Movement Disorders (revue)

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Neurostimulation of the ventral intermediate thalamic nucleus in inherited myoclonus-dystonia syndrome

Identifieur interne : 002947 ( PascalFrancis/Checkpoint ); précédent : 002946; suivant : 002948

Neurostimulation of the ventral intermediate thalamic nucleus in inherited myoclonus-dystonia syndrome

Auteurs : Thomas Trottenberg [Allemagne] ; Wassilios Meissner [Allemagne] ; Guy Arnold [Allemagne] ; Karl-Max Einhaupl [Allemagne] ; Andreas Kupsch [Allemagne] ; Christian Kabus [Allemagne] ; Thomas Funk [Allemagne]

Source :

RBID : Pascal:01-0429780

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English descriptors

Abstract

We report on the effects of bilateral neurostimulation of the ventral intermediate thalamic nucleus (VIM) in a patient with medically intractable and progressing inherited myoclonus dystonia syndrome (IMDS). Postoperatively, the patient improved by approximately 80% on the modified version of a myoclonus score without any significant change in the dystonic symptoms. This suggests that neurostimulation of the VIM may be an effective treatment for myoclonus in pharmacologically intractable IMDS.


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Pascal:01-0429780

Le document en format XML

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<s0>Mouvement involontaire</s0>
<s5>39</s5>
</fC07>
<fC07 i1="03" i2="X" l="ENG">
<s0>Involuntary movement</s0>
<s5>39</s5>
</fC07>
<fC07 i1="03" i2="X" l="SPA">
<s0>Movimiento involuntario</s0>
<s5>39</s5>
</fC07>
<fC07 i1="04" i2="X" l="FRE">
<s0>Muscle strié pathologie</s0>
<s5>45</s5>
</fC07>
<fC07 i1="04" i2="X" l="ENG">
<s0>Striated muscle disease</s0>
<s5>45</s5>
</fC07>
<fC07 i1="04" i2="X" l="SPA">
<s0>Músculo estriado patología</s0>
<s5>45</s5>
</fC07>
<fC07 i1="05" i2="X" l="FRE">
<s0>Extrapyramidal syndrome</s0>
<s5>49</s5>
</fC07>
<fC07 i1="05" i2="X" l="ENG">
<s0>Extrapyramidal syndrome</s0>
<s5>49</s5>
</fC07>
<fC07 i1="05" i2="X" l="SPA">
<s0>Extrapiramidal síndrome</s0>
<s5>49</s5>
</fC07>
<fC07 i1="06" i2="X" l="FRE">
<s0>Traitement instrumental</s0>
<s5>53</s5>
</fC07>
<fC07 i1="06" i2="X" l="ENG">
<s0>Instrumentation therapy</s0>
<s5>53</s5>
</fC07>
<fC07 i1="06" i2="X" l="SPA">
<s0>Tratamiento instrumental</s0>
<s5>53</s5>
</fC07>
<fC07 i1="07" i2="X" l="FRE">
<s0>Encéphale</s0>
<s5>69</s5>
</fC07>
<fC07 i1="07" i2="X" l="ENG">
<s0>Brain (vertebrata)</s0>
<s5>69</s5>
</fC07>
<fC07 i1="07" i2="X" l="SPA">
<s0>Encéfalo</s0>
<s5>69</s5>
</fC07>
<fN21>
<s1>302</s1>
</fN21>
</pA>
</standard>
</inist>
<affiliations>
<list>
<country>
<li>Allemagne</li>
</country>
<region>
<li>Berlin</li>
</region>
<settlement>
<li>Berlin</li>
</settlement>
</list>
<tree>
<country name="Allemagne">
<region name="Berlin">
<name sortKey="Trottenberg, Thomas" sort="Trottenberg, Thomas" uniqKey="Trottenberg T" first="Thomas" last="Trottenberg">Thomas Trottenberg</name>
</region>
<name sortKey="Arnold, Guy" sort="Arnold, Guy" uniqKey="Arnold G" first="Guy" last="Arnold">Guy Arnold</name>
<name sortKey="Einhaupl, Karl Max" sort="Einhaupl, Karl Max" uniqKey="Einhaupl K" first="Karl-Max" last="Einhaupl">Karl-Max Einhaupl</name>
<name sortKey="Funk, Thomas" sort="Funk, Thomas" uniqKey="Funk T" first="Thomas" last="Funk">Thomas Funk</name>
<name sortKey="Kabus, Christian" sort="Kabus, Christian" uniqKey="Kabus C" first="Christian" last="Kabus">Christian Kabus</name>
<name sortKey="Kupsch, Andreas" sort="Kupsch, Andreas" uniqKey="Kupsch A" first="Andreas" last="Kupsch">Andreas Kupsch</name>
<name sortKey="Meissner, Wassilios" sort="Meissner, Wassilios" uniqKey="Meissner W" first="Wassilios" last="Meissner">Wassilios Meissner</name>
</country>
</tree>
</affiliations>
</record>

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