MovDisordV3, PascalFrancis, Curation, bibRecord, 001F84

Postural Tremor in X-Linked Spinal and Bulbar Muscular Atrophy

Identifieur interne : 001F84 ( PascalFrancis/Curation ); précédent : 001F83; suivant : 001F85

Postural Tremor in X-Linked Spinal and Bulbar Muscular Atrophy

Auteurs : Ritsuko Hanajima [Japon] ; Yasuo Terao [Japon] ; Setsu Nakatani-Enomoto [Japon] ; Masashi Hamada [Japon] ; Akihiro Yugeta [Japon] ; Hideyuki Matsumoto [Japon] ; Tomotaka Yamamoto [Japon] ; Shoji Tsuji [Japon] ; Yoshikazu Ugawa [Japon]

Source :

Movement disorders [ 0885-3185 ] ; 2009.

RBID : Pascal:09-0482368

Descripteurs français

Pascal (Inist)
- Tremblement, Maladie de Kennedy, Pathologie du système nerveux, Réflexe, Cohérence.

English descriptors

KwdEn :
- Coherence, Kennedy's disease, Nervous system diseases, Reflex, Tremor.

Abstract

Postural tremor is a common initial symptom in spinal and bulbar muscular atrophy (SBMA), but its pathophysiological mechanisms remain to be studied. This study was undertaken to examine the physiological mechanisms underlying postural tremor in SBMA. For eight patients (36-63 years old) with genetically confirmed SBMA, we recorded surface electromyograms (EMGs) from the forearm muscles and hand movements with an accelerometer (ACC) while maintaining a posture with and without a weight load. We then analyzed their power spectra and coherence. The peak tremor frequency was 6-9 Hz in seven patients and 2-3 Hz in one patient. Oscillatory movements were associated with EMG activity in five patients, but not in three patients. Weight loads and postural changes affected the tremor frequency in all patients. Tremor was classified as "reflex tremor" in five patients and "mechanical tremor" in three patients. These results suggest that peripheral factors play important roles in tremor genesis in SBMA, although its clinical features resemble essential tremor. Subclinical sensory disturbance or a decrease of motor unit numbers might be candidates for such peripheral factors contributing to tremor genesis in SBMA.

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A05				`@2 24`
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A08	`01`	`1`	`ENG`	`@1 Postural Tremor in X-Linked Spinal and Bulbar Muscular Atrophy`
A11	`01`	`1`		`@1 HANAJIMA (Ritsuko)`
A11	`02`	`1`		`@1 TERAO (Yasuo)`
A11	`03`	`1`		`@1 NAKATANI-ENOMOTO (Setsu)`
A11	`04`	`1`		`@1 HAMADA (Masashi)`
A11	`05`	`1`		`@1 YUGETA (Akihiro)`
A11	`06`	`1`		`@1 MATSUMOTO (Hideyuki)`
A11	`07`	`1`		`@1 YAMAMOTO (Tomotaka)`
A11	`08`	`1`		`@1 TSUJI (Shoji)`
A11	`09`	`1`		`@1 UGAWA (Yoshikazu)`
A14	`01`			`@1 Department of Neurology, The University of Tokyo Hospital @2 Tokyo @3 JPN @Z 1 aut. @Z 2 aut. @Z 3 aut. @Z 4 aut. @Z 5 aut. @Z 6 aut. @Z 7 aut. @Z 8 aut.`
A14	`02`			`@1 Department of Neurology, Fukushima Medical University @2 Fukushima @3 JPN @Z 3 aut. @Z 9 aut.`
A20				`@1 2063-2069`
A21				`@1 2009`
A23	`01`			`@0 ENG`
A43	`01`			`@1 INIST @2 20953 @5 354000171427050040`
A44				`@0 0000 @1 © 2009 INIST-CNRS. All rights reserved.`
A45				`@0 27 ref.`
A47	`01`	`1`		`@0 09-0482368`
A60				`@1 P`
A61				`@0 A`
A64	`01`	`1`		`@0 Movement disorders`
A66	`01`			`@0 USA`
C01	`01`		`ENG`	@0 Postural tremor is a common initial symptom in spinal and bulbar muscular atrophy (SBMA), but its pathophysiological mechanisms remain to be studied. This study was undertaken to examine the physiological mechanisms underlying postural tremor in SBMA. For eight patients (36-63 years old) with genetically confirmed SBMA, we recorded surface electromyograms (EMGs) from the forearm muscles and hand movements with an accelerometer (ACC) while maintaining a posture with and without a weight load. We then analyzed their power spectra and coherence. The peak tremor frequency was 6-9 Hz in seven patients and 2-3 Hz in one patient. Oscillatory movements were associated with EMG activity in five patients, but not in three patients. Weight loads and postural changes affected the tremor frequency in all patients. Tremor was classified as "reflex tremor" in five patients and "mechanical tremor" in three patients. These results suggest that peripheral factors play important roles in tremor genesis in SBMA, although its clinical features resemble essential tremor. Subclinical sensory disturbance or a decrease of motor unit numbers might be candidates for such peripheral factors contributing to tremor genesis in SBMA.
C02	`01`	`X`		`@0 002B17`
C02	`02`	`X`		`@0 002B16B`
C03	`01`	`X`	`FRE`	`@0 Tremblement @5 01`
C03	`01`	`X`	`ENG`	`@0 Tremor @5 01`
C03	`01`	`X`	`SPA`	`@0 Temblor @5 01`
C03	`02`	`X`	`FRE`	`@0 Maladie de Kennedy @2 NM @5 02`
C03	`02`	`X`	`ENG`	`@0 Kennedy's disease @2 NM @5 02`
C03	`02`	`X`	`SPA`	`@0 Enfermedad de Kennedy @2 NM @5 02`
C03	`03`	`X`	`FRE`	`@0 Pathologie du système nerveux @5 03`
C03	`03`	`X`	`ENG`	`@0 Nervous system diseases @5 03`
C03	`03`	`X`	`SPA`	`@0 Sistema nervioso patología @5 03`
C03	`04`	`X`	`FRE`	`@0 Réflexe @5 09`
C03	`04`	`X`	`ENG`	`@0 Reflex @5 09`
C03	`04`	`X`	`SPA`	`@0 Reflejo @5 09`
C03	`05`	`X`	`FRE`	`@0 Cohérence @5 10`
C03	`05`	`X`	`ENG`	`@0 Coherence @5 10`
C03	`05`	`X`	`SPA`	`@0 Coherencia @5 10`
C07	`01`	`X`	`FRE`	`@0 Mouvement involontaire @5 37`
C07	`01`	`X`	`ENG`	`@0 Involuntary movement @5 37`
C07	`01`	`X`	`SPA`	`@0 Movimiento involuntario @5 37`
C07	`02`	`X`	`FRE`	`@0 Trouble neurologique @5 39`
C07	`02`	`X`	`ENG`	`@0 Neurological disorder @5 39`
C07	`02`	`X`	`SPA`	`@0 Trastorno neurológico @5 39`
N21				`@1 348`
N44	`01`			`@1 OTO`
N82				`@1 OTO`

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Pascal:09-0482368

Le document en format XML

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<sourceDesc><biblStruct><analytic><title xml:lang="en" level="a">Postural Tremor in X-Linked Spinal and Bulbar Muscular Atrophy</title>
<author><name sortKey="Hanajima, Ritsuko" sort="Hanajima, Ritsuko" uniqKey="Hanajima R" first="Ritsuko" last="Hanajima">Ritsuko Hanajima</name>
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<author><name sortKey="Terao, Yasuo" sort="Terao, Yasuo" uniqKey="Terao Y" first="Yasuo" last="Terao">Yasuo Terao</name>
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<author><name sortKey="Nakatani Enomoto, Setsu" sort="Nakatani Enomoto, Setsu" uniqKey="Nakatani Enomoto S" first="Setsu" last="Nakatani-Enomoto">Setsu Nakatani-Enomoto</name>
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<author><name sortKey="Hamada, Masashi" sort="Hamada, Masashi" uniqKey="Hamada M" first="Masashi" last="Hamada">Masashi Hamada</name>
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<author><name sortKey="Yugeta, Akihiro" sort="Yugeta, Akihiro" uniqKey="Yugeta A" first="Akihiro" last="Yugeta">Akihiro Yugeta</name>
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<author><name sortKey="Matsumoto, Hideyuki" sort="Matsumoto, Hideyuki" uniqKey="Matsumoto H" first="Hideyuki" last="Matsumoto">Hideyuki Matsumoto</name>
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<author><name sortKey="Yamamoto, Tomotaka" sort="Yamamoto, Tomotaka" uniqKey="Yamamoto T" first="Tomotaka" last="Yamamoto">Tomotaka Yamamoto</name>
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<author><name sortKey="Tsuji, Shoji" sort="Tsuji, Shoji" uniqKey="Tsuji S" first="Shoji" last="Tsuji">Shoji Tsuji</name>
<affiliation wicri:level="1"><inist:fA14 i1="01"><s1>Department of Neurology, The University of Tokyo Hospital</s1>
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<author><name sortKey="Ugawa, Yoshikazu" sort="Ugawa, Yoshikazu" uniqKey="Ugawa Y" first="Yoshikazu" last="Ugawa">Yoshikazu Ugawa</name>
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<s2>Fukushima</s2>
<s3>JPN</s3>
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<series><title level="j" type="main">Movement disorders</title>
<title level="j" type="abbreviated">Mov. disord.</title>
<idno type="ISSN">0885-3185</idno>
<imprint><date when="2009">2009</date>
</imprint>
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<seriesStmt><title level="j" type="main">Movement disorders</title>
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<idno type="ISSN">0885-3185</idno>
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</fileDesc>
<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Coherence</term>
<term>Kennedy's disease</term>
<term>Nervous system diseases</term>
<term>Reflex</term>
<term>Tremor</term>
</keywords>
<keywords scheme="Pascal" xml:lang="fr"><term>Tremblement</term>
<term>Maladie de Kennedy</term>
<term>Pathologie du   système nerveux</term>
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<term>Cohérence</term>
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<front><div type="abstract" xml:lang="en">Postural tremor is a common initial symptom in spinal and bulbar muscular atrophy (SBMA), but its pathophysiological mechanisms remain to be studied. This study was undertaken to examine the physiological mechanisms underlying postural tremor in SBMA. For eight patients (36-63 years old) with genetically confirmed SBMA, we recorded surface electromyograms (EMGs) from the forearm muscles and hand movements with an accelerometer (ACC) while maintaining a posture with and without a weight load. We then analyzed their power spectra and coherence. The peak tremor frequency was 6-9 Hz in seven patients and 2-3 Hz in one patient. Oscillatory movements were associated with EMG activity in five patients, but not in three patients. Weight loads and postural changes affected the tremor frequency in all patients. Tremor was classified as "reflex tremor" in five patients and "mechanical tremor" in three patients. These results suggest that peripheral factors play important roles in tremor genesis in SBMA, although its clinical features resemble essential tremor. Subclinical sensory disturbance or a decrease of motor unit numbers might be candidates for such peripheral factors contributing to tremor genesis in SBMA.</div>
</front>
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<fA11 i1="01" i2="1"><s1>HANAJIMA (Ritsuko)</s1>
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<fA11 i1="07" i2="1"><s1>YAMAMOTO (Tomotaka)</s1>
</fA11>
<fA11 i1="08" i2="1"><s1>TSUJI (Shoji)</s1>
</fA11>
<fA11 i1="09" i2="1"><s1>UGAWA (Yoshikazu)</s1>
</fA11>
<fA14 i1="01"><s1>Department of Neurology, The University of Tokyo Hospital</s1>
<s2>Tokyo</s2>
<s3>JPN</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>3 aut.</sZ>
<sZ>4 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
</fA14>
<fA14 i1="02"><s1>Department of Neurology, Fukushima Medical University</s1>
<s2>Fukushima</s2>
<s3>JPN</s3>
<sZ>3 aut.</sZ>
<sZ>9 aut.</sZ>
</fA14>
<fA20><s1>2063-2069</s1>
</fA20>
<fA21><s1>2009</s1>
</fA21>
<fA23 i1="01"><s0>ENG</s0>
</fA23>
<fA43 i1="01"><s1>INIST</s1>
<s2>20953</s2>
<s5>354000171427050040</s5>
</fA43>
<fA44><s0>0000</s0>
<s1>© 2009 INIST-CNRS. All rights reserved.</s1>
</fA44>
<fA45><s0>27 ref.</s0>
</fA45>
<fA47 i1="01" i2="1"><s0>09-0482368</s0>
</fA47>
<fA60><s1>P</s1>
</fA60>
<fA61><s0>A</s0>
</fA61>
<fA64 i1="01" i2="1"><s0>Movement disorders</s0>
</fA64>
<fA66 i1="01"><s0>USA</s0>
</fA66>
<fC01 i1="01" l="ENG"><s0>Postural tremor is a common initial symptom in spinal and bulbar muscular atrophy (SBMA), but its pathophysiological mechanisms remain to be studied. This study was undertaken to examine the physiological mechanisms underlying postural tremor in SBMA. For eight patients (36-63 years old) with genetically confirmed SBMA, we recorded surface electromyograms (EMGs) from the forearm muscles and hand movements with an accelerometer (ACC) while maintaining a posture with and without a weight load. We then analyzed their power spectra and coherence. The peak tremor frequency was 6-9 Hz in seven patients and 2-3 Hz in one patient. Oscillatory movements were associated with EMG activity in five patients, but not in three patients. Weight loads and postural changes affected the tremor frequency in all patients. Tremor was classified as "reflex tremor" in five patients and "mechanical tremor" in three patients. These results suggest that peripheral factors play important roles in tremor genesis in SBMA, although its clinical features resemble essential tremor. Subclinical sensory disturbance or a decrease of motor unit numbers might be candidates for such peripheral factors contributing to tremor genesis in SBMA.</s0>
</fC01>
<fC02 i1="01" i2="X"><s0>002B17</s0>
</fC02>
<fC02 i1="02" i2="X"><s0>002B16B</s0>
</fC02>
<fC03 i1="01" i2="X" l="FRE"><s0>Tremblement</s0>
<s5>01</s5>
</fC03>
<fC03 i1="01" i2="X" l="ENG"><s0>Tremor</s0>
<s5>01</s5>
</fC03>
<fC03 i1="01" i2="X" l="SPA"><s0>Temblor</s0>
<s5>01</s5>
</fC03>
<fC03 i1="02" i2="X" l="FRE"><s0>Maladie de Kennedy</s0>
<s2>NM</s2>
<s5>02</s5>
</fC03>
<fC03 i1="02" i2="X" l="ENG"><s0>Kennedy's disease</s0>
<s2>NM</s2>
<s5>02</s5>
</fC03>
<fC03 i1="02" i2="X" l="SPA"><s0>Enfermedad de Kennedy</s0>
<s2>NM</s2>
<s5>02</s5>
</fC03>
<fC03 i1="03" i2="X" l="FRE"><s0>Pathologie du   système nerveux</s0>
<s5>03</s5>
</fC03>
<fC03 i1="03" i2="X" l="ENG"><s0>Nervous system diseases</s0>
<s5>03</s5>
</fC03>
<fC03 i1="03" i2="X" l="SPA"><s0>Sistema nervioso patología</s0>
<s5>03</s5>
</fC03>
<fC03 i1="04" i2="X" l="FRE"><s0>Réflexe</s0>
<s5>09</s5>
</fC03>
<fC03 i1="04" i2="X" l="ENG"><s0>Reflex</s0>
<s5>09</s5>
</fC03>
<fC03 i1="04" i2="X" l="SPA"><s0>Reflejo</s0>
<s5>09</s5>
</fC03>
<fC03 i1="05" i2="X" l="FRE"><s0>Cohérence</s0>
<s5>10</s5>
</fC03>
<fC03 i1="05" i2="X" l="ENG"><s0>Coherence</s0>
<s5>10</s5>
</fC03>
<fC03 i1="05" i2="X" l="SPA"><s0>Coherencia</s0>
<s5>10</s5>
</fC03>
<fC07 i1="01" i2="X" l="FRE"><s0>Mouvement involontaire</s0>
<s5>37</s5>
</fC07>
<fC07 i1="01" i2="X" l="ENG"><s0>Involuntary movement</s0>
<s5>37</s5>
</fC07>
<fC07 i1="01" i2="X" l="SPA"><s0>Movimiento involuntario</s0>
<s5>37</s5>
</fC07>
<fC07 i1="02" i2="X" l="FRE"><s0>Trouble neurologique</s0>
<s5>39</s5>
</fC07>
<fC07 i1="02" i2="X" l="ENG"><s0>Neurological disorder</s0>
<s5>39</s5>
</fC07>
<fC07 i1="02" i2="X" l="SPA"><s0>Trastorno neurológico</s0>
<s5>39</s5>
</fC07>
<fN21><s1>348</s1>
</fN21>
<fN44 i1="01"><s1>OTO</s1>
</fN44>
<fN82><s1>OTO</s1>
</fN82>
</pA>
</standard>
</inist>
</record>

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	Movement Disorders (revue)
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Movement Disorders (revue)

Postural Tremor in X-Linked Spinal and Bulbar Muscular Atrophy

Postural Tremor in X-Linked Spinal and Bulbar Muscular Atrophy

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