Unified Wilson's Disease Rating Scale - a proposal for the neurological scoring of Wilson's disease patients.
Identifieur interne : 000E19 ( PubMed/Corpus ); précédent : 000E18; suivant : 000E20Unified Wilson's Disease Rating Scale - a proposal for the neurological scoring of Wilson's disease patients.
Auteurs : Anna Członkowska ; Beata Tarnacka ; Jens Carsten Möller ; Barbara Leinweber ; Oliver Bandmann ; France Woimant ; Wolfgang H. OertelSource :
- Neurologia i neurochirurgia polska [ 0028-3843 ]
English descriptors
- KwdEn :
- MESH :
Abstract
The clinical forms of Wilson's disease (WD) neurological manifestations can be divided into three movement disorder syndromes: a) dystonic, b) ataxic, c) parkinsonian syndrome. These syndromes in WD seldom occur in isolation. Clinical rating scales such as the Unified Parkinson;s Disease Rating Scale (UPDRS), the International Cooperative Ataxia Rating Scale (ICARS) and the Rating Scale for Dystonia (RSD), focusing on either parkinsonism or ataxia or dystonia alone, are not sufficient to reflect accurately the motor impairment of WD patients. The aim of the study was to develop a novel rating scale for WD, because as far as we know no scale for the clinical rating in WD has been designed before.
PubMed: 17330175
Links to Exploration step
pubmed:17330175Le document en format XML
<record><TEI><teiHeader><fileDesc><titleStmt><title xml:lang="en">Unified Wilson's Disease Rating Scale - a proposal for the neurological scoring of Wilson's disease patients.</title>
<author><name sortKey="Czlonkowska, Anna" sort="Czlonkowska, Anna" uniqKey="Czlonkowska A" first="Anna" last="Członkowska">Anna Członkowska</name>
<affiliation><nlm:affiliation>2nd Neurological Department, Institute of Psychiatry and Neurology, Warsaw, Poland. czlonkow@ipin.edu.pl</nlm:affiliation>
</affiliation>
</author>
<author><name sortKey="Tarnacka, Beata" sort="Tarnacka, Beata" uniqKey="Tarnacka B" first="Beata" last="Tarnacka">Beata Tarnacka</name>
</author>
<author><name sortKey="Moller, Jens Carsten" sort="Moller, Jens Carsten" uniqKey="Moller J" first="Jens Carsten" last="Möller">Jens Carsten Möller</name>
</author>
<author><name sortKey="Leinweber, Barbara" sort="Leinweber, Barbara" uniqKey="Leinweber B" first="Barbara" last="Leinweber">Barbara Leinweber</name>
</author>
<author><name sortKey="Bandmann, Oliver" sort="Bandmann, Oliver" uniqKey="Bandmann O" first="Oliver" last="Bandmann">Oliver Bandmann</name>
</author>
<author><name sortKey="Woimant, France" sort="Woimant, France" uniqKey="Woimant F" first="France" last="Woimant">France Woimant</name>
</author>
<author><name sortKey="Oertel, Wolfgang H" sort="Oertel, Wolfgang H" uniqKey="Oertel W" first="Wolfgang H" last="Oertel">Wolfgang H. Oertel</name>
</author>
</titleStmt>
<publicationStmt><idno type="wicri:source">PubMed</idno>
<date when="????"><PubDate><MedlineDate>2007 Jan-Feb</MedlineDate>
</PubDate>
</date>
<idno type="RBID">pubmed:17330175</idno>
<idno type="pmid">17330175</idno>
<idno type="wicri:Area/PubMed/Corpus">000E19</idno>
<idno type="wicri:explorRef" wicri:stream="PubMed" wicri:step="Corpus" wicri:corpus="PubMed">000E19</idno>
</publicationStmt>
<sourceDesc><biblStruct><analytic><title xml:lang="en">Unified Wilson's Disease Rating Scale - a proposal for the neurological scoring of Wilson's disease patients.</title>
<author><name sortKey="Czlonkowska, Anna" sort="Czlonkowska, Anna" uniqKey="Czlonkowska A" first="Anna" last="Członkowska">Anna Członkowska</name>
<affiliation><nlm:affiliation>2nd Neurological Department, Institute of Psychiatry and Neurology, Warsaw, Poland. czlonkow@ipin.edu.pl</nlm:affiliation>
</affiliation>
</author>
<author><name sortKey="Tarnacka, Beata" sort="Tarnacka, Beata" uniqKey="Tarnacka B" first="Beata" last="Tarnacka">Beata Tarnacka</name>
</author>
<author><name sortKey="Moller, Jens Carsten" sort="Moller, Jens Carsten" uniqKey="Moller J" first="Jens Carsten" last="Möller">Jens Carsten Möller</name>
</author>
<author><name sortKey="Leinweber, Barbara" sort="Leinweber, Barbara" uniqKey="Leinweber B" first="Barbara" last="Leinweber">Barbara Leinweber</name>
</author>
<author><name sortKey="Bandmann, Oliver" sort="Bandmann, Oliver" uniqKey="Bandmann O" first="Oliver" last="Bandmann">Oliver Bandmann</name>
</author>
<author><name sortKey="Woimant, France" sort="Woimant, France" uniqKey="Woimant F" first="France" last="Woimant">France Woimant</name>
</author>
<author><name sortKey="Oertel, Wolfgang H" sort="Oertel, Wolfgang H" uniqKey="Oertel W" first="Wolfgang H" last="Oertel">Wolfgang H. Oertel</name>
</author>
</analytic>
<series><title level="j">Neurologia i neurochirurgia polska</title>
<idno type="ISSN">0028-3843</idno>
</series>
</biblStruct>
</sourceDesc>
</fileDesc>
<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Adolescent</term>
<term>Adult</term>
<term>Female</term>
<term>Hepatolenticular Degeneration (diagnosis)</term>
<term>Humans</term>
<term>Male</term>
<term>Neurologic Examination</term>
<term>Reproducibility of Results</term>
<term>Severity of Illness Index</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en"><term>Hepatolenticular Degeneration</term>
</keywords>
<keywords scheme="MESH" xml:lang="en"><term>Adolescent</term>
<term>Adult</term>
<term>Female</term>
<term>Humans</term>
<term>Male</term>
<term>Neurologic Examination</term>
<term>Reproducibility of Results</term>
<term>Severity of Illness Index</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front><div type="abstract" xml:lang="en">The clinical forms of Wilson's disease (WD) neurological manifestations can be divided into three movement disorder syndromes: a) dystonic, b) ataxic, c) parkinsonian syndrome. These syndromes in WD seldom occur in isolation. Clinical rating scales such as the Unified Parkinson;s Disease Rating Scale (UPDRS), the International Cooperative Ataxia Rating Scale (ICARS) and the Rating Scale for Dystonia (RSD), focusing on either parkinsonism or ataxia or dystonia alone, are not sufficient to reflect accurately the motor impairment of WD patients. The aim of the study was to develop a novel rating scale for WD, because as far as we know no scale for the clinical rating in WD has been designed before.</div>
</front>
</TEI>
<pubmed><MedlineCitation Status="MEDLINE" Owner="NLM"><PMID Version="1">17330175</PMID>
<DateCreated><Year>2007</Year>
<Month>03</Month>
<Day>01</Day>
</DateCreated>
<DateCompleted><Year>2007</Year>
<Month>07</Month>
<Day>17</Day>
</DateCompleted>
<DateRevised><Year>2015</Year>
<Month>02</Month>
<Day>16</Day>
</DateRevised>
<Article PubModel="Print"><Journal><ISSN IssnType="Print">0028-3843</ISSN>
<JournalIssue CitedMedium="Print"><Volume>41</Volume>
<Issue>1</Issue>
<PubDate><MedlineDate>2007 Jan-Feb</MedlineDate>
</PubDate>
</JournalIssue>
<Title>Neurologia i neurochirurgia polska</Title>
<ISOAbbreviation>Neurol. Neurochir. Pol.</ISOAbbreviation>
</Journal>
<ArticleTitle>Unified Wilson's Disease Rating Scale - a proposal for the neurological scoring of Wilson's disease patients.</ArticleTitle>
<Pagination><MedlinePgn>1-12</MedlinePgn>
</Pagination>
<Abstract><AbstractText Label="BACKGROUND AND PURPOSE" NlmCategory="OBJECTIVE">The clinical forms of Wilson's disease (WD) neurological manifestations can be divided into three movement disorder syndromes: a) dystonic, b) ataxic, c) parkinsonian syndrome. These syndromes in WD seldom occur in isolation. Clinical rating scales such as the Unified Parkinson;s Disease Rating Scale (UPDRS), the International Cooperative Ataxia Rating Scale (ICARS) and the Rating Scale for Dystonia (RSD), focusing on either parkinsonism or ataxia or dystonia alone, are not sufficient to reflect accurately the motor impairment of WD patients. The aim of the study was to develop a novel rating scale for WD, because as far as we know no scale for the clinical rating in WD has been designed before.</AbstractText>
<AbstractText Label="MATERIAL AND METHODS" NlmCategory="METHODS">In 2004 the EuroWilson consortium was founded, to create a European WD database. Members of the consortium from Poland, Germany, and France prepared a new scale using clinical rating scales as the UPDRS, ICARS, and RSD. Prepared drafts were discussed several times in detail at the first international neurological EuroWilson meeting in September 2004 in Paris and in November in Warsaw.</AbstractText>
<AbstractText Label="RESULTS AND CONCLUSIONS" NlmCategory="CONCLUSIONS">The novel scale for WD consists of 3 parts, including: consciousness, a historical review based on the Barthel scale (2-11 items), and neurological examination (12-35, items). The maximum score for the first part is 3, for the second 39 points, and for the last 143 points. The initial reliability of the scale on the basis of 6 patients (on DVD) and 8 investigators was assessed. Inter-rater agreement was high. Now the scale is used by the EuroWilson and GeNeMove consortia.</AbstractText>
</Abstract>
<AuthorList CompleteYN="Y"><Author ValidYN="Y"><LastName>Członkowska</LastName>
<ForeName>Anna</ForeName>
<Initials>A</Initials>
<AffiliationInfo><Affiliation>2nd Neurological Department, Institute of Psychiatry and Neurology, Warsaw, Poland. czlonkow@ipin.edu.pl</Affiliation>
</AffiliationInfo>
</Author>
<Author ValidYN="Y"><LastName>Tarnacka</LastName>
<ForeName>Beata</ForeName>
<Initials>B</Initials>
</Author>
<Author ValidYN="Y"><LastName>Möller</LastName>
<ForeName>Jens Carsten</ForeName>
<Initials>JC</Initials>
</Author>
<Author ValidYN="Y"><LastName>Leinweber</LastName>
<ForeName>Barbara</ForeName>
<Initials>B</Initials>
</Author>
<Author ValidYN="Y"><LastName>Bandmann</LastName>
<ForeName>Oliver</ForeName>
<Initials>O</Initials>
</Author>
<Author ValidYN="Y"><LastName>Woimant</LastName>
<ForeName>France</ForeName>
<Initials>F</Initials>
</Author>
<Author ValidYN="Y"><LastName>Oertel</LastName>
<ForeName>Wolfgang H</ForeName>
<Initials>WH</Initials>
</Author>
</AuthorList>
<Language>eng</Language>
<PublicationTypeList><PublicationType UI="D016428">Journal Article</PublicationType>
<PublicationType UI="D013485">Research Support, Non-U.S. Gov't</PublicationType>
</PublicationTypeList>
</Article>
<MedlineJournalInfo><Country>Poland</Country>
<MedlineTA>Neurol Neurochir Pol</MedlineTA>
<NlmUniqueID>0101265</NlmUniqueID>
<ISSNLinking>0028-3843</ISSNLinking>
</MedlineJournalInfo>
<CitationSubset>IM</CitationSubset>
<MeshHeadingList><MeshHeading><DescriptorName UI="D000293" MajorTopicYN="N">Adolescent</DescriptorName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D000328" MajorTopicYN="N">Adult</DescriptorName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D005260" MajorTopicYN="N">Female</DescriptorName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D006527" MajorTopicYN="N">Hepatolenticular Degeneration</DescriptorName>
<QualifierName UI="Q000175" MajorTopicYN="Y">diagnosis</QualifierName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D006801" MajorTopicYN="N">Humans</DescriptorName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D008297" MajorTopicYN="N">Male</DescriptorName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D009460" MajorTopicYN="N">Neurologic Examination</DescriptorName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D015203" MajorTopicYN="N">Reproducibility of Results</DescriptorName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D012720" MajorTopicYN="N">Severity of Illness Index</DescriptorName>
</MeshHeading>
</MeshHeadingList>
</MedlineCitation>
<PubmedData><History><PubMedPubDate PubStatus="pubmed"><Year>2007</Year>
<Month>3</Month>
<Day>3</Day>
<Hour>9</Hour>
<Minute>0</Minute>
</PubMedPubDate>
<PubMedPubDate PubStatus="medline"><Year>2007</Year>
<Month>7</Month>
<Day>18</Day>
<Hour>9</Hour>
<Minute>0</Minute>
</PubMedPubDate>
<PubMedPubDate PubStatus="entrez"><Year>2007</Year>
<Month>3</Month>
<Day>3</Day>
<Hour>9</Hour>
<Minute>0</Minute>
</PubMedPubDate>
</History>
<PublicationStatus>ppublish</PublicationStatus>
<ArticleIdList><ArticleId IdType="pubmed">17330175</ArticleId>
<ArticleId IdType="pii">7545</ArticleId>
</ArticleIdList>
</PubmedData>
</pubmed>
</record>
Pour manipuler ce document sous Unix (Dilib)
EXPLOR_STEP=$WICRI_ROOT/Wicri/Sante/explor/ParkinsonFranceV1/Data/PubMed/Corpus
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 000E19 | SxmlIndent | more
Ou
HfdSelect -h $EXPLOR_AREA/Data/PubMed/Corpus/biblio.hfd -nk 000E19 | SxmlIndent | more
Pour mettre un lien sur cette page dans le réseau Wicri
{{Explor lien |wiki= Wicri/Sante |area= ParkinsonFranceV1 |flux= PubMed |étape= Corpus |type= RBID |clé= pubmed:17330175 |texte= Unified Wilson's Disease Rating Scale - a proposal for the neurological scoring of Wilson's disease patients. }}
Pour générer des pages wiki
HfdIndexSelect -h $EXPLOR_AREA/Data/PubMed/Corpus/RBID.i -Sk "pubmed:17330175" \ | HfdSelect -Kh $EXPLOR_AREA/Data/PubMed/Corpus/biblio.hfd \ | NlmPubMed2Wicri -a ParkinsonFranceV1
![]() | This area was generated with Dilib version V0.6.29. | ![]() |