Movement Disorders (revue)

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Persisting hyperekplexia after idiopathic, self-limiting brainstem encephalopathy

Identifieur interne : 001663 ( PascalFrancis/Corpus ); précédent : 001662; suivant : 001664

Persisting hyperekplexia after idiopathic, self-limiting brainstem encephalopathy

Auteurs : Bart P. C. Van De Warrenburg ; Carla Cordivari ; Peter Brown ; Kailash P. Bhatia

Source :

RBID : Pascal:07-0314960

Descripteurs français

English descriptors

Abstract

Symptomatic hyperekplexia is a relatively rare entity, but has been documented in various, mostly brainstem diseases. We report the clinical and neurophysiologic vignette of a patient with a self-limiting, possibly inflammatory brainstem encephalopathy. Trismus was the presenting feature, but she later developed hyperekplexia. Although most brainstem features resolved spontaneously, the hyperekplexia has persisted.

Notice en format standard (ISO 2709)

Pour connaître la documentation sur le format Inist Standard.

pA  
A01 01  1    @0 0885-3185
A03   1    @0 Mov. disord.
A05       @2 22
A06       @2 7
A08 01  1  ENG  @1 Persisting hyperekplexia after idiopathic, self-limiting brainstem encephalopathy
A11 01  1    @1 VAN DE WARRENBURG (Bart P. C.)
A11 02  1    @1 CORDIVARI (Carla)
A11 03  1    @1 BROWN (Peter)
A11 04  1    @1 BHATIA (Kailash P.)
A14 01      @1 Sobell Department of Motor Neuroscience and Movement Disorders, Institute of Neurology @2 London @3 GBR @Z 1 aut. @Z 3 aut. @Z 4 aut.
A14 02      @1 Department of Neurology, Radboud University Nijmegen Medical Centre @2 Nijmegen @3 NLD @Z 1 aut.
A14 03      @1 Department of Neurophysiology, National Hospital of Neurology and Neurosurgery @2 London @3 GBR @Z 2 aut.
A20       @1 1017-1020
A21       @1 2007
A23 01      @0 ENG
A43 01      @1 INIST @2 20953 @5 354000149881420180
A44       @0 0000 @1 © 2007 INIST-CNRS. All rights reserved.
A45       @0 9 ref.
A47 01  1    @0 07-0314960
A60       @1 P
A61       @0 A
A64 01  1    @0 Movement disorders
A66 01      @0 USA
C01 01    ENG  @0 Symptomatic hyperekplexia is a relatively rare entity, but has been documented in various, mostly brainstem diseases. We report the clinical and neurophysiologic vignette of a patient with a self-limiting, possibly inflammatory brainstem encephalopathy. Trismus was the presenting feature, but she later developed hyperekplexia. Although most brainstem features resolved spontaneously, the hyperekplexia has persisted.
C02 01  X    @0 002B17
C02 02  X    @0 002B05C02A
C02 03  X    @0 002A26D05
C03 01  X  FRE  @0 Système nerveux pathologie @5 01
C03 01  X  ENG  @0 Nervous system diseases @5 01
C03 01  X  SPA  @0 Sistema nervioso patología @5 01
C03 02  X  FRE  @0 Encéphalopathie @5 02
C03 02  X  ENG  @0 Encephalopathy @5 02
C03 02  X  SPA  @0 Encefalopatía @5 02
C03 03  X  FRE  @0 Trismus @5 03
C03 03  X  ENG  @0 Trismus @5 03
C03 03  X  SPA  @0 Trismo @5 03
C03 04  X  FRE  @0 Autoimmunité @5 04
C03 04  X  ENG  @0 Autoimmunity @5 04
C03 04  X  SPA  @0 Autoinmunidad @5 04
C03 05  X  FRE  @0 Myoclonie @5 05
C03 05  X  ENG  @0 Myoclonus @5 05
C03 05  X  SPA  @0 Mioclonia @5 05
C03 06  X  FRE  @0 Idiopathique @5 09
C03 06  X  ENG  @0 Idiopathic @5 09
C03 06  X  SPA  @0 Idiopático @5 09
C03 07  X  FRE  @0 Réflexe @5 10
C03 07  X  ENG  @0 Reflex @5 10
C03 07  X  SPA  @0 Reflejo @5 10
C03 08  X  FRE  @0 Muscle masticateur @5 78
C03 08  X  ENG  @0 Masticatory muscle @5 78
C03 08  X  SPA  @0 Músculo masticatorio @5 78
C03 09  X  FRE  @0 Hyperekplexie @4 CD @5 96
C03 09  X  ENG  @0 Hyperekplexia @4 CD @5 96
C07 01  X  FRE  @0 Muscle strié pathologie @5 37
C07 01  X  ENG  @0 Striated muscle disease @5 37
C07 01  X  SPA  @0 Músculo estriado patología @5 37
C07 02  X  FRE  @0 Encéphale pathologie @5 38
C07 02  X  ENG  @0 Cerebral disorder @5 38
C07 02  X  SPA  @0 Encéfalo patología @5 38
C07 03  X  FRE  @0 Système nerveux central pathologie @5 39
C07 03  X  ENG  @0 Central nervous system disease @5 39
C07 03  X  SPA  @0 Sistema nervosio central patología @5 39
C07 04  X  FRE  @0 Mouvement involontaire @5 40
C07 04  X  ENG  @0 Involuntary movement @5 40
C07 04  X  SPA  @0 Movimiento involuntario @5 40
C07 05  X  FRE  @0 Trouble neurologique @5 41
C07 05  X  ENG  @0 Neurological disorder @5 41
C07 05  X  SPA  @0 Trastorno neurológico @5 41
N21       @1 204
N44 01      @1 OTO
N82       @1 OTO

Format Inist (serveur)

NO : PASCAL 07-0314960 INIST
ET : Persisting hyperekplexia after idiopathic, self-limiting brainstem encephalopathy
AU : VAN DE WARRENBURG (Bart P. C.); CORDIVARI (Carla); BROWN (Peter); BHATIA (Kailash P.)
AF : Sobell Department of Motor Neuroscience and Movement Disorders, Institute of Neurology/London/Royaume-Uni (1 aut., 3 aut., 4 aut.); Department of Neurology, Radboud University Nijmegen Medical Centre/Nijmegen/Pays-Bas (1 aut.); Department of Neurophysiology, National Hospital of Neurology and Neurosurgery/London/Royaume-Uni (2 aut.)
DT : Publication en série; Niveau analytique
SO : Movement disorders; ISSN 0885-3185; Etats-Unis; Da. 2007; Vol. 22; No. 7; Pp. 1017-1020; Bibl. 9 ref.
LA : Anglais
EA : Symptomatic hyperekplexia is a relatively rare entity, but has been documented in various, mostly brainstem diseases. We report the clinical and neurophysiologic vignette of a patient with a self-limiting, possibly inflammatory brainstem encephalopathy. Trismus was the presenting feature, but she later developed hyperekplexia. Although most brainstem features resolved spontaneously, the hyperekplexia has persisted.
CC : 002B17; 002B05C02A; 002A26D05
FD : Système nerveux pathologie; Encéphalopathie; Trismus; Autoimmunité; Myoclonie; Idiopathique; Réflexe; Muscle masticateur; Hyperekplexie
FG : Muscle strié pathologie; Encéphale pathologie; Système nerveux central pathologie; Mouvement involontaire; Trouble neurologique
ED : Nervous system diseases; Encephalopathy; Trismus; Autoimmunity; Myoclonus; Idiopathic; Reflex; Masticatory muscle; Hyperekplexia
EG : Striated muscle disease; Cerebral disorder; Central nervous system disease; Involuntary movement; Neurological disorder
SD : Sistema nervioso patología; Encefalopatía; Trismo; Autoinmunidad; Mioclonia; Idiopático; Reflejo; Músculo masticatorio
LO : INIST-20953.354000149881420180
ID : 07-0314960

Links to Exploration step

Pascal:07-0314960

Le document en format XML

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<s0>Mouvement involontaire</s0>
<s5>40</s5>
</fC07>
<fC07 i1="04" i2="X" l="ENG">
<s0>Involuntary movement</s0>
<s5>40</s5>
</fC07>
<fC07 i1="04" i2="X" l="SPA">
<s0>Movimiento involuntario</s0>
<s5>40</s5>
</fC07>
<fC07 i1="05" i2="X" l="FRE">
<s0>Trouble neurologique</s0>
<s5>41</s5>
</fC07>
<fC07 i1="05" i2="X" l="ENG">
<s0>Neurological disorder</s0>
<s5>41</s5>
</fC07>
<fC07 i1="05" i2="X" l="SPA">
<s0>Trastorno neurológico</s0>
<s5>41</s5>
</fC07>
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<s1>204</s1>
</fN21>
<fN44 i1="01">
<s1>OTO</s1>
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<s1>OTO</s1>
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<server>
<NO>PASCAL 07-0314960 INIST</NO>
<ET>Persisting hyperekplexia after idiopathic, self-limiting brainstem encephalopathy</ET>
<AU>VAN DE WARRENBURG (Bart P. C.); CORDIVARI (Carla); BROWN (Peter); BHATIA (Kailash P.)</AU>
<AF>Sobell Department of Motor Neuroscience and Movement Disorders, Institute of Neurology/London/Royaume-Uni (1 aut., 3 aut., 4 aut.); Department of Neurology, Radboud University Nijmegen Medical Centre/Nijmegen/Pays-Bas (1 aut.); Department of Neurophysiology, National Hospital of Neurology and Neurosurgery/London/Royaume-Uni (2 aut.)</AF>
<DT>Publication en série; Niveau analytique</DT>
<SO>Movement disorders; ISSN 0885-3185; Etats-Unis; Da. 2007; Vol. 22; No. 7; Pp. 1017-1020; Bibl. 9 ref.</SO>
<LA>Anglais</LA>
<EA>Symptomatic hyperekplexia is a relatively rare entity, but has been documented in various, mostly brainstem diseases. We report the clinical and neurophysiologic vignette of a patient with a self-limiting, possibly inflammatory brainstem encephalopathy. Trismus was the presenting feature, but she later developed hyperekplexia. Although most brainstem features resolved spontaneously, the hyperekplexia has persisted.</EA>
<CC>002B17; 002B05C02A; 002A26D05</CC>
<FD>Système nerveux pathologie; Encéphalopathie; Trismus; Autoimmunité; Myoclonie; Idiopathique; Réflexe; Muscle masticateur; Hyperekplexie</FD>
<FG>Muscle strié pathologie; Encéphale pathologie; Système nerveux central pathologie; Mouvement involontaire; Trouble neurologique</FG>
<ED>Nervous system diseases; Encephalopathy; Trismus; Autoimmunity; Myoclonus; Idiopathic; Reflex; Masticatory muscle; Hyperekplexia</ED>
<EG>Striated muscle disease; Cerebral disorder; Central nervous system disease; Involuntary movement; Neurological disorder</EG>
<SD>Sistema nervioso patología; Encefalopatía; Trismo; Autoinmunidad; Mioclonia; Idiopático; Reflejo; Músculo masticatorio</SD>
<LO>INIST-20953.354000149881420180</LO>
<ID>07-0314960</ID>
</server>
</inist>
</record>

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