Traumatic lesions from congenital insensitivity to pain with anhidrosis in a pediatric patient: dental management
Identifieur interne : 005A10 ( Main/Curation ); précédent : 005A09; suivant : 005A11Traumatic lesions from congenital insensitivity to pain with anhidrosis in a pediatric patient: dental management
Auteurs : Beatriz Gonçalves Neves [Brésil] ; Rosemere Teixeira Roza [Brésil] ; Gloria Fernanda Castro [Brésil]Source :
- Dental Traumatology [ 1600-4469 ] ; 2009-10.
English descriptors
- KwdEn :
- Alveolar ridges, Amputation, Anesthesia, Anhidrosis, Appropriate management, Autonomic neuropathy, Autonomic neuropathy type, Bers, Case report, Cipa, Congenital, Congenital insensitivity, Deep ulcers, Dental implications, Dental treatment, Dentition, Digital amputation, Digital amputations, Federal university, Further injury, General anesthesia, Hospital admission, Hsan, Insensitivity, John wiley sons, Lesion, Local anesthesia, Mental retardation, Mouth guards, Multidisciplinary team, Neurol, Neuropathy, Ngers, Oral mucosa, Oral pathol, Oral surg, Paediatr dent, Pain insensitivity, Pain sensation, Pediatr, Pediatr neurol, Permanent dentition, Permanent tooth germ, Premature loss, Pressure sensitivity, Protective plates, Radiol endod, Selfmutilating behavior, Several methods, Severe injuries, Sharp edges, Speech therapist, Sweat glands, Traumatic lesions, Treatment plan, Weekly intervals.
- Teeft :
- Alveolar ridges, Amputation, Anesthesia, Anhidrosis, Appropriate management, Autonomic neuropathy, Autonomic neuropathy type, Bers, Case report, Cipa, Congenital, Congenital insensitivity, Deep ulcers, Dental implications, Dental treatment, Dentition, Digital amputation, Digital amputations, Federal university, Further injury, General anesthesia, Hospital admission, Hsan, Insensitivity, John wiley sons, Lesion, Local anesthesia, Mental retardation, Mouth guards, Multidisciplinary team, Neurol, Neuropathy, Ngers, Oral mucosa, Oral pathol, Oral surg, Paediatr dent, Pain insensitivity, Pain sensation, Pediatr, Pediatr neurol, Permanent dentition, Permanent tooth germ, Premature loss, Pressure sensitivity, Protective plates, Radiol endod, Selfmutilating behavior, Several methods, Severe injuries, Sharp edges, Speech therapist, Sweat glands, Traumatic lesions, Treatment plan, Weekly intervals.
Abstract
Abstract – Congenital insensitivity to pain with anhidrosis is a rare autosomal‐recessive disorder characterized by unexplained fever episodes, anhidrosis, pain insensitivity, self‐mutilating behavior, and mental retardation. The lack of sensitivity to pain results in traumatic lesions, such as ulcers, fractures, burns, bites, scars, and digital amputations. Several methods have been suggested to treat these patients; however, appropriate management is difficult, especially when the mutilation is particularly severe. This report describes the case of a 2‐year‐old female patient who had severe self‐mutilating injuries to her tongue, hands, lips, and oral mucosa caused by biting. The patient presented digital amputation and also a premature loss of a permanent tooth germ during the treatment. The dental management is described and discussed. It is important to include the dentist on the multidisciplinary team to reduce the frequency and severity of the self‐inflicted lesions in these patients, also to prevent complications.
Url:
DOI: 10.1111/j.1600-9657.2009.00810.x
Links toward previous steps (curation, corpus...)
- to stream Istex, to step Corpus: Pour aller vers cette notice dans l'étape Curation :007621
- to stream Istex, to step Curation: Pour aller vers cette notice dans l'étape Curation :007621
- to stream Istex, to step Checkpoint: Pour aller vers cette notice dans l'étape Curation :002087
- to stream Main, to step Merge: Pour aller vers cette notice dans l'étape Curation :005A74
Links to Exploration step
ISTEX:EE65610212437D41A4CFB59BBE2CED4596E6005DLe document en format XML
<record><TEI wicri:istexFullTextTei="biblStruct"><teiHeader><fileDesc><titleStmt><title xml:lang="en">Traumatic lesions from congenital insensitivity to pain with anhidrosis in a pediatric patient: dental management</title>
<author><name sortKey="Neves, Beatriz Goncalves" sort="Neves, Beatriz Goncalves" uniqKey="Neves B" first="Beatriz Gonçalves" last="Neves">Beatriz Gonçalves Neves</name>
</author>
<author><name sortKey="Roza, Rosemere Teixeira" sort="Roza, Rosemere Teixeira" uniqKey="Roza R" first="Rosemere Teixeira" last="Roza">Rosemere Teixeira Roza</name>
</author>
<author><name sortKey="Castro, Gloria Fernanda" sort="Castro, Gloria Fernanda" uniqKey="Castro G" first="Gloria Fernanda" last="Castro">Gloria Fernanda Castro</name>
</author>
</titleStmt>
<publicationStmt><idno type="wicri:source">ISTEX</idno>
<idno type="RBID">ISTEX:EE65610212437D41A4CFB59BBE2CED4596E6005D</idno>
<date when="2009" year="2009">2009</date>
<idno type="doi">10.1111/j.1600-9657.2009.00810.x</idno>
<idno type="url">https://api.istex.fr/document/EE65610212437D41A4CFB59BBE2CED4596E6005D/fulltext/pdf</idno>
<idno type="wicri:Area/Istex/Corpus">007621</idno>
<idno type="wicri:explorRef" wicri:stream="Istex" wicri:step="Corpus" wicri:corpus="ISTEX">007621</idno>
<idno type="wicri:Area/Istex/Curation">007621</idno>
<idno type="wicri:Area/Istex/Checkpoint">002087</idno>
<idno type="wicri:explorRef" wicri:stream="Istex" wicri:step="Checkpoint">002087</idno>
<idno type="wicri:doubleKey">1600-4469:2009:Neves B:traumatic:lesions:from</idno>
<idno type="wicri:Area/Main/Merge">005A74</idno>
<idno type="wicri:Area/Main/Curation">005A10</idno>
</publicationStmt>
<sourceDesc><biblStruct><analytic><title level="a" type="main">Traumatic lesions from congenital insensitivity to pain with anhidrosis in a pediatric patient: dental management</title>
<author><name sortKey="Neves, Beatriz Goncalves" sort="Neves, Beatriz Goncalves" uniqKey="Neves B" first="Beatriz Gonçalves" last="Neves">Beatriz Gonçalves Neves</name>
<affiliation wicri:level="3"><country xml:lang="fr">Brésil</country>
<wicri:regionArea>Department of Pediatric Dentistry and Orthodontics, Federal University of Rio de Janeiro, Rio de Janeiro</wicri:regionArea>
<placeName><settlement type="city">Rio de Janeiro</settlement>
<region type="state">État de Rio de Janeiro</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Roza, Rosemere Teixeira" sort="Roza, Rosemere Teixeira" uniqKey="Roza R" first="Rosemere Teixeira" last="Roza">Rosemere Teixeira Roza</name>
<affiliation wicri:level="3"><country xml:lang="fr">Brésil</country>
<wicri:regionArea>Department of Pediatric Dentistry and Orthodontics, Federal University of Rio de Janeiro, Rio de Janeiro</wicri:regionArea>
<placeName><settlement type="city">Rio de Janeiro</settlement>
<region type="state">État de Rio de Janeiro</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Castro, Gloria Fernanda" sort="Castro, Gloria Fernanda" uniqKey="Castro G" first="Gloria Fernanda" last="Castro">Gloria Fernanda Castro</name>
<affiliation wicri:level="3"><country xml:lang="fr">Brésil</country>
<wicri:regionArea>Department of Pediatric Dentistry and Orthodontics, Federal University of Rio de Janeiro, Rio de Janeiro</wicri:regionArea>
<placeName><settlement type="city">Rio de Janeiro</settlement>
<region type="state">État de Rio de Janeiro</region>
</placeName>
</affiliation>
</author>
</analytic>
<monogr></monogr>
<series><title level="j" type="main">Dental Traumatology</title>
<title level="j" type="alt">DENTAL TRAUMATOLOGY</title>
<idno type="ISSN">1600-4469</idno>
<idno type="eISSN">1600-9657</idno>
<imprint><biblScope unit="vol">25</biblScope>
<biblScope unit="issue">5</biblScope>
<biblScope unit="page" from="545">545</biblScope>
<biblScope unit="page" to="549">549</biblScope>
<biblScope unit="page-count">5</biblScope>
<publisher>Blackwell Publishing Ltd</publisher>
<pubPlace>Oxford, UK</pubPlace>
<date type="published" when="2009-10">2009-10</date>
</imprint>
<idno type="ISSN">1600-4469</idno>
</series>
</biblStruct>
</sourceDesc>
<seriesStmt><idno type="ISSN">1600-4469</idno>
</seriesStmt>
</fileDesc>
<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Alveolar ridges</term>
<term>Amputation</term>
<term>Anesthesia</term>
<term>Anhidrosis</term>
<term>Appropriate management</term>
<term>Autonomic neuropathy</term>
<term>Autonomic neuropathy type</term>
<term>Bers</term>
<term>Case report</term>
<term>Cipa</term>
<term>Congenital</term>
<term>Congenital insensitivity</term>
<term>Deep ulcers</term>
<term>Dental implications</term>
<term>Dental treatment</term>
<term>Dentition</term>
<term>Digital amputation</term>
<term>Digital amputations</term>
<term>Federal university</term>
<term>Further injury</term>
<term>General anesthesia</term>
<term>Hospital admission</term>
<term>Hsan</term>
<term>Insensitivity</term>
<term>John wiley sons</term>
<term>Lesion</term>
<term>Local anesthesia</term>
<term>Mental retardation</term>
<term>Mouth guards</term>
<term>Multidisciplinary team</term>
<term>Neurol</term>
<term>Neuropathy</term>
<term>Ngers</term>
<term>Oral mucosa</term>
<term>Oral pathol</term>
<term>Oral surg</term>
<term>Paediatr dent</term>
<term>Pain insensitivity</term>
<term>Pain sensation</term>
<term>Pediatr</term>
<term>Pediatr neurol</term>
<term>Permanent dentition</term>
<term>Permanent tooth germ</term>
<term>Premature loss</term>
<term>Pressure sensitivity</term>
<term>Protective plates</term>
<term>Radiol endod</term>
<term>Selfmutilating behavior</term>
<term>Several methods</term>
<term>Severe injuries</term>
<term>Sharp edges</term>
<term>Speech therapist</term>
<term>Sweat glands</term>
<term>Traumatic lesions</term>
<term>Treatment plan</term>
<term>Weekly intervals</term>
</keywords>
<keywords scheme="Teeft" xml:lang="en"><term>Alveolar ridges</term>
<term>Amputation</term>
<term>Anesthesia</term>
<term>Anhidrosis</term>
<term>Appropriate management</term>
<term>Autonomic neuropathy</term>
<term>Autonomic neuropathy type</term>
<term>Bers</term>
<term>Case report</term>
<term>Cipa</term>
<term>Congenital</term>
<term>Congenital insensitivity</term>
<term>Deep ulcers</term>
<term>Dental implications</term>
<term>Dental treatment</term>
<term>Dentition</term>
<term>Digital amputation</term>
<term>Digital amputations</term>
<term>Federal university</term>
<term>Further injury</term>
<term>General anesthesia</term>
<term>Hospital admission</term>
<term>Hsan</term>
<term>Insensitivity</term>
<term>John wiley sons</term>
<term>Lesion</term>
<term>Local anesthesia</term>
<term>Mental retardation</term>
<term>Mouth guards</term>
<term>Multidisciplinary team</term>
<term>Neurol</term>
<term>Neuropathy</term>
<term>Ngers</term>
<term>Oral mucosa</term>
<term>Oral pathol</term>
<term>Oral surg</term>
<term>Paediatr dent</term>
<term>Pain insensitivity</term>
<term>Pain sensation</term>
<term>Pediatr</term>
<term>Pediatr neurol</term>
<term>Permanent dentition</term>
<term>Permanent tooth germ</term>
<term>Premature loss</term>
<term>Pressure sensitivity</term>
<term>Protective plates</term>
<term>Radiol endod</term>
<term>Selfmutilating behavior</term>
<term>Several methods</term>
<term>Severe injuries</term>
<term>Sharp edges</term>
<term>Speech therapist</term>
<term>Sweat glands</term>
<term>Traumatic lesions</term>
<term>Treatment plan</term>
<term>Weekly intervals</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front><div type="abstract">Abstract – Congenital insensitivity to pain with anhidrosis is a rare autosomal‐recessive disorder characterized by unexplained fever episodes, anhidrosis, pain insensitivity, self‐mutilating behavior, and mental retardation. The lack of sensitivity to pain results in traumatic lesions, such as ulcers, fractures, burns, bites, scars, and digital amputations. Several methods have been suggested to treat these patients; however, appropriate management is difficult, especially when the mutilation is particularly severe. This report describes the case of a 2‐year‐old female patient who had severe self‐mutilating injuries to her tongue, hands, lips, and oral mucosa caused by biting. The patient presented digital amputation and also a premature loss of a permanent tooth germ during the treatment. The dental management is described and discussed. It is important to include the dentist on the multidisciplinary team to reduce the frequency and severity of the self‐inflicted lesions in these patients, also to prevent complications.</div>
</front>
</TEI>
</record>
Pour manipuler ce document sous Unix (Dilib)
EXPLOR_STEP=$WICRI_ROOT/Wicri/Santé/explor/EdenteV2/Data/Main/Curation
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 005A10 | SxmlIndent | more
Ou
HfdSelect -h $EXPLOR_AREA/Data/Main/Curation/biblio.hfd -nk 005A10 | SxmlIndent | more
Pour mettre un lien sur cette page dans le réseau Wicri
{{Explor lien |wiki= Wicri/Santé |area= EdenteV2 |flux= Main |étape= Curation |type= RBID |clé= ISTEX:EE65610212437D41A4CFB59BBE2CED4596E6005D |texte= Traumatic lesions from congenital insensitivity to pain with anhidrosis in a pediatric patient: dental management }}
![]() | This area was generated with Dilib version V0.6.32. | ![]() |