Movement Disorders (revue)

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Forty-one-year follow-up of childhood-onset opsoclonus-myoclonus-ataxia: Cerebellar atrophy, multiphasic relapses, and response to IVIG

Identifieur interne : 002585 ( PascalFrancis/Corpus ); précédent : 002584; suivant : 002586

Forty-one-year follow-up of childhood-onset opsoclonus-myoclonus-ataxia: Cerebellar atrophy, multiphasic relapses, and response to IVIG

Auteurs : Michael R. Pranzatelli ; Elizabeth D. Tate ; Marcel Kinshourne ; Verne S. Jr Caviness ; Bibhuti Mishra

Source :

RBID : Pascal:03-0038727

Descripteurs français

English descriptors

Abstract

We report on an adult with opsoclonus-myoclonus-ataxia syndrome experiencing widely spaced neurological relapses, who was followed for 41 years. His responses to treatment are described.

Notice en format standard (ISO 2709)

Pour connaître la documentation sur le format Inist Standard.

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A03   1    @0 Mov. disord.
A05       @2 17
A06       @2 6
A08 01  1  ENG  @1 Forty-one-year follow-up of childhood-onset opsoclonus-myoclonus-ataxia: Cerebellar atrophy, multiphasic relapses, and response to IVIG
A11 01  1    @1 PRANZATELLI (Michael R.)
A11 02  1    @1 TATE (Elizabeth D.)
A11 03  1    @1 KINSHOURNE (Marcel)
A11 04  1    @1 CAVINESS (Verne S. JR)
A11 05  1    @1 MISHRA (Bibhuti)
A14 01      @1 The National Pediatric Myoclonus Center, Departments of Neurology and Pediatrics, Southern Illinois University School of Medicine @2 Springfield, Illinois @3 USA @Z 1 aut. @Z 2 aut.
A14 02      @1 New School University and Tufts University @2 Winchester, Massachusetts @3 USA @Z 3 aut.
A14 03      @1 Massachusetts General Hospital @2 Boston, Massachusetts @3 USA @Z 4 aut.
A14 04      @1 Temple University @2 Philadelphia, Pennsylvania @3 USA @Z 5 aut.
A20       @1 1387-1390
A21       @1 2002
A23 01      @0 ENG
A43 01      @1 INIST @2 20953 @5 354000105559450430
A44       @0 0000 @1 © 2003 INIST-CNRS. All rights reserved.
A45       @0 20 ref.
A47 01  1    @0 03-0038727
A60       @1 P
A61       @0 A
A64 01  1    @0 Movement disorders
A66 01      @0 USA
C01 01    ENG  @0 We report on an adult with opsoclonus-myoclonus-ataxia syndrome experiencing widely spaced neurological relapses, who was followed for 41 years. His responses to treatment are described.
C02 01  X    @0 002B17A01
C03 01  X  FRE  @0 Ataxie @5 01
C03 01  X  ENG  @0 Ataxia @5 01
C03 01  X  SPA  @0 Ataxia @5 01
C03 02  X  FRE  @0 Cervelet @5 02
C03 02  X  ENG  @0 Cerebellum @5 02
C03 02  X  SPA  @0 Cerebelo @5 02
C03 03  X  FRE  @0 Opsoclonie @5 04
C03 03  X  ENG  @0 Opsoclonus @5 04
C03 03  X  SPA  @0 Opsoclonación @5 04
C03 04  X  FRE  @0 Myoclonie @5 07
C03 04  X  ENG  @0 Myoclonus @5 07
C03 04  X  SPA  @0 Mioclonia @5 07
C03 05  X  FRE  @0 Immunoglobuline @5 10
C03 05  X  ENG  @0 Immunoglobulins @5 10
C03 05  X  SPA  @0 Inmunoglobulina @5 10
C03 06  X  FRE  @0 Voie intraveineuse @5 13
C03 06  X  ENG  @0 Intravenous administration @5 13
C03 06  X  SPA  @0 Vía intravenosa @5 13
C03 07  X  FRE  @0 Etude cas @5 16
C03 07  X  ENG  @0 Case study @5 16
C03 07  X  SPA  @0 Estudio caso @5 16
C03 08  X  FRE  @0 Evolution @5 17
C03 08  X  ENG  @0 Evolution @5 17
C03 08  X  SPA  @0 Evolución @5 17
C03 09  X  FRE  @0 Récidive @5 18
C03 09  X  ENG  @0 Relapse @5 18
C03 09  X  SPA  @0 Recaida @5 18
C03 10  X  FRE  @0 Adulte @5 20
C03 10  X  ENG  @0 Adult @5 20
C03 10  X  SPA  @0 Adulto @5 20
C03 11  X  FRE  @0 Chimiothérapie @5 23
C03 11  X  ENG  @0 Chemotherapy @5 23
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C07 01  X  FRE  @0 Homme
C07 01  X  ENG  @0 Human
C07 01  X  SPA  @0 Hombre
C07 02  X  FRE  @0 Système nerveux pathologie @5 37
C07 02  X  ENG  @0 Nervous system diseases @5 37
C07 02  X  SPA  @0 Sistema nervioso patología @5 37
C07 03  X  FRE  @0 Système nerveux central pathologie @5 38
C07 03  X  ENG  @0 Central nervous system disease @5 38
C07 03  X  SPA  @0 Sistema nervosio central patología @5 38
C07 04  X  FRE  @0 Encéphale pathologie @5 39
C07 04  X  ENG  @0 Cerebral disorder @5 39
C07 04  X  SPA  @0 Encéfalo patología @5 39
C07 05  X  FRE  @0 Cervelet pathologie @5 40
C07 05  X  ENG  @0 Cerebellar disease @5 40
C07 05  X  SPA  @0 Cerebelar enfermedad @5 40
C07 06  X  FRE  @0 Trouble neurologique @5 41
C07 06  X  ENG  @0 Neurological disorder @5 41
C07 06  X  SPA  @0 Trastorno neurológico @5 41
C07 07  X  FRE  @0 Oeil pathologie @5 45
C07 07  X  ENG  @0 Eye disease @5 45
C07 07  X  SPA  @0 Ojo patología @5 45
C07 08  X  FRE  @0 Oculomotricité syndrome @5 46
C07 08  X  ENG  @0 Oculomotor syndrome @5 46
C07 08  X  SPA  @0 Oculomotricidad síndrome @5 46
C07 09  X  FRE  @0 Mouvement involontaire @5 55
C07 09  X  ENG  @0 Involuntary movement @5 55
C07 09  X  SPA  @0 Movimiento involuntario @5 55
C07 10  X  FRE  @0 Voie administration @5 69
C07 10  X  ENG  @0 Route of administration @5 69
C07 10  X  SPA  @0 Vía administración @5 69
N21       @1 020
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Format Inist (serveur)

NO : PASCAL 03-0038727 INIST
ET : Forty-one-year follow-up of childhood-onset opsoclonus-myoclonus-ataxia: Cerebellar atrophy, multiphasic relapses, and response to IVIG
AU : PRANZATELLI (Michael R.); TATE (Elizabeth D.); KINSHOURNE (Marcel); CAVINESS (Verne S. JR); MISHRA (Bibhuti)
AF : The National Pediatric Myoclonus Center, Departments of Neurology and Pediatrics, Southern Illinois University School of Medicine/Springfield, Illinois/Etats-Unis (1 aut., 2 aut.); New School University and Tufts University/Winchester, Massachusetts/Etats-Unis (3 aut.); Massachusetts General Hospital/Boston, Massachusetts/Etats-Unis (4 aut.); Temple University/Philadelphia, Pennsylvania/Etats-Unis (5 aut.)
DT : Publication en série; Niveau analytique
SO : Movement disorders; ISSN 0885-3185; Etats-Unis; Da. 2002; Vol. 17; No. 6; Pp. 1387-1390; Bibl. 20 ref.
LA : Anglais
EA : We report on an adult with opsoclonus-myoclonus-ataxia syndrome experiencing widely spaced neurological relapses, who was followed for 41 years. His responses to treatment are described.
CC : 002B17A01
FD : Ataxie; Cervelet; Opsoclonie; Myoclonie; Immunoglobuline; Voie intraveineuse; Etude cas; Evolution; Récidive; Adulte; Chimiothérapie
FG : Homme; Système nerveux pathologie; Système nerveux central pathologie; Encéphale pathologie; Cervelet pathologie; Trouble neurologique; Oeil pathologie; Oculomotricité syndrome; Mouvement involontaire; Voie administration
ED : Ataxia; Cerebellum; Opsoclonus; Myoclonus; Immunoglobulins; Intravenous administration; Case study; Evolution; Relapse; Adult; Chemotherapy
EG : Human; Nervous system diseases; Central nervous system disease; Cerebral disorder; Cerebellar disease; Neurological disorder; Eye disease; Oculomotor syndrome; Involuntary movement; Route of administration
SD : Ataxia; Cerebelo; Opsoclonación; Mioclonia; Inmunoglobulina; Vía intravenosa; Estudio caso; Evolución; Recaida; Adulto; Quimioterapia
LO : INIST-20953.354000105559450430
ID : 03-0038727

Links to Exploration step

Pascal:03-0038727

Le document en format XML

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<fC03 i1="09" i2="X" l="SPA">
<s0>Recaida</s0>
<s5>18</s5>
</fC03>
<fC03 i1="10" i2="X" l="FRE">
<s0>Adulte</s0>
<s5>20</s5>
</fC03>
<fC03 i1="10" i2="X" l="ENG">
<s0>Adult</s0>
<s5>20</s5>
</fC03>
<fC03 i1="10" i2="X" l="SPA">
<s0>Adulto</s0>
<s5>20</s5>
</fC03>
<fC03 i1="11" i2="X" l="FRE">
<s0>Chimiothérapie</s0>
<s5>23</s5>
</fC03>
<fC03 i1="11" i2="X" l="ENG">
<s0>Chemotherapy</s0>
<s5>23</s5>
</fC03>
<fC03 i1="11" i2="X" l="SPA">
<s0>Quimioterapia</s0>
<s5>23</s5>
</fC03>
<fC07 i1="01" i2="X" l="FRE">
<s0>Homme</s0>
</fC07>
<fC07 i1="01" i2="X" l="ENG">
<s0>Human</s0>
</fC07>
<fC07 i1="01" i2="X" l="SPA">
<s0>Hombre</s0>
</fC07>
<fC07 i1="02" i2="X" l="FRE">
<s0>Système nerveux pathologie</s0>
<s5>37</s5>
</fC07>
<fC07 i1="02" i2="X" l="ENG">
<s0>Nervous system diseases</s0>
<s5>37</s5>
</fC07>
<fC07 i1="02" i2="X" l="SPA">
<s0>Sistema nervioso patología</s0>
<s5>37</s5>
</fC07>
<fC07 i1="03" i2="X" l="FRE">
<s0>Système nerveux central pathologie</s0>
<s5>38</s5>
</fC07>
<fC07 i1="03" i2="X" l="ENG">
<s0>Central nervous system disease</s0>
<s5>38</s5>
</fC07>
<fC07 i1="03" i2="X" l="SPA">
<s0>Sistema nervosio central patología</s0>
<s5>38</s5>
</fC07>
<fC07 i1="04" i2="X" l="FRE">
<s0>Encéphale pathologie</s0>
<s5>39</s5>
</fC07>
<fC07 i1="04" i2="X" l="ENG">
<s0>Cerebral disorder</s0>
<s5>39</s5>
</fC07>
<fC07 i1="04" i2="X" l="SPA">
<s0>Encéfalo patología</s0>
<s5>39</s5>
</fC07>
<fC07 i1="05" i2="X" l="FRE">
<s0>Cervelet pathologie</s0>
<s5>40</s5>
</fC07>
<fC07 i1="05" i2="X" l="ENG">
<s0>Cerebellar disease</s0>
<s5>40</s5>
</fC07>
<fC07 i1="05" i2="X" l="SPA">
<s0>Cerebelar enfermedad</s0>
<s5>40</s5>
</fC07>
<fC07 i1="06" i2="X" l="FRE">
<s0>Trouble neurologique</s0>
<s5>41</s5>
</fC07>
<fC07 i1="06" i2="X" l="ENG">
<s0>Neurological disorder</s0>
<s5>41</s5>
</fC07>
<fC07 i1="06" i2="X" l="SPA">
<s0>Trastorno neurológico</s0>
<s5>41</s5>
</fC07>
<fC07 i1="07" i2="X" l="FRE">
<s0>Oeil pathologie</s0>
<s5>45</s5>
</fC07>
<fC07 i1="07" i2="X" l="ENG">
<s0>Eye disease</s0>
<s5>45</s5>
</fC07>
<fC07 i1="07" i2="X" l="SPA">
<s0>Ojo patología</s0>
<s5>45</s5>
</fC07>
<fC07 i1="08" i2="X" l="FRE">
<s0>Oculomotricité syndrome</s0>
<s5>46</s5>
</fC07>
<fC07 i1="08" i2="X" l="ENG">
<s0>Oculomotor syndrome</s0>
<s5>46</s5>
</fC07>
<fC07 i1="08" i2="X" l="SPA">
<s0>Oculomotricidad síndrome</s0>
<s5>46</s5>
</fC07>
<fC07 i1="09" i2="X" l="FRE">
<s0>Mouvement involontaire</s0>
<s5>55</s5>
</fC07>
<fC07 i1="09" i2="X" l="ENG">
<s0>Involuntary movement</s0>
<s5>55</s5>
</fC07>
<fC07 i1="09" i2="X" l="SPA">
<s0>Movimiento involuntario</s0>
<s5>55</s5>
</fC07>
<fC07 i1="10" i2="X" l="FRE">
<s0>Voie administration</s0>
<s5>69</s5>
</fC07>
<fC07 i1="10" i2="X" l="ENG">
<s0>Route of administration</s0>
<s5>69</s5>
</fC07>
<fC07 i1="10" i2="X" l="SPA">
<s0>Vía administración</s0>
<s5>69</s5>
</fC07>
<fN21>
<s1>020</s1>
</fN21>
<fN82>
<s1>PSI</s1>
</fN82>
</pA>
</standard>
<server>
<NO>PASCAL 03-0038727 INIST</NO>
<ET>Forty-one-year follow-up of childhood-onset opsoclonus-myoclonus-ataxia: Cerebellar atrophy, multiphasic relapses, and response to IVIG</ET>
<AU>PRANZATELLI (Michael R.); TATE (Elizabeth D.); KINSHOURNE (Marcel); CAVINESS (Verne S. JR); MISHRA (Bibhuti)</AU>
<AF>The National Pediatric Myoclonus Center, Departments of Neurology and Pediatrics, Southern Illinois University School of Medicine/Springfield, Illinois/Etats-Unis (1 aut., 2 aut.); New School University and Tufts University/Winchester, Massachusetts/Etats-Unis (3 aut.); Massachusetts General Hospital/Boston, Massachusetts/Etats-Unis (4 aut.); Temple University/Philadelphia, Pennsylvania/Etats-Unis (5 aut.)</AF>
<DT>Publication en série; Niveau analytique</DT>
<SO>Movement disorders; ISSN 0885-3185; Etats-Unis; Da. 2002; Vol. 17; No. 6; Pp. 1387-1390; Bibl. 20 ref.</SO>
<LA>Anglais</LA>
<EA>We report on an adult with opsoclonus-myoclonus-ataxia syndrome experiencing widely spaced neurological relapses, who was followed for 41 years. His responses to treatment are described.</EA>
<CC>002B17A01</CC>
<FD>Ataxie; Cervelet; Opsoclonie; Myoclonie; Immunoglobuline; Voie intraveineuse; Etude cas; Evolution; Récidive; Adulte; Chimiothérapie</FD>
<FG>Homme; Système nerveux pathologie; Système nerveux central pathologie; Encéphale pathologie; Cervelet pathologie; Trouble neurologique; Oeil pathologie; Oculomotricité syndrome; Mouvement involontaire; Voie administration</FG>
<ED>Ataxia; Cerebellum; Opsoclonus; Myoclonus; Immunoglobulins; Intravenous administration; Case study; Evolution; Relapse; Adult; Chemotherapy</ED>
<EG>Human; Nervous system diseases; Central nervous system disease; Cerebral disorder; Cerebellar disease; Neurological disorder; Eye disease; Oculomotor syndrome; Involuntary movement; Route of administration</EG>
<SD>Ataxia; Cerebelo; Opsoclonación; Mioclonia; Inmunoglobulina; Vía intravenosa; Estudio caso; Evolución; Recaida; Adulto; Quimioterapia</SD>
<LO>INIST-20953.354000105559450430</LO>
<ID>03-0038727</ID>
</server>
</inist>
</record>

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