Movement Disorders (revue)

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Forty‐one year follow‐up of childhood‐onset opsoclonus‐myoclonus‐ataxia: Cerebellar atrophy, multiphasic relapses, and response to IVIG

Identifieur interne : 004456 ( Main/Curation ); précédent : 004455; suivant : 004457

Forty‐one year follow‐up of childhood‐onset opsoclonus‐myoclonus‐ataxia: Cerebellar atrophy, multiphasic relapses, and response to IVIG

Auteurs : Michael R. Pranzatelli [États-Unis] ; Elizabeth D. Tate [États-Unis] ; Marcel Kinsbourne [États-Unis] ; Verne S. Caviness Jr. [États-Unis] ; Bibhuti Mishra [États-Unis]

Source :

RBID : ISTEX:2AFDE518A95D227143DDFE3C079A00475A22D4F0

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English descriptors

Abstract

We report on an adult with opsoclonus‐myoclonus‐ataxia syndrome experiencing widely spaced neurological relapses, who was followed for 41 years. His responses to treatment are described. © 2002 Movement Disorder Society

Url:
DOI: 10.1002/mds.10283

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ISTEX:2AFDE518A95D227143DDFE3C079A00475A22D4F0

Le document en format XML

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<title level="a" type="main" xml:lang="en">Forty‐one year follow‐up of childhood‐onset opsoclonus‐myoclonus‐ataxia: Cerebellar atrophy, multiphasic relapses, and response to IVIG</title>
<author>
<name sortKey="Pranzatelli, Michael R" sort="Pranzatelli, Michael R" uniqKey="Pranzatelli M" first="Michael R." last="Pranzatelli">Michael R. Pranzatelli</name>
<affiliation wicri:level="2">
<country xml:lang="fr">États-Unis</country>
<wicri:regionArea>The National Pediatric Myoclonus Center, Departments of Neurology and Pediatrics, Southern Illinois University School of Medicine, Springfield, Illinois</wicri:regionArea>
<placeName>
<region type="state">Illinois</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Tate, Elizabeth D" sort="Tate, Elizabeth D" uniqKey="Tate E" first="Elizabeth D." last="Tate">Elizabeth D. Tate</name>
<affiliation wicri:level="2">
<country xml:lang="fr">États-Unis</country>
<wicri:regionArea>The National Pediatric Myoclonus Center, Departments of Neurology and Pediatrics, Southern Illinois University School of Medicine, Springfield, Illinois</wicri:regionArea>
<placeName>
<region type="state">Illinois</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Kinsbourne, Marcel" sort="Kinsbourne, Marcel" uniqKey="Kinsbourne M" first="Marcel" last="Kinsbourne">Marcel Kinsbourne</name>
<affiliation wicri:level="2">
<country xml:lang="fr">États-Unis</country>
<wicri:regionArea>New School University and Tufts University, Winchester, Massachusetts</wicri:regionArea>
<placeName>
<region type="state">Massachusetts</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Caviness Jr, Verne S" sort="Caviness Jr, Verne S" uniqKey="Caviness Jr V" first="Verne S." last="Caviness Jr.">Verne S. Caviness Jr.</name>
<affiliation wicri:level="2">
<country xml:lang="fr">États-Unis</country>
<wicri:regionArea>Massachusetts General Hospital, Boston, Massachusetts</wicri:regionArea>
<placeName>
<region type="state">Massachusetts</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Mishra, Bibhuti" sort="Mishra, Bibhuti" uniqKey="Mishra B" first="Bibhuti" last="Mishra">Bibhuti Mishra</name>
<affiliation wicri:level="2">
<country xml:lang="fr">États-Unis</country>
<wicri:regionArea>Temple University, Philadelphia, Pennsylvania</wicri:regionArea>
<placeName>
<region type="state">Pennsylvanie</region>
</placeName>
</affiliation>
</author>
</analytic>
<monogr></monogr>
<series>
<title level="j">Movement Disorders</title>
<title level="j" type="sub">Official Journal of the Movement Disorder Society</title>
<title level="j" type="abbrev">Mov. Disord.</title>
<idno type="ISSN">0885-3185</idno>
<idno type="eISSN">1531-8257</idno>
<imprint>
<publisher>Wiley Subscription Services, Inc., A Wiley Company</publisher>
<pubPlace>New York</pubPlace>
<date type="published" when="2002-11">2002-11</date>
<biblScope unit="vol">17</biblScope>
<biblScope unit="issue">6</biblScope>
<biblScope unit="page" from="1387">1387</biblScope>
<biblScope unit="page" to="1390">1390</biblScope>
</imprint>
<idno type="ISSN">0885-3185</idno>
</series>
<idno type="istex">2AFDE518A95D227143DDFE3C079A00475A22D4F0</idno>
<idno type="DOI">10.1002/mds.10283</idno>
<idno type="ArticleID">MDS10283</idno>
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<idno type="ISSN">0885-3185</idno>
</seriesStmt>
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<keywords scheme="KwdEn" xml:lang="en">
<term>ACTH</term>
<term>Adolescent</term>
<term>Adrenocorticotropic Hormone (therapeutic use)</term>
<term>Adult</term>
<term>Atrophy</term>
<term>Cerebellar Ataxia (diagnosis)</term>
<term>Cerebellar Ataxia (drug therapy)</term>
<term>Cerebellum (pathology)</term>
<term>Child</term>
<term>Child, Preschool</term>
<term>Follow-Up Studies</term>
<term>Humans</term>
<term>IVIG</term>
<term>Immunization, Passive</term>
<term>Infant</term>
<term>Kinsbourne syndrome</term>
<term>Magnetic Resonance Imaging</term>
<term>Male</term>
<term>Neurologic Examination</term>
<term>Neuropsychological Tests</term>
<term>Paraneoplastic Syndromes, Nervous System (diagnosis)</term>
<term>Paraneoplastic Syndromes, Nervous System (drug therapy)</term>
<term>Recurrence</term>
<term>Treatment Outcome</term>
<term>cerebellar ataxia</term>
<term>dancing eyes</term>
<term>myoclonus</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="therapeutic use" xml:lang="en">
<term>Adrenocorticotropic Hormone</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en">
<term>Cerebellar Ataxia</term>
<term>Paraneoplastic Syndromes, Nervous System</term>
</keywords>
<keywords scheme="MESH" qualifier="drug therapy" xml:lang="en">
<term>Cerebellar Ataxia</term>
<term>Paraneoplastic Syndromes, Nervous System</term>
</keywords>
<keywords scheme="MESH" qualifier="pathology" xml:lang="en">
<term>Cerebellum</term>
</keywords>
<keywords scheme="MESH" xml:lang="en">
<term>Adolescent</term>
<term>Adult</term>
<term>Atrophy</term>
<term>Child</term>
<term>Child, Preschool</term>
<term>Follow-Up Studies</term>
<term>Humans</term>
<term>Immunization, Passive</term>
<term>Infant</term>
<term>Magnetic Resonance Imaging</term>
<term>Male</term>
<term>Neurologic Examination</term>
<term>Neuropsychological Tests</term>
<term>Recurrence</term>
<term>Treatment Outcome</term>
</keywords>
</textClass>
<langUsage>
<language ident="en">en</language>
</langUsage>
</profileDesc>
</teiHeader>
<front>
<div type="abstract" xml:lang="en">We report on an adult with opsoclonus‐myoclonus‐ataxia syndrome experiencing widely spaced neurological relapses, who was followed for 41 years. His responses to treatment are described. © 2002 Movement Disorder Society</div>
</front>
</TEI>
</ISTEX>
</double>
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