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Reticular erythematous mucinosis and thrombocytopenic purpura

Identifieur interne : 003239 ( Main/Curation ); précédent : 003238; suivant : 003240

Reticular erythematous mucinosis and thrombocytopenic purpura

Auteurs : Suzanne W. Braddock [États-Unis] ; Catharine S. Davis [États-Unis] ; Richard B. Davis [États-Unis]

Source :

RBID : ISTEX:DA2BB316F69C20EB9E106EA3640EB7DEE2F279DF

English descriptors

Abstract

A case of reticular erythematous mucinosis associated with chronic idiopathic thrombocytopenic purpura and circulating immune complexes is described. We compare reticular erythematous mucinosis with the similar plaquelike cutaneous mucinosis. We discuss the apparent photosensitivity of reticular erythematous mucinosis and its possible relationship with altered states of immune function such as diabetes, thyroid disease, and neoplasia. The somewhat varied but characteristic histopathologic findings and staining are reviewed, including the characteristic perivascular and occasional perifollicular lymphocytic infiltrate and Alcian blue-positive dermal mucin. Treatment with antimalarial drugs still appears to be the most uniformly successful therapeutic approach to the management of this chronic dermatosis. Further research efforts should be directed at understanding its link with altered states of immune function.

Url:
DOI: 10.1016/S0190-9622(88)70246-7

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ISTEX:DA2BB316F69C20EB9E106EA3640EB7DEE2F279DF

Le document en format XML

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