Neurostimulation of the ventral intermediate thalamic nucleus in inherited myoclonus-dystonia syndrome
Identifieur interne : 000360 ( PascalFrancis/Curation ); précédent : 000359; suivant : 000361Neurostimulation of the ventral intermediate thalamic nucleus in inherited myoclonus-dystonia syndrome
Auteurs : Thomas Trottenberg [Allemagne] ; Wassilios Meissner [Allemagne] ; Guy Arnold [Allemagne] ; Karl-Max Einhaupl [Allemagne] ; Andreas Kupsch [Allemagne] ; Christian Kabus [Allemagne] ; Thomas Funk [Allemagne]Source :
- Movement disorders [ 0885-3185 ] ; 2001.
Descripteurs français
- Pascal (Inist)
- Wicri :
- topic : Homme.
English descriptors
- KwdEn :
Abstract
We report on the effects of bilateral neurostimulation of the ventral intermediate thalamic nucleus (VIM) in a patient with medically intractable and progressing inherited myoclonus dystonia syndrome (IMDS). Postoperatively, the patient improved by approximately 80% on the modified version of a myoclonus score without any significant change in the dystonic symptoms. This suggests that neurostimulation of the VIM may be an effective treatment for myoclonus in pharmacologically intractable IMDS.
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<front><div type="abstract" xml:lang="en">We report on the effects of bilateral neurostimulation of the ventral intermediate thalamic nucleus (VIM) in a patient with medically intractable and progressing inherited myoclonus dystonia syndrome (IMDS). Postoperatively, the patient improved by approximately 80% on the modified version of a myoclonus score without any significant change in the dystonic symptoms. This suggests that neurostimulation of the VIM may be an effective treatment for myoclonus in pharmacologically intractable IMDS.</div>
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