Extraocular Muscle Dystonia Due to Acquired (non-Wilsonian) Hepatocerebral Degeneration
Identifieur interne : 003865 ( Main/Merge ); précédent : 003864; suivant : 003866Extraocular Muscle Dystonia Due to Acquired (non-Wilsonian) Hepatocerebral Degeneration
Auteurs : Joseph Ferrara [États-Unis] ; Deepak Gupta [États-Unis] ; Emily Foster [États-Unis] ; Katherine Garman [États-Unis] ; Mark Stacy [États-Unis]Source :
- Movement disorders [ 0885-3185 ] ; 2008.
Descripteurs français
- Pascal (Inist)
English descriptors
Abstract
We present a video report of a patient with advanced non-Wilsonian cirrhotic liver disease who developed extraocular muscle dystonia (oculogyric crisis) and severe orofaciolingual dyskinesias. Acquired hepatocerebral degeneration causes choreic movements, especially of cranial muscles, but dystonic ocular spasm is an infrequent manifestation of this disorder. This case illustrates that AHD should be considered in the differential diagnosis of extraocular muscle dystonia.
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Pascal:08-0251876Le document en format XML
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<sourceDesc><biblStruct><analytic><title xml:lang="en" level="a">Extraocular Muscle Dystonia Due to Acquired (non-Wilsonian) Hepatocerebral Degeneration</title>
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<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Degeneration</term>
<term>Dystonia</term>
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<term>Nervous system diseases</term>
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<keywords scheme="Pascal" xml:lang="fr"><term>Dystonie</term>
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<front><div type="abstract" xml:lang="en">We present a video report of a patient with advanced non-Wilsonian cirrhotic liver disease who developed extraocular muscle dystonia (oculogyric crisis) and severe orofaciolingual dyskinesias. Acquired hepatocerebral degeneration causes choreic movements, especially of cranial muscles, but dystonic ocular spasm is an infrequent manifestation of this disorder. This case illustrates that AHD should be considered in the differential diagnosis of extraocular muscle dystonia.</div>
</front>
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<affiliations><list><country><li>États-Unis</li>
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<region><li>Caroline du Nord</li>
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<tree><country name="États-Unis"><region name="Caroline du Nord"><name sortKey="Ferrara, Joseph" sort="Ferrara, Joseph" uniqKey="Ferrara J" first="Joseph" last="Ferrara">Joseph Ferrara</name>
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<name sortKey="Foster, Emily" sort="Foster, Emily" uniqKey="Foster E" first="Emily" last="Foster">Emily Foster</name>
<name sortKey="Garman, Katherine" sort="Garman, Katherine" uniqKey="Garman K" first="Katherine" last="Garman">Katherine Garman</name>
<name sortKey="Gupta, Deepak" sort="Gupta, Deepak" uniqKey="Gupta D" first="Deepak" last="Gupta">Deepak Gupta</name>
<name sortKey="Stacy, Mark" sort="Stacy, Mark" uniqKey="Stacy M" first="Mark" last="Stacy">Mark Stacy</name>
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