Management of status dystonicus: our experience and review of the literature.
Identifieur interne : 002774 ( PubMed/Corpus ); précédent : 002773; suivant : 002775Management of status dystonicus: our experience and review of the literature.
Auteurs : Paolo Mariotti ; Alfonso Fasano ; M Fiorella Contarino ; Giacomo Della Marca ; Marco Piastra ; Orazio Genovese ; Silvia Pulitan ; Antonio Chiaretti ; Anna Rita BentivoglioSource :
- Movement disorders : official journal of the Movement Disorder Society [ 0885-3185 ] ; 2007.
English descriptors
- KwdEn :
- MESH :
- therapy : Spinal Dysraphism.
- Adolescent, Humans, Male.
Abstract
Status dystonicus (SD) is a life threatening disorder that develops in patients with both primary and secondary dystonia, characterized by acute worsening of symptoms with generalized and severe muscle contractions. To date, no information is available on the best way to treat this disorder. We review the previously described cases of SD and two new cases are reported, one of which occurring in a child with static encephalopathy, and the other one in a patient with pantothenate kinase-associated neurodegeneration. Both patients were admitted to an intensive care unit and treated with midazolam and propofol. This approach proved to be useful in the former while the progressive nature of the dystonia of the second patient required the combination of intrathecal baclofen infusion and bilateral pallidal deep brain stimulation. We believe that a rapid and aggressive approach is justified to avoid the great morbidity and mortality which characterize SD. Our experience, combined with the data available in the literature, might permit to establish the best strategies in managing this rare and severe condition.
DOI: 10.1002/mds.21471
PubMed: 17427939
Links to Exploration step
pubmed:17427939Le document en format XML
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<author><name sortKey="Mariotti, Paolo" sort="Mariotti, Paolo" uniqKey="Mariotti P" first="Paolo" last="Mariotti">Paolo Mariotti</name>
<affiliation><nlm:affiliation>Istituto di Neuropsichiatria Infantile, Università Cattolica del Sacro Cuore, Roma, Italia.</nlm:affiliation>
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<author><name sortKey="Fasano, Alfonso" sort="Fasano, Alfonso" uniqKey="Fasano A" first="Alfonso" last="Fasano">Alfonso Fasano</name>
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<author><name sortKey="Contarino, M Fiorella" sort="Contarino, M Fiorella" uniqKey="Contarino M" first="M Fiorella" last="Contarino">M Fiorella Contarino</name>
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<author><name sortKey="Della Marca, Giacomo" sort="Della Marca, Giacomo" uniqKey="Della Marca G" first="Giacomo" last="Della Marca">Giacomo Della Marca</name>
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<author><name sortKey="Piastra, Marco" sort="Piastra, Marco" uniqKey="Piastra M" first="Marco" last="Piastra">Marco Piastra</name>
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<author><name sortKey="Genovese, Orazio" sort="Genovese, Orazio" uniqKey="Genovese O" first="Orazio" last="Genovese">Orazio Genovese</name>
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<author><name sortKey="Pulitan, Silvia" sort="Pulitan, Silvia" uniqKey="Pulitan S" first="Silvia" last="Pulitan">Silvia Pulitan</name>
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<author><name sortKey="Chiaretti, Antonio" sort="Chiaretti, Antonio" uniqKey="Chiaretti A" first="Antonio" last="Chiaretti">Antonio Chiaretti</name>
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<author><name sortKey="Bentivoglio, Anna Rita" sort="Bentivoglio, Anna Rita" uniqKey="Bentivoglio A" first="Anna Rita" last="Bentivoglio">Anna Rita Bentivoglio</name>
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<author><name sortKey="Fasano, Alfonso" sort="Fasano, Alfonso" uniqKey="Fasano A" first="Alfonso" last="Fasano">Alfonso Fasano</name>
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<author><name sortKey="Piastra, Marco" sort="Piastra, Marco" uniqKey="Piastra M" first="Marco" last="Piastra">Marco Piastra</name>
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<author><name sortKey="Genovese, Orazio" sort="Genovese, Orazio" uniqKey="Genovese O" first="Orazio" last="Genovese">Orazio Genovese</name>
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<author><name sortKey="Pulitan, Silvia" sort="Pulitan, Silvia" uniqKey="Pulitan S" first="Silvia" last="Pulitan">Silvia Pulitan</name>
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<author><name sortKey="Chiaretti, Antonio" sort="Chiaretti, Antonio" uniqKey="Chiaretti A" first="Antonio" last="Chiaretti">Antonio Chiaretti</name>
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<author><name sortKey="Bentivoglio, Anna Rita" sort="Bentivoglio, Anna Rita" uniqKey="Bentivoglio A" first="Anna Rita" last="Bentivoglio">Anna Rita Bentivoglio</name>
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<front><div type="abstract" xml:lang="en">Status dystonicus (SD) is a life threatening disorder that develops in patients with both primary and secondary dystonia, characterized by acute worsening of symptoms with generalized and severe muscle contractions. To date, no information is available on the best way to treat this disorder. We review the previously described cases of SD and two new cases are reported, one of which occurring in a child with static encephalopathy, and the other one in a patient with pantothenate kinase-associated neurodegeneration. Both patients were admitted to an intensive care unit and treated with midazolam and propofol. This approach proved to be useful in the former while the progressive nature of the dystonia of the second patient required the combination of intrathecal baclofen infusion and bilateral pallidal deep brain stimulation. We believe that a rapid and aggressive approach is justified to avoid the great morbidity and mortality which characterize SD. Our experience, combined with the data available in the literature, might permit to establish the best strategies in managing this rare and severe condition.</div>
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<Abstract><AbstractText>Status dystonicus (SD) is a life threatening disorder that develops in patients with both primary and secondary dystonia, characterized by acute worsening of symptoms with generalized and severe muscle contractions. To date, no information is available on the best way to treat this disorder. We review the previously described cases of SD and two new cases are reported, one of which occurring in a child with static encephalopathy, and the other one in a patient with pantothenate kinase-associated neurodegeneration. Both patients were admitted to an intensive care unit and treated with midazolam and propofol. This approach proved to be useful in the former while the progressive nature of the dystonia of the second patient required the combination of intrathecal baclofen infusion and bilateral pallidal deep brain stimulation. We believe that a rapid and aggressive approach is justified to avoid the great morbidity and mortality which characterize SD. Our experience, combined with the data available in the literature, might permit to establish the best strategies in managing this rare and severe condition.</AbstractText>
<CopyrightInformation>(c) 2007 Movement Disorder Society.</CopyrightInformation>
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<AuthorList CompleteYN="Y"><Author ValidYN="Y"><LastName>Mariotti</LastName>
<ForeName>Paolo</ForeName>
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<AffiliationInfo><Affiliation>Istituto di Neuropsichiatria Infantile, Università Cattolica del Sacro Cuore, Roma, Italia.</Affiliation>
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