Movement Disorders (revue)

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Extraocular Muscle Dystonia Due to Acquired (non-Wilsonian) Hepatocerebral Degeneration

Identifieur interne : 003865 ( Main/Merge ); précédent : 003864; suivant : 003866

Extraocular Muscle Dystonia Due to Acquired (non-Wilsonian) Hepatocerebral Degeneration

Auteurs : Joseph Ferrara [États-Unis] ; Deepak Gupta [États-Unis] ; Emily Foster [États-Unis] ; Katherine Garman [États-Unis] ; Mark Stacy [États-Unis]

Source :

RBID : Pascal:08-0251876

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English descriptors

Abstract

We present a video report of a patient with advanced non-Wilsonian cirrhotic liver disease who developed extraocular muscle dystonia (oculogyric crisis) and severe orofaciolingual dyskinesias. Acquired hepatocerebral degeneration causes choreic movements, especially of cranial muscles, but dystonic ocular spasm is an infrequent manifestation of this disorder. This case illustrates that AHD should be considered in the differential diagnosis of extraocular muscle dystonia.

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Pascal:08-0251876

Le document en format XML

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<div type="abstract" xml:lang="en">We present a video report of a patient with advanced non-Wilsonian cirrhotic liver disease who developed extraocular muscle dystonia (oculogyric crisis) and severe orofaciolingual dyskinesias. Acquired hepatocerebral degeneration causes choreic movements, especially of cranial muscles, but dystonic ocular spasm is an infrequent manifestation of this disorder. This case illustrates that AHD should be considered in the differential diagnosis of extraocular muscle dystonia.</div>
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