A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome
Identifieur interne : 002423 ( Main/Exploration ); précédent : 002422; suivant : 002424A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome
Auteurs : S. C. Lee ; S. J. Yun ; J-B. Lee ; S-S. Lee ; Y. H. WonSource :
- British Journal of Dermatology [ 0007-0963 ] ; 2001-01.
Abstract
We report a 56‐year‐old Korean woman with porphyria cutanea tarda (PCT), showing multiple scarring bullae and hypertrichosis on sun‐exposed areas of skin with postinflammatory hyperpigmentation. Sclerodermoid changes were also found on both hands, the face and neck. The patient had suffered from CREST syndrome, manifesting with Raynaud’s phenomenon and sclerodactyly, for more than 15 years. Anticentromere antibody was positive. She had presented with splenomegaly 3 years before the development of PCT, and was diagnosed as having idiopathic myelofibrosis, based on bone marrow biopsy. In summary, she had had CREST syndrome for 15 years and later developed idiopathic myelofibrosis and PCT. This is the first reported case of PCT in association with idiopathic myelofibrosis and CREST syndrome.
Url:
DOI: 10.1046/j.1365-2133.2001.03971.x
Affiliations:
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C." last="Lee">S. C. Lee</name><affiliation><wicri:noCountry code="no comma">Departments of Dermatology and</wicri:noCountry></affiliation></author><author><name sortKey="Yun, S J" sort="Yun, S J" uniqKey="Yun S" first="S. J." last="Yun">S. J. Yun</name><affiliation><wicri:noCountry code="no comma">Departments of Dermatology and</wicri:noCountry></affiliation></author><author><name sortKey="Lee, J" sort="Lee, J" uniqKey="Lee J" first="J-B." last="Lee">J-B. Lee</name><affiliation><wicri:noCountry code="no comma">Departments of Dermatology and</wicri:noCountry></affiliation></author><author><name sortKey="Lee, S" sort="Lee, S" uniqKey="Lee S" first="S-S." last="Lee">S-S. Lee</name><affiliation><wicri:noCountry code="subField">(South)</wicri:noCountry></affiliation></author><author><name sortKey="Won, Y H" sort="Won, Y H" uniqKey="Won Y" first="Y. H." last="Won">Y. H. Won</name><affiliation><wicri:noCountry code="no comma">Departments of Dermatology and</wicri:noCountry></affiliation></author></analytic><monogr></monogr><series><title level="j" type="main">British Journal of Dermatology</title><title level="j" type="alt">BRITISH JOURNAL OF DERMATOLOGY</title><idno type="ISSN">0007-0963</idno><idno type="eISSN">1365-2133</idno><imprint><biblScope unit="vol">144</biblScope><biblScope unit="issue">1</biblScope><biblScope unit="page" from="182">182</biblScope><biblScope unit="page" to="185">185</biblScope><biblScope unit="page-count">4</biblScope><publisher>Blackwell Science Ltd</publisher><pubPlace>Oxford, UK</pubPlace><date type="published" when="2001-01">2001-01</date></imprint><idno type="ISSN">0007-0963</idno></series></biblStruct></sourceDesc><seriesStmt><idno type="ISSN">0007-0963</idno></seriesStmt></fileDesc><profileDesc><textClass></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">We report a 56‐year‐old Korean woman with porphyria cutanea tarda (PCT), showing multiple scarring bullae and hypertrichosis on sun‐exposed areas of skin with postinflammatory hyperpigmentation. Sclerodermoid changes were also found on both hands, the face and neck. The patient had suffered from CREST syndrome, manifesting with Raynaud’s phenomenon and sclerodactyly, for more than 15 years. Anticentromere antibody was positive. She had presented with splenomegaly 3 years before the development of PCT, and was diagnosed as having idiopathic myelofibrosis, based on bone marrow biopsy. In summary, she had had CREST syndrome for 15 years and later developed idiopathic myelofibrosis and PCT. This is the first reported case of PCT in association with idiopathic myelofibrosis and CREST syndrome.</div></front></TEI><affiliations><list></list><tree><noCountry><name sortKey="Lee, J" sort="Lee, J" uniqKey="Lee J" first="J-B." last="Lee">J-B. Lee</name><name sortKey="Lee, S" sort="Lee, S" uniqKey="Lee S" first="S-S." last="Lee">S-S. Lee</name><name sortKey="Lee, S C" sort="Lee, S C" uniqKey="Lee S" first="S. C." last="Lee">S. C. Lee</name><name sortKey="Won, Y H" sort="Won, Y H" uniqKey="Won Y" first="Y. H." last="Won">Y. H. Won</name><name sortKey="Yun, S J" sort="Yun, S J" uniqKey="Yun S" first="S. J." last="Yun">S. J. Yun</name></noCountry></tree></affiliations></record>Pour manipuler ce document sous Unix (Dilib)
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