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Spontaneous pneumomediastinum secondary to refractory dermatomyositis successfully treated with rituximab

Identifieur interne : 001665 ( Main/Exploration ); précédent : 001664; suivant : 001666

Spontaneous pneumomediastinum secondary to refractory dermatomyositis successfully treated with rituximab

Auteurs : Martin A. Lee [Royaume-Uni] ; David G. Hutchinson [Royaume-Uni]

Source :

RBID : ISTEX:01EF3373AFBCCAD4AB1530241638ACDC60D2D29F

English descriptors

Abstract

Abstract: Spontaneous pneumomediastinum has been described in patients with dermatomyositis (DM) and polymyositis (Korkmaz et al., Rheumatology 40:476–478, 2001; Maruoka et al., Mod Rheumatol 16:55–57, 2006; Kono et al., Ann Rheum Dis 59:372–376, 2000; Neves et al., Clin Rheumatol 26:105–107, 2007). Literature reviews suggest that this complication has a mortality of between 27% and 41% ( Kono et al., Ann Rheum Dis 59:372–376, 2000; Neves et al., Clin Rheumatol 26:105–107, 2007; Goff et al., Arthritis Rheum 61:108–118, 2009). This is the first report of rituximab being used successfully as part of the treatment for DM complicated by pneumomediastinum.

Url:
DOI: 10.1007/s10067-010-1399-1


Affiliations:


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Le document en format XML

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<div type="abstract" xml:lang="en">Abstract: Spontaneous pneumomediastinum has been described in patients with dermatomyositis (DM) and polymyositis (Korkmaz et al., Rheumatology 40:476–478, 2001; Maruoka et al., Mod Rheumatol 16:55–57, 2006; Kono et al., Ann Rheum Dis 59:372–376, 2000; Neves et al., Clin Rheumatol 26:105–107, 2007). Literature reviews suggest that this complication has a mortality of between 27% and 41% ( Kono et al., Ann Rheum Dis 59:372–376, 2000; Neves et al., Clin Rheumatol 26:105–107, 2007; Goff et al., Arthritis Rheum 61:108–118, 2009). This is the first report of rituximab being used successfully as part of the treatment for DM complicated by pneumomediastinum.</div>
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