Reticular erythematous mucinosis and thrombocytopenic purpura
Identifieur interne : 003310 ( Main/Merge ); précédent : 003309; suivant : 003311Reticular erythematous mucinosis and thrombocytopenic purpura
Auteurs : Suzanne W. Braddock [États-Unis] ; Catharine S. Davis [États-Unis] ; Richard B. Davis [États-Unis]Source :
- Journal of the American Academy of Dermatology [ 0190-9622 ] ; 1988.
English descriptors
- Teeft :
- Abdomen chest, Alcian, American academy, Antimalarial drugs, Arch dermatol, Braddock, Chest chest, Cutaneous, Dermal, Dermatol, Dermis, Discoid lupus erythematosus, Electron microscopy, Eruption, Erythematous, Fibroblast, Hautkr, Hyperthyroidism, Idiopathic, Idiopathic thrombocytopenic purpura, Immune, Immune complexes, Immune function, Mucin, Mucinosis, Other diseases, Photosensitivity, Plaquelike, Plaquelike cutaneous mucinosis, Platelet, Pruritus, Purpura, Rash, Reticular, Reticular erythematous mucinosis, Reticular erythematous mucinosis syndrome, Solar sensitivity, Solar simulator, Steigleder, Syndrome, Thrombocytopenic, Thrombocytopenic purpura, Viral, World literature.
Abstract
A case of reticular erythematous mucinosis associated with chronic idiopathic thrombocytopenic purpura and circulating immune complexes is described. We compare reticular erythematous mucinosis with the similar plaquelike cutaneous mucinosis. We discuss the apparent photosensitivity of reticular erythematous mucinosis and its possible relationship with altered states of immune function such as diabetes, thyroid disease, and neoplasia. The somewhat varied but characteristic histopathologic findings and staining are reviewed, including the characteristic perivascular and occasional perifollicular lymphocytic infiltrate and Alcian blue-positive dermal mucin. Treatment with antimalarial drugs still appears to be the most uniformly successful therapeutic approach to the management of this chronic dermatosis. Further research efforts should be directed at understanding its link with altered states of immune function.
Url:
DOI: 10.1016/S0190-9622(88)70246-7
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ISTEX:DA2BB316F69C20EB9E106EA3640EB7DEE2F279DFLe document en format XML
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<term>Arch dermatol</term>
<term>Braddock</term>
<term>Chest chest</term>
<term>Cutaneous</term>
<term>Dermal</term>
<term>Dermatol</term>
<term>Dermis</term>
<term>Discoid lupus erythematosus</term>
<term>Electron microscopy</term>
<term>Eruption</term>
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<term>Photosensitivity</term>
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<front><div type="abstract">A case of reticular erythematous mucinosis associated with chronic idiopathic thrombocytopenic purpura and circulating immune complexes is described. We compare reticular erythematous mucinosis with the similar plaquelike cutaneous mucinosis. We discuss the apparent photosensitivity of reticular erythematous mucinosis and its possible relationship with altered states of immune function such as diabetes, thyroid disease, and neoplasia. The somewhat varied but characteristic histopathologic findings and staining are reviewed, including the characteristic perivascular and occasional perifollicular lymphocytic infiltrate and Alcian blue-positive dermal mucin. Treatment with antimalarial drugs still appears to be the most uniformly successful therapeutic approach to the management of this chronic dermatosis. Further research efforts should be directed at understanding its link with altered states of immune function.</div>
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