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Nonspecific interstitial pneumonia in refractory systemic juvenile idiopathic arthritis responded to tocilizumab treatment.

Identifieur interne : 002681 ( Ncbi/Merge ); précédent : 002680; suivant : 002682

Nonspecific interstitial pneumonia in refractory systemic juvenile idiopathic arthritis responded to tocilizumab treatment.

Auteurs : Maynart Sukharomana [Thaïlande] ; Kanokporn Udomittipong [Thaïlande] ; Ruchira Ruangchira-Urai [Thaïlande] ; Sirirat Charuvanij [Thaïlande]

Source :

RBID : pubmed:31837211

Abstract

Nonspecific interstitial pneumonia (NSIP) is a rare pulmonary complication in systemic juvenile idiopathic arthritis (SJIA).

DOI: 10.12932/AP-050819-0616
PubMed: 31837211

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pubmed:31837211

Le document en format XML

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<name sortKey="Sukharomana, Maynart" sort="Sukharomana, Maynart" uniqKey="Sukharomana M" first="Maynart" last="Sukharomana">Maynart Sukharomana</name>
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<nlm:affiliation>Division of Rheumatology, Department of Pediatrics, Faculty of Medicine Siriraj Hospital, Mahidol University, Bangkok, Thailand.</nlm:affiliation>
<country xml:lang="fr">Thaïlande</country>
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<name sortKey="Udomittipong, Kanokporn" sort="Udomittipong, Kanokporn" uniqKey="Udomittipong K" first="Kanokporn" last="Udomittipong">Kanokporn Udomittipong</name>
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<name sortKey="Ruangchira Urai, Ruchira" sort="Ruangchira Urai, Ruchira" uniqKey="Ruangchira Urai R" first="Ruchira" last="Ruangchira-Urai">Ruchira Ruangchira-Urai</name>
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<name sortKey="Charuvanij, Sirirat" sort="Charuvanij, Sirirat" uniqKey="Charuvanij S" first="Sirirat" last="Charuvanij">Sirirat Charuvanij</name>
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<name sortKey="Ruangchira Urai, Ruchira" sort="Ruangchira Urai, Ruchira" uniqKey="Ruangchira Urai R" first="Ruchira" last="Ruangchira-Urai">Ruchira Ruangchira-Urai</name>
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<div type="abstract" xml:lang="en">Nonspecific interstitial pneumonia (NSIP) is a rare pulmonary complication in systemic juvenile idiopathic arthritis (SJIA).</div>
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<ArticleTitle>Nonspecific interstitial pneumonia in refractory systemic juvenile idiopathic arthritis responded to tocilizumab treatment.</ArticleTitle>
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<AbstractText Label="BACKGROUND" NlmCategory="BACKGROUND">Nonspecific interstitial pneumonia (NSIP) is a rare pulmonary complication in systemic juvenile idiopathic arthritis (SJIA).</AbstractText>
<AbstractText Label="OBJECTIVE" NlmCategory="OBJECTIVE">To present a case with NSIP in SJIA METHODS: Case report RESULTS: We report the case of a 4-year-old boy with SJIA complicated by macrophage activation syndrome (MAS) refractory to conventional therapy, and who later developed NSIP confirmed by high-resolution computerized tomography of the chest and lung histopathology. The patient received tocilizumab, a monoclonal antibody to interleukin-6 receptor, to control his disease. Data relating to tocilizumab treatment of NSIP in refractory SJIA is limited.</AbstractText>
<AbstractText Label="CONCLUSIONS" NlmCategory="CONCLUSIONS">The data from this case report suggests that NSIP could be a pulmonary complication of SJIA complicated by MAS that is refractory to conventional therapy. Early initiation of tocilizumab should be considered to achieve disease remission in this pediatric patient population.</AbstractText>
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