THE PORPHYRIAS
Identifieur interne : 002F20 ( Main/Merge ); précédent : 002F19; suivant : 002F21THE PORPHYRIAS
Auteurs : David A. Paslin [États-Unis]Source :
- International Journal of Dermatology [ 0011-9059 ] ; 1992-08.
English descriptors
- Teeft :
- Acta, Acta derm venereol, Acute attacks, Acute porphyria, Amino acids, Arch dermatol, Biochem, Biosynthesis, Cell fragility, Chloroquine, Congenital, Congenital erythropoietic porphyria, Coproporphyria, Coproporphyrin, Coproporphyrinogen, Cutanea, Cutaneous, Cutaneous porphyria, Cutaneous porphyrias, Cytochrome, Cytosol, Decarboxylase, Dermatol, Dermatology, Engl, Enzyme, Enzyme activity, Enzyme deficiencies, Erythropoietic, Erythropoietic porphyrias, Erythropoietic protoporphyria, Excretion, Ferrochelatase, Glin, Gonadal steroids, Heme, Heme biosynthetic pathway, Hepatic, Hepatic porphyrias, Hepatoerythropoietic porphyria, Hereditary coproporphyria, Human genet, International journal, Iron overload, Isomer, Lancet, Liver cells, Liver damage, Liver disease, Microsomal enzymes, Mitochondrial, Mitochondrion, Oxidase, Oxidative phosphorylation, Pathway, Photosensitivity, Porphobilinogen synthase, Porphyria, Porphyria cutanea tarda, Porphyria variegata, Porphyrin, Porphyrin levels, Porphyrin metabolism, Porphyrinogenic, Porphyrinogenic drugs, Protoporphyria, Protoporphyrin, Protoporphyrinogen, Protoporphyrinogen oxidase, Protoporphyrins, Soret band light, Steroid, Synthase, Tarda, Urine, Uroporphyrin, Uroporphyrinogen, Uroporphyrinogen decarboxylase, Variegate, Variegate porphyria.
Url:
DOI: 10.1111/j.1365-4362.1992.tb02712.x
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<author><name sortKey="Paslin, David A" sort="Paslin, David A" uniqKey="Paslin D" first="David A." last="Paslin">David A. Paslin</name>
<affiliation wicri:level="2"><country>États-Unis</country>
<placeName><region type="state">Californie</region>
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<wicri:cityArea>From the Department of Dermatology, University of California School of Medicine, San Francisco</wicri:cityArea>
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<affiliation wicri:level="2"><country xml:lang="fr">États-Unis</country>
<placeName><region type="state">Californie</region>
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<wicri:cityArea>Correspondence address: Address for correspondence: David A. Paslin, M.D., 460 34th Street, Oakland</wicri:cityArea>
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<series><title level="j" type="main">International Journal of Dermatology</title>
<title level="j" type="alt">INTERNATIONAL JOURNAL OF DERMATOLOGY</title>
<idno type="ISSN">0011-9059</idno>
<idno type="eISSN">1365-4632</idno>
<imprint><biblScope unit="vol">31</biblScope>
<biblScope unit="issue">8</biblScope>
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<biblScope unit="page" to="539">539</biblScope>
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<publisher>Blackwell Publishing Ltd</publisher>
<pubPlace>Oxford, UK</pubPlace>
<date type="published" when="1992-08">1992-08</date>
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<idno type="ISSN">0011-9059</idno>
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<profileDesc><textClass><keywords scheme="Teeft" xml:lang="en"><term>Acta</term>
<term>Acta derm venereol</term>
<term>Acute attacks</term>
<term>Acute porphyria</term>
<term>Amino acids</term>
<term>Arch dermatol</term>
<term>Biochem</term>
<term>Biosynthesis</term>
<term>Cell fragility</term>
<term>Chloroquine</term>
<term>Congenital</term>
<term>Congenital erythropoietic porphyria</term>
<term>Coproporphyria</term>
<term>Coproporphyrin</term>
<term>Coproporphyrinogen</term>
<term>Cutanea</term>
<term>Cutaneous</term>
<term>Cutaneous porphyria</term>
<term>Cutaneous porphyrias</term>
<term>Cytochrome</term>
<term>Cytosol</term>
<term>Decarboxylase</term>
<term>Dermatol</term>
<term>Dermatology</term>
<term>Engl</term>
<term>Enzyme</term>
<term>Enzyme activity</term>
<term>Enzyme deficiencies</term>
<term>Erythropoietic</term>
<term>Erythropoietic porphyrias</term>
<term>Erythropoietic protoporphyria</term>
<term>Excretion</term>
<term>Ferrochelatase</term>
<term>Glin</term>
<term>Gonadal steroids</term>
<term>Heme</term>
<term>Heme biosynthetic pathway</term>
<term>Hepatic</term>
<term>Hepatic porphyrias</term>
<term>Hepatoerythropoietic porphyria</term>
<term>Hereditary coproporphyria</term>
<term>Human genet</term>
<term>International journal</term>
<term>Iron overload</term>
<term>Isomer</term>
<term>Lancet</term>
<term>Liver cells</term>
<term>Liver damage</term>
<term>Liver disease</term>
<term>Microsomal enzymes</term>
<term>Mitochondrial</term>
<term>Mitochondrion</term>
<term>Oxidase</term>
<term>Oxidative phosphorylation</term>
<term>Pathway</term>
<term>Photosensitivity</term>
<term>Porphobilinogen synthase</term>
<term>Porphyria</term>
<term>Porphyria cutanea tarda</term>
<term>Porphyria variegata</term>
<term>Porphyrin</term>
<term>Porphyrin levels</term>
<term>Porphyrin metabolism</term>
<term>Porphyrinogenic</term>
<term>Porphyrinogenic drugs</term>
<term>Protoporphyria</term>
<term>Protoporphyrin</term>
<term>Protoporphyrinogen</term>
<term>Protoporphyrinogen oxidase</term>
<term>Protoporphyrins</term>
<term>Soret band light</term>
<term>Steroid</term>
<term>Synthase</term>
<term>Tarda</term>
<term>Urine</term>
<term>Uroporphyrin</term>
<term>Uroporphyrinogen</term>
<term>Uroporphyrinogen decarboxylase</term>
<term>Variegate</term>
<term>Variegate porphyria</term>
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