</fC07>
<fC07 i1="02" i2="X" l="ENG">
<s0>Nervous system diseases</s0>
<s5>37</s5>
</fC07>
<fC07 i1="02" i2="X" l="SPA">
<s0>Sistema nervioso patología</s0>
<s5>37</s5>
</fC07>
<fC07 i1="03" i2="X" l="FRE">
<s0>Système nerveux central pathologie</s0>
<s5>38</s5>
</fC07>
<fC07 i1="03" i2="X" l="ENG">
<s0>Central nervous system disease</s0>
<s5>38</s5>
</fC07>
<fC07 i1="03" i2="X" l="SPA">
<s0>Sistema nervosio central patología</s0>
<s5>38</s5>
</fC07>
<fC07 i1="04" i2="X" l="FRE">
<s0>Encéphale pathologie</s0>
<s5>39</s5>
</fC07>
<fC07 i1="04" i2="X" l="ENG">
<s0>Cerebral disorder</s0>
<s5>39</s5>
</fC07>
<fC07 i1="04" i2="X" l="SPA">
<s0>Encéfalo patología</s0>
<s5>39</s5>
</fC07>
<fC07 i1="05" i2="X" l="FRE">
<s0>Maladie dégénérative</s0>
<s5>40</s5>
</fC07>
<fC07 i1="05" i2="X" l="ENG">
<s0>Degenerative disease</s0>
<s5>40</s5>
</fC07>
<fC07 i1="05" i2="X" l="SPA">
<s0>Enfermedad degenerativa</s0>
<s5>40</s5>
</fC07>
<fC07 i1="06" i2="X" l="FRE">
<s0>Muscle strié pathologie</s0>
<s5>45</s5>
</fC07>
<fC07 i1="06" i2="X" l="ENG">
<s0>Striated muscle disease</s0>
<s5>45</s5>
</fC07>
<fC07 i1="06" i2="X" l="SPA">
<s0>Músculo estriado patología</s0>
<s5>45</s5>
</fC07>
<fC07 i1="07" i2="X" l="FRE">
<s0>Trouble neurologique</s0>
<s5>47</s5>
</fC07>
<fC07 i1="07" i2="X" l="ENG">
<s0>Neurological disorder</s0>
<s5>47</s5>
</fC07>
<fC07 i1="07" i2="X" l="SPA">
<s0>Trastorno neurológico</s0>
<s5>47</s5>
</fC07>
<fC07 i1="08" i2="X" l="FRE">
<s0>Mouvement involontaire</s0>
<s5>48</s5>
</fC07>
<fC07 i1="08" i2="X" l="ENG">
<s0>Involuntary movement</s0>
<s5>48</s5>
</fC07>
<fC07 i1="08" i2="X" l="SPA">
<s0>Movimiento involuntario</s0>
<s5>48</s5>
</fC07>
<fC07 i1="09" i2="X" l="FRE">
<s0>Extrapyramidal syndrome</s0>
<s5>49</s5>
</fC07>
<fC07 i1="09" i2="X" l="ENG">
<s0>Extrapyramidal syndrome</s0>
<s5>49</s5>
</fC07>
<fC07 i1="09" i2="X" l="SPA">
<s0>Extrapiramidal síndrome</s0>
<s5>49</s5>
</fC07>
<fN21>
<s1>343</s1>
</fN21>
<fN82>
<s1>PSI</s1>
</fN82>
</pA>
</standard>
<server>
<NO>PASCAL 02-0584388 INIST</NO>
<ET>Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease</ET>
<AU>HELLMANN (Mark A.); MELAMED (Eldad)</AU>
<AF>Department of Neurology, Rabin Medical Centre, Beilinson Campus and Tel Aviv University School of Medicine/Petah Tiqva/Israël (1 aut., 2 aut.)</AF>
<DT>Publication en série; Niveau analytique</DT>
<SO>Movement disorders; ISSN 0885-3185; Etats-Unis; Da. 2002; Vol. 17; No. 5; Pp. 1097-1098; Bibl. 7 ref.</SO>
<LA>Anglais</LA>
<EA>A variety of movement disorders may occur during the course of prion disease. We describe a unique patient who had focal upper limb dystonia as the presenting symptom of familial codon 200 mutation-positive Creutzfeldt-Jakob disease.</EA>
<CC>002B17G; 235</CC>
<FD>Encéphalopathie spongiforme Creutzfeldt Jakob; Dystonie; Lésion focale; Etude cas; Signe inaugural; Homme; Prion</FD>
<FG>Infection; Système nerveux pathologie; Système nerveux central pathologie; Encéphale pathologie; Maladie dégénérative; Muscle strié pathologie; Trouble neurologique; Mouvement involontaire; Extrapyramidal syndrome</FG>
<ED>Creutzfeldt Jakob disease; Dystonia; Focal lesion; Case study; Inaugural sign; Human; Prion</ED>
<EG>Infection; Nervous system diseases; Central nervous system disease; Cerebral disorder; Degenerative disease; Striated muscle disease; Neurological disorder; Involuntary movement; Extrapyramidal syndrome</EG>
<SD>Encefalopatía espongiforme Creutzfeldt Jakob; Distonía; Lesión focal; Estudio caso; Signo inaugural; Hombre; Prión</SD>
<LO>INIST-20953.354000105152380370</LO>
<ID>02-0584388</ID>
</server>
</inist>
</record>

Pour manipuler ce document sous Unix (Dilib)

EXPLOR_STEP=$WICRI_ROOT/Wicri/Santé/explor/MovDisordV3/Data/PascalFrancis/Corpus
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 002629 | SxmlIndent | more

Ou

HfdSelect -h $EXPLOR_AREA/Data/PascalFrancis/Corpus/biblio.hfd -nk 002629 | SxmlIndent | more

Pour mettre un lien sur cette page dans le réseau Wicri

{{Explor lien
   |wiki=    Wicri/Santé
   |area=    MovDisordV3
   |flux=    PascalFrancis
   |étape=   Corpus
   |type=    RBID
   |clé=     Pascal:02-0584388
   |texte=   Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease
}}

Wicri

This area was generated with Dilib version V0.6.23.
Data generation: Sun Jul 3 12:29:32 2016. Site generation: Wed Feb 14 10:52:30 2024