Morbihan disease complicated by dermatosis neglecta: An unique presentation.
Identifieur interne : 000413 ( PubMed/Corpus ); précédent : 000412; suivant : 000414Morbihan disease complicated by dermatosis neglecta: An unique presentation.
Auteurs : Ariel E. Eber ; Stephanie Mlacker ; Sebastian Verne ; Robert Griffith ; Jennifer Ledon ; Marina Perper ; Keyvan Nouri ; Jeong Hee Cho-VegaSource :
- Journal of cutaneous pathology [ 1600-0560 ] ; 2017.
English descriptors
- KwdEn :
- MESH :
- complications : Edema, Erythema, Facial Dermatoses, Rosacea.
- pathology : Edema, Erythema, Facial Dermatoses, Rosacea.
- Female, Humans, Middle Aged.
Abstract
Morbihan disease, also referred to as solid facial edema, or rosacea lymphedema, is a rare disorder that involves chronic erythema and solid edema of the cheeks, eyelids, forehead and glabella and may arise as a complication of acne vulgaris or rosacea. Of note, it may be the only initial presenting symptom of these associated diseases. Few cases have been described in the literature, as its first description by Robert Degos in 1957. The condition is characterized by its chronicity, a typical clinical appearance and the lack of specific histopathologic or laboratory findings. The condition may wax and wane but typically does not resolve without treatment. Many cases of this condition tend to be recalcitrant to therapy, with topical and oral antibiotics regimens commonly used for rosacea generally being ineffective. The disease may easily go undiagnosed, as it mimics other more common skin conditions. We present a case of originally undiagnosed Morbihan disease mistaken for an atypical allergic rash, resistant to treatment, and complicated by dermatosis neglecta.
DOI: 10.1111/cup.12902
PubMed: 28097676
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Eber</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Mlacker, Stephanie" sort="Mlacker, Stephanie" uniqKey="Mlacker S" first="Stephanie" last="Mlacker">Stephanie Mlacker</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Verne, Sebastian" sort="Verne, Sebastian" uniqKey="Verne S" first="Sebastian" last="Verne">Sebastian Verne</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Griffith, Robert" sort="Griffith, Robert" uniqKey="Griffith R" first="Robert" last="Griffith">Robert Griffith</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Ledon, Jennifer" sort="Ledon, Jennifer" uniqKey="Ledon J" first="Jennifer" last="Ledon">Jennifer Ledon</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Perper, Marina" sort="Perper, Marina" uniqKey="Perper M" first="Marina" last="Perper">Marina Perper</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Nouri, Keyvan" sort="Nouri, Keyvan" uniqKey="Nouri K" first="Keyvan" last="Nouri">Keyvan Nouri</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Cho Vega, Jeong Hee" sort="Cho Vega, Jeong Hee" uniqKey="Cho Vega J" first="Jeong Hee" last="Cho-Vega">Jeong Hee Cho-Vega</name><affiliation><nlm:affiliation>Dermatopathology Division, Department of Pathology, Sylvester Comprehensive Cancer Center, Miami, Florida.</nlm:affiliation></affiliation></author></titleStmt><publicationStmt><idno type="wicri:source">PubMed</idno><date when="2017">2017</date><idno type="RBID">pubmed:28097676</idno><idno type="pmid">28097676</idno><idno type="doi">10.1111/cup.12902</idno><idno type="wicri:Area/PubMed/Corpus">000413</idno><idno type="wicri:explorRef" wicri:stream="PubMed" wicri:step="Corpus" wicri:corpus="PubMed">000413</idno></publicationStmt><sourceDesc><biblStruct><analytic><title xml:lang="en">Morbihan disease complicated by dermatosis neglecta: An unique presentation.</title><author><name sortKey="Eber, Ariel E" sort="Eber, Ariel E" uniqKey="Eber A" first="Ariel E" last="Eber">Ariel E. Eber</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Mlacker, Stephanie" sort="Mlacker, Stephanie" uniqKey="Mlacker S" first="Stephanie" last="Mlacker">Stephanie Mlacker</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Verne, Sebastian" sort="Verne, Sebastian" uniqKey="Verne S" first="Sebastian" last="Verne">Sebastian Verne</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Griffith, Robert" sort="Griffith, Robert" uniqKey="Griffith R" first="Robert" last="Griffith">Robert Griffith</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Ledon, Jennifer" sort="Ledon, Jennifer" uniqKey="Ledon J" first="Jennifer" last="Ledon">Jennifer Ledon</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Perper, Marina" sort="Perper, Marina" uniqKey="Perper M" first="Marina" last="Perper">Marina Perper</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Nouri, Keyvan" sort="Nouri, Keyvan" uniqKey="Nouri K" first="Keyvan" last="Nouri">Keyvan Nouri</name><affiliation><nlm:affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</nlm:affiliation></affiliation></author><author><name sortKey="Cho Vega, Jeong Hee" sort="Cho Vega, Jeong Hee" uniqKey="Cho Vega J" first="Jeong Hee" last="Cho-Vega">Jeong Hee Cho-Vega</name><affiliation><nlm:affiliation>Dermatopathology Division, Department of Pathology, Sylvester Comprehensive Cancer Center, Miami, Florida.</nlm:affiliation></affiliation></author></analytic><series><title level="j">Journal of cutaneous pathology</title><idno type="eISSN">1600-0560</idno><imprint><date when="2017" type="published">2017</date></imprint></series></biblStruct></sourceDesc></fileDesc><profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Edema (complications)</term><term>Edema (pathology)</term><term>Erythema (complications)</term><term>Erythema (pathology)</term><term>Facial Dermatoses (complications)</term><term>Facial Dermatoses (pathology)</term><term>Female</term><term>Humans</term><term>Middle Aged</term><term>Rosacea (complications)</term><term>Rosacea (pathology)</term></keywords><keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Edema</term><term>Erythema</term><term>Facial Dermatoses</term><term>Rosacea</term></keywords><keywords scheme="MESH" qualifier="pathology" xml:lang="en"><term>Edema</term><term>Erythema</term><term>Facial Dermatoses</term><term>Rosacea</term></keywords><keywords scheme="MESH" xml:lang="en"><term>Female</term><term>Humans</term><term>Middle Aged</term></keywords></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">Morbihan disease, also referred to as solid facial edema, or rosacea lymphedema, is a rare disorder that involves chronic erythema and solid edema of the cheeks, eyelids, forehead and glabella and may arise as a complication of acne vulgaris or rosacea. Of note, it may be the only initial presenting symptom of these associated diseases. Few cases have been described in the literature, as its first description by Robert Degos in 1957. The condition is characterized by its chronicity, a typical clinical appearance and the lack of specific histopathologic or laboratory findings. The condition may wax and wane but typically does not resolve without treatment. Many cases of this condition tend to be recalcitrant to therapy, with topical and oral antibiotics regimens commonly used for rosacea generally being ineffective. The disease may easily go undiagnosed, as it mimics other more common skin conditions. We present a case of originally undiagnosed Morbihan disease mistaken for an atypical allergic rash, resistant to treatment, and complicated by dermatosis neglecta.</div></front></TEI><pubmed><MedlineCitation Status="MEDLINE" Owner="NLM"><PMID Version="1">28097676</PMID><DateCreated><Year>2017</Year><Month>01</Month><Day>18</Day></DateCreated><DateCompleted><Year>2017</Year><Month>07</Month><Day>21</Day></DateCompleted><DateRevised><Year>2017</Year><Month>07</Month><Day>21</Day></DateRevised><Article PubModel="Print-Electronic"><Journal><ISSN IssnType="Electronic">1600-0560</ISSN><JournalIssue CitedMedium="Internet"><Volume>44</Volume><Issue>5</Issue><PubDate><Year>2017</Year><Month>May</Month></PubDate></JournalIssue><Title>Journal of cutaneous pathology</Title><ISOAbbreviation>J. Cutan. Pathol.</ISOAbbreviation></Journal><ArticleTitle>Morbihan disease complicated by dermatosis neglecta: An unique presentation.</ArticleTitle><Pagination><MedlinePgn>470-473</MedlinePgn></Pagination><ELocationID EIdType="doi" ValidYN="Y">10.1111/cup.12902</ELocationID><Abstract><AbstractText>Morbihan disease, also referred to as solid facial edema, or rosacea lymphedema, is a rare disorder that involves chronic erythema and solid edema of the cheeks, eyelids, forehead and glabella and may arise as a complication of acne vulgaris or rosacea. Of note, it may be the only initial presenting symptom of these associated diseases. Few cases have been described in the literature, as its first description by Robert Degos in 1957. The condition is characterized by its chronicity, a typical clinical appearance and the lack of specific histopathologic or laboratory findings. The condition may wax and wane but typically does not resolve without treatment. Many cases of this condition tend to be recalcitrant to therapy, with topical and oral antibiotics regimens commonly used for rosacea generally being ineffective. The disease may easily go undiagnosed, as it mimics other more common skin conditions. We present a case of originally undiagnosed Morbihan disease mistaken for an atypical allergic rash, resistant to treatment, and complicated by dermatosis neglecta.</AbstractText><CopyrightInformation>© 2017 John Wiley & Sons A/S. Published by John Wiley & Sons Ltd.</CopyrightInformation></Abstract><AuthorList CompleteYN="Y"><Author ValidYN="Y"><LastName>Eber</LastName><ForeName>Ariel E</ForeName><Initials>AE</Initials><Identifier Source="ORCID">http://orcid.org/0000-0002-8802-1003</Identifier><AffiliationInfo><Affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Mlacker</LastName><ForeName>Stephanie</ForeName><Initials>S</Initials><AffiliationInfo><Affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Verne</LastName><ForeName>Sebastian</ForeName><Initials>S</Initials><AffiliationInfo><Affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Griffith</LastName><ForeName>Robert</ForeName><Initials>R</Initials><AffiliationInfo><Affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Ledon</LastName><ForeName>Jennifer</ForeName><Initials>J</Initials><AffiliationInfo><Affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Perper</LastName><ForeName>Marina</ForeName><Initials>M</Initials><AffiliationInfo><Affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Nouri</LastName><ForeName>Keyvan</ForeName><Initials>K</Initials><AffiliationInfo><Affiliation>Department of Dermatology and Cutaneous Surgery, Miller School of Medicine,University of Miami, Miami, Florida.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Cho-Vega</LastName><ForeName>Jeong Hee</ForeName><Initials>JH</Initials><AffiliationInfo><Affiliation>Dermatopathology Division, Department of Pathology, Sylvester Comprehensive Cancer Center, Miami, Florida.</Affiliation></AffiliationInfo></Author></AuthorList><Language>eng</Language><PublicationTypeList><PublicationType UI="D002363">Case Reports</PublicationType></PublicationTypeList><ArticleDate DateType="Electronic"><Year>2017</Year><Month>02</Month><Day>16</Day></ArticleDate></Article><MedlineJournalInfo><Country>United States</Country><MedlineTA>J Cutan Pathol</MedlineTA><NlmUniqueID>0425124</NlmUniqueID><ISSNLinking>0303-6987</ISSNLinking></MedlineJournalInfo><CitationSubset>IM</CitationSubset><MeshHeadingList><MeshHeading><DescriptorName UI="D004487" MajorTopicYN="Y">Edema</DescriptorName><QualifierName UI="Q000150" MajorTopicYN="N">complications</QualifierName><QualifierName UI="Q000473" MajorTopicYN="N">pathology</QualifierName></MeshHeading><MeshHeading><DescriptorName UI="D004890" MajorTopicYN="Y">Erythema</DescriptorName><QualifierName UI="Q000150" MajorTopicYN="N">complications</QualifierName><QualifierName UI="Q000473" MajorTopicYN="N">pathology</QualifierName></MeshHeading><MeshHeading><DescriptorName UI="D005148" MajorTopicYN="Y">Facial Dermatoses</DescriptorName><QualifierName UI="Q000150" MajorTopicYN="N">complications</QualifierName><QualifierName UI="Q000473" MajorTopicYN="N">pathology</QualifierName></MeshHeading><MeshHeading><DescriptorName UI="D005260" MajorTopicYN="N">Female</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D006801" MajorTopicYN="N">Humans</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D008875" MajorTopicYN="N">Middle Aged</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D012393" MajorTopicYN="Y">Rosacea</DescriptorName><QualifierName UI="Q000150" MajorTopicYN="N">complications</QualifierName><QualifierName UI="Q000473" MajorTopicYN="N">pathology</QualifierName></MeshHeading></MeshHeadingList><KeywordList Owner="NOTNLM"><Keyword MajorTopicYN="N">Morbihan</Keyword><Keyword MajorTopicYN="N">acne</Keyword><Keyword MajorTopicYN="N">acne vulgaris</Keyword><Keyword MajorTopicYN="N">dermatosis neglecta</Keyword><Keyword MajorTopicYN="N">rosacea</Keyword></KeywordList></MedlineCitation><PubmedData><History><PubMedPubDate PubStatus="received"><Year>2016</Year><Month>09</Month><Day>12</Day></PubMedPubDate><PubMedPubDate PubStatus="revised"><Year>2017</Year><Month>01</Month><Day>04</Day></PubMedPubDate><PubMedPubDate PubStatus="accepted"><Year>2017</Year><Month>01</Month><Day>11</Day></PubMedPubDate><PubMedPubDate PubStatus="pubmed"><Year>2017</Year><Month>1</Month><Day>18</Day><Hour>6</Hour><Minute>0</Minute></PubMedPubDate><PubMedPubDate PubStatus="medline"><Year>2017</Year><Month>7</Month><Day>22</Day><Hour>6</Hour><Minute>0</Minute></PubMedPubDate><PubMedPubDate PubStatus="entrez"><Year>2017</Year><Month>1</Month><Day>19</Day><Hour>6</Hour><Minute>0</Minute></PubMedPubDate></History><PublicationStatus>ppublish</PublicationStatus><ArticleIdList><ArticleId IdType="pubmed">28097676</ArticleId><ArticleId IdType="doi">10.1111/cup.12902</ArticleId></ArticleIdList></PubmedData></pubmed></record>Pour manipuler ce document sous Unix (Dilib)
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