Movement Disorders (revue)

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Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease

Identifieur interne : 006794 ( Main/Merge ); précédent : 006793; suivant : 006795

Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease

Auteurs : Mark A. Hellmann [Israël] ; Eldad Melamed [Israël]

Source :

RBID : Pascal:02-0584388

Descripteurs français

English descriptors

Abstract

A variety of movement disorders may occur during the course of prion disease. We describe a unique patient who had focal upper limb dystonia as the presenting symptom of familial codon 200 mutation-positive Creutzfeldt-Jakob disease.

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Pascal:02-0584388

Le document en format XML

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<title xml:lang="en" level="a">Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease</title>
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<s1>Department of Neurology, Rabin Medical Centre, Beilinson Campus and Tel Aviv University School of Medicine</s1>
<s2>Petah Tiqva</s2>
<s3>ISR</s3>
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<country>Israël</country>
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<term>Focal lesion</term>
<term>Human</term>
<term>Inaugural sign</term>
<term>Prion</term>
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<term>Encéphalopathie spongiforme Creutzfeldt Jakob</term>
<term>Dystonie</term>
<term>Lésion focale</term>
<term>Etude cas</term>
<term>Signe inaugural</term>
<term>Homme</term>
<term>Prion</term>
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<div type="abstract" xml:lang="en">A variety of movement disorders may occur during the course of prion disease. We describe a unique patient who had focal upper limb dystonia as the presenting symptom of familial codon 200 mutation-positive Creutzfeldt-Jakob disease.</div>
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EXPLOR_STEP=$WICRI_ROOT/Wicri/Santé/explor/MovDisordV3/Data/Main/Merge
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{{Explor lien
   |wiki=    Wicri/Santé
   |area=    MovDisordV3
   |flux=    Main
   |étape=   Merge
   |type=    RBID
   |clé=     Pascal:02-0584388
   |texte=   Focal dystonia as the presenting sign in Creutzfeldt-Jakob disease
}}

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