Persisting hyperekplexia after idiopathic, self-limiting brainstem encephalopathy
Identifieur interne : 004128 ( Main/Merge ); précédent : 004127; suivant : 004129Persisting hyperekplexia after idiopathic, self-limiting brainstem encephalopathy
Auteurs : Bart P. C. Van De Warrenburg [Royaume-Uni, Pays-Bas] ; Carla Cordivari [Royaume-Uni] ; Peter Brown [Royaume-Uni] ; Kailash P. Bhatia [Royaume-Uni]Source :
- Movement disorders [ 0885-3185 ] ; 2007.
Descripteurs français
- Pascal (Inist)
English descriptors
- KwdEn :
Abstract
Symptomatic hyperekplexia is a relatively rare entity, but has been documented in various, mostly brainstem diseases. We report the clinical and neurophysiologic vignette of a patient with a self-limiting, possibly inflammatory brainstem encephalopathy. Trismus was the presenting feature, but she later developed hyperekplexia. Although most brainstem features resolved spontaneously, the hyperekplexia has persisted.
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Pascal:07-0314960Le document en format XML
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<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Autoimmunity</term>
<term>Encephalopathy</term>
<term>Hyperekplexia</term>
<term>Idiopathic</term>
<term>Masticatory muscle</term>
<term>Myoclonus</term>
<term>Nervous system diseases</term>
<term>Reflex</term>
<term>Trismus</term>
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<keywords scheme="Pascal" xml:lang="fr"><term>Système nerveux pathologie</term>
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<term>Autoimmunité</term>
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<front><div type="abstract" xml:lang="en">Symptomatic hyperekplexia is a relatively rare entity, but has been documented in various, mostly brainstem diseases. We report the clinical and neurophysiologic vignette of a patient with a self-limiting, possibly inflammatory brainstem encephalopathy. Trismus was the presenting feature, but she later developed hyperekplexia. Although most brainstem features resolved spontaneously, the hyperekplexia has persisted.</div>
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