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Complex care by multiple medical and dental specialists of a patient with aggressive Gorlin-Goltz syndrome

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Complex care by multiple medical and dental specialists of a patient with aggressive Gorlin-Goltz syndrome

Auteurs : K. Nagy [Hongrie] ; E. Kiss ; C. Erdei [Hongrie] ; F. Oberna [Hongrie] ; P. Fejerdy [Hongrie] ; K. Marton [Hongrie] ; Z. Vajo [Hongrie]

Source :

Postgraduate medical journal [ 0032-5473 ] ; 2008.

RBID : Pascal:08-0375122

Descripteurs français

Pascal (Inist)
- Syndrome du naevus basocellulaire, Complexité, Complexe, Soin, Multiple, Médecine, Dent, Homme, Malade, Haute malignité.
Wicri :
- topic : Médecine, Homme.

English descriptors

KwdEn :
- Basal cell nevus syndrome, Care, Complexes, Complexity, High malignancy, Human, Medicine, Multiple, Patient, Tooth.

Abstract

Gorlin-Goltz syndrome is a genetically predisposed disease characterised by multiple basal cell carcinomas, odontogenic keratocysts and ectopic calcifications. The aim of this study was to show successful treatment of a 37-year-old male patient by cooperation between different dental and medical specialists. Because of the recurrence of a large basal cell carcinoma after multiple operations and a total dose telecobalt irradiation of 66 Gy, the patient's nose was ablated, with resection of the upper lip and part of the maxilla. The intraoral prosthetic treatment helped to restore the subtotal edentulousness. In order to enhance the application of the dental prosthesis, an Abbe plasty was performed at the second stage of surgery. As previous irradiation of the area precluded the use of facial implants immediately after the intraoral treatment, a temporary artificial nose prosthesis was created. The patient tolerated the procedures well and is completely disease-free 12 months after the surgery. Besides presenting a rare and complicated case of Gorlin-Goltz syndrome, the main purpose of this report is to show that, if different specialists in a dental-clinical team (maxillofacial surgeon, oncologist, radiation oncologist, prosthodontist and psychiatrist) combine their skills and expertise, successful management is possible even in a challenging complex case.

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Le document en format XML

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<term>Care</term>
<term>Complexes</term>
<term>Complexity</term>
<term>High malignancy</term>
<term>Human</term>
<term>Medicine</term>
<term>Multiple</term>
<term>Patient</term>
<term>Tooth</term>
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<keywords scheme="Pascal" xml:lang="fr"><term>Syndrome du naevus basocellulaire</term>
<term>Complexité</term>
<term>Complexe</term>
<term>Soin</term>
<term>Multiple</term>
<term>Médecine</term>
<term>Dent</term>
<term>Homme</term>
<term>Malade</term>
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<front><div type="abstract" xml:lang="en">Gorlin-Goltz syndrome is a genetically predisposed disease characterised by multiple basal cell carcinomas, odontogenic keratocysts and ectopic calcifications. The aim of this study was to show successful treatment of a 37-year-old male patient by cooperation between different dental and medical specialists. Because of the recurrence of a large basal cell carcinoma after multiple operations and a total dose telecobalt irradiation of 66 Gy, the patient's nose was ablated, with resection of the upper lip and part of the maxilla. The intraoral prosthetic treatment helped to restore the subtotal edentulousness. In order to enhance the application of the dental prosthesis, an Abbe plasty was performed at the second stage of surgery. As previous irradiation of the area precluded the use of facial implants immediately after the intraoral treatment, a temporary artificial nose prosthesis was created. The patient tolerated the procedures well and is completely disease-free 12 months after the surgery. Besides presenting a rare and complicated case of Gorlin-Goltz syndrome, the main purpose of this report is to show that, if different specialists in a dental-clinical team (maxillofacial surgeon, oncologist, radiation oncologist, prosthodontist and psychiatrist) combine their skills and expertise, successful management is possible even in a challenging complex case.</div>
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Complex care by multiple medical and dental specialists of a patient with aggressive Gorlin-Goltz syndrome

Complex care by multiple medical and dental specialists of a patient with aggressive Gorlin-Goltz syndrome

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Links to Exploration step

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri