Serveur d'exploration Chloroquine

Attention, ce site est en cours de développement !
Attention, site généré par des moyens informatiques à partir de corpus bruts.
Les informations ne sont donc pas validées.

THE PORPHYRIAS

Identifieur interne : 001098 ( Istex/Corpus ); précédent : 001097; suivant : 001099

THE PORPHYRIAS

Auteurs : David A. Paslin

Source :

RBID : ISTEX:7A7385B2C1D99839C39032A6FED1A69554FD09FC

English descriptors


Url:
DOI: 10.1111/j.1365-4362.1992.tb02712.x

Links to Exploration step

ISTEX:7A7385B2C1D99839C39032A6FED1A69554FD09FC

Le document en format XML

<record>
<TEI wicri:istexFullTextTei="biblStruct">
<teiHeader>
<fileDesc>
<titleStmt>
<title xml:lang="en">THE PORPHYRIAS</title>
<author>
<name sortKey="Paslin, David A" sort="Paslin, David A" uniqKey="Paslin D" first="David A." last="Paslin">David A. Paslin</name>
<affiliation>
<mods:affiliation>From the Department of Dermatology, University of California School of Medicine, San Francisco, California.</mods:affiliation>
</affiliation>
<affiliation>
<mods:affiliation>Correspondence address: Address for correspondence: David A. Paslin, M.D., 460 34th Street, Oakland, CA 94609.</mods:affiliation>
</affiliation>
</author>
</titleStmt>
<publicationStmt>
<idno type="wicri:source">ISTEX</idno>
<idno type="RBID">ISTEX:7A7385B2C1D99839C39032A6FED1A69554FD09FC</idno>
<date when="1992" year="1992">1992</date>
<idno type="doi">10.1111/j.1365-4362.1992.tb02712.x</idno>
<idno type="url">https://api.istex.fr/ark:/67375/WNG-K3T5GTGP-Q/fulltext.pdf</idno>
<idno type="wicri:Area/Istex/Corpus">001098</idno>
<idno type="wicri:explorRef" wicri:stream="Istex" wicri:step="Corpus" wicri:corpus="ISTEX">001098</idno>
</publicationStmt>
<sourceDesc>
<biblStruct>
<analytic>
<title level="a" type="main">THE PORPHYRIAS</title>
<author>
<name sortKey="Paslin, David A" sort="Paslin, David A" uniqKey="Paslin D" first="David A." last="Paslin">David A. Paslin</name>
<affiliation>
<mods:affiliation>From the Department of Dermatology, University of California School of Medicine, San Francisco, California.</mods:affiliation>
</affiliation>
<affiliation>
<mods:affiliation>Correspondence address: Address for correspondence: David A. Paslin, M.D., 460 34th Street, Oakland, CA 94609.</mods:affiliation>
</affiliation>
</author>
</analytic>
<monogr></monogr>
<series>
<title level="j" type="main">International Journal of Dermatology</title>
<title level="j" type="alt">INTERNATIONAL JOURNAL OF DERMATOLOGY</title>
<idno type="ISSN">0011-9059</idno>
<idno type="eISSN">1365-4632</idno>
<imprint>
<biblScope unit="vol">31</biblScope>
<biblScope unit="issue">8</biblScope>
<biblScope unit="page" from="527">527</biblScope>
<biblScope unit="page" to="539">539</biblScope>
<biblScope unit="page-count">13</biblScope>
<publisher>Blackwell Publishing Ltd</publisher>
<pubPlace>Oxford, UK</pubPlace>
<date type="published" when="1992-08">1992-08</date>
</imprint>
<idno type="ISSN">0011-9059</idno>
</series>
</biblStruct>
</sourceDesc>
<seriesStmt>
<idno type="ISSN">0011-9059</idno>
</seriesStmt>
</fileDesc>
<profileDesc>
<textClass>
<keywords scheme="Teeft" xml:lang="en">
<term>Acta</term>
<term>Acta derm venereol</term>
<term>Acute attacks</term>
<term>Acute porphyria</term>
<term>Amino acids</term>
<term>Arch dermatol</term>
<term>Biochem</term>
<term>Biosynthesis</term>
<term>Cell fragility</term>
<term>Chloroquine</term>
<term>Congenital</term>
<term>Congenital erythropoietic porphyria</term>
<term>Coproporphyria</term>
<term>Coproporphyrin</term>
<term>Coproporphyrinogen</term>
<term>Cutanea</term>
<term>Cutaneous</term>
<term>Cutaneous porphyria</term>
<term>Cutaneous porphyrias</term>
<term>Cytochrome</term>
<term>Cytosol</term>
<term>Decarboxylase</term>
<term>Dermatol</term>
<term>Dermatology</term>
<term>Engl</term>
<term>Enzyme</term>
<term>Enzyme activity</term>
<term>Enzyme deficiencies</term>
<term>Erythropoietic</term>
<term>Erythropoietic porphyrias</term>
<term>Erythropoietic protoporphyria</term>
<term>Excretion</term>
<term>Ferrochelatase</term>
<term>Glin</term>
<term>Gonadal steroids</term>
<term>Heme</term>
<term>Heme biosynthetic pathway</term>
<term>Hepatic</term>
<term>Hepatic porphyrias</term>
<term>Hepatoerythropoietic porphyria</term>
<term>Hereditary coproporphyria</term>
<term>Human genet</term>
<term>International journal</term>
<term>Iron overload</term>
<term>Isomer</term>
<term>Lancet</term>
<term>Liver cells</term>
<term>Liver damage</term>
<term>Liver disease</term>
<term>Microsomal enzymes</term>
<term>Mitochondrial</term>
<term>Mitochondrion</term>
<term>Oxidase</term>
<term>Oxidative phosphorylation</term>
<term>Pathway</term>
<term>Photosensitivity</term>
<term>Porphobilinogen synthase</term>
<term>Porphyria</term>
<term>Porphyria cutanea tarda</term>
<term>Porphyria variegata</term>
<term>Porphyrin</term>
<term>Porphyrin levels</term>
<term>Porphyrin metabolism</term>
<term>Porphyrinogenic</term>
<term>Porphyrinogenic drugs</term>
<term>Protoporphyria</term>
<term>Protoporphyrin</term>
<term>Protoporphyrinogen</term>
<term>Protoporphyrinogen oxidase</term>
<term>Protoporphyrins</term>
<term>Soret band light</term>
<term>Steroid</term>
<term>Synthase</term>
<term>Tarda</term>
<term>Urine</term>
<term>Uroporphyrin</term>
<term>Uroporphyrinogen</term>
<term>Uroporphyrinogen decarboxylase</term>
<term>Variegate</term>
<term>Variegate porphyria</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
</TEI>
<istex>
<corpusName>wiley</corpusName>
<keywords>
<teeft>
<json:string>porphyria</json:string>
<json:string>porphyrin</json:string>
<json:string>dermatol</json:string>
<json:string>erythropoietic</json:string>
<json:string>uroporphyrinogen</json:string>
<json:string>heme</json:string>
<json:string>synthase</json:string>
<json:string>protoporphyria</json:string>
<json:string>cutanea</json:string>
<json:string>tarda</json:string>
<json:string>protoporphyrin</json:string>
<json:string>pathway</json:string>
<json:string>porphyria cutanea tarda</json:string>
<json:string>porphyrinogenic</json:string>
<json:string>erythropoietic protoporphyria</json:string>
<json:string>hepatic</json:string>
<json:string>coproporphyrin</json:string>
<json:string>coproporphyrinogen</json:string>
<json:string>cutaneous</json:string>
<json:string>arch dermatol</json:string>
<json:string>photosensitivity</json:string>
<json:string>glin</json:string>
<json:string>protoporphyrinogen</json:string>
<json:string>urine</json:string>
<json:string>isomer</json:string>
<json:string>coproporphyria</json:string>
<json:string>oxidase</json:string>
<json:string>engl</json:string>
<json:string>mitochondrion</json:string>
<json:string>cytochrome</json:string>
<json:string>lancet</json:string>
<json:string>variegate</json:string>
<json:string>acta</json:string>
<json:string>uroporphyrin</json:string>
<json:string>decarboxylase</json:string>
<json:string>variegate porphyria</json:string>
<json:string>acute attacks</json:string>
<json:string>chloroquine</json:string>
<json:string>ferrochelatase</json:string>
<json:string>steroid</json:string>
<json:string>biosynthesis</json:string>
<json:string>mitochondrial</json:string>
<json:string>protoporphyrins</json:string>
<json:string>uroporphyrinogen decarboxylase</json:string>
<json:string>dermatology</json:string>
<json:string>hereditary coproporphyria</json:string>
<json:string>biochem</json:string>
<json:string>cytosol</json:string>
<json:string>liver cells</json:string>
<json:string>enzyme activity</json:string>
<json:string>congenital erythropoietic porphyria</json:string>
<json:string>liver disease</json:string>
<json:string>international journal</json:string>
<json:string>excretion</json:string>
<json:string>protoporphyrinogen oxidase</json:string>
<json:string>gonadal steroids</json:string>
<json:string>hepatoerythropoietic porphyria</json:string>
<json:string>porphyria variegata</json:string>
<json:string>hepatic porphyrias</json:string>
<json:string>liver damage</json:string>
<json:string>heme biosynthetic pathway</json:string>
<json:string>congenital</json:string>
<json:string>acute porphyria</json:string>
<json:string>cutaneous porphyrias</json:string>
<json:string>oxidative phosphorylation</json:string>
<json:string>cell fragility</json:string>
<json:string>iron overload</json:string>
<json:string>porphyrinogenic drugs</json:string>
<json:string>porphyrin metabolism</json:string>
<json:string>soret band light</json:string>
<json:string>porphobilinogen synthase</json:string>
<json:string>human genet</json:string>
<json:string>cutaneous porphyria</json:string>
<json:string>acta derm venereol</json:string>
<json:string>porphyrin levels</json:string>
<json:string>microsomal enzymes</json:string>
<json:string>enzyme deficiencies</json:string>
<json:string>amino acids</json:string>
<json:string>erythropoietic porphyrias</json:string>
<json:string>enzyme</json:string>
<json:string>metabolism</json:string>
</teeft>
</keywords>
<author>
<json:item>
<name>DAVID A. PASLIN M.D.</name>
<affiliations>
<json:string>From the Department of Dermatology, University of California School of Medicine, San Francisco, California.</json:string>
<json:string>Correspondence address: Address for correspondence: David A. Paslin, M.D., 460 34th Street, Oakland, CA 94609.</json:string>
</affiliations>
</json:item>
</author>
<articleId>
<json:string>IJD527</json:string>
</articleId>
<arkIstex>ark:/67375/WNG-K3T5GTGP-Q</arkIstex>
<language>
<json:string>eng</json:string>
</language>
<originalGenre>
<json:string>reviewArticle</json:string>
</originalGenre>
<qualityIndicators>
<score>7.012</score>
<pdfWordCount>8986</pdfWordCount>
<pdfCharCount>60272</pdfCharCount>
<pdfVersion>1.6</pdfVersion>
<pdfPageCount>14</pdfPageCount>
<pdfPageSize>543 x 757 pts</pdfPageSize>
<pdfWordsPerPage>642</pdfWordsPerPage>
<pdfText>true</pdfText>
<refBibsNative>true</refBibsNative>
<abstractWordCount>1</abstractWordCount>
<abstractCharCount>0</abstractCharCount>
<keywordCount>0</keywordCount>
</qualityIndicators>
<title>THE PORPHYRIAS</title>
<pmid>
<json:string>1428440</json:string>
</pmid>
<genre>
<json:string>review-article</json:string>
</genre>
<host>
<title>International Journal of Dermatology</title>
<language>
<json:string>unknown</json:string>
</language>
<doi>
<json:string>10.1111/(ISSN)1365-4632</json:string>
</doi>
<issn>
<json:string>0011-9059</json:string>
</issn>
<eissn>
<json:string>1365-4632</json:string>
</eissn>
<publisherId>
<json:string>IJD</json:string>
</publisherId>
<volume>31</volume>
<issue>8</issue>
<pages>
<first>527</first>
<last>539</last>
<total>13</total>
</pages>
<genre>
<json:string>journal</json:string>
</genre>
</host>
<namedEntities>
<unitex>
<date>
<json:string>1974</json:string>
<json:string>1992</json:string>
<json:string>from 1955 through 1959</json:string>
<json:string>1975</json:string>
<json:string>1961</json:string>
<json:string>1908</json:string>
<json:string>1977</json:string>
</date>
<geogName></geogName>
<orgName>
<json:string>University of Washington</json:string>
</orgName>
<orgName_funder></orgName_funder>
<orgName_provider></orgName_provider>
<persName>
<json:string>David A. Paslin</json:string>
<json:string>Occasional</json:string>
<json:string>Spanish</json:string>
<json:string>ALA Synthase</json:string>
<json:string>Africa</json:string>
</persName>
<placeName>
<json:string>Seattle</json:string>
<json:string>CA</json:string>
<json:string>Goldberg</json:string>
</placeName>
<ref_url></ref_url>
<ref_bibl>
<json:string>Tephy et al.</json:string>
<json:string>Donald et al.</json:string>
<json:string>August 1992</json:string>
<json:string>Jaeger et al.</json:string>
</ref_bibl>
<bibl></bibl>
</unitex>
</namedEntities>
<ark>
<json:string>ark:/67375/WNG-K3T5GTGP-Q</json:string>
</ark>
<categories>
<wos>
<json:string>1 - science</json:string>
<json:string>2 - dermatology</json:string>
</wos>
<scienceMetrix>
<json:string>1 - health sciences</json:string>
<json:string>2 - clinical medicine</json:string>
<json:string>3 - dermatology & venereal diseases</json:string>
</scienceMetrix>
<scopus>
<json:string>1 - Health Sciences</json:string>
<json:string>2 - Medicine</json:string>
<json:string>3 - Dermatology</json:string>
</scopus>
</categories>
<publicationDate>1992</publicationDate>
<copyrightDate>1992</copyrightDate>
<doi>
<json:string>10.1111/j.1365-4362.1992.tb02712.x</json:string>
</doi>
<id>7A7385B2C1D99839C39032A6FED1A69554FD09FC</id>
<score>1</score>
<fulltext>
<json:item>
<extension>pdf</extension>
<original>true</original>
<mimetype>application/pdf</mimetype>
<uri>https://api.istex.fr/ark:/67375/WNG-K3T5GTGP-Q/fulltext.pdf</uri>
</json:item>
<json:item>
<extension>zip</extension>
<original>false</original>
<mimetype>application/zip</mimetype>
<uri>https://api.istex.fr/ark:/67375/WNG-K3T5GTGP-Q/bundle.zip</uri>
</json:item>
<istex:fulltextTEI uri="https://api.istex.fr/ark:/67375/WNG-K3T5GTGP-Q/fulltext.tei">
<teiHeader>
<fileDesc>
<titleStmt>
<title level="a" type="main">THE PORPHYRIAS</title>
</titleStmt>
<publicationStmt>
<authority>ISTEX</authority>
<publisher>Blackwell Publishing Ltd</publisher>
<pubPlace>Oxford, UK</pubPlace>
<date type="published" when="1992-08"></date>
</publicationStmt>
<notesStmt>
<note type="content-type" subtype="review-article" source="reviewArticle" scheme="https://content-type.data.istex.fr/ark:/67375/XTP-L5L7X3NF-P">review-article</note>
<note type="publication-type" subtype="journal" scheme="https://publication-type.data.istex.fr/ark:/67375/JMC-0GLKJH51-B">journal</note>
</notesStmt>
<sourceDesc>
<biblStruct type="review-article">
<analytic>
<title level="a" type="main">THE PORPHYRIAS</title>
<author xml:id="author-0000" role="corresp">
<persName>
<forename type="first">DAVID A.</forename>
<surname>PASLIN</surname>
<roleName type="degree">M.D.</roleName>
</persName>
<affiliation>
<orgName type="department">From the Department of Dermatology</orgName>
<orgName type="institution">University of California School of Medicine</orgName>
<address>
<addrLine>San Francisco</addrLine>
<addrLine>California.</addrLine>
<country key="US" xml:lang="en">UNITED STATES</country>
</address>
</affiliation>
</author>
<idno type="istex">7A7385B2C1D99839C39032A6FED1A69554FD09FC</idno>
<idno type="ark">ark:/67375/WNG-K3T5GTGP-Q</idno>
<idno type="DOI">10.1111/j.1365-4362.1992.tb02712.x</idno>
<idno type="unit">IJD527</idno>
<idno type="toTypesetVersion">file:IJD.IJD527.pdf</idno>
</analytic>
<monogr>
<title level="j" type="main">International Journal of Dermatology</title>
<title level="j" type="alt">INTERNATIONAL JOURNAL OF DERMATOLOGY</title>
<idno type="pISSN">0011-9059</idno>
<idno type="eISSN">1365-4632</idno>
<idno type="book-DOI">10.1111/(ISSN)1365-4632</idno>
<idno type="book-part-DOI">10.1111/ijd.1992.31.issue-8</idno>
<idno type="product">IJD</idno>
<idno type="publisherDivision">ST</idno>
<imprint>
<biblScope unit="vol">31</biblScope>
<biblScope unit="issue">8</biblScope>
<biblScope unit="page" from="527">527</biblScope>
<biblScope unit="page" to="539">539</biblScope>
<biblScope unit="page-count">13</biblScope>
<publisher>Blackwell Publishing Ltd</publisher>
<pubPlace>Oxford, UK</pubPlace>
<date type="published" when="1992-08"></date>
</imprint>
</monogr>
</biblStruct>
</sourceDesc>
</fileDesc>
<encodingDesc>
<schemaRef type="ODD" url="https://xml-schema.delivery.istex.fr/tei-istex.odd"></schemaRef>
<appInfo>
<application ident="pub2tei" version="1.0.10" when="2019-12-20">
<label>pub2TEI-ISTEX</label>
<desc>A set of style sheets for converting XML documents encoded in various scientific publisher formats into a common TEI format.
<ref target="http://www.tei-c.org/">We use TEI</ref>
</desc>
</application>
</appInfo>
</encodingDesc>
<revisionDesc>
<change when="2019-12-20" who="#istex" xml:id="pub2tei">formatting</change>
</revisionDesc>
</teiHeader>
</istex:fulltextTEI>
<json:item>
<extension>txt</extension>
<original>false</original>
<mimetype>text/plain</mimetype>
<uri>https://api.istex.fr/ark:/67375/WNG-K3T5GTGP-Q/fulltext.txt</uri>
</json:item>
</fulltext>
<metadata>
<istex:metadataXml wicri:clean="Wiley, elements deleted: body">
<istex:xmlDeclaration>version="1.0" encoding="UTF-8" standalone="yes"</istex:xmlDeclaration>
<istex:document>
<component version="2.0" type="serialArticle" xml:lang="en">
<header>
<publicationMeta level="product">
<publisherInfo>
<publisherName>Blackwell Publishing Ltd</publisherName>
<publisherLoc>Oxford, UK</publisherLoc>
</publisherInfo>
<doi origin="wiley" registered="yes">10.1111/(ISSN)1365-4632</doi>
<issn type="print">0011-9059</issn>
<issn type="electronic">1365-4632</issn>
<idGroup>
<id type="product" value="IJD"></id>
<id type="publisherDivision" value="ST"></id>
</idGroup>
<titleGroup>
<title type="main" sort="INTERNATIONAL JOURNAL OF DERMATOLOGY">International Journal of Dermatology</title>
</titleGroup>
</publicationMeta>
<publicationMeta level="part" position="08008">
<doi origin="wiley">10.1111/ijd.1992.31.issue-8</doi>
<numberingGroup>
<numbering type="journalVolume" number="31">31</numbering>
<numbering type="journalIssue" number="8">8</numbering>
</numberingGroup>
<coverDate startDate="1992-08">August 1992</coverDate>
</publicationMeta>
<publicationMeta level="unit" type="reviewArticle" position="0052700" status="forIssue">
<doi origin="wiley">10.1111/j.1365-4362.1992.tb02712.x</doi>
<idGroup>
<id type="unit" value="IJD527"></id>
</idGroup>
<countGroup>
<count type="pageTotal" number="13"></count>
</countGroup>
<titleGroup>
<title type="tocHeading1">Review</title>
</titleGroup>
<eventGroup>
<event type="firstOnline" date="2007-05-31"></event>
<event type="publishedOnlineFinalForm" date="2007-05-31"></event>
<event type="xmlConverted" agent="Converter:BPG_TO_WML3G version:2.3.5 mode:FullText source:HeaderRef result:HeaderRef" date="2010-04-07"></event>
<event type="xmlConverted" agent="Converter:WILEY_ML3G_TO_WILEY_ML3GV2 version:4.0.1" date="2014-03-13"></event>
<event type="xmlConverted" agent="Converter:WML3G_To_WML3G version:4.1.7 mode:FullText,remove_FC" date="2014-10-24"></event>
</eventGroup>
<numberingGroup>
<numbering type="pageFirst" number="527">527</numbering>
<numbering type="pageLast" number="539">539</numbering>
</numberingGroup>
<correspondenceTo>Address for correspondence: David A. Paslin, M.D., 460 34th Street, Oakland, CA 94609.</correspondenceTo>
<linkGroup>
<link type="toTypesetVersion" href="file:IJD.IJD527.pdf"></link>
</linkGroup>
</publicationMeta>
<contentMeta>
<countGroup>
<count type="referenceTotal" number="161"></count>
<count type="linksCrossRef" number="2"></count>
</countGroup>
<titleGroup>
<title type="main">THE PORPHYRIAS</title>
</titleGroup>
<creators>
<creator creatorRole="author" xml:id="cr1" affiliationRef="#a1" corresponding="yes">
<personName>
<givenNames>DAVID A.</givenNames>
<familyName>PASLIN</familyName>
<degrees>M.D.</degrees>
</personName>
</creator>
</creators>
<affiliationGroup>
<affiliation xml:id="a1" countryCode="US">
<unparsedAffiliation>From the Department of Dermatology, University of California School of Medicine, San Francisco, California.</unparsedAffiliation>
</affiliation>
</affiliationGroup>
</contentMeta>
</header>
</component>
</istex:document>
</istex:metadataXml>
<mods version="3.6">
<titleInfo lang="en">
<title>THE PORPHYRIAS</title>
</titleInfo>
<titleInfo type="alternative" contentType="CDATA" lang="en">
<title>THE PORPHYRIAS</title>
</titleInfo>
<name type="personal">
<namePart type="given">DAVID A.</namePart>
<namePart type="family">PASLIN</namePart>
<namePart type="termsOfAddress">M.D.</namePart>
<affiliation>From the Department of Dermatology, University of California School of Medicine, San Francisco, California.</affiliation>
<affiliation>Correspondence address: Address for correspondence: David A. Paslin, M.D., 460 34th Street, Oakland, CA 94609.</affiliation>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<typeOfResource>text</typeOfResource>
<genre type="review-article" displayLabel="reviewArticle" authority="ISTEX" authorityURI="https://content-type.data.istex.fr" valueURI="https://content-type.data.istex.fr/ark:/67375/XTP-L5L7X3NF-P">review-article</genre>
<originInfo>
<publisher>Blackwell Publishing Ltd</publisher>
<place>
<placeTerm type="text">Oxford, UK</placeTerm>
</place>
<dateIssued encoding="w3cdtf">1992-08</dateIssued>
<copyrightDate encoding="w3cdtf">1992</copyrightDate>
</originInfo>
<language>
<languageTerm type="code" authority="rfc3066">en</languageTerm>
<languageTerm type="code" authority="iso639-2b">eng</languageTerm>
</language>
<physicalDescription>
<extent unit="references">161</extent>
<extent unit="linksCrossRef">2</extent>
</physicalDescription>
<relatedItem type="host">
<titleInfo>
<title>International Journal of Dermatology</title>
</titleInfo>
<genre type="journal" authority="ISTEX" authorityURI="https://publication-type.data.istex.fr" valueURI="https://publication-type.data.istex.fr/ark:/67375/JMC-0GLKJH51-B">journal</genre>
<identifier type="ISSN">0011-9059</identifier>
<identifier type="eISSN">1365-4632</identifier>
<identifier type="DOI">10.1111/(ISSN)1365-4632</identifier>
<identifier type="PublisherID">IJD</identifier>
<part>
<date>1992</date>
<detail type="volume">
<caption>vol.</caption>
<number>31</number>
</detail>
<detail type="issue">
<caption>no.</caption>
<number>8</number>
</detail>
<extent unit="pages">
<start>527</start>
<end>539</end>
<total>13</total>
</extent>
</part>
</relatedItem>
<relatedItem type="references" displayLabel="cit1">
<titleInfo>
<title>Biosynthesis of the pigments of life: formation of the macrocycle</title>
</titleInfo>
<name type="personal">
<namePart type="given">AR</namePart>
<namePart type="family">Battersby</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">CJR</namePart>
<namePart type="family">Fookes</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">GWJ</namePart>
<namePart type="family">Matcham</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Battersby AR, Fookes CJR, Matcham GWJ, et al. Biosynthesis of the pigments of life: formation of the macrocycle. Nature 1980; 285:17–21.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>285</number>
</detail>
<extent unit="pages">
<start>17</start>
<end>21</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Nature</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>285</number>
</detail>
<extent unit="pages">
<start>17</start>
<end>21</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit2">
<titleInfo>
<title>Prebiotic porphyrin genesis: porphyrins from electrical discharge in methane, ammonia and water vapor</title>
</titleInfo>
<name type="personal">
<namePart type="given">GW</namePart>
<namePart type="family">Hodgson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">C.</namePart>
<namePart type="family">Ponnamperuma</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Hodgson GW, Ponnamperuma C. Prebiotic porphyrin genesis: porphyrins from electrical discharge in methane, ammonia and water vapor. Proc Natl Acad Sci 1968; 59:22–28.</note>
<part>
<date>1968</date>
<detail type="volume">
<caption>vol.</caption>
<number>59</number>
</detail>
<extent unit="pages">
<start>22</start>
<end>28</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Proc Natl Acad Sci</title>
</titleInfo>
<part>
<date>1968</date>
<detail type="volume">
<caption>vol.</caption>
<number>59</number>
</detail>
<extent unit="pages">
<start>22</start>
<end>28</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit3">
<titleInfo>
<title>Porphyrin metabolism and the porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">DP</namePart>
<namePart type="family">Tschudy</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JM</namePart>
<namePart type="family">Lamon</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>book-chapter</genre>
<relatedItem type="host">
<titleInfo>
<title>Duncan's diseases of metabolism</title>
</titleInfo>
<originInfo>
<publisher>WB Saunders</publisher>
</originInfo>
<part>
<date>1980</date>
<extent unit="pages">
<start>939</start>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit4">
<titleInfo>
<title>Distribution, structure and properties of the tetrapyrroles</title>
</titleInfo>
<name type="personal">
<namePart type="given">S</namePart>
<namePart type="family">Granick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">H.</namePart>
<namePart type="family">Gilder</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Granick S, Gilder H. Distribution, structure and properties of the tetrapyrroles. Adv Enzymol 1947; 7: 305–368.</note>
<part>
<date>1947</date>
<detail type="volume">
<caption>vol.</caption>
<number>7</number>
</detail>
<extent unit="pages">
<start>305</start>
<end>368</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Adv Enzymol</title>
</titleInfo>
<part>
<date>1947</date>
<detail type="volume">
<caption>vol.</caption>
<number>7</number>
</detail>
<extent unit="pages">
<start>305</start>
<end>368</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit5">
<titleInfo>
<title>Biochemical and clinical aspects of the porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">RD</namePart>
<namePart type="family">Levere</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A.</namePart>
<namePart type="family">Kappas</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Levere RD, Kappas A. Biochemical and clinical aspects of the porphyrias. Adv Clin Chem 1968; 11:133–177.</note>
<part>
<date>1968</date>
<detail type="volume">
<caption>vol.</caption>
<number>11</number>
</detail>
<extent unit="pages">
<start>133</start>
<end>177</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Adv Clin Chem</title>
</titleInfo>
<part>
<date>1968</date>
<detail type="volume">
<caption>vol.</caption>
<number>11</number>
</detail>
<extent unit="pages">
<start>133</start>
<end>177</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit6">
<titleInfo>
<title>Mg‐protoporphyrin‐IX and delta‐aminolevulinic acid synthesis from glutamate in isolated greening chloroplasts</title>
</titleInfo>
<name type="personal">
<namePart type="given">PA</namePart>
<namePart type="family">Castelfranco</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">S.</namePart>
<namePart type="family">Schwarcz</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Castelfranco PA, Schwarcz S. Mg‐protoporphyrin‐IX and delta‐aminolevulinic acid synthesis from glutamate in isolated greening chloroplasts. Arch Biochem Biophys 1978; 186:365–375.</note>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>186</number>
</detail>
<extent unit="pages">
<start>365</start>
<end>375</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Biochem Biophys</title>
</titleInfo>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>186</number>
</detail>
<extent unit="pages">
<start>365</start>
<end>375</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit7">
<titleInfo>
<title>Porphyrin biosynthesis in erythrocytes III Uroporphyrinogen and its decarboxylase</title>
</titleInfo>
<name type="personal">
<namePart type="given">D</namePart>
<namePart type="family">Mauzerall</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">S.</namePart>
<namePart type="family">Granick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Mauzerall D, Granick S. Porphyrin biosynthesis in erythrocytes III Uroporphyrinogen and its decarboxylase. J Biol Chem 1958; 232:1141–1162.</note>
<part>
<date>1958</date>
<detail type="volume">
<caption>vol.</caption>
<number>232</number>
</detail>
<extent unit="pages">
<start>1141</start>
<end>1162</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>J Biol Chem</title>
</titleInfo>
<part>
<date>1958</date>
<detail type="volume">
<caption>vol.</caption>
<number>232</number>
</detail>
<extent unit="pages">
<start>1141</start>
<end>1162</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit8">
<titleInfo>
<title>Uroporphyrinogen decarboxylase from mouse spleen</title>
</titleInfo>
<name type="personal">
<namePart type="given">G</namePart>
<namePart type="family">Romeo</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">EY</namePart>
<namePart type="family">Levin</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Romeo G, Levin EY. Uroporphyrinogen decarboxylase from mouse spleen. Biochim Biophys Acta 1971; 230: 330–341.</note>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>230</number>
</detail>
<extent unit="pages">
<start>330</start>
<end>341</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Biochim Biophys Acta</title>
</titleInfo>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>230</number>
</detail>
<extent unit="pages">
<start>330</start>
<end>341</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit9">
<titleInfo>
<title>Macroycyclic intermediates in the biosynthesis of porphyrins</title>
</titleInfo>
<name type="personal">
<namePart type="given">AJ</namePart>
<namePart type="family">Jackson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">HA</namePart>
<namePart type="family">Sancovich</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">AM</namePart>
<namePart type="family">Ferramola</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Jackson AJ, Sancovich HA, Ferramola AM, et al. Macroycyclic intermediates in the biosynthesis of porphyrins. Philos Trans R Soc B 1976; 273:191–206.</note>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>273</number>
</detail>
<extent unit="pages">
<start>191</start>
<end>206</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Philos Trans R Soc B</title>
</titleInfo>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>273</number>
</detail>
<extent unit="pages">
<start>191</start>
<end>206</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit10">
<titleInfo>
<title>Enzyme deficiencies in the porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">S</namePart>
<namePart type="family">Kramer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">DM</namePart>
<namePart type="family">Becker</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JD</namePart>
<namePart type="family">Viljoen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Kramer S, Becker DM, Viljoen JD. Enzyme deficiencies in the porphyrias. Br J Haem 1977; 37:439–445.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>37</number>
</detail>
<extent unit="pages">
<start>439</start>
<end>445</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Haem</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>37</number>
</detail>
<extent unit="pages">
<start>439</start>
<end>445</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit11">
<titleInfo>
<title>Mitochondrial coproporphyrinogen oxidase and protoporphyrin formation</title>
</titleInfo>
<name type="personal">
<namePart type="given">S</namePart>
<namePart type="family">Sano</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">S.</namePart>
<namePart type="family">Granick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Sano S, Granick S. Mitochondrial coproporphyrinogen oxidase and protoporphyrin formation. J Biol Chem 1961; 236:1173–1180.</note>
<part>
<date>1961</date>
<detail type="volume">
<caption>vol.</caption>
<number>236</number>
</detail>
<extent unit="pages">
<start>1173</start>
<end>1180</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>J Biol Chem</title>
</titleInfo>
<part>
<date>1961</date>
<detail type="volume">
<caption>vol.</caption>
<number>236</number>
</detail>
<extent unit="pages">
<start>1173</start>
<end>1180</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit12">
<titleInfo>
<title>The enzymatic conversion of coproporphyrinogen III into protoporphyrin IX</title>
</titleInfo>
<name type="personal">
<namePart type="given">RJ</namePart>
<namePart type="family">Porra</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JE</namePart>
<namePart type="family">Falk</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Porra RJ, Falk JE. The enzymatic conversion of coproporphyrinogen III into protoporphyrin IX. Biochem J 1964; 90:69–75.</note>
<part>
<date>1964</date>
<detail type="volume">
<caption>vol.</caption>
<number>90</number>
</detail>
<extent unit="pages">
<start>69</start>
<end>75</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Biochem J</title>
</titleInfo>
<part>
<date>1964</date>
<detail type="volume">
<caption>vol.</caption>
<number>90</number>
</detail>
<extent unit="pages">
<start>69</start>
<end>75</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit13">
<titleInfo>
<title>Conversion of coproporphyrinogen III to protoporphyrin IX</title>
</titleInfo>
<name type="personal">
<namePart type="given">AH</namePart>
<namePart type="family">Jackson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">DE</namePart>
<namePart type="family">Gomes</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">P</namePart>
<namePart type="family">Couch</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Jackson AH, Gomes DE, Couch P, et al. Conversion of coproporphyrinogen III to protoporphyrin IX. Enzyme 1974; 17:81–87.</note>
<part>
<date>1974</date>
<detail type="volume">
<caption>vol.</caption>
<number>17</number>
</detail>
<extent unit="pages">
<start>81</start>
<end>87</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Enzyme</title>
</titleInfo>
<part>
<date>1974</date>
<detail type="volume">
<caption>vol.</caption>
<number>17</number>
</detail>
<extent unit="pages">
<start>81</start>
<end>87</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit14">
<titleInfo>
<title>Studies on ferrochelatase. 1. Assay and properties of ferrochelatase from a pig liver mitochondrial extract</title>
</titleInfo>
<name type="personal">
<namePart type="given">RJ</namePart>
<namePart type="family">Porra</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">OTG.</namePart>
<namePart type="family">Jones</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Porra RJ, Jones OTG. Studies on ferrochelatase. 1. Assay and properties of ferrochelatase from a pig liver mitochondrial extract. Biochem J 1963; 87:181–185.</note>
<part>
<date>1963</date>
<detail type="volume">
<caption>vol.</caption>
<number>87</number>
</detail>
<extent unit="pages">
<start>181</start>
<end>185</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Biochem J</title>
</titleInfo>
<part>
<date>1963</date>
<detail type="volume">
<caption>vol.</caption>
<number>87</number>
</detail>
<extent unit="pages">
<start>181</start>
<end>185</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit15">
<titleInfo>
<title>Analytical review. Enzymatic defects of hereditary porphyrias: an explanation of dominance at the molecular level</title>
</titleInfo>
<name type="personal">
<namePart type="given">G.</namePart>
<namePart type="family">Romeo</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Romeo G. Analytical review. Enzymatic defects of hereditary porphyrias: an explanation of dominance at the molecular level. Human Genet 1977; 39:261–276.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>39</number>
</detail>
<extent unit="pages">
<start>261</start>
<end>276</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Human Genet</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>39</number>
</detail>
<extent unit="pages">
<start>261</start>
<end>276</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit16">
<titleInfo>
<title>Urinary excretion of D‐glutaric acid, total glucuronic acid and total porphyrins in porphyria cutanea tarda</title>
</titleInfo>
<name type="personal">
<namePart type="given">G</namePart>
<namePart type="family">Budillon</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">F</namePart>
<namePart type="family">Ayala</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Carrella</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Budillon G, Ayala F, Carrella M, et al. Urinary excretion of D‐glutaric acid, total glucuronic acid and total porphyrins in porphyria cutanea tarda. Acta Hepato-Gastro 1978; 25:267–270.</note>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>25</number>
</detail>
<extent unit="pages">
<start>267</start>
<end>270</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Acta Hepato-Gastro</title>
</titleInfo>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>25</number>
</detail>
<extent unit="pages">
<start>267</start>
<end>270</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit17">
<titleInfo>
<title>Acute intermittent porphyria: clinical and selected research aspects</title>
</titleInfo>
<name type="personal">
<namePart type="given">DP</namePart>
<namePart type="family">Tschudy</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Valsanis</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">CR</namePart>
<namePart type="family">Magnussen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Tschudy DP, Valsanis M, Magnussen CR. Acute intermittent porphyria: clinical and selected research aspects. Ann Intern Med 1975; 83:851–864.</note>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>83</number>
</detail>
<extent unit="pages">
<start>851</start>
<end>864</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Ann Intern Med</title>
</titleInfo>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>83</number>
</detail>
<extent unit="pages">
<start>851</start>
<end>864</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit18">
<titleInfo>
<title>Acute intermittent porphyria: a clinical and biochemical study of 46 patients</title>
</titleInfo>
<name type="personal">
<namePart type="given">JA</namePart>
<namePart type="family">Stein</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">DP</namePart>
<namePart type="family">Tschudy</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Stein JA, Tschudy DP. Acute intermittent porphyria: a clinical and biochemical study of 46 patients. Medicine 1970; 49:1–16.</note>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>49</number>
</detail>
<extent unit="pages">
<start>1</start>
<end>16</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Medicine</title>
</titleInfo>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>49</number>
</detail>
<extent unit="pages">
<start>1</start>
<end>16</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit19">
<titleInfo>
<title>Contraindications of biological oxidation inhibitors in the treatment of porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">ML</namePart>
<namePart type="family">Cowger</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">RF</namePart>
<namePart type="family">Labbe</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Cowger ML, Labbe RF. Contraindications of biological oxidation inhibitors in the treatment of porphyria. Lancet 1965; i:88–89.</note>
<part>
<date>1965</date>
<detail type="volume">
<caption>vol.</caption>
<number>i</number>
</detail>
<extent unit="pages">
<start>88</start>
<end>89</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Lancet</title>
</titleInfo>
<part>
<date>1965</date>
<detail type="volume">
<caption>vol.</caption>
<number>i</number>
</detail>
<extent unit="pages">
<start>88</start>
<end>89</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit20">
<titleInfo>
<title>Acute porphyria: the precipitating and aggravating factors</title>
</titleInfo>
<name type="personal">
<namePart type="given">L.</namePart>
<namePart type="family">Eales</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Eales L. Acute porphyria: the precipitating and aggravating factors. S Afr J Lab Clin Med 1971; 17:120–125.</note>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>17</number>
</detail>
<extent unit="pages">
<start>120</start>
<end>125</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>S Afr J Lab Clin Med</title>
</titleInfo>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>17</number>
</detail>
<extent unit="pages">
<start>120</start>
<end>125</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit21">
<titleInfo>
<title>Precipitation of acute intermittent porphyria by griseofulvin therapy</title>
</titleInfo>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Berman</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">RL</namePart>
<namePart type="family">Franklin</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Berman A, Franklin RL. Precipitation of acute intermittent porphyria by griseofulvin therapy. JAMA 1965; 102:1005–1007.</note>
<part>
<date>1965</date>
<detail type="volume">
<caption>vol.</caption>
<number>102</number>
</detail>
<extent unit="pages">
<start>1005</start>
<end>1007</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>JAMA</title>
</titleInfo>
<part>
<date>1965</date>
<detail type="volume">
<caption>vol.</caption>
<number>102</number>
</detail>
<extent unit="pages">
<start>1005</start>
<end>1007</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit22">
<titleInfo>
<title>Estrogen‐induced porphyria cutanea tarda</title>
</titleInfo>
<name type="personal">
<namePart type="given">JJ</namePart>
<namePart type="family">Roenigk Jr</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">ME</namePart>
<namePart type="family">Gottlob</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Roenigk JJ Jr, Gottlob ME. Estrogen‐induced porphyria cutanea tarda. Arch Dermatol 1970; 102:260–266.</note>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>102</number>
</detail>
<extent unit="pages">
<start>260</start>
<end>266</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>102</number>
</detail>
<extent unit="pages">
<start>260</start>
<end>266</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit23">
<titleInfo>
<title>Goldberg A, Rimington C. Diseases of porphyrin metabolism. Springfield , IL : Charles C. Thomas1962: 115.</title>
</titleInfo>
<note type="citation/reference">Goldberg A, Rimington C. Diseases of porphyrin metabolism. Springfield , IL : Charles C. Thomas 1962: 115.</note>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Goldberg</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">C.</namePart>
<namePart type="family">Rimington</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>book</genre>
<originInfo>
<publisher>Charles C. Thomas</publisher>
</originInfo>
<part>
<date>1962</date>
<extent unit="pages">
<start>115</start>
</extent>
</part>
</relatedItem>
<relatedItem type="references" displayLabel="cit24">
<titleInfo>
<title>Gynecomastia</title>
</titleInfo>
<name type="personal">
<namePart type="given">HE</namePart>
<namePart type="family">Carlsen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Carlsen HE. Gynecomastia. N Engl J Med 1980; 303: 795–799.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>303</number>
</detail>
<extent unit="pages">
<start>795</start>
<end>799</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>303</number>
</detail>
<extent unit="pages">
<start>795</start>
<end>799</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit25">
<titleInfo>
<title>Effect of diet on the induction of experimental porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">JA</namePart>
<namePart type="family">Rose</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">ES</namePart>
<namePart type="family">Hellman</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">DP</namePart>
<namePart type="family">Tschudy</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Rose JA, Hellman ES, Tschudy DP. Effect of diet on the induction of experimental porphyria. Metabolism 1961; 10:514–521.</note>
<part>
<date>1961</date>
<detail type="volume">
<caption>vol.</caption>
<number>10</number>
</detail>
<extent unit="pages">
<start>514</start>
<end>521</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Metabolism</title>
</titleInfo>
<part>
<date>1961</date>
<detail type="volume">
<caption>vol.</caption>
<number>10</number>
</detail>
<extent unit="pages">
<start>514</start>
<end>521</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit26">
<titleInfo>
<title>The effect of carbohydrate feeding on the induction of delta‐aminolevulinic acid synthetase</title>
</titleInfo>
<name type="personal">
<namePart type="given">DP</namePart>
<namePart type="family">Tschudy</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">FH</namePart>
<namePart type="family">Welland</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Collins</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Tschudy DP, Welland FH, Collins A, et al. The effect of carbohydrate feeding on the induction of delta‐aminolevulinic acid synthetase. Metabolism 1964; 13:396–406.</note>
<part>
<date>1964</date>
<detail type="volume">
<caption>vol.</caption>
<number>13</number>
</detail>
<extent unit="pages">
<start>396</start>
<end>406</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Metabolism</title>
</titleInfo>
<part>
<date>1964</date>
<detail type="volume">
<caption>vol.</caption>
<number>13</number>
</detail>
<extent unit="pages">
<start>396</start>
<end>406</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit27">
<titleInfo>
<title>Hormonal effects on the regulation of hepatic heme biosynthesis</title>
</titleInfo>
<name type="personal">
<namePart type="given">GS</namePart>
<namePart type="family">Marks</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JK</namePart>
<namePart type="family">Stephens</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">PWF</namePart>
<namePart type="family">Fischer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Marks GS, Stephens JK, Fischer PWF, et al. Hormonal effects on the regulation of hepatic heme biosynthesis. Molec Cell Biochem 1979; 25:111–123.</note>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>25</number>
</detail>
<extent unit="pages">
<start>111</start>
<end>123</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Molec Cell Biochem</title>
</titleInfo>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>25</number>
</detail>
<extent unit="pages">
<start>111</start>
<end>123</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit28">
<titleInfo>
<title>Glucose administration and heme catabolism after caloric restriction</title>
</titleInfo>
<name type="personal">
<namePart type="given">B</namePart>
<namePart type="family">Lundh</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">L.</namePart>
<namePart type="family">Ugander</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Lundh B, Ugander L. Glucose administration and heme catabolism after caloric restriction. Gastroenterol 1976; 71:1061–1063.</note>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>71</number>
</detail>
<extent unit="pages">
<start>1061</start>
<end>1063</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Gastroenterol</title>
</titleInfo>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>71</number>
</detail>
<extent unit="pages">
<start>1061</start>
<end>1063</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit29">
<titleInfo>
<title>Prenatal exclusion of congenital erythropoietic porphyria (Gunther's Disease) in a fetus at risk</title>
</titleInfo>
<name type="personal">
<namePart type="given">JCH</namePart>
<namePart type="family">Deybach</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">B</namePart>
<namePart type="family">Grandchamp</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Grelier</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Deybach JCH, Grandchamp B, Grelier M, et al. Prenatal exclusion of congenital erythropoietic porphyria (Gunther's Disease) in a fetus at risk. Human Genet 1980; 53:217–221.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>53</number>
</detail>
<extent unit="pages">
<start>217</start>
<end>221</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Human Genet</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>53</number>
</detail>
<extent unit="pages">
<start>217</start>
<end>221</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit30">
<titleInfo>
<title>The porphyrias. A genetic problem</title>
</titleInfo>
<name type="personal">
<namePart type="given">J</namePart>
<namePart type="family">Waldenstrom</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">B.</namePart>
<namePart type="family">Haeger‐Aronsen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Waldenstrom J, Haeger‐Aronsen B. The porphyrias. A genetic problem. Prog Med Genet 1967; 5:58–101.</note>
<part>
<date>1967</date>
<detail type="volume">
<caption>vol.</caption>
<number>5</number>
</detail>
<extent unit="pages">
<start>58</start>
<end>101</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Prog Med Genet</title>
</titleInfo>
<part>
<date>1967</date>
<detail type="volume">
<caption>vol.</caption>
<number>5</number>
</detail>
<extent unit="pages">
<start>58</start>
<end>101</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit31">
<titleInfo>
<title>Porphyria cutanea tarda in three generations of a single family</title>
</titleInfo>
<name type="personal">
<namePart type="given">AV</namePart>
<namePart type="family">Benedetto</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JP</namePart>
<namePart type="family">Kushner</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JS</namePart>
<namePart type="family">Taylor</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Benedetto AV, Kushner JP, Taylor JS. Porphyria cutanea tarda in three generations of a single family. N Engl J Med 1978; 298:358–362.</note>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>298</number>
</detail>
<extent unit="pages">
<start>358</start>
<end>362</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>298</number>
</detail>
<extent unit="pages">
<start>358</start>
<end>362</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit32">
<titleInfo>
<title>Laboratory diagnosis of the porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">JP</namePart>
<namePart type="family">Kushner</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Kushner JP. Laboratory diagnosis of the porphyrias. N Engl J Med 1991; 324:1432–1434.</note>
<part>
<date>1991</date>
<detail type="volume">
<caption>vol.</caption>
<number>324</number>
</detail>
<extent unit="pages">
<start>1432</start>
<end>1434</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1991</date>
<detail type="volume">
<caption>vol.</caption>
<number>324</number>
</detail>
<extent unit="pages">
<start>1432</start>
<end>1434</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit33">
<titleInfo>
<title>Hereditary coproporphyria. Demonstration of the abnormalities in haem biosynthesis in peripheral blood</title>
</titleInfo>
<name type="personal">
<namePart type="given">JJ</namePart>
<namePart type="family">Brodie</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">GG</namePart>
<namePart type="family">Thompson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MR</namePart>
<namePart type="family">Moore</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Brodie JJ, Thompson GG, Moore MR, et al. Hereditary coproporphyria. Demonstration of the abnormalities in haem biosynthesis in peripheral blood. Q J Med 1976; 46:229–241.</note>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>46</number>
</detail>
<extent unit="pages">
<start>229</start>
<end>241</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Q J Med</title>
</titleInfo>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>46</number>
</detail>
<extent unit="pages">
<start>229</start>
<end>241</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit34">
<titleInfo>
<title>The primary enzyme defect in hereditary coproporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">GH</namePart>
<namePart type="family">Elder</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JO</namePart>
<namePart type="family">Evans</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">N</namePart>
<namePart type="family">Thomas</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Elder GH, Evans JO, Thomas N, et al. The primary enzyme defect in hereditary coproporphyria. Lancet 1976; 9:145–151.</note>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>145</start>
<end>151</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Lancet</title>
</titleInfo>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>145</start>
<end>151</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit35">
<titleInfo>
<title>The prevalence of the porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">G.</namePart>
<namePart type="family">Dean</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Dean G. The prevalence of the porphyrias. S Afr J Lab Clin Med 1963; 9: 145–151.</note>
<part>
<date>1963</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>145</start>
<end>151</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>S Afr J Lab Clin Med</title>
</titleInfo>
<part>
<date>1963</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>145</start>
<end>151</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit36">
<titleInfo>
<title>Enzyme abnormalities in the porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">MJ</namePart>
<namePart type="family">Brodie</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MR</namePart>
<namePart type="family">Moore</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A.</namePart>
<namePart type="family">Goldberg</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Brodie MJ, Moore MR, Goldberg A. Enzyme abnormalities in the porphyrias. Lancet 1977; ii:699–701.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>ii</number>
</detail>
<extent unit="pages">
<start>699</start>
<end>701</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Lancet</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>ii</number>
</detail>
<extent unit="pages">
<start>699</start>
<end>701</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit37">
<titleInfo>
<title>Inheritance in protoporphyria: comparison of haem synthetase activity in skin hbroblasts with clinical features</title>
</titleInfo>
<name type="personal">
<namePart type="given">JR</namePart>
<namePart type="family">Bloomer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">HL</namePart>
<namePart type="family">Bonkowsky</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">PS</namePart>
<namePart type="family">Ebert</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Bloomer JR, Bonkowsky HL, Ebert PS, et al. Inheritance in protoporphyria: comparison of haem synthetase activity in skin hbroblasts with clinical features. Lancet 1976; ii:226–228.</note>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>ii</number>
</detail>
<extent unit="pages">
<start>226</start>
<end>228</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Lancet</title>
</titleInfo>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>ii</number>
</detail>
<extent unit="pages">
<start>226</start>
<end>228</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit38">
<titleInfo>
<title>Diminished erythroid ferrochelatase activity in protoporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">SS</namePart>
<namePart type="family">Bottomly</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Tanake</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MA</namePart>
<namePart type="family">Everett</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Bottomly SS, Tanake M, Everett MA. Diminished erythroid ferrochelatase activity in protoporphyria. J Lab ClinMed 1975; 86:126–131.</note>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>86</number>
</detail>
<extent unit="pages">
<start>126</start>
<end>131</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>J Lab ClinMed</title>
</titleInfo>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>86</number>
</detail>
<extent unit="pages">
<start>126</start>
<end>131</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit39">
<titleInfo>
<title>Reduced ferrochelatase activity: a defect common to porphyria variegata and protoporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">DM</namePart>
<namePart type="family">Becker</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JD</namePart>
<namePart type="family">Viljoen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">J</namePart>
<namePart type="family">Katz</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Becker DM, Viljoen JD, Katz J, et al. Reduced ferrochelatase activity: a defect common to porphyria variegata and protoporphyria. Br J Haematol 1977; 36: 171–179.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>36</number>
</detail>
<extent unit="pages">
<start>171</start>
<end>179</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Haematol</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>36</number>
</detail>
<extent unit="pages">
<start>171</start>
<end>179</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit40">
<titleInfo>
<title>Inherited deficiency of delta‐aminolevulinic acid dehydratase</title>
</titleInfo>
<name type="personal">
<namePart type="given">TD</namePart>
<namePart type="family">Bird</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">P</namePart>
<namePart type="family">Hamernyik</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JY</namePart>
<namePart type="family">Nutter</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Bird TD, Hamernyik P, Nutter JY, et al. Inherited deficiency of delta‐aminolevulinic acid dehydratase. Am J Human Genet 1979; 31:662–668.</note>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>31</number>
</detail>
<extent unit="pages">
<start>662</start>
<end>668</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Am J Human Genet</title>
</titleInfo>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>31</number>
</detail>
<extent unit="pages">
<start>662</start>
<end>668</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit41">
<titleInfo>
<title>Biochemical lesions in porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">DP</namePart>
<namePart type="family">Tschudy</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Tschudy DP. Biochemical lesions in porphyria. JAMA 1965; 191:718–730.</note>
<part>
<date>1965</date>
<detail type="volume">
<caption>vol.</caption>
<number>191</number>
</detail>
<extent unit="pages">
<start>718</start>
<end>730</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>JAMA</title>
</titleInfo>
<part>
<date>1965</date>
<detail type="volume">
<caption>vol.</caption>
<number>191</number>
</detail>
<extent unit="pages">
<start>718</start>
<end>730</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit42">
<titleInfo>
<title>Uroporphyrinogen III cosyn‐thetase in human congenital erythropoietic porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">G</namePart>
<namePart type="family">Romeo</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">EY</namePart>
<namePart type="family">Levin</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Romeo G, Levin EY. Uroporphyrinogen III cosyn‐thetase in human congenital erythropoietic porphyria. Proc Natl Acad Sci 1969; 63:856–863.</note>
<part>
<date>1969</date>
<detail type="volume">
<caption>vol.</caption>
<number>63</number>
</detail>
<extent unit="pages">
<start>856</start>
<end>863</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Proc Natl Acad Sci</title>
</titleInfo>
<part>
<date>1969</date>
<detail type="volume">
<caption>vol.</caption>
<number>63</number>
</detail>
<extent unit="pages">
<start>856</start>
<end>863</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit43">
<titleInfo>
<title>The activities of Uroporphyrinogen synthetase and cosynthetase in congenital erythropoiectic porphyria (CEP)</title>
</titleInfo>
<name type="personal">
<namePart type="given">K</namePart>
<namePart type="family">Miyagi</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">ZJ</namePart>
<namePart type="family">Petryka</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">I</namePart>
<namePart type="family">Bossenmaier</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Miyagi K, Petryka ZJ, Bossenmaier I, et al. The activities of Uroporphyrinogen synthetase and cosynthetase in congenital erythropoiectic porphyria (CEP). Am J Hematol 1976; 1:3–21.</note>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>1</number>
</detail>
<extent unit="pages">
<start>3</start>
<end>21</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Am J Hematol</title>
</titleInfo>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>1</number>
</detail>
<extent unit="pages">
<start>3</start>
<end>21</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit44">
<titleInfo>
<title>Patterns of porphyrin excretion and their interpretation</title>
</titleInfo>
<name type="personal">
<namePart type="given">C.</namePart>
<namePart type="family">Rimington</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Rimington C. Patterns of porphyrin excretion and their interpretation. S Afr J Lab Clin Med 1963; 9:255–261.</note>
<part>
<date>1963</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>255</start>
<end>261</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>S Afr J Lab Clin Med</title>
</titleInfo>
<part>
<date>1963</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>255</start>
<end>261</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit45">
<titleInfo>
<title>Urinary porphyrin excretion pattern and isomer distribution of I and III in human porphyrin disorders</title>
</titleInfo>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Doss</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">E.</namePart>
<namePart type="family">Schermuly</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>book-chapter</genre>
<relatedItem type="host">
<titleInfo>
<title>Porphyrins in human diseases</title>
</titleInfo>
<originInfo>
<publisher>S. Karger</publisher>
</originInfo>
<part>
<date>1976</date>
<extent unit="pages">
<start>189</start>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit46">
<titleInfo>
<title>The pattern of porphyrin isomer accumulation and excretion in symptomatic porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">E</namePart>
<namePart type="family">Dowdle</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">P</namePart>
<namePart type="family">Goldswain</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">N</namePart>
<namePart type="family">Song</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Dowdle E, Goldswain P, Song N, et al. The pattern of porphyrin isomer accumulation and excretion in symptomatic porphyria. Clin Sci 1970; 39:147–158.</note>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>39</number>
</detail>
<extent unit="pages">
<start>147</start>
<end>158</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Clin Sci</title>
</titleInfo>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>39</number>
</detail>
<extent unit="pages">
<start>147</start>
<end>158</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit47">
<titleInfo>
<title>Chronic hepatic porphyrias in humans (endo‐genic factors)</title>
</titleInfo>
<name type="personal">
<namePart type="given">M.</namePart>
<namePart type="family">Doss</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>book-chapter</genre>
<relatedItem type="host">
<titleInfo>
<title>Chemical porphyria in man</title>
</titleInfo>
<originInfo>
<publisher>Elsevier/North‐Holland Biomedical Press</publisher>
</originInfo>
<part>
<date>1979</date>
<extent unit="pages">
<start>11</start>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit48">
<titleInfo>
<title>Hereditary coproporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Goldberg</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">C</namePart>
<namePart type="family">Rimington</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A.</namePart>
<namePart type="family">Lockhead</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Goldberg A, Rimington C, Lockhead A. Hereditary coproporphyria. Lancet 1967; i:632–636.</note>
<part>
<date>1967</date>
<detail type="volume">
<caption>vol.</caption>
<number>i</number>
</detail>
<extent unit="pages">
<start>632</start>
<end>636</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Lancet</title>
</titleInfo>
<part>
<date>1967</date>
<detail type="volume">
<caption>vol.</caption>
<number>i</number>
</detail>
<extent unit="pages">
<start>632</start>
<end>636</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit49">
<titleInfo>
<title>The porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">UA</namePart>
<namePart type="family">Meyer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">R.</namePart>
<namePart type="family">Schmid</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>book-chapter</genre>
<relatedItem type="host">
<titleInfo>
<title>The metabolic basis of inherited disease</title>
</titleInfo>
<originInfo>
<publisher>McGraw Hill</publisher>
</originInfo>
<part>
<date>1980</date>
<extent unit="pages">
<start>1166</start>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit50">
<titleInfo>
<title>Harderopor‐phyrin coproporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Doss</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">R</namePart>
<namePart type="family">Von Tiepermann</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">W.</namePart>
<namePart type="family">Kopp</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Doss M, Von Tiepermann R, Kopp W. Harderopor‐phyrin coproporphyria. Lancet 1984; i:292.</note>
<part>
<date>1984</date>
<detail type="volume">
<caption>vol.</caption>
<number>i</number>
</detail>
<extent unit="pages">
<start>292</start>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Lancet</title>
</titleInfo>
<part>
<date>1984</date>
<detail type="volume">
<caption>vol.</caption>
<number>i</number>
</detail>
<extent unit="pages">
<start>292</start>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit51">
<titleInfo>
<title>The enzymatic defect in variegate porphyria. Studies with human cultured skin fibroblasts</title>
</titleInfo>
<name type="personal">
<namePart type="given">DA</namePart>
<namePart type="family">Brenner</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JR</namePart>
<namePart type="family">Bloomer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Brenner DA, Bloomer JR. The enzymatic defect in variegate porphyria. Studies with human cultured skin fibroblasts. N Engl J Med 1980; 302:765–768.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>302</number>
</detail>
<extent unit="pages">
<start>765</start>
<end>768</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>302</number>
</detail>
<extent unit="pages">
<start>765</start>
<end>768</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit52">
<titleInfo>
<title>Variegate porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">P.</namePart>
<namePart type="family">Mustajoki</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Mustajoki P. Variegate porphyria. Ann Intern Med 1978; 89:238–244.</note>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>89</number>
</detail>
<extent unit="pages">
<start>238</start>
<end>244</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Ann Intern Med</title>
</titleInfo>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>89</number>
</detail>
<extent unit="pages">
<start>238</start>
<end>244</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit53">
<titleInfo>
<title>Variegate porphyria. Clinical and laboratory features</title>
</titleInfo>
<name type="personal">
<namePart type="given">TJ</namePart>
<namePart type="family">Corey</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">VA</namePart>
<namePart type="family">DeLeo</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">H</namePart>
<namePart type="family">Christiansen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Corey TJ, DeLeo VA, Christiansen H, et al. Variegate porphyria. Clinical and laboratory features. J Am Acad Dermatol 1980; 2:36–43.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>2</number>
</detail>
<extent unit="pages">
<start>36</start>
<end>43</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>J Am Acad Dermatol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>2</number>
</detail>
<extent unit="pages">
<start>36</start>
<end>43</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit54">
<titleInfo>
<title>Faecal “x‐porphyria” in the hepatic porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">GH</namePart>
<namePart type="family">Elder</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">IA</namePart>
<namePart type="family">Magnus</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">F</namePart>
<namePart type="family">Handa</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Elder GH, Magnus IA, Handa F, et al. Faecal “x‐porphyria” in the hepatic porphyrias. Enzyme 1974; 17:29–38.</note>
<part>
<date>1974</date>
<detail type="volume">
<caption>vol.</caption>
<number>17</number>
</detail>
<extent unit="pages">
<start>29</start>
<end>38</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Enzyme</title>
</titleInfo>
<part>
<date>1974</date>
<detail type="volume">
<caption>vol.</caption>
<number>17</number>
</detail>
<extent unit="pages">
<start>29</start>
<end>38</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit55">
<titleInfo>
<title>A plasma porphyrin fluorescence marker for variegate porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">MB</namePart>
<namePart type="family">Poh‐Fitzpatrick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Poh‐Fitzpatrick MB. A plasma porphyrin fluorescence marker for variegate porphyria. Arch Dermatol 1980; 116:543–547.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>116</number>
</detail>
<extent unit="pages">
<start>543</start>
<end>547</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>116</number>
</detail>
<extent unit="pages">
<start>543</start>
<end>547</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit56">
<titleInfo>
<title>Laboratory testing in the porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">MB</namePart>
<namePart type="family">Poh‐Fitzpatrick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Poh‐Fitzpatrick MB. Laboratory testing in the porphyrias. Int J Dermatol 1979; 18:453–460.</note>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>18</number>
</detail>
<extent unit="pages">
<start>453</start>
<end>460</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Int J Dermatol</title>
</titleInfo>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>18</number>
</detail>
<extent unit="pages">
<start>453</start>
<end>460</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit57">
<titleInfo>
<title>Porphyrin production and liver involvement in a patient with erythropoietic protoporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">I</namePart>
<namePart type="family">Romslo</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">G</namePart>
<namePart type="family">Hovding</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">E</namePart>
<namePart type="family">Hamre</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Romslo I, Hovding G, Hamre E, et al. Porphyrin production and liver involvement in a patient with erythropoietic protoporphyria. Scand J Clin Lab Invest 1978; 38:529–535.</note>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>38</number>
</detail>
<extent unit="pages">
<start>529</start>
<end>535</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Scand J Clin Lab Invest</title>
</titleInfo>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>38</number>
</detail>
<extent unit="pages">
<start>529</start>
<end>535</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit58">
<titleInfo>
<title>The clinical chemistry of the porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">TK</namePart>
<namePart type="family">With</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">With TK. The clinical chemistry of the porphyrias. Clin Biochem 1968; 1:224–242.</note>
<part>
<date>1968</date>
<detail type="volume">
<caption>vol.</caption>
<number>1</number>
</detail>
<extent unit="pages">
<start>224</start>
<end>242</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Clin Biochem</title>
</titleInfo>
<part>
<date>1968</date>
<detail type="volume">
<caption>vol.</caption>
<number>1</number>
</detail>
<extent unit="pages">
<start>224</start>
<end>242</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit59">
<titleInfo>
<title>Cryer PE. Diagnostic endocrinology. New York : Oxford University Press, 1976:80.</title>
</titleInfo>
<note type="citation/reference">Cryer PE. Diagnostic endocrinology. New York : Oxford University Press, 1976:80.</note>
<name type="personal">
<namePart type="given">PE</namePart>
<namePart type="family">Cryer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>book</genre>
<originInfo>
<publisher>Oxford University Press</publisher>
</originInfo>
<part>
<date>1976</date>
<extent unit="pages">
<start>80</start>
</extent>
</part>
</relatedItem>
<relatedItem type="references" displayLabel="cit60">
<titleInfo>
<title>Nelson WE, ed. Textbook of pediatrics. 8th Ed. Philadelphia : WB Saunders, 1964:1294.</title>
</titleInfo>
<note type="citation/reference">Nelson WE, ed. Textbook of pediatrics. 8th Ed. Philadelphia : WB Saunders, 1964:1294.</note>
<name type="personal">
<namePart type="given">WE</namePart>
<namePart type="family">Nelson</namePart>
<role>
<roleTerm type="text">editor</roleTerm>
</role>
</name>
<genre>book</genre>
<originInfo>
<publisher>WB Saunders</publisher>
</originInfo>
<part>
<date>1964</date>
<extent unit="pages">
<start>1294</start>
</extent>
</part>
</relatedItem>
<relatedItem type="references" displayLabel="cit61">
<titleInfo>
<title>Acute hepatic porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">MJ</namePart>
<namePart type="family">Brodie</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A.</namePart>
<namePart type="family">Goldberg</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Brodie MJ, Goldberg A. Acute hepatic porphyrias. Clin Haematol 1980; 9:253–272.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>253</start>
<end>272</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Clin Haematol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>253</start>
<end>272</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit62">
<titleInfo>
<title>Hereditary coproporphyria and epilepsy</title>
</titleInfo>
<name type="personal">
<namePart type="given">AB</namePart>
<namePart type="family">Houston</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MJ</namePart>
<namePart type="family">Brodie</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MR</namePart>
<namePart type="family">Moore</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Houston AB, Brodie MJ, Moore MR, et al. Hereditary coproporphyria and epilepsy. Arch Dis Childhood 1977; 52:646–650.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>52</number>
</detail>
<extent unit="pages">
<start>646</start>
<end>650</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dis Childhood</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>52</number>
</detail>
<extent unit="pages">
<start>646</start>
<end>650</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit63">
<titleInfo>
<title>Acute intermittent porphyria in childhood. A neglected diagnosis</title>
</titleInfo>
<name type="personal">
<namePart type="given">N.</namePart>
<namePart type="family">Barclay</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Barclay N. Acute intermittent porphyria in childhood. A neglected diagnosis Arch Dis Childhood 1974; 49: 404–406.</note>
<part>
<date>1974</date>
<detail type="volume">
<caption>vol.</caption>
<number>49</number>
</detail>
<extent unit="pages">
<start>404</start>
<end>406</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dis Childhood</title>
</titleInfo>
<part>
<date>1974</date>
<detail type="volume">
<caption>vol.</caption>
<number>49</number>
</detail>
<extent unit="pages">
<start>404</start>
<end>406</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit64">
<titleInfo>
<title>Congenital erythropoietic porphyria. An autopsy report</title>
</titleInfo>
<name type="personal">
<namePart type="given">LK</namePart>
<namePart type="family">Bhutani</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">SK</namePart>
<namePart type="family">Sood</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">PK</namePart>
<namePart type="family">Das</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Bhutani LK, Sood SK, Das PK, et al. Congenital erythropoietic porphyria. An autopsy report. Arch Dermatol 1974; 110:427–431.</note>
<part>
<date>1974</date>
<detail type="volume">
<caption>vol.</caption>
<number>110</number>
</detail>
<extent unit="pages">
<start>427</start>
<end>431</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1974</date>
<detail type="volume">
<caption>vol.</caption>
<number>110</number>
</detail>
<extent unit="pages">
<start>427</start>
<end>431</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit65">
<titleInfo>
<title>The histo‐pathology and infrastructure of liver disease in erythropoietic protoporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">DM</namePart>
<namePart type="family">MacDonald</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">D</namePart>
<namePart type="family">Dermain</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">H.</namePart>
<namePart type="family">Pernot</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">MacDonald DM, Dermain D, Pernot H. The histo‐pathology and infrastructure of liver disease in erythropoietic protoporphyria. Br J Dermatol 1981; 104:7–17.</note>
<part>
<date>1981</date>
<detail type="volume">
<caption>vol.</caption>
<number>104</number>
</detail>
<extent unit="pages">
<start>7</start>
<end>17</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1981</date>
<detail type="volume">
<caption>vol.</caption>
<number>104</number>
</detail>
<extent unit="pages">
<start>7</start>
<end>17</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit66">
<titleInfo>
<title>The consequences of not diagnosing erythropoietic protoporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">MM</namePart>
<namePart type="family">Mathews‐Roth</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Mathews‐Roth MM. The consequences of not diagnosing erythropoietic protoporphyria. Arch Dermatol 1980; 116:407.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>116</number>
</detail>
<extent unit="pages">
<start>407</start>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>116</number>
</detail>
<extent unit="pages">
<start>407</start>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit67">
<titleInfo>
<title>Mishell DR Jr, Davajan V, eds. Reproductive endocrinology, infertility and contraception. Philadelphia : FA Davis, 1979:47.</title>
</titleInfo>
<note type="citation/reference">Mishell DR Jr, Davajan V, eds. Reproductive endocrinology, infertility and contraception. Philadelphia : FA Davis, 1979:47.</note>
<name type="personal">
<namePart type="given">DR</namePart>
<namePart type="family">Mishell Jr</namePart>
<role>
<roleTerm type="text">editor</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">V</namePart>
<namePart type="family">Davajan</namePart>
<role>
<roleTerm type="text">editor</roleTerm>
</role>
</name>
<genre>book</genre>
<originInfo>
<publisher>FA Davis</publisher>
</originInfo>
<part>
<date>1979</date>
<extent unit="pages">
<start>47</start>
</extent>
</part>
</relatedItem>
<relatedItem type="references" displayLabel="cit68">
<titleInfo>
<title>Steroid control of porphyrin and heme biosynthesis: a new biological function of steroid hormone metabolites</title>
</titleInfo>
<name type="personal">
<namePart type="given">S</namePart>
<namePart type="family">Granick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A.</namePart>
<namePart type="family">Kappas</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Granick S, Kappas A. Steroid control of porphyrin and heme biosynthesis: a new biological function of steroid hormone metabolites. Proc Natl Aca Sci 1967; 57: 1463–1467.</note>
<part>
<date>1967</date>
<detail type="volume">
<caption>vol.</caption>
<number>57</number>
</detail>
<extent unit="pages">
<start>1463</start>
<end>1467</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Proc Natl Aca Sci</title>
</titleInfo>
<part>
<date>1967</date>
<detail type="volume">
<caption>vol.</caption>
<number>57</number>
</detail>
<extent unit="pages">
<start>1463</start>
<end>1467</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit69">
<titleInfo>
<title>Erzin C, ed. Systematic endocrinology. 2nd Ed. Hagers‐town , MD : Harper & Row, 1979:198.</title>
</titleInfo>
<note type="citation/reference">Erzin C, ed. Systematic endocrinology. 2nd Ed. Hagers‐town , MD : Harper & Row, 1979:198.</note>
<name type="personal">
<namePart type="given">C</namePart>
<namePart type="family">Erzin</namePart>
<role>
<roleTerm type="text">editor</roleTerm>
</role>
</name>
<genre>book</genre>
<originInfo>
<publisher>Harper & Row</publisher>
</originInfo>
<part>
<date>1979</date>
<extent unit="pages">
<start>198</start>
</extent>
</part>
</relatedItem>
<relatedItem type="references" displayLabel="cit70">
<titleInfo>
<title>Davis JC, Hipkin LJ. Clinical endocrine pathology. Philadelphia : Blackwell Scientific Publications, 1977: 174.</title>
</titleInfo>
<note type="citation/reference">Davis JC, Hipkin LJ. Clinical endocrine pathology. Philadelphia : Blackwell Scientific Publications, 1977: 174.</note>
<name type="personal">
<namePart type="given">JC</namePart>
<namePart type="family">Davis</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">LJ</namePart>
<namePart type="family">Hipkin</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>book</genre>
<originInfo>
<publisher>Blackwell Scientific Publications</publisher>
</originInfo>
<part>
<date>1977</date>
<extent unit="pages">
<start>174</start>
</extent>
</part>
</relatedItem>
<relatedItem type="references" displayLabel="cit71">
<titleInfo>
<title>Porphyrie hepatoerythrocytaire, une nouvelle forme de porphyrie</title>
</titleInfo>
<name type="personal">
<namePart type="given">AJ</namePart>
<namePart type="family">Pinol</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">C</namePart>
<namePart type="family">Herrero</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">J</namePart>
<namePart type="family">Almeida</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Pinol AJ, Herrero C, Almeida J, et al. Porphyrie hepatoerythrocytaire, une nouvelle forme de porphyrie. Ann Dermatol Syphiiol 1975; 102:129–136.</note>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>102</number>
</detail>
<extent unit="pages">
<start>129</start>
<end>136</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Ann Dermatol Syphiiol</title>
</titleInfo>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>102</number>
</detail>
<extent unit="pages">
<start>129</start>
<end>136</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit72">
<titleInfo>
<title>Hepatoerythropoietic porphyria presenting as scleroderma and acrosclerosis in a sibling pair</title>
</titleInfo>
<name type="personal">
<namePart type="given">N</namePart>
<namePart type="family">Simon</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">GY</namePart>
<namePart type="family">Berko</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">I.</namePart>
<namePart type="family">Schneider</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Simon N, Berko GY, Schneider I. Hepatoerythropoietic porphyria presenting as scleroderma and acrosclerosis in a sibling pair. Br J Dermatol 1977; 96:663–668.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>96</number>
</detail>
<extent unit="pages">
<start>663</start>
<end>668</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>96</number>
</detail>
<extent unit="pages">
<start>663</start>
<end>668</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit73">
<titleInfo>
<title>Porphyria cutanea tarda. Clinical features and laboratory findings in 40 patients</title>
</titleInfo>
<name type="personal">
<namePart type="given">ME</namePart>
<namePart type="family">Grossman</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">DR</namePart>
<namePart type="family">Bickers</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MB</namePart>
<namePart type="family">Poh‐Fitzpatrick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Grossman ME, Bickers DR, Poh‐Fitzpatrick MB, et al. Porphyria cutanea tarda. Clinical features and laboratory findings in 40 patients. Am J Med 1979; 67:277–286.</note>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>67</number>
</detail>
<extent unit="pages">
<start>277</start>
<end>286</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Am J Med</title>
</titleInfo>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>67</number>
</detail>
<extent unit="pages">
<start>277</start>
<end>286</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit74">
<titleInfo>
<title>Erythropoietic protoporphyria: hepatic cirrhosis</title>
</titleInfo>
<name type="personal">
<namePart type="given">DJ</namePart>
<namePart type="family">Cripps</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">SS</namePart>
<namePart type="family">Goldfarb</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Cripps DJ, Goldfarb SS. Erythropoietic protoporphyria: hepatic cirrhosis. Br J Dermatol 1978; 98:349–354.</note>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>98</number>
</detail>
<extent unit="pages">
<start>349</start>
<end>354</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>98</number>
</detail>
<extent unit="pages">
<start>349</start>
<end>354</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit75">
<titleInfo>
<title>Hepatoerythropoietic porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">DB</namePart>
<namePart type="family">Czarnecki</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Czarnecki DB. Hepatoerythropoietic porphyria. Arch Dermatol 1980; 116:307–311.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>116</number>
</detail>
<extent unit="pages">
<start>307</start>
<end>311</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>116</number>
</detail>
<extent unit="pages">
<start>307</start>
<end>311</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit76">
<titleInfo>
<title>Hepatoerythropoietic porphyria: a new Uroporphyrinogen decarboxylase defect or homozygous porphyria cutanea tarda</title>
</titleInfo>
<name type="personal">
<namePart type="given">GH</namePart>
<namePart type="family">Elder</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">SG</namePart>
<namePart type="family">Smith</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">C</namePart>
<namePart type="family">Herrero</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Elder GH, Smith SG, Herrero C, et al. Hepatoerythropoietic porphyria: a new Uroporphyrinogen decarboxylase defect or homozygous porphyria cutanea tarda Lancet 1981; i:916–919.</note>
<part>
<date>1981</date>
<detail type="volume">
<caption>vol.</caption>
<number>i</number>
</detail>
<extent unit="pages">
<start>916</start>
<end>919</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Lancet</title>
</titleInfo>
<part>
<date>1981</date>
<detail type="volume">
<caption>vol.</caption>
<number>i</number>
</detail>
<extent unit="pages">
<start>916</start>
<end>919</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit77">
<titleInfo>
<title>Acute intermittent porphyria in childhood: a neglected diagnosis</title>
</titleInfo>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Kreimer‐Birnbaum</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">RM</namePart>
<namePart type="family">Bannennan</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Kreimer‐Birnbaum M, Bannennan RM. Acute intermittent porphyria in childhood: a neglected diagnosis Arch Dis Childhood 1975; 50:494–495.</note>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>50</number>
</detail>
<extent unit="pages">
<start>494</start>
<end>495</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dis Childhood</title>
</titleInfo>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>50</number>
</detail>
<extent unit="pages">
<start>494</start>
<end>495</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit78">
<titleInfo>
<title>Acute intermittent porphyria and epilepsy</title>
</titleInfo>
<name type="personal">
<namePart type="given">R</namePart>
<namePart type="family">Biagini</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">R</namePart>
<namePart type="family">Tignani</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">AR</namePart>
<namePart type="family">Fifi</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Biagini R, Tignani R, Fifi AR, et al. Acute intermittent porphyria and epilepsy. Arch Dis Childhood 1979; 54: 644–645.</note>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>54</number>
</detail>
<extent unit="pages">
<start>644</start>
<end>645</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dis Childhood</title>
</titleInfo>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>54</number>
</detail>
<extent unit="pages">
<start>644</start>
<end>645</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit79">
<titleInfo>
<title>Two cases of infantile and familial porphyria cutanea tarda</title>
</titleInfo>
<name type="personal">
<namePart type="given">MJC</namePart>
<namePart type="family">Prado</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">RE</namePart>
<namePart type="family">de Salamanca</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MV</namePart>
<namePart type="family">Hernando</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Prado MJC, de Salamanca RE, Hernando MV, et al. Two cases of infantile and familial porphyria cutanea tarda. Dermatologica 1980; 161:205–210.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>161</number>
</detail>
<extent unit="pages">
<start>205</start>
<end>210</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Dermatologica</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>161</number>
</detail>
<extent unit="pages">
<start>205</start>
<end>210</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit80">
<titleInfo>
<title>Porphyria cutanea tarda bei 6 jahrigem madchen mit unerwartetem rezidiv</title>
</titleInfo>
<name type="personal">
<namePart type="given">I.</namePart>
<namePart type="family">Peschlow</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Peschlow I. Porphyria cutanea tarda bei 6 jahrigem madchen mit unerwartetem rezidiv. Dermatol Monatss-chr 1979; 165:425–431.</note>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>165</number>
</detail>
<extent unit="pages">
<start>425</start>
<end>431</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Dermatol Monatss-chr</title>
</titleInfo>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>165</number>
</detail>
<extent unit="pages">
<start>425</start>
<end>431</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit81">
<titleInfo>
<title>Acquired toxic porphyria cutanea tarda due to hexachlorohenzene</title>
</titleInfo>
<name type="personal">
<namePart type="given">C</namePart>
<namePart type="family">Cam</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">G.</namePart>
<namePart type="family">Nigogosyan</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Cam C, Nigogosyan G. Acquired toxic porphyria cutanea tarda due to hexachlorohenzene. JAMA 1963; 183:88–91.</note>
<part>
<date>1963</date>
<detail type="volume">
<caption>vol.</caption>
<number>183</number>
</detail>
<extent unit="pages">
<start>88</start>
<end>91</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>JAMA</title>
</titleInfo>
<part>
<date>1963</date>
<detail type="volume">
<caption>vol.</caption>
<number>183</number>
</detail>
<extent unit="pages">
<start>88</start>
<end>91</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit82">
<titleInfo>
<title>Porphyria turcica. Twenty years after hexachlorobenzene intoxication</title>
</titleInfo>
<name type="personal">
<namePart type="given">DJ</namePart>
<namePart type="family">Cripps</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Gocmen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">HA</namePart>
<namePart type="family">Peters</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Cripps DJ, Gocmen A, Peters HA. Porphyria turcica. Twenty years after hexachlorobenzene intoxication. Arch Dermatol 1980; 116:46–50.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>116</number>
</detail>
<extent unit="pages">
<start>46</start>
<end>50</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>116</number>
</detail>
<extent unit="pages">
<start>46</start>
<end>50</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit83">
<titleInfo>
<title>Hereditary coproporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">H</namePart>
<namePart type="family">Berger</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A.</namePart>
<namePart type="family">Goldberg</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Berger H, Goldberg A. Hereditary coproporphyria. BMJ 1955; 2:85–94.</note>
<part>
<date>1955</date>
<detail type="volume">
<caption>vol.</caption>
<number>2</number>
</detail>
<extent unit="pages">
<start>85</start>
<end>94</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>BMJ</title>
</titleInfo>
<part>
<date>1955</date>
<detail type="volume">
<caption>vol.</caption>
<number>2</number>
</detail>
<extent unit="pages">
<start>85</start>
<end>94</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit84">
<titleInfo>
<title>La coproporphyrie hereditaire. Sept observations</title>
</titleInfo>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Jaeger</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JD</namePart>
<namePart type="family">Tempe</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">F</namePart>
<namePart type="family">Geisler</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Jaeger A, Tempe JD, Geisler F, et al. La coproporphyrie hereditaire. Sept observations. Nouvelle Press, Medicale 1975; 4:2783–2787.</note>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>4</number>
</detail>
<extent unit="pages">
<start>2783</start>
<end>2787</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Nouvelle Press, Medicale</title>
</titleInfo>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>4</number>
</detail>
<extent unit="pages">
<start>2783</start>
<end>2787</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit85">
<titleInfo>
<title>Porphyria variegata</title>
</titleInfo>
<name type="personal">
<namePart type="given">S.</namePart>
<namePart type="family">Kramer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Kramer S. Porphyria variegata. Clin Haematol 1980; 9: 303–322.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>303</start>
<end>322</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Clin Haematol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>303</start>
<end>322</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit86">
<titleInfo>
<title>Porphyria variegata in a 9 year old girl</title>
</titleInfo>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Krauze</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">E</namePart>
<namePart type="family">Kobusmska</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">W.</namePart>
<namePart type="family">Helis</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Krauze M, Kobusmska E, Helis W. Porphyria variegata in a 9 year old girl. Pediatr Pol 1980; 55:241–243.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>55</number>
</detail>
<extent unit="pages">
<start>241</start>
<end>243</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Pediatr Pol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>55</number>
</detail>
<extent unit="pages">
<start>241</start>
<end>243</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit87">
<titleInfo>
<title>The hepatic porphyrias. Pathogenesis, manifestations and management</title>
</titleInfo>
<name type="personal">
<namePart type="given">JR</namePart>
<namePart type="family">Bloomer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Bloomer JR. The hepatic porphyrias. Pathogenesis, manifestations and management. Gastroenterology 1976; 71:689–701.</note>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>71</number>
</detail>
<extent unit="pages">
<start>689</start>
<end>701</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Gastroenterology</title>
</titleInfo>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>71</number>
</detail>
<extent unit="pages">
<start>689</start>
<end>701</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit88">
<titleInfo>
<title>Factors affecting the induction of porphyria in the laboratory rat. Biochemical and photobiological studies with diethy‐1, 4‐dehy‐dro‐2, 4, 6‐trimethylpyridine‐3, 5‐dicarboxylatc (DDC) as a porphyrinogenic agent</title>
</titleInfo>
<name type="personal">
<namePart type="given">IA</namePart>
<namePart type="family">Magnus</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">DA</namePart>
<namePart type="family">Roe</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">LK</namePart>
<namePart type="family">Bhutani</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Magnus IA, Roe DA, Bhutani LK. Factors affecting the induction of porphyria in the laboratory rat. Biochemical and photobiological studies with diethy‐1, 4‐dehy‐dro‐2, 4, 6‐trimethylpyridine‐3, 5‐dicarboxylatc (DDC) as a porphyrinogenic agent. J Invest Dermatol 1969; 53:400–413.</note>
<part>
<date>1969</date>
<detail type="volume">
<caption>vol.</caption>
<number>53</number>
</detail>
<extent unit="pages">
<start>400</start>
<end>413</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>J Invest Dermatol</title>
</titleInfo>
<part>
<date>1969</date>
<detail type="volume">
<caption>vol.</caption>
<number>53</number>
</detail>
<extent unit="pages">
<start>400</start>
<end>413</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit89">
<titleInfo>
<title>Skin porphyrin assay in porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">L</namePart>
<namePart type="family">Malina</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">V</namePart>
<namePart type="family">Miller</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">IA</namePart>
<namePart type="family">Magnus</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Malina L, Miller V, Magnus IA. Skin porphyrin assay in porphyria. Clinica Chimica Acta 1978; 83:55–59.</note>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>83</number>
</detail>
<extent unit="pages">
<start>55</start>
<end>59</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Clinica Chimica Acta</title>
</titleInfo>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>83</number>
</detail>
<extent unit="pages">
<start>55</start>
<end>59</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit90">
<titleInfo>
<title>Skin porphyrin and photosensitivity in the porphyrinic rat</title>
</titleInfo>
<name type="personal">
<namePart type="given">T</namePart>
<namePart type="family">Miura</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">IA</namePart>
<namePart type="family">Magnus</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">K</namePart>
<namePart type="family">Jones</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Miura T, Magnus IA, Jones K, et al. Skin porphyrin and photosensitivity in the porphyrinic rat. Dermatologica 1975; 151:80–88.</note>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>151</number>
</detail>
<extent unit="pages">
<start>80</start>
<end>88</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Dermatologica</title>
</titleInfo>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>151</number>
</detail>
<extent unit="pages">
<start>80</start>
<end>88</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit91">
<titleInfo>
<title>Studies of photosensitization by porphyrins</title>
</titleInfo>
<name type="personal">
<namePart type="given">HF</namePart>
<namePart type="family">Blum</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">N.</namePart>
<namePart type="family">Pace</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Blum HF, Pace N. Studies of photosensitization by porphyrins. Br J Dermatol 1937; 49:465–485.</note>
<part>
<date>1937</date>
<detail type="volume">
<caption>vol.</caption>
<number>49</number>
</detail>
<extent unit="pages">
<start>465</start>
<end>485</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1937</date>
<detail type="volume">
<caption>vol.</caption>
<number>49</number>
</detail>
<extent unit="pages">
<start>465</start>
<end>485</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit92">
<titleInfo>
<title>On the mechanism of photosensitization in man</title>
</titleInfo>
<name type="personal">
<namePart type="given">HF</namePart>
<namePart type="family">Blum</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">WG</namePart>
<namePart type="family">Watrous</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">RJ</namePart>
<namePart type="family">West</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Blum HF, Watrous WG, West RJ. On the mechanism of photosensitization in man. Am J Physiol 1975; 113: 350–353.</note>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>113</number>
</detail>
<extent unit="pages">
<start>350</start>
<end>353</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Am J Physiol</title>
</titleInfo>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>113</number>
</detail>
<extent unit="pages">
<start>350</start>
<end>353</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit93">
<titleInfo>
<title>Cutaneous porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">IA</namePart>
<namePart type="family">Magnus</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Magnus IA. Cutaneous porphyria. Clin Haematol 1980; 9:273–302.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>273</start>
<end>302</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Clin Haematol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>273</start>
<end>302</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit94">
<titleInfo>
<title>Protoporphyrin‐induced photodynamic effects in transport processes across the membrane of human erythrocytes</title>
</titleInfo>
<name type="personal">
<namePart type="given">TMAR</namePart>
<namePart type="family">Dubbleman</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">AFPM</namePart>
<namePart type="family">De Goeij</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">J.</namePart>
<namePart type="family">Van Steveninck</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Dubbleman TMAR, De Goeij AFPM, Van Steveninck J. Protoporphyrin‐induced photodynamic effects in transport processes across the membrane of human erythrocytes. Biochim Biophys Acta 1980; 595:133–139.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>595</number>
</detail>
<extent unit="pages">
<start>133</start>
<end>139</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Biochim Biophys Acta</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>595</number>
</detail>
<extent unit="pages">
<start>133</start>
<end>139</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit95">
<titleInfo>
<title>Protoporphyrin‐sensirized photodamage in isolated membranes of human erythrocytes</title>
</titleInfo>
<name type="personal">
<namePart type="given">AW</namePart>
<namePart type="family">Girotti</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Girotti AW. Protoporphyrin‐sensirized photodamage in isolated membranes of human erythrocytes. Biochemistry 1979; 18:4403–4411.</note>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>18</number>
</detail>
<extent unit="pages">
<start>4403</start>
<end>4411</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Biochemistry</title>
</titleInfo>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>18</number>
</detail>
<extent unit="pages">
<start>4403</start>
<end>4411</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit96">
<titleInfo>
<title>Photolysis of protoporphyrin‐treated human fibroblasts in vitro: studies on mechanism</title>
</titleInfo>
<name type="personal">
<namePart type="given">SD</namePart>
<namePart type="family">Wakulchik</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JR</namePart>
<namePart type="family">Schiltz</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">DR</namePart>
<namePart type="family">Bickers</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Wakulchik SD, Schiltz JR, Bickers DR. Photolysis of protoporphyrin‐treated human fibroblasts in vitro: studies on mechanism. J Lab Clin Med 1980; 96:158–167.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>96</number>
</detail>
<extent unit="pages">
<start>158</start>
<end>167</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>J Lab Clin Med</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>96</number>
</detail>
<extent unit="pages">
<start>158</start>
<end>167</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit97">
<titleInfo>
<title>Porphyrin‐sensitized cutaneous photosensitivity pathogenesis and treatment</title>
</titleInfo>
<name type="personal">
<namePart type="given">MB</namePart>
<namePart type="family">Poh‐Fitzpatrick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Poh‐Fitzpatrick MB. Porphyrin‐sensitized cutaneous photosensitivity pathogenesis and treatment. Clin Dermatol 1985; 3:41–82.</note>
<part>
<date>1985</date>
<detail type="volume">
<caption>vol.</caption>
<number>3</number>
</detail>
<extent unit="pages">
<start>41</start>
<end>82</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Clin Dermatol</title>
</titleInfo>
<part>
<date>1985</date>
<detail type="volume">
<caption>vol.</caption>
<number>3</number>
</detail>
<extent unit="pages">
<start>41</start>
<end>82</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit98">
<titleInfo>
<title>Light‐induced electron transfer between chlorophyll and hydroxyquinone and the effect of oxygen and beta‐carotene</title>
</titleInfo>
<name type="personal">
<namePart type="given">E</namePart>
<namePart type="family">Fugimari</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">M.</namePart>
<namePart type="family">Tavla</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Fugimari E, Tavla M. Light‐induced electron transfer between chlorophyll and hydroxyquinone and the effect of oxygen and beta‐carotene. Photochem Photobiol 1966; 5:877–887.</note>
<part>
<date>1966</date>
<detail type="volume">
<caption>vol.</caption>
<number>5</number>
</detail>
<extent unit="pages">
<start>877</start>
<end>887</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Photochem Photobiol</title>
</titleInfo>
<part>
<date>1966</date>
<detail type="volume">
<caption>vol.</caption>
<number>5</number>
</detail>
<extent unit="pages">
<start>877</start>
<end>887</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit99">
<titleInfo>
<title>Erythropoietic protoporphyria— diagnosis and treatment</title>
</titleInfo>
<name type="personal">
<namePart type="given">MM</namePart>
<namePart type="family">Mathews‐Roth</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Mathews‐Roth MM. Erythropoietic protoporphyria— diagnosis and treatment. N Engl J Med 1977; 297: 98–100.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>297</number>
</detail>
<extent unit="pages">
<start>98</start>
<end>100</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>297</number>
</detail>
<extent unit="pages">
<start>98</start>
<end>100</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit100">
<titleInfo>
<title>Erythropoietic protoporphyria. Photoactivation of the complement system</title>
</titleInfo>
<name type="personal">
<namePart type="given">I</namePart>
<namePart type="family">Gigli</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">AA</namePart>
<namePart type="family">Schothorst</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">NA</namePart>
<namePart type="family">Soter</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Gigli I, Schothorst AA, Soter NA, et al. Erythropoietic protoporphyria. Photoactivation of the complement system. J Clin Invest 1980; 66:517–522.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>66</number>
</detail>
<extent unit="pages">
<start>517</start>
<end>522</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>J Clin Invest</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>66</number>
</detail>
<extent unit="pages">
<start>517</start>
<end>522</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit101">
<titleInfo>
<title>Generation of chemotactic activity in serum from patients with erythropoietic protoporphyria and porphyria cutanea tarda</title>
</titleInfo>
<name type="personal">
<namePart type="given">HW</namePart>
<namePart type="family">Lim</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">HD</namePart>
<namePart type="family">Perez</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Poh‐Fitzpatrick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Lim HW, Perez HD, Poh‐Fitzpatrick M, et al. Generation of chemotactic activity in serum from patients with erythropoietic protoporphyria and porphyria cutanea tarda. N Engl J Med 1981; 304:212–216.</note>
<part>
<date>1981</date>
<detail type="volume">
<caption>vol.</caption>
<number>304</number>
</detail>
<extent unit="pages">
<start>212</start>
<end>216</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1981</date>
<detail type="volume">
<caption>vol.</caption>
<number>304</number>
</detail>
<extent unit="pages">
<start>212</start>
<end>216</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit102">
<titleInfo>
<title>Porphyrin‐induced photodamage as related to the subcellular localization of the porphyrins</title>
</titleInfo>
<name type="personal">
<namePart type="given">S</namePart>
<namePart type="family">Sandberg</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">I</namePart>
<namePart type="family">Romslo</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">G</namePart>
<namePart type="family">Hovding</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">T.</namePart>
<namePart type="family">Bjorndal</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Sandberg S, Romslo I, Hovding G, Bjorndal T. Porphyrin‐induced photodamage as related to the subcellular localization of the porphyrins. Acta Derm Venereol 1982; suppl 100:75–80.</note>
<part>
<date>1982</date>
<detail type="issue">
<caption>no.</caption>
<number>suppl 100</number>
</detail>
<extent unit="pages">
<start>75</start>
<end>80</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Acta Derm Venereol</title>
</titleInfo>
<part>
<date>1982</date>
<detail type="issue">
<caption>no.</caption>
<number>suppl 100</number>
</detail>
<extent unit="pages">
<start>75</start>
<end>80</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit103">
<titleInfo>
<title>On the mode of cytotoxic action of photoactivated porphyrins</title>
</titleInfo>
<name type="personal">
<namePart type="given">K</namePart>
<namePart type="family">Kohn</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">D.</namePart>
<namePart type="family">Kessel</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Kohn K, Kessel D. On the mode of cytotoxic action of photoactivated porphyrins. Biochem Pharm 1979; 28: 2465–2470.</note>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>28</number>
</detail>
<extent unit="pages">
<start>2465</start>
<end>2470</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Biochem Pharm</title>
</titleInfo>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>28</number>
</detail>
<extent unit="pages">
<start>2465</start>
<end>2470</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit104">
<titleInfo>
<title>Uber die sensibilisierende wirkung tierische Farbstoffe und ihre physiologische Bedeutung</title>
</titleInfo>
<name type="personal">
<namePart type="given">W.</namePart>
<namePart type="family">Hausmann</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Hausmann W. Uber die sensibilisierende wirkung tierische Farbstoffe und ihre physiologische Bedeutung. Biochem A 1908; 14:275–278.</note>
<part>
<date>1908</date>
<detail type="volume">
<caption>vol.</caption>
<number>14</number>
</detail>
<extent unit="pages">
<start>275</start>
<end>278</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Biochem A</title>
</titleInfo>
<part>
<date>1908</date>
<detail type="volume">
<caption>vol.</caption>
<number>14</number>
</detail>
<extent unit="pages">
<start>275</start>
<end>278</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit105">
<titleInfo>
<title>The anemia of erythropoietic porphyria with the first description of the disease in an elderly patient</title>
</titleInfo>
<name type="personal">
<namePart type="given">S</namePart>
<namePart type="family">Kramer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">E</namePart>
<namePart type="family">Viljoen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">AM</namePart>
<namePart type="family">Mayer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Kramer S, Viljoen E, Mayer AM, et al. The anemia of erythropoietic porphyria with the first description of the disease in an elderly patient. Br J Haematol 1965; 11:666–675.</note>
<part>
<date>1965</date>
<detail type="volume">
<caption>vol.</caption>
<number>11</number>
</detail>
<extent unit="pages">
<start>666</start>
<end>675</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Haematol</title>
</titleInfo>
<part>
<date>1965</date>
<detail type="volume">
<caption>vol.</caption>
<number>11</number>
</detail>
<extent unit="pages">
<start>666</start>
<end>675</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit106">
<titleInfo>
<title>Photoprotection in erythropoietic protoporphyria: mechanism of protoportection by beta‐carotene</title>
</titleInfo>
<name type="personal">
<namePart type="given">AN</namePart>
<namePart type="family">Moshell</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">L.</namePart>
<namePart type="family">Bjornson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Moshell AN, Bjornson L. Photoprotection in erythropoietic protoporphyria: mechanism of protoportection by beta‐carotene. J Invest Dermatol 1977; 68:157–160.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>68</number>
</detail>
<extent unit="pages">
<start>157</start>
<end>160</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>J Invest Dermatol</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>68</number>
</detail>
<extent unit="pages">
<start>157</start>
<end>160</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit107">
<titleInfo>
<title>Studies on free erythrocyte protoporphyrin plasma iron, and plasma copper in normal and anemic subjects</title>
</titleInfo>
<name type="personal">
<namePart type="given">GE</namePart>
<namePart type="family">Cartwright</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">CM</namePart>
<namePart type="family">Huguley</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">H</namePart>
<namePart type="family">Ashenbrucker</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Cartwright GE, Huguley CM, Ashenbrucker H, et al. Studies on free erythrocyte protoporphyrin plasma iron, and plasma copper in normal and anemic subjects. Blood 1948; 3:501–525.</note>
<part>
<date>1948</date>
<detail type="volume">
<caption>vol.</caption>
<number>3</number>
</detail>
<extent unit="pages">
<start>501</start>
<end>525</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Blood</title>
</titleInfo>
<part>
<date>1948</date>
<detail type="volume">
<caption>vol.</caption>
<number>3</number>
</detail>
<extent unit="pages">
<start>501</start>
<end>525</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit108">
<titleInfo>
<title>Erythropoietic uroporphyria of Gunther first presenting at 58 years with positive family studies</title>
</titleInfo>
<name type="personal">
<namePart type="given">RW</namePart>
<namePart type="family">Pain</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">FW</namePart>
<namePart type="family">Welch</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">R</namePart>
<namePart type="family">Woodroffe</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Pain RW, Welch FW, Woodroffe R, et al. Erythropoietic uroporphyria of Gunther first presenting at 58 years with positive family studies. BMJ 1975; 3:621–623.</note>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>3</number>
</detail>
<extent unit="pages">
<start>621</start>
<end>623</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>BMJ</title>
</titleInfo>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>3</number>
</detail>
<extent unit="pages">
<start>621</start>
<end>623</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit109">
<titleInfo>
<title>Congenital porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">H</namePart>
<namePart type="family">Ippen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">T.</namePart>
<namePart type="family">Fuchs</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Ippen H, Fuchs T. Congenital porphyria. Clin Hematol 1980; 9:323–344.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>323</start>
<end>344</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Clin Hematol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>9</number>
</detail>
<extent unit="pages">
<start>323</start>
<end>344</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit110">
<titleInfo>
<title>Complete porphyrin analysis of pathologic urines</title>
</titleInfo>
<name type="personal">
<namePart type="given">SL</namePart>
<namePart type="family">Sweinsson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">C</namePart>
<namePart type="family">Rimington</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">HD</namePart>
<namePart type="family">Barnes</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Sweinsson SL, Rimington C, Barnes HD. Complete porphyrin analysis of pathologic urines. Scand J Clin Lab Invest 1949; 1:2–11.</note>
<part>
<date>1949</date>
<detail type="volume">
<caption>vol.</caption>
<number>1</number>
</detail>
<extent unit="pages">
<start>2</start>
<end>11</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Scand J Clin Lab Invest</title>
</titleInfo>
<part>
<date>1949</date>
<detail type="volume">
<caption>vol.</caption>
<number>1</number>
</detail>
<extent unit="pages">
<start>2</start>
<end>11</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit111">
<titleInfo>
<title>Erythropoietic protoporphyria—a new porphyria syndrome with solar urticaria due to protoporphyrinemia</title>
</titleInfo>
<name type="personal">
<namePart type="given">IA</namePart>
<namePart type="family">Magnus</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Jarrett</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">TAJ</namePart>
<namePart type="family">Prankerd</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Magnus IA, Jarrett A, Prankerd TAJ, et al. Erythropoietic protoporphyria—a new porphyria syndrome with solar urticaria due to protoporphyrinemia. Lancet 1961; ii:448–451.</note>
<part>
<date>1961</date>
<detail type="volume">
<caption>vol.</caption>
<number>ii</number>
</detail>
<extent unit="pages">
<start>448</start>
<end>451</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Lancet</title>
</titleInfo>
<part>
<date>1961</date>
<detail type="volume">
<caption>vol.</caption>
<number>ii</number>
</detail>
<extent unit="pages">
<start>448</start>
<end>451</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit112">
<titleInfo>
<title>Erythropoietic protoporphyria: ten years experience</title>
</titleInfo>
<name type="personal">
<namePart type="given">VA</namePart>
<namePart type="family">DeLeo</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Poh‐Fitzpatrick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Mathews‐Roth</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">DeLeo VA, Poh‐Fitzpatrick M, Mathews‐Roth M, et al. Erythropoietic protoporphyria: ten years experience. Am J Med 1976; 60:8–22.</note>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>60</number>
</detail>
<extent unit="pages">
<start>8</start>
<end>22</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Am J Med</title>
</titleInfo>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>60</number>
</detail>
<extent unit="pages">
<start>8</start>
<end>22</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit113">
<titleInfo>
<title>Birefringence of hepatic pigment deposits in erythropoietic protoporphyria. Specificity of polarization microscopy in the identification of hepatic protoporphyrin deposits</title>
</titleInfo>
<name type="personal">
<namePart type="given">G</namePart>
<namePart type="family">Klatskin</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JR</namePart>
<namePart type="family">Bloomer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Klatskin G, Bloomer JR. Birefringence of hepatic pigment deposits in erythropoietic protoporphyria. Specificity of polarization microscopy in the identification of hepatic protoporphyrin deposits. Gastroenterol 1974; 67:294–302.</note>
<part>
<date>1974</date>
<detail type="volume">
<caption>vol.</caption>
<number>67</number>
</detail>
<extent unit="pages">
<start>294</start>
<end>302</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Gastroenterol</title>
</titleInfo>
<part>
<date>1974</date>
<detail type="volume">
<caption>vol.</caption>
<number>67</number>
</detail>
<extent unit="pages">
<start>294</start>
<end>302</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit114">
<titleInfo>
<title>Erythropoietic protoporphyria with hepatic cirrhosis</title>
</titleInfo>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Wells</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">LE</namePart>
<namePart type="family">Golitz</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">BJ</namePart>
<namePart type="family">Bender</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Wells M, Golitz LE, Bender BJ. Erythropoietic protoporphyria with hepatic cirrhosis. Arch Dermatol 1980; 116:429–432.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>116</number>
</detail>
<extent unit="pages">
<start>429</start>
<end>432</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>116</number>
</detail>
<extent unit="pages">
<start>429</start>
<end>432</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit115">
<titleInfo>
<title>Pathogenesis and therapy of liver disease in protoporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">JR</namePart>
<namePart type="family">Bloomer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Bloomer JR. Pathogenesis and therapy of liver disease in protoporphyria. Yale J Biol Med 1979; 52:39–48.</note>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>52</number>
</detail>
<extent unit="pages">
<start>39</start>
<end>48</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Yale J Biol Med</title>
</titleInfo>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>52</number>
</detail>
<extent unit="pages">
<start>39</start>
<end>48</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit116">
<titleInfo>
<title>Erythropoietic protoporphyria. Evidence for multiple sites of excess protoporphyria formation</title>
</titleInfo>
<name type="personal">
<namePart type="given">P</namePart>
<namePart type="family">Scolnick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">HS</namePart>
<namePart type="family">Marver</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">R.</namePart>
<namePart type="family">Schmid</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Scolnick P, Marver HS, Schmid R. Erythropoietic protoporphyria. Evidence for multiple sites of excess protoporphyria formation. J Clin Invest 1971; 50:203–207.</note>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>50</number>
</detail>
<extent unit="pages">
<start>203</start>
<end>207</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>J Clin Invest</title>
</titleInfo>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>50</number>
</detail>
<extent unit="pages">
<start>203</start>
<end>207</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit117">
<titleInfo>
<title>The histopathology and infrastructure of liver disease in erythropoietic protoporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">DM</namePart>
<namePart type="family">MacDonald</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">D</namePart>
<namePart type="family">Germain</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">H.</namePart>
<namePart type="family">Perrot</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">MacDonald DM, Germain D, Perrot H. The histopathology and infrastructure of liver disease in erythropoietic protoporphyria. Br J Dermatol 1981; 104:7–17.</note>
<part>
<date>1981</date>
<detail type="volume">
<caption>vol.</caption>
<number>104</number>
</detail>
<extent unit="pages">
<start>7</start>
<end>17</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1981</date>
<detail type="volume">
<caption>vol.</caption>
<number>104</number>
</detail>
<extent unit="pages">
<start>7</start>
<end>17</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit118">
<titleInfo>
<title>Why is the patient with lead intoxication not light sensitive</title>
</titleInfo>
<name type="personal">
<namePart type="given">B.</namePart>
<namePart type="family">Haeger‐Aronsen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Haeger‐Aronsen B. Why is the patient with lead intoxication not light sensitive Acta Derm Venereol 1982; 100:67–71.</note>
<part>
<date>1982</date>
<detail type="volume">
<caption>vol.</caption>
<number>100</number>
</detail>
<extent unit="pages">
<start>67</start>
<end>71</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Acta Derm Venereol</title>
</titleInfo>
<part>
<date>1982</date>
<detail type="volume">
<caption>vol.</caption>
<number>100</number>
</detail>
<extent unit="pages">
<start>67</start>
<end>71</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit119">
<titleInfo>
<title>Hereditary coproporphyria. Photosensitivity, jaundice and neuropsychiatric manifestations associated with pregnancy</title>
</titleInfo>
<name type="personal">
<namePart type="given">JAA</namePart>
<namePart type="family">Hunter</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">SA</namePart>
<namePart type="family">Khan</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">E</namePart>
<namePart type="family">Hope</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Hunter JAA, Khan SA, Hope E, et al. Hereditary coproporphyria. Photosensitivity, jaundice and neuropsychiatric manifestations associated with pregnancy. Br J Dermatol 1971; 84:301–310.</note>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>84</number>
</detail>
<extent unit="pages">
<start>301</start>
<end>310</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>84</number>
</detail>
<extent unit="pages">
<start>301</start>
<end>310</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit120">
<titleInfo>
<title>Hereditary coproporphyria presenting with photosensitivity induced by the contraceptive pill</title>
</titleInfo>
<name type="personal">
<namePart type="given">DT</namePart>
<namePart type="family">Roberts</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MJ</namePart>
<namePart type="family">Brodie</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MR</namePart>
<namePart type="family">Moore</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Roberts DT, Brodie MJ, Moore MR, et al. Hereditary coproporphyria presenting with photosensitivity induced by the contraceptive pill. Br J Dermatol 1977; 96:549–554.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>96</number>
</detail>
<extent unit="pages">
<start>549</start>
<end>554</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>96</number>
</detail>
<extent unit="pages">
<start>549</start>
<end>554</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit121">
<titleInfo>
<title>Porphyria cutanea tarda</title>
</titleInfo>
<name type="personal">
<namePart type="given">AV</namePart>
<namePart type="family">Benedetto</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JS</namePart>
<namePart type="family">Taylor</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Benedetto AV, Taylor JS. Porphyria cutanea tarda. Cuds 1978; 21:483–488.</note>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>21</number>
</detail>
<extent unit="pages">
<start>483</start>
<end>488</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Cuds</title>
</titleInfo>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>21</number>
</detail>
<extent unit="pages">
<start>483</start>
<end>488</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit122">
<titleInfo>
<title>Cutaneous porphyria. Observations on 111 cases in three racial groups</title>
</titleInfo>
<name type="personal">
<namePart type="given">L.</namePart>
<namePart type="family">Eales</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Eales L. Cutaneous porphyria. Observations on 111 cases in three racial groups. S Afr J Lab Clin Med 1960; 6:63–86.</note>
<part>
<date>1960</date>
<detail type="volume">
<caption>vol.</caption>
<number>6</number>
</detail>
<extent unit="pages">
<start>63</start>
<end>86</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>S Afr J Lab Clin Med</title>
</titleInfo>
<part>
<date>1960</date>
<detail type="volume">
<caption>vol.</caption>
<number>6</number>
</detail>
<extent unit="pages">
<start>63</start>
<end>86</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit123">
<titleInfo>
<title>Biochemical diagnosis of the porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">MR</namePart>
<namePart type="family">Moore</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">PB</namePart>
<namePart type="family">Disler</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Moore MR, Disler PB. Biochemical diagnosis of the porphyrias. Clin Dermatol 1985; 3:24–40.</note>
<part>
<date>1985</date>
<detail type="volume">
<caption>vol.</caption>
<number>3</number>
</detail>
<extent unit="pages">
<start>24</start>
<end>40</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Clin Dermatol</title>
</titleInfo>
<part>
<date>1985</date>
<detail type="volume">
<caption>vol.</caption>
<number>3</number>
</detail>
<extent unit="pages">
<start>24</start>
<end>40</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit124">
<titleInfo>
<title>Iron metabolism in the porphyrias</title>
</titleInfo>
<name type="personal">
<namePart type="given">A.</namePart>
<namePart type="family">Turnbull</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Turnbull A. Iron metabolism in the porphyrias. Br J Dermatol 1971; 84:380–383.</note>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>84</number>
</detail>
<extent unit="pages">
<start>380</start>
<end>383</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>84</number>
</detail>
<extent unit="pages">
<start>380</start>
<end>383</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit125">
<titleInfo>
<title>Iron storage in porphyria cutanea tarda</title>
</titleInfo>
<name type="personal">
<namePart type="given">O</namePart>
<namePart type="family">Lundvall</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Weinfeld</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">P.</namePart>
<namePart type="family">Lundin</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Lundvall O, Weinfeld A, Lundin P. Iron storage in porphyria cutanea tarda. Acta Med Scand 1970; 188:37–53.</note>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>188</number>
</detail>
<extent unit="pages">
<start>37</start>
<end>53</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Acta Med Scand</title>
</titleInfo>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>188</number>
</detail>
<extent unit="pages">
<start>37</start>
<end>53</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit126">
<titleInfo>
<title>Liver in porphyria cutanea tarda</title>
</titleInfo>
<name type="personal">
<namePart type="given">GC</namePart>
<namePart type="family">Topi</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">CL</namePart>
<namePart type="family">D'Alessandre</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>book-chapter</genre>
<relatedItem type="host">
<titleInfo>
<title>Porphyrins in human diseases</title>
</titleInfo>
<originInfo>
<publisher>Karger</publisher>
</originInfo>
<part>
<date>1976</date>
<extent unit="pages">
<start>312</start>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit127">
<titleInfo>
<title>Allgemein Symptome der spaten Hautoporphyrie (porphyria cutanea tarda) als hinweise fur deren Behandlung</title>
</titleInfo>
<name type="personal">
<namePart type="given">H.</namePart>
<namePart type="family">Ippen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Ippen H. Allgemein Symptome der spaten Hautoporphyrie (porphyria cutanea tarda) als hinweise fur deren Behandlung. Dtsch Med Wochenschr 1961; 86:127–133.</note>
<part>
<date>1961</date>
<detail type="volume">
<caption>vol.</caption>
<number>86</number>
</detail>
<extent unit="pages">
<start>127</start>
<end>133</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Dtsch Med Wochenschr</title>
</titleInfo>
<part>
<date>1961</date>
<detail type="volume">
<caption>vol.</caption>
<number>86</number>
</detail>
<extent unit="pages">
<start>127</start>
<end>133</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit128">
<titleInfo>
<title>Porphyria cutanea tarda symptomatica</title>
</titleInfo>
<name type="personal">
<namePart type="given">JH</namePart>
<namePart type="family">Epstein</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Epstein JH. Porphyria cutanea tarda symptomatica. Arch Dermatol 1965; 92:286–290.</note>
<part>
<date>1965</date>
<detail type="volume">
<caption>vol.</caption>
<number>92</number>
</detail>
<extent unit="pages">
<start>286</start>
<end>290</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1965</date>
<detail type="volume">
<caption>vol.</caption>
<number>92</number>
</detail>
<extent unit="pages">
<start>286</start>
<end>290</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit129">
<titleInfo>
<title>The effect of phlebotomy therapy in porphyria cutanea tarda</title>
</titleInfo>
<name type="personal">
<namePart type="given">O.</namePart>
<namePart type="family">Lundvall</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Lundvall O. The effect of phlebotomy therapy in porphyria cutanea tarda. Acta Med Scand 1971; 189: 33–49.</note>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>189</number>
</detail>
<extent unit="pages">
<start>33</start>
<end>49</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Acta Med Scand</title>
</titleInfo>
<part>
<date>1971</date>
<detail type="volume">
<caption>vol.</caption>
<number>189</number>
</detail>
<extent unit="pages">
<start>33</start>
<end>49</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit130">
<titleInfo>
<title>Continuous subcutaneous administration of deferoxamine in patients with iron overload</title>
</titleInfo>
<name type="personal">
<namePart type="given">RO</namePart>
<namePart type="family">Propper</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">B</namePart>
<namePart type="family">Cooper</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">RR</namePart>
<namePart type="family">Rufo</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Propper RO, Cooper B, Rufo RR, et al. Continuous subcutaneous administration of deferoxamine in patients with iron overload. N Engl J Med 1977; 297:418–423.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>297</number>
</detail>
<extent unit="pages">
<start>418</start>
<end>423</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>297</number>
</detail>
<extent unit="pages">
<start>418</start>
<end>423</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit131">
<titleInfo>
<title>Clinical trial of desferrioxamine entrapped in red cell ghosts</title>
</titleInfo>
<name type="personal">
<namePart type="given">R</namePart>
<namePart type="family">Green</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">J</namePart>
<namePart type="family">Lamon</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">D.</namePart>
<namePart type="family">Curran</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Green R, Lamon J, Curran D. Clinical trial of desferrioxamine entrapped in red cell ghosts. Lancet 1980; ii:327–330.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>ii</number>
</detail>
<extent unit="pages">
<start>327</start>
<end>330</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Lancet</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>ii</number>
</detail>
<extent unit="pages">
<start>327</start>
<end>330</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit132">
<titleInfo>
<title>Current concepts of cutaneous porphyria and its treatment with particular reference to the use of sodium calcium edetate</title>
</titleInfo>
<name type="personal">
<namePart type="given">GF</namePart>
<namePart type="family">Donald</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">GA</namePart>
<namePart type="family">Hunter</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">W</namePart>
<namePart type="family">Roman</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Donald GF, Hunter GA, Roman W, et al. Current concepts of cutaneous porphyria and its treatment with particular reference to the use of sodium calcium edetate. Br J Dermatol 1970; 82:70–75.</note>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>82</number>
</detail>
<extent unit="pages">
<start>70</start>
<end>75</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>82</number>
</detail>
<extent unit="pages">
<start>70</start>
<end>75</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit133">
<titleInfo>
<title>Treatment of hemodialysis‐related porphyria cutanea tarda with deferoxamine</title>
</titleInfo>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Praga</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">E</namePart>
<namePart type="family">de Salamanca</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Andres</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Praga M, de Salamanca E, Andres A, et al. Treatment of hemodialysis‐related porphyria cutanea tarda with deferoxamine. N Engl J Med 1987; 316:547–548.</note>
<part>
<date>1987</date>
<detail type="volume">
<caption>vol.</caption>
<number>316</number>
</detail>
<extent unit="pages">
<start>547</start>
<end>548</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1987</date>
<detail type="volume">
<caption>vol.</caption>
<number>316</number>
</detail>
<extent unit="pages">
<start>547</start>
<end>548</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit134">
<titleInfo>
<title>Erythropoietin for the treatment of porphyria cutanea tarda in a patient on long‐term hemodialysis</title>
</titleInfo>
<name type="personal">
<namePart type="given">KE</namePart>
<namePart type="family">Anderson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">DE</namePart>
<namePart type="family">Goeger</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">RW</namePart>
<namePart type="family">Carson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Anderson KE, Goeger DE, Carson RW, et al. Erythropoietin for the treatment of porphyria cutanea tarda in a patient on long‐term hemodialysis. N Engl J Med 1990; 322:315–317.</note>
<part>
<date>1990</date>
<detail type="volume">
<caption>vol.</caption>
<number>322</number>
</detail>
<extent unit="pages">
<start>315</start>
<end>317</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1990</date>
<detail type="volume">
<caption>vol.</caption>
<number>322</number>
</detail>
<extent unit="pages">
<start>315</start>
<end>317</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit135">
<titleInfo>
<title>Traitement d'un cas de prophyrie cutanee tardive par les plasmaphere‐ses</title>
</titleInfo>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Dupre</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">J‐L</namePart>
<namePart type="family">Bonafe</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">J‐P</namePart>
<namePart type="family">Callot</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Dupre A, Bonafe J‐L, Callot J‐P, et al. Traitement d'un cas de prophyrie cutanee tardive par les plasmaphere‐ses. Ann Dermatol Venereol 1980; 107:693–695.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>107</number>
</detail>
<extent unit="pages">
<start>693</start>
<end>695</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Ann Dermatol Venereol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>107</number>
</detail>
<extent unit="pages">
<start>693</start>
<end>695</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit136">
<titleInfo>
<title>Small volume plasma‐pheresis in the management of porphyria cutanea tarda</title>
</titleInfo>
<name type="personal">
<namePart type="given">S</namePart>
<namePart type="family">Miyauchi</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">S</namePart>
<namePart type="family">Shiraishi</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">Y.</namePart>
<namePart type="family">Miki</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Miyauchi S, Shiraishi S, Miki Y. Small volume plasma‐pheresis in the management of porphyria cutanea tarda. Arch Dermatol 1983; 119:752–755.</note>
<part>
<date>1983</date>
<detail type="volume">
<caption>vol.</caption>
<number>119</number>
</detail>
<extent unit="pages">
<start>752</start>
<end>755</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1983</date>
<detail type="volume">
<caption>vol.</caption>
<number>119</number>
</detail>
<extent unit="pages">
<start>752</start>
<end>755</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit137">
<titleInfo>
<title>Porphyria cutanea tarda Remission following chloroquine administration without adverse effects</title>
</titleInfo>
<name type="personal">
<namePart type="given">El</namePart>
<namePart type="family">Saltzer</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">AG</namePart>
<namePart type="family">Redeker</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JW</namePart>
<namePart type="family">Wilson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Saltzer El, Redeker AG, Wilson JW. Porphyria cutanea tarda Remission following chloroquine administration without adverse effects. Arch Dermatol 1968; 98: 496–498.</note>
<part>
<date>1968</date>
<detail type="volume">
<caption>vol.</caption>
<number>98</number>
</detail>
<extent unit="pages">
<start>496</start>
<end>498</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1968</date>
<detail type="volume">
<caption>vol.</caption>
<number>98</number>
</detail>
<extent unit="pages">
<start>496</start>
<end>498</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit138">
<titleInfo>
<title>Liver changes in porphyria cutanea tarda patients treated with chloroquine</title>
</titleInfo>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Chlumska</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">J</namePart>
<namePart type="family">Chlumsky</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">L.</namePart>
<namePart type="family">Malina</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Chlumska A, Chlumsky J, Malina L. Liver changes in porphyria cutanea tarda patients treated with chloroquine. Br J Dermatol 1980; 102:261–266.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>102</number>
</detail>
<extent unit="pages">
<start>261</start>
<end>266</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>102</number>
</detail>
<extent unit="pages">
<start>261</start>
<end>266</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit139">
<titleInfo>
<title>Porphyria variegata: failure of chloroquine treatment</title>
</titleInfo>
<name type="personal">
<namePart type="given">M</namePart>
<namePart type="family">Cramers</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">LV</namePart>
<namePart type="family">Jepsen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Cramers M, Jepsen LV. Porphyria variegata: failure of chloroquine treatment. Acta Derm Venereol 1980; 60: 89–91.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>60</number>
</detail>
<extent unit="pages">
<start>89</start>
<end>91</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Acta Derm Venereol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>60</number>
</detail>
<extent unit="pages">
<start>89</start>
<end>91</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit140">
<titleInfo>
<title>Porphyria ery‐thropoetica Gunther und chloroquine</title>
</titleInfo>
<name type="personal">
<namePart type="given">H</namePart>
<namePart type="family">Ippen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">K</namePart>
<namePart type="family">Tillmann</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">S</namePart>
<namePart type="family">Seubert</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Ippen H, Tillmann K, Seubert S, et al. Porphyria ery‐thropoetica Gunther und chloroquine. Klinische Wochen-schrift 1978; 56:623–624.</note>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>56</number>
</detail>
<extent unit="pages">
<start>623</start>
<end>624</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Klinische Wochen-schrift</title>
</titleInfo>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>56</number>
</detail>
<extent unit="pages">
<start>623</start>
<end>624</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit141">
<titleInfo>
<title>Treatment of porphyria cutanea tarda with chloroquine and phlebotomy</title>
</titleInfo>
<name type="personal">
<namePart type="given">G</namePart>
<namePart type="family">Swanbeck</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">G.</namePart>
<namePart type="family">Wennersten</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Swanbeck G, Wennersten G. Treatment of porphyria cutanea tarda with chloroquine and phlebotomy. Br J Dermatol 1977; 97:77–81.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>97</number>
</detail>
<extent unit="pages">
<start>77</start>
<end>81</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>97</number>
</detail>
<extent unit="pages">
<start>77</start>
<end>81</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit142">
<titleInfo>
<title>Metabolic alkalinization therapy in porphyria cutanea tarda</title>
</titleInfo>
<name type="personal">
<namePart type="given">HO</namePart>
<namePart type="family">Perry</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MC</namePart>
<namePart type="family">Mullanax</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">SE</namePart>
<namePart type="family">Wiegand</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Perry HO, Mullanax MC, Wiegand SE. Metabolic alkalinization therapy in porphyria cutanea tarda. Arch Dermatol 1970; 102:359–367.</note>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>102</number>
</detail>
<extent unit="pages">
<start>359</start>
<end>367</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>102</number>
</detail>
<extent unit="pages">
<start>359</start>
<end>367</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit143">
<titleInfo>
<title>Erythropoietic porphyria Two cases and the results of alkalinization</title>
</titleInfo>
<name type="personal">
<namePart type="given">GS</namePart>
<namePart type="family">Stretcher</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Stretcher GS. Erythropoietic porphyria Two cases and the results of alkalinization. Arch Dermatol 1977; 113: 1553–1557.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>113</number>
</detail>
<extent unit="pages">
<start>1553</start>
<end>1557</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>113</number>
</detail>
<extent unit="pages">
<start>1553</start>
<end>1557</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit144">
<titleInfo>
<title>Variegate porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">H.</namePart>
<namePart type="family">Wechsler</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Wechsler H. Variegate porphyria. Arch Dermatol 1975; 111:926–927.</note>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>111</number>
</detail>
<extent unit="pages">
<start>926</start>
<end>927</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1975</date>
<detail type="volume">
<caption>vol.</caption>
<number>111</number>
</detail>
<extent unit="pages">
<start>926</start>
<end>927</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit145">
<titleInfo>
<title>Therapeutic efficacy of oral charcoal in congenital erythropoietic porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">NR</namePart>
<namePart type="family">Pimstone</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">SN</namePart>
<namePart type="family">Gandhi</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">SK</namePart>
<namePart type="family">Mukerji</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Pimstone NR, Gandhi SN, Mukerji SK. Therapeutic efficacy of oral charcoal in congenital erythropoietic porphyria. N Engl J Med 1987; 316:390–393.</note>
<part>
<date>1987</date>
<detail type="volume">
<caption>vol.</caption>
<number>316</number>
</detail>
<extent unit="pages">
<start>390</start>
<end>393</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1987</date>
<detail type="volume">
<caption>vol.</caption>
<number>316</number>
</detail>
<extent unit="pages">
<start>390</start>
<end>393</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit146">
<titleInfo>
<title>Protoporphyrin removal in intrahepatic porphyrostasis</title>
</titleInfo>
<name type="personal">
<namePart type="given">JC</namePart>
<namePart type="family">Kniffen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Kniffen JC. Protoporphyrin removal in intrahepatic porphyrostasis. Gastroenterol 1970; 88:1027–1030.</note>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>88</number>
</detail>
<extent unit="pages">
<start>1027</start>
<end>1030</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Gastroenterol</title>
</titleInfo>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>88</number>
</detail>
<extent unit="pages">
<start>1027</start>
<end>1030</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit147">
<titleInfo>
<title>The regulation of heme synthesis related to drug metabolism</title>
</titleInfo>
<name type="personal">
<namePart type="given">TR</namePart>
<namePart type="family">Tephly</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">C</namePart>
<namePart type="family">Webb</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">P</namePart>
<namePart type="family">Trussler</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Tephly TR, Webb C, Trussler P, et al. The regulation of heme synthesis related to drug metabolism. Drug Metab Dis 1973; 1:259–266.</note>
<part>
<date>1973</date>
<detail type="volume">
<caption>vol.</caption>
<number>1</number>
</detail>
<extent unit="pages">
<start>259</start>
<end>266</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Drug Metab Dis</title>
</titleInfo>
<part>
<date>1973</date>
<detail type="volume">
<caption>vol.</caption>
<number>1</number>
</detail>
<extent unit="pages">
<start>259</start>
<end>266</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit148">
<titleInfo>
<title>Porphyria cutanea tarda: normalisierung der porphyrin‐ausscheidung unter p‐aminobenzoat (Potaba)</title>
</titleInfo>
<name type="personal">
<namePart type="given">G</namePart>
<namePart type="family">Goers</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">T</namePart>
<namePart type="family">Krieg</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">K.</namePart>
<namePart type="family">Bolsen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Goers G, Krieg T, Bolsen K. Porphyria cutanea tarda: normalisierung der porphyrin‐ausscheidung unter p‐aminobenzoat (Potaba). Arch Dermatol Res 1976; 255: 331–335.</note>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>255</number>
</detail>
<extent unit="pages">
<start>331</start>
<end>335</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol Res</title>
</titleInfo>
<part>
<date>1976</date>
<detail type="volume">
<caption>vol.</caption>
<number>255</number>
</detail>
<extent unit="pages">
<start>331</start>
<end>335</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit149">
<titleInfo>
<title>Haematin therapy and leucocyte delta‐aminolaevulinic‐acid‐synthase activity in prolonged attack of acute porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">KEL</namePart>
<namePart type="family">McColl</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">GT</namePart>
<namePart type="family">Thompson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MR</namePart>
<namePart type="family">Moore</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">McColl KEL, Thompson GT, Moore MR, et al. Haematin therapy and leucocyte delta‐aminolaevulinic‐acid‐synthase activity in prolonged attack of acute porphyria. Lancet 1979; i: 133–134.</note>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>i</number>
</detail>
<extent unit="pages">
<start>133</start>
<end>134</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Lancet</title>
</titleInfo>
<part>
<date>1979</date>
<detail type="volume">
<caption>vol.</caption>
<number>i</number>
</detail>
<extent unit="pages">
<start>133</start>
<end>134</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit150">
<titleInfo>
<title>Effect of haem arginate therapy on porphyrin metabolism and mixed function oxygenase activity in acute hepatic porphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">Herrick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">KEL</namePart>
<namePart type="family">McColl</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">A</namePart>
<namePart type="family">McLellan</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Herrick A, McColl KEL, McLellan A, et al. Effect of haem arginate therapy on porphyrin metabolism and mixed function oxygenase activity in acute hepatic porphyria. Lancet 1987; ii: 1178–1179.</note>
<part>
<date>1987</date>
<detail type="volume">
<caption>vol.</caption>
<number>ii</number>
</detail>
<extent unit="pages">
<start>1178</start>
<end>1179</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Lancet</title>
</titleInfo>
<part>
<date>1987</date>
<detail type="volume">
<caption>vol.</caption>
<number>ii</number>
</detail>
<extent unit="pages">
<start>1178</start>
<end>1179</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit151">
<titleInfo>
<title>Congenital erythropoietic porphyria The effect of light shielding</title>
</titleInfo>
<name type="personal">
<namePart type="given">L</namePart>
<namePart type="family">Eriksen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">F</namePart>
<namePart type="family">Hofstad</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">M.</namePart>
<namePart type="family">Seip</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Eriksen L, Hofstad F, Seip M. Congenital erythropoietic porphyria The effect of light shielding. Acta Paediatr Scand 1973; 62:385–390.</note>
<part>
<date>1973</date>
<detail type="volume">
<caption>vol.</caption>
<number>62</number>
</detail>
<extent unit="pages">
<start>385</start>
<end>390</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Acta Paediatr Scand</title>
</titleInfo>
<part>
<date>1973</date>
<detail type="volume">
<caption>vol.</caption>
<number>62</number>
</detail>
<extent unit="pages">
<start>385</start>
<end>390</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit152">
<titleInfo>
<title>Efficiency of opaque photoprotective agents in the visible light range</title>
</titleInfo>
<name type="personal">
<namePart type="given">ET</namePart>
<namePart type="family">Kaye</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JA</namePart>
<namePart type="family">Levin</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">IH</namePart>
<namePart type="family">Blank</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Kaye ET, Levin JA, Blank IH, et al. Efficiency of opaque photoprotective agents in the visible light range. Arch Dermatol 1991; 127:351–355.</note>
<part>
<date>1991</date>
<detail type="volume">
<caption>vol.</caption>
<number>127</number>
</detail>
<extent unit="pages">
<start>351</start>
<end>355</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1991</date>
<detail type="volume">
<caption>vol.</caption>
<number>127</number>
</detail>
<extent unit="pages">
<start>351</start>
<end>355</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit153">
<titleInfo>
<title>Porphyria cutanea tarda: response to vitamin E. A review and 2 case reports</title>
</titleInfo>
<name type="personal">
<namePart type="given">S JR</namePart>
<namePart type="family">Ayres</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">R.</namePart>
<namePart type="family">Mihan</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Ayres S JR, Mihan R. Porphyria cutanea tarda: response to vitamin E. A review and 2 case reports. Cutis 1978; 22:50–52.</note>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>22</number>
</detail>
<extent unit="pages">
<start>50</start>
<end>52</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Cutis</title>
</titleInfo>
<part>
<date>1978</date>
<detail type="volume">
<caption>vol.</caption>
<number>22</number>
</detail>
<extent unit="pages">
<start>50</start>
<end>52</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit154">
<titleInfo>
<title>Beta‐carotene as a photoprotective agent in erythropoietic protoporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">MM</namePart>
<namePart type="family">Mathews‐Roth</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MA</namePart>
<namePart type="family">Pathak</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">TB</namePart>
<namePart type="family">Fitzpatrick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Mathews‐Roth MM, Pathak MA, Fitzpatrick TB, et al. Beta‐carotene as a photoprotective agent in erythropoietic protoporphyria. N Engl J Med 1970; 282:1231–1234.</note>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>282</number>
</detail>
<extent unit="pages">
<start>1231</start>
<end>1234</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1970</date>
<detail type="volume">
<caption>vol.</caption>
<number>282</number>
</detail>
<extent unit="pages">
<start>1231</start>
<end>1234</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit155">
<titleInfo>
<title>Beta‐carotene therapy for erythropoietic protoporphyria and other photosensitivity diseases</title>
</titleInfo>
<name type="personal">
<namePart type="given">MM</namePart>
<namePart type="family">Mathews‐Roth</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MA</namePart>
<namePart type="family">Pathak</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">TB</namePart>
<namePart type="family">Fitzpatrick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Mathews‐Roth MM, Pathak MA, Fitzpatrick TB, et al. Beta‐carotene therapy for erythropoietic protoporphyria and other photosensitivity diseases. Arch Dermatol 1977; 113:1229–1232.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>113</number>
</detail>
<extent unit="pages">
<start>1229</start>
<end>1232</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>113</number>
</detail>
<extent unit="pages">
<start>1229</start>
<end>1232</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit156">
<titleInfo>
<title>Photoprotection in erythropoietic protoporphyria: mechanism of photoprotection by beta‐carotene</title>
</titleInfo>
<name type="personal">
<namePart type="given">AN</namePart>
<namePart type="family">Moshell</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">L.</namePart>
<namePart type="family">Bjornson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Moshell AN, Bjornson L. Photoprotection in erythropoietic protoporphyria: mechanism of photoprotection by beta‐carotene. J Invest Dermatol 1977; 68:157–160.</note>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>68</number>
</detail>
<extent unit="pages">
<start>157</start>
<end>160</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>J Invest Dermatol</title>
</titleInfo>
<part>
<date>1977</date>
<detail type="volume">
<caption>vol.</caption>
<number>68</number>
</detail>
<extent unit="pages">
<start>157</start>
<end>160</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit157">
<titleInfo>
<title>Transfusion therapy in a patient with erythropoietic protoporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">MA</namePart>
<namePart type="family">Bechtel</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">SJ</namePart>
<namePart type="family">Bertolone</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">SJ</namePart>
<namePart type="family">Hodge</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Bechtel MA, Bertolone SJ, Hodge SJ. Transfusion therapy in a patient with erythropoietic protoporphyria. Arch Dermatol 1981; 117:99–101.</note>
<part>
<date>1981</date>
<detail type="volume">
<caption>vol.</caption>
<number>117</number>
</detail>
<extent unit="pages">
<start>99</start>
<end>101</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Arch Dermatol</title>
</titleInfo>
<part>
<date>1981</date>
<detail type="volume">
<caption>vol.</caption>
<number>117</number>
</detail>
<extent unit="pages">
<start>99</start>
<end>101</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit158">
<titleInfo>
<title>Complete suppression of the symptoms of congenital erythropoietic porphyria by long‐term treatment with high‐level transfusions</title>
</titleInfo>
<name type="personal">
<namePart type="given">S</namePart>
<namePart type="family">Piomelli</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">MB</namePart>
<namePart type="family">Pob‐Fitzpatrick</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">C</namePart>
<namePart type="family">Seaman</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Piomelli S, Pob‐Fitzpatrick MB, Seaman C, et al. Complete suppression of the symptoms of congenital erythropoietic porphyria by long‐term treatment with high‐level transfusions. N Engl J Med 1986; 314:1029–1031.</note>
<part>
<date>1986</date>
<detail type="volume">
<caption>vol.</caption>
<number>314</number>
</detail>
<extent unit="pages">
<start>1029</start>
<end>1031</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>N Engl J Med</title>
</titleInfo>
<part>
<date>1986</date>
<detail type="volume">
<caption>vol.</caption>
<number>314</number>
</detail>
<extent unit="pages">
<start>1029</start>
<end>1031</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit159">
<titleInfo>
<title>Variegate porphyria Clinical and laboratory features</title>
</titleInfo>
<name type="personal">
<namePart type="given">TJ</namePart>
<namePart type="family">Corey</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">VA</namePart>
<namePart type="family">DeLeo</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">H</namePart>
<namePart type="family">Christiansen</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Corey TJ, DeLeo VA, Christiansen H, et al. Variegate porphyria Clinical and laboratory features. J Am Acad Dermatol 1980; 2:36–43.</note>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>2</number>
</detail>
<extent unit="pages">
<start>36</start>
<end>43</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>J Am Acad Dermatol</title>
</titleInfo>
<part>
<date>1980</date>
<detail type="volume">
<caption>vol.</caption>
<number>2</number>
</detail>
<extent unit="pages">
<start>36</start>
<end>43</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit160">
<titleInfo>
<title>Chenodeoxycholic acid treatment in erythrohepatic protoporphyria</title>
</titleInfo>
<name type="personal">
<namePart type="given">J</namePart>
<namePart type="family">Van Hattum</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">H</namePart>
<namePart type="family">Baart de la Faille</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JHP</namePart>
<namePart type="family">Wilson</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Van Hattum J, Baart de la Faille H, Wilson JHP, et al. Chenodeoxycholic acid treatment in erythrohepatic protoporphyria. Br J Dermatol 1984; 11:480–481.</note>
<part>
<date>1984</date>
<detail type="volume">
<caption>vol.</caption>
<number>11</number>
</detail>
<extent unit="pages">
<start>480</start>
<end>481</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1984</date>
<detail type="volume">
<caption>vol.</caption>
<number>11</number>
</detail>
<extent unit="pages">
<start>480</start>
<end>481</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<relatedItem type="references" displayLabel="cit161">
<titleInfo>
<title>Inhibition of photosensitivity in erythropoietic protoporphyria with terfenadine</title>
</titleInfo>
<name type="personal">
<namePart type="given">PM</namePart>
<namePart type="family">Farr</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">BL</namePart>
<namePart type="family">Diffey</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<name type="personal">
<namePart type="given">JNS.</namePart>
<namePart type="family">Matthews</namePart>
<role>
<roleTerm type="text">author</roleTerm>
</role>
</name>
<genre>journal-article</genre>
<note type="citation/reference">Farr PM, Diffey BL, Matthews JNS. Inhibition of photosensitivity in erythropoietic protoporphyria with terfenadine. Br J Dermatol 1990; 122:809–815.</note>
<part>
<date>1990</date>
<detail type="volume">
<caption>vol.</caption>
<number>122</number>
</detail>
<extent unit="pages">
<start>809</start>
<end>815</end>
</extent>
</part>
<relatedItem type="host">
<titleInfo>
<title>Br J Dermatol</title>
</titleInfo>
<part>
<date>1990</date>
<detail type="volume">
<caption>vol.</caption>
<number>122</number>
</detail>
<extent unit="pages">
<start>809</start>
<end>815</end>
</extent>
</part>
</relatedItem>
</relatedItem>
<identifier type="istex">7A7385B2C1D99839C39032A6FED1A69554FD09FC</identifier>
<identifier type="ark">ark:/67375/WNG-K3T5GTGP-Q</identifier>
<identifier type="DOI">10.1111/j.1365-4362.1992.tb02712.x</identifier>
<identifier type="ArticleID">IJD527</identifier>
<accessCondition type="use and reproduction" contentType="copyright">© Wiley. All rights reserved.</accessCondition>
<recordInfo>
<recordContentSource authority="ISTEX" authorityURI="https://loaded-corpus.data.istex.fr" valueURI="https://loaded-corpus.data.istex.fr/ark:/67375/XBH-L0C46X92-X">wiley</recordContentSource>
<recordOrigin>Converted from (version ) to MODS version 3.6.</recordOrigin>
<recordCreationDate encoding="w3cdtf">2019-11-15</recordCreationDate>
</recordInfo>
</mods>
<json:item>
<extension>json</extension>
<original>false</original>
<mimetype>application/json</mimetype>
<uri>https://api.istex.fr/ark:/67375/WNG-K3T5GTGP-Q/record.json</uri>
</json:item>
</metadata>
<serie></serie>
</istex>
</record>

Pour manipuler ce document sous Unix (Dilib)

EXPLOR_STEP=$WICRI_ROOT/Sante/explor/ChloroquineV1/Data/Istex/Corpus
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 001098 | SxmlIndent | more

Ou

HfdSelect -h $EXPLOR_AREA/Data/Istex/Corpus/biblio.hfd -nk 001098 | SxmlIndent | more

Pour mettre un lien sur cette page dans le réseau Wicri

{{Explor lien
   |wiki=    Sante
   |area=    ChloroquineV1
   |flux=    Istex
   |étape=   Corpus
   |type=    RBID
   |clé=     ISTEX:7A7385B2C1D99839C39032A6FED1A69554FD09FC
   |texte=   THE PORPHYRIAS
}}

Wicri

This area was generated with Dilib version V0.6.33.
Data generation: Wed Mar 25 22:43:59 2020. Site generation: Sun Jan 31 12:44:45 2021