Traumatic lesions from congenital insensitivity to pain with anhidrosis in a pediatric patient: dental management
Identifieur interne : 007621 ( Istex/Corpus ); précédent : 007620; suivant : 007622Traumatic lesions from congenital insensitivity to pain with anhidrosis in a pediatric patient: dental management
Auteurs : Beatriz Gonçalves Neves ; Rosemere Teixeira Roza ; Gloria Fernanda CastroSource :
- Dental Traumatology [ 1600-4469 ] ; 2009-10.
English descriptors
- KwdEn :
- Alveolar ridges, Amputation, Anesthesia, Anhidrosis, Appropriate management, Autonomic neuropathy, Autonomic neuropathy type, Bers, Case report, Cipa, Congenital, Congenital insensitivity, Deep ulcers, Dental implications, Dental treatment, Dentition, Digital amputation, Digital amputations, Federal university, Further injury, General anesthesia, Hospital admission, Hsan, Insensitivity, John wiley sons, Lesion, Local anesthesia, Mental retardation, Mouth guards, Multidisciplinary team, Neurol, Neuropathy, Ngers, Oral mucosa, Oral pathol, Oral surg, Paediatr dent, Pain insensitivity, Pain sensation, Pediatr, Pediatr neurol, Permanent dentition, Permanent tooth germ, Premature loss, Pressure sensitivity, Protective plates, Radiol endod, Selfmutilating behavior, Several methods, Severe injuries, Sharp edges, Speech therapist, Sweat glands, Traumatic lesions, Treatment plan, Weekly intervals.
- Teeft :
- Alveolar ridges, Amputation, Anesthesia, Anhidrosis, Appropriate management, Autonomic neuropathy, Autonomic neuropathy type, Bers, Case report, Cipa, Congenital, Congenital insensitivity, Deep ulcers, Dental implications, Dental treatment, Dentition, Digital amputation, Digital amputations, Federal university, Further injury, General anesthesia, Hospital admission, Hsan, Insensitivity, John wiley sons, Lesion, Local anesthesia, Mental retardation, Mouth guards, Multidisciplinary team, Neurol, Neuropathy, Ngers, Oral mucosa, Oral pathol, Oral surg, Paediatr dent, Pain insensitivity, Pain sensation, Pediatr, Pediatr neurol, Permanent dentition, Permanent tooth germ, Premature loss, Pressure sensitivity, Protective plates, Radiol endod, Selfmutilating behavior, Several methods, Severe injuries, Sharp edges, Speech therapist, Sweat glands, Traumatic lesions, Treatment plan, Weekly intervals.
Abstract
Abstract – Congenital insensitivity to pain with anhidrosis is a rare autosomal‐recessive disorder characterized by unexplained fever episodes, anhidrosis, pain insensitivity, self‐mutilating behavior, and mental retardation. The lack of sensitivity to pain results in traumatic lesions, such as ulcers, fractures, burns, bites, scars, and digital amputations. Several methods have been suggested to treat these patients; however, appropriate management is difficult, especially when the mutilation is particularly severe. This report describes the case of a 2‐year‐old female patient who had severe self‐mutilating injuries to her tongue, hands, lips, and oral mucosa caused by biting. The patient presented digital amputation and also a premature loss of a permanent tooth germ during the treatment. The dental management is described and discussed. It is important to include the dentist on the multidisciplinary team to reduce the frequency and severity of the self‐inflicted lesions in these patients, also to prevent complications.
Url:
DOI: 10.1111/j.1600-9657.2009.00810.x
Links to Exploration step
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<front><div type="abstract">Abstract – Congenital insensitivity to pain with anhidrosis is a rare autosomal‐recessive disorder characterized by unexplained fever episodes, anhidrosis, pain insensitivity, self‐mutilating behavior, and mental retardation. The lack of sensitivity to pain results in traumatic lesions, such as ulcers, fractures, burns, bites, scars, and digital amputations. Several methods have been suggested to treat these patients; however, appropriate management is difficult, especially when the mutilation is particularly severe. This report describes the case of a 2‐year‐old female patient who had severe self‐mutilating injuries to her tongue, hands, lips, and oral mucosa caused by biting. The patient presented digital amputation and also a premature loss of a permanent tooth germ during the treatment. The dental management is described and discussed. It is important to include the dentist on the multidisciplinary team to reduce the frequency and severity of the self‐inflicted lesions in these patients, also to prevent complications.</div>
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Congenital insensitivity to pain with anhidrosis is a rare autosomal‐recessive disorder characterized by unexplained fever episodes, anhidrosis, pain insensitivity, self‐mutilating behavior, and mental retardation. The lack of sensitivity to pain results in traumatic lesions, such as ulcers, fractures, burns, bites, scars, and digital amputations. Several methods have been suggested to treat these patients; however, appropriate management is difficult, especially when the mutilation is particularly severe. This report describes the case of a 2‐year‐old female patient who had severe self‐mutilating injuries to her tongue, hands, lips, and oral mucosa caused by biting. The patient presented digital amputation and also a premature loss of a permanent tooth germ during the treatment. The dental management is described and discussed. It is important to include the dentist on the multidisciplinary team to reduce the frequency and severity of the self‐inflicted lesions in these patients, also to prevent complications.</p>
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<titleGroup><title type="main" sort="DENTAL TRAUMATOLOGY">Dental Traumatology</title>
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<coverDate startDate="2009-10">October 2009</coverDate>
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<titleGroup><title type="tocHeading1">CASE REPORTS</title>
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<copyright>© 2009 John Wiley & Sons A/S</copyright>
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<correspondenceTo>Gloria Fernanda Castro, Travessa Alfredo Botelho, No. 66, Apt. 201 – Méier, Rio de Janeiro‐RJ – Brazil, Zip code: 20720‐200
Tel.: +55 21 3979 9820
Fax: +55 21 2562 2098
e‐mail: <email>gfbacastro@yahoo.com.br</email>
or <email>beatriz_gneves@yahoo.com.br</email>
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<contentMeta><unparsedEditorialHistory>Accepted 17 April, 2009</unparsedEditorialHistory>
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<titleGroup><title type="main">Traumatic lesions from congenital insensitivity to pain with anhidrosis in a pediatric patient: dental management</title>
<title type="shortAuthors"><i>Neves et al.</i>
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<title type="short"><i>Traumatic lesions in CIPA</i>
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<creators><creator creatorRole="author" xml:id="cr1" affiliationRef="#aff-1-1"><personName><givenNames>Beatriz Gonçalves</givenNames>
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<creator creatorRole="author" xml:id="cr2" affiliationRef="#aff-1-1"><personName><givenNames>Rosemere Teixeira</givenNames>
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<creator creatorRole="author" xml:id="cr3" affiliationRef="#aff-1-1"><personName><givenNames>Gloria Fernanda</givenNames>
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<affiliationGroup><affiliation xml:id="aff-1-1" countryCode="BR"><unparsedAffiliation>Department of Pediatric Dentistry and Orthodontics, Federal University of Rio de Janeiro, Rio de Janeiro, Brazil</unparsedAffiliation>
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<abstractGroup><abstract type="main" xml:lang="en"><p><b>Abstract – </b>
Congenital insensitivity to pain with anhidrosis is a rare autosomal‐recessive disorder characterized by unexplained fever episodes, anhidrosis, pain insensitivity, self‐mutilating behavior, and mental retardation. The lack of sensitivity to pain results in traumatic lesions, such as ulcers, fractures, burns, bites, scars, and digital amputations. Several methods have been suggested to treat these patients; however, appropriate management is difficult, especially when the mutilation is particularly severe. This report describes the case of a 2‐year‐old female patient who had severe self‐mutilating injuries to her tongue, hands, lips, and oral mucosa caused by biting. The patient presented digital amputation and also a premature loss of a permanent tooth germ during the treatment. The dental management is described and discussed. It is important to include the dentist on the multidisciplinary team to reduce the frequency and severity of the self‐inflicted lesions in these patients, also to prevent complications.</p>
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<abstract>Abstract – Congenital insensitivity to pain with anhidrosis is a rare autosomal‐recessive disorder characterized by unexplained fever episodes, anhidrosis, pain insensitivity, self‐mutilating behavior, and mental retardation. The lack of sensitivity to pain results in traumatic lesions, such as ulcers, fractures, burns, bites, scars, and digital amputations. Several methods have been suggested to treat these patients; however, appropriate management is difficult, especially when the mutilation is particularly severe. This report describes the case of a 2‐year‐old female patient who had severe self‐mutilating injuries to her tongue, hands, lips, and oral mucosa caused by biting. The patient presented digital amputation and also a premature loss of a permanent tooth germ during the treatment. The dental management is described and discussed. It is important to include the dentist on the multidisciplinary team to reduce the frequency and severity of the self‐inflicted lesions in these patients, also to prevent complications.</abstract>
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