MovDisordV3, PascalFrancis, Curation, bibRecord, 001649

Management of Status dystonicus: Our experience and review of the literature

Identifieur interne : 001649 ( PascalFrancis/Curation ); précédent : 001648; suivant : 001650

Management of Status dystonicus: Our experience and review of the literature

Auteurs : Paolo Mariotti [Italie] ; Alfonso Fasano [Italie] ; M. Fiorella Contarino [Pays-Bas] ; Giacomo Della Marca [Italie] ; Marco Piastra [Italie] ; Orazio Genovese [Italie] ; Silvia Pulitano [Italie] ; Antonio Chiaretti [Italie] ; Anna Rita Bentivoglio [Italie]

Source :

Movement disorders [ 0885-3185 ] ; 2007.

RBID : Pascal:07-0314951

Descripteurs français

Pascal (Inist)
- Système nerveux pathologie, Dystonie, Conduite à tenir, Expérience, Midazolam, Pantothenate kinase.

English descriptors

KwdEn :
- Clinical management, Dystonia, Experience, Midazolam, Nervous system diseases, Pantothenate kinase.

Abstract

Status dystonicus (SD) is a life threatening disorder that develops in patients with both primary and secondary dystonia, characterized by acute worsening of symptoms with generalized and severe muscle contractions. To date, no information is available on the best way to treat this disorder. We review the previously described cases of SD and two new cases are reported, one of which occurring in a child with static encephalopathy, and the other one in a patient with pantothenate kinase-associated neurodegeneration. Both patients were admitted to an intensive care unit and treated with midazolam and propofol. This approach proved to be useful in the former while the progressive nature of the dystonia of the second patient required the combination of intrathecal baclofen infusion and bilateral pallidal deep brain stimulation. We believe that a rapid and aggressive approach is justified to avoid the great morbidity and mortality which characterize SD. Our experience, combined with the data available in the literature, might permit to establish the best strategies in managing this rare and severe condition.

A01	`01`	`1`		`@0 0885-3185`
A03		`1`		`@0 Mov. disord.`
A05				`@2 22`
A06				`@2 7`
A08	`01`	`1`	`ENG`	`@1 Management of Status dystonicus: Our experience and review of the literature`
A11	`01`	`1`		`@1 MARIOTTI (Paolo)`
A11	`02`	`1`		`@1 FASANO (Alfonso)`
A11	`03`	`1`		`@1 CONTARINO (M. Fiorella)`
A11	`04`	`1`		`@1 DELLA MARCA (Giacomo)`
A11	`05`	`1`		`@1 PIASTRA (Marco)`
A11	`06`	`1`		`@1 GENOVESE (Orazio)`
A11	`07`	`1`		`@1 PULITANO (Silvia)`
A11	`08`	`1`		`@1 CHIARETTI (Antonio)`
A11	`09`	`1`		`@1 BENTIVOGLIO (Anna Rita)`
A14	`01`			`@1 Istituto di Neuropsichiatria Infantile, Università Cattolica del Sacro Cuore @2 Roma @3 ITA @Z 1 aut.`
A14	`02`			`@1 Istituto di Neurologia, Università Cattolica del Sacro Cuore @2 Roma @3 ITA @Z 2 aut. @Z 4 aut. @Z 9 aut.`
A14	`03`			`@1 Department of Neurology, Academic Medical Center, University of Amsterdam @3 NLD @Z 3 aut.`
A14	`04`			`@1 Istituto di Pediatria, Università Cattolica del Sacro Cuore @2 Roma @3 ITA @Z 5 aut. @Z 6 aut. @Z 7 aut. @Z 8 aut.`
A20				`@1 963-968`
A21				`@1 2007`
A23	`01`			`@0 ENG`
A43	`01`			`@1 INIST @2 20953 @5 354000149881420090`
A44				`@0 0000 @1 © 2007 INIST-CNRS. All rights reserved.`
A45				`@0 23 ref.`
A47	`01`	`1`		`@0 07-0314951`
A60				`@1 P`
A61				`@0 A`
A64	`01`	`1`		`@0 Movement disorders`
A66	`01`			`@0 USA`
C01	`01`		`ENG`	@0 Status dystonicus (SD) is a life threatening disorder that develops in patients with both primary and secondary dystonia, characterized by acute worsening of symptoms with generalized and severe muscle contractions. To date, no information is available on the best way to treat this disorder. We review the previously described cases of SD and two new cases are reported, one of which occurring in a child with static encephalopathy, and the other one in a patient with pantothenate kinase-associated neurodegeneration. Both patients were admitted to an intensive care unit and treated with midazolam and propofol. This approach proved to be useful in the former while the progressive nature of the dystonia of the second patient required the combination of intrathecal baclofen infusion and bilateral pallidal deep brain stimulation. We believe that a rapid and aggressive approach is justified to avoid the great morbidity and mortality which characterize SD. Our experience, combined with the data available in the literature, might permit to establish the best strategies in managing this rare and severe condition.
C02	`01`	`X`		`@0 002B17`
C02	`02`	`X`		`@0 002B17E`
C02	`03`	`X`		`@0 002B17A03`
C03	`01`	`X`	`FRE`	`@0 Système nerveux pathologie @5 01`
C03	`01`	`X`	`ENG`	`@0 Nervous system diseases @5 01`
C03	`01`	`X`	`SPA`	`@0 Sistema nervioso patología @5 01`
C03	`02`	`X`	`FRE`	`@0 Dystonie @5 02`
C03	`02`	`X`	`ENG`	`@0 Dystonia @5 02`
C03	`02`	`X`	`SPA`	`@0 Distonía @5 02`
C03	`03`	`X`	`FRE`	`@0 Conduite à tenir @5 09`
C03	`03`	`X`	`ENG`	`@0 Clinical management @5 09`
C03	`03`	`X`	`SPA`	`@0 Actitud médica @5 09`
C03	`04`	`X`	`FRE`	`@0 Expérience @5 10`
C03	`04`	`X`	`ENG`	`@0 Experience @5 10`
C03	`04`	`X`	`SPA`	`@0 Experiencia @5 10`
C03	`05`	`X`	`FRE`	`@0 Midazolam @2 NK @2 FR @5 11`
C03	`05`	`X`	`ENG`	`@0 Midazolam @2 NK @2 FR @5 11`
C03	`05`	`X`	`SPA`	`@0 Midazolam @2 NK @2 FR @5 11`
C03	`06`	`X`	`FRE`	`@0 Pantothenate kinase @2 FE @5 12`
C03	`06`	`X`	`ENG`	`@0 Pantothenate kinase @2 FE @5 12`
C03	`06`	`X`	`SPA`	`@0 Pantothenate kinase @2 FE @5 12`
C07	`01`	`X`	`FRE`	`@0 Transferases @2 FE`
C07	`01`	`X`	`ENG`	`@0 Transferases @2 FE`
C07	`01`	`X`	`SPA`	`@0 Transferases @2 FE`
C07	`02`	`X`	`FRE`	`@0 Enzyme @2 FE`
C07	`02`	`X`	`ENG`	`@0 Enzyme @2 FE`
C07	`02`	`X`	`SPA`	`@0 Enzima @2 FE`
C07	`03`	`X`	`FRE`	`@0 Extrapyramidal syndrome @5 37`
C07	`03`	`X`	`ENG`	`@0 Extrapyramidal syndrome @5 37`
C07	`03`	`X`	`SPA`	`@0 Extrapiramidal síndrome @5 37`
C07	`04`	`X`	`FRE`	`@0 Mouvement involontaire @5 38`
C07	`04`	`X`	`ENG`	`@0 Involuntary movement @5 38`
C07	`04`	`X`	`SPA`	`@0 Movimiento involuntario @5 38`
C07	`05`	`X`	`FRE`	`@0 Muscle strié pathologie @5 39`
C07	`05`	`X`	`ENG`	`@0 Striated muscle disease @5 39`
C07	`05`	`X`	`SPA`	`@0 Músculo estriado patología @5 39`
C07	`06`	`X`	`FRE`	`@0 Trouble neurologique @5 40`
C07	`06`	`X`	`ENG`	`@0 Neurological disorder @5 40`
C07	`06`	`X`	`SPA`	`@0 Trastorno neurológico @5 40`
C07	`07`	`X`	`FRE`	`@0 Encéphale pathologie @5 41`
C07	`07`	`X`	`ENG`	`@0 Cerebral disorder @5 41`
C07	`07`	`X`	`SPA`	`@0 Encéfalo patología @5 41`
C07	`08`	`X`	`FRE`	`@0 Système nerveux central pathologie @5 42`
C07	`08`	`X`	`ENG`	`@0 Central nervous system disease @5 42`
C07	`08`	`X`	`SPA`	`@0 Sistema nervosio central patología @5 42`
N21				`@1 204`
N44	`01`			`@1 OTO`
N82				`@1 OTO`

Links toward previous steps (curation, corpus...)

to stream PascalFrancis, to step Corpus: Pour aller vers cette notice dans l'étape Curation :001672

Links to Exploration step

Pascal:07-0314951

Le document en format XML

<record><TEI><teiHeader><fileDesc><titleStmt><title xml:lang="en" level="a">Management of Status dystonicus: Our experience and review of the literature</title>
<author><name sortKey="Mariotti, Paolo" sort="Mariotti, Paolo" uniqKey="Mariotti P" first="Paolo" last="Mariotti">Paolo Mariotti</name>
<affiliation wicri:level="1"><inist:fA14 i1="01"><s1>Istituto di Neuropsichiatria Infantile, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>1 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Fasano, Alfonso" sort="Fasano, Alfonso" uniqKey="Fasano A" first="Alfonso" last="Fasano">Alfonso Fasano</name>
<affiliation wicri:level="1"><inist:fA14 i1="02"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>2 aut.</sZ>
<sZ>4 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Contarino, M Fiorella" sort="Contarino, M Fiorella" uniqKey="Contarino M" first="M. Fiorella" last="Contarino">M. Fiorella Contarino</name>
<affiliation wicri:level="1"><inist:fA14 i1="03"><s1>Department of Neurology, Academic Medical Center, University of Amsterdam</s1>
<s3>NLD</s3>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Pays-Bas</country>
</affiliation>
</author>
<author><name sortKey="Della Marca, Giacomo" sort="Della Marca, Giacomo" uniqKey="Della Marca G" first="Giacomo" last="Della Marca">Giacomo Della Marca</name>
<affiliation wicri:level="1"><inist:fA14 i1="02"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>2 aut.</sZ>
<sZ>4 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Piastra, Marco" sort="Piastra, Marco" uniqKey="Piastra M" first="Marco" last="Piastra">Marco Piastra</name>
<affiliation wicri:level="1"><inist:fA14 i1="04"><s1>Istituto di Pediatria, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Genovese, Orazio" sort="Genovese, Orazio" uniqKey="Genovese O" first="Orazio" last="Genovese">Orazio Genovese</name>
<affiliation wicri:level="1"><inist:fA14 i1="04"><s1>Istituto di Pediatria, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Pulitano, Silvia" sort="Pulitano, Silvia" uniqKey="Pulitano S" first="Silvia" last="Pulitano">Silvia Pulitano</name>
<affiliation wicri:level="1"><inist:fA14 i1="04"><s1>Istituto di Pediatria, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Chiaretti, Antonio" sort="Chiaretti, Antonio" uniqKey="Chiaretti A" first="Antonio" last="Chiaretti">Antonio Chiaretti</name>
<affiliation wicri:level="1"><inist:fA14 i1="04"><s1>Istituto di Pediatria, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Bentivoglio, Anna Rita" sort="Bentivoglio, Anna Rita" uniqKey="Bentivoglio A" first="Anna Rita" last="Bentivoglio">Anna Rita Bentivoglio</name>
<affiliation wicri:level="1"><inist:fA14 i1="02"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>2 aut.</sZ>
<sZ>4 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
</titleStmt>
<publicationStmt><idno type="wicri:source">INIST</idno>
<idno type="inist">07-0314951</idno>
<date when="2007">2007</date>
<idno type="stanalyst">PASCAL 07-0314951 INIST</idno>
<idno type="RBID">Pascal:07-0314951</idno>
<idno type="wicri:Area/PascalFrancis/Corpus">001672</idno>
<idno type="wicri:Area/PascalFrancis/Curation">001649</idno>
</publicationStmt>
<sourceDesc><biblStruct><analytic><title xml:lang="en" level="a">Management of Status dystonicus: Our experience and review of the literature</title>
<author><name sortKey="Mariotti, Paolo" sort="Mariotti, Paolo" uniqKey="Mariotti P" first="Paolo" last="Mariotti">Paolo Mariotti</name>
<affiliation wicri:level="1"><inist:fA14 i1="01"><s1>Istituto di Neuropsichiatria Infantile, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>1 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Fasano, Alfonso" sort="Fasano, Alfonso" uniqKey="Fasano A" first="Alfonso" last="Fasano">Alfonso Fasano</name>
<affiliation wicri:level="1"><inist:fA14 i1="02"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>2 aut.</sZ>
<sZ>4 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Contarino, M Fiorella" sort="Contarino, M Fiorella" uniqKey="Contarino M" first="M. Fiorella" last="Contarino">M. Fiorella Contarino</name>
<affiliation wicri:level="1"><inist:fA14 i1="03"><s1>Department of Neurology, Academic Medical Center, University of Amsterdam</s1>
<s3>NLD</s3>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Pays-Bas</country>
</affiliation>
</author>
<author><name sortKey="Della Marca, Giacomo" sort="Della Marca, Giacomo" uniqKey="Della Marca G" first="Giacomo" last="Della Marca">Giacomo Della Marca</name>
<affiliation wicri:level="1"><inist:fA14 i1="02"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>2 aut.</sZ>
<sZ>4 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Piastra, Marco" sort="Piastra, Marco" uniqKey="Piastra M" first="Marco" last="Piastra">Marco Piastra</name>
<affiliation wicri:level="1"><inist:fA14 i1="04"><s1>Istituto di Pediatria, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Genovese, Orazio" sort="Genovese, Orazio" uniqKey="Genovese O" first="Orazio" last="Genovese">Orazio Genovese</name>
<affiliation wicri:level="1"><inist:fA14 i1="04"><s1>Istituto di Pediatria, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Pulitano, Silvia" sort="Pulitano, Silvia" uniqKey="Pulitano S" first="Silvia" last="Pulitano">Silvia Pulitano</name>
<affiliation wicri:level="1"><inist:fA14 i1="04"><s1>Istituto di Pediatria, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Chiaretti, Antonio" sort="Chiaretti, Antonio" uniqKey="Chiaretti A" first="Antonio" last="Chiaretti">Antonio Chiaretti</name>
<affiliation wicri:level="1"><inist:fA14 i1="04"><s1>Istituto di Pediatria, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
<author><name sortKey="Bentivoglio, Anna Rita" sort="Bentivoglio, Anna Rita" uniqKey="Bentivoglio A" first="Anna Rita" last="Bentivoglio">Anna Rita Bentivoglio</name>
<affiliation wicri:level="1"><inist:fA14 i1="02"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>2 aut.</sZ>
<sZ>4 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>Italie</country>
</affiliation>
</author>
</analytic>
<series><title level="j" type="main">Movement disorders</title>
<title level="j" type="abbreviated">Mov. disord.</title>
<idno type="ISSN">0885-3185</idno>
<imprint><date when="2007">2007</date>
</imprint>
</series>
</biblStruct>
</sourceDesc>
<seriesStmt><title level="j" type="main">Movement disorders</title>
<title level="j" type="abbreviated">Mov. disord.</title>
<idno type="ISSN">0885-3185</idno>
</seriesStmt>
</fileDesc>
<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Clinical management</term>
<term>Dystonia</term>
<term>Experience</term>
<term>Midazolam</term>
<term>Nervous system diseases</term>
<term>Pantothenate kinase</term>
</keywords>
<keywords scheme="Pascal" xml:lang="fr"><term>Système nerveux pathologie</term>
<term>Dystonie</term>
<term>Conduite à tenir</term>
<term>Expérience</term>
<term>Midazolam</term>
<term>Pantothenate kinase</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front><div type="abstract" xml:lang="en">Status dystonicus (SD) is a life threatening disorder that develops in patients with both primary and secondary dystonia, characterized by acute worsening of symptoms with generalized and severe muscle contractions. To date, no information is available on the best way to treat this disorder. We review the previously described cases of SD and two new cases are reported, one of which occurring in a child with static encephalopathy, and the other one in a patient with pantothenate kinase-associated neurodegeneration. Both patients were admitted to an intensive care unit and treated with midazolam and propofol. This approach proved to be useful in the former while the progressive nature of the dystonia of the second patient required the combination of intrathecal baclofen infusion and bilateral pallidal deep brain stimulation. We believe that a rapid and aggressive approach is justified to avoid the great morbidity and mortality which characterize SD. Our experience, combined with the data available in the literature, might permit to establish the best strategies in managing this rare and severe condition.</div>
</front>
</TEI>
<inist><standard h6="B"><pA><fA01 i1="01" i2="1"><s0>0885-3185</s0>
</fA01>
<fA03 i2="1"><s0>Mov. disord.</s0>
</fA03>
<fA05><s2>22</s2>
</fA05>
<fA06><s2>7</s2>
</fA06>
<fA08 i1="01" i2="1" l="ENG"><s1>Management of Status dystonicus: Our experience and review of the literature</s1>
</fA08>
<fA11 i1="01" i2="1"><s1>MARIOTTI (Paolo)</s1>
</fA11>
<fA11 i1="02" i2="1"><s1>FASANO (Alfonso)</s1>
</fA11>
<fA11 i1="03" i2="1"><s1>CONTARINO (M. Fiorella)</s1>
</fA11>
<fA11 i1="04" i2="1"><s1>DELLA MARCA (Giacomo)</s1>
</fA11>
<fA11 i1="05" i2="1"><s1>PIASTRA (Marco)</s1>
</fA11>
<fA11 i1="06" i2="1"><s1>GENOVESE (Orazio)</s1>
</fA11>
<fA11 i1="07" i2="1"><s1>PULITANO (Silvia)</s1>
</fA11>
<fA11 i1="08" i2="1"><s1>CHIARETTI (Antonio)</s1>
</fA11>
<fA11 i1="09" i2="1"><s1>BENTIVOGLIO (Anna Rita)</s1>
</fA11>
<fA14 i1="01"><s1>Istituto di Neuropsichiatria Infantile, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>1 aut.</sZ>
</fA14>
<fA14 i1="02"><s1>Istituto di Neurologia, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>2 aut.</sZ>
<sZ>4 aut.</sZ>
<sZ>9 aut.</sZ>
</fA14>
<fA14 i1="03"><s1>Department of Neurology, Academic Medical Center, University of Amsterdam</s1>
<s3>NLD</s3>
<sZ>3 aut.</sZ>
</fA14>
<fA14 i1="04"><s1>Istituto di Pediatria, Università Cattolica del Sacro Cuore</s1>
<s2>Roma</s2>
<s3>ITA</s3>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
</fA14>
<fA20><s1>963-968</s1>
</fA20>
<fA21><s1>2007</s1>
</fA21>
<fA23 i1="01"><s0>ENG</s0>
</fA23>
<fA43 i1="01"><s1>INIST</s1>
<s2>20953</s2>
<s5>354000149881420090</s5>
</fA43>
<fA44><s0>0000</s0>
<s1>© 2007 INIST-CNRS. All rights reserved.</s1>
</fA44>
<fA45><s0>23 ref.</s0>
</fA45>
<fA47 i1="01" i2="1"><s0>07-0314951</s0>
</fA47>
<fA60><s1>P</s1>
</fA60>
<fA61><s0>A</s0>
</fA61>
<fA64 i1="01" i2="1"><s0>Movement disorders</s0>
</fA64>
<fA66 i1="01"><s0>USA</s0>
</fA66>
<fC01 i1="01" l="ENG"><s0>Status dystonicus (SD) is a life threatening disorder that develops in patients with both primary and secondary dystonia, characterized by acute worsening of symptoms with generalized and severe muscle contractions. To date, no information is available on the best way to treat this disorder. We review the previously described cases of SD and two new cases are reported, one of which occurring in a child with static encephalopathy, and the other one in a patient with pantothenate kinase-associated neurodegeneration. Both patients were admitted to an intensive care unit and treated with midazolam and propofol. This approach proved to be useful in the former while the progressive nature of the dystonia of the second patient required the combination of intrathecal baclofen infusion and bilateral pallidal deep brain stimulation. We believe that a rapid and aggressive approach is justified to avoid the great morbidity and mortality which characterize SD. Our experience, combined with the data available in the literature, might permit to establish the best strategies in managing this rare and severe condition.</s0>
</fC01>
<fC02 i1="01" i2="X"><s0>002B17</s0>
</fC02>
<fC02 i1="02" i2="X"><s0>002B17E</s0>
</fC02>
<fC02 i1="03" i2="X"><s0>002B17A03</s0>
</fC02>
<fC03 i1="01" i2="X" l="FRE"><s0>Système nerveux pathologie</s0>
<s5>01</s5>
</fC03>
<fC03 i1="01" i2="X" l="ENG"><s0>Nervous system diseases</s0>
<s5>01</s5>
</fC03>
<fC03 i1="01" i2="X" l="SPA"><s0>Sistema nervioso patología</s0>
<s5>01</s5>
</fC03>
<fC03 i1="02" i2="X" l="FRE"><s0>Dystonie</s0>
<s5>02</s5>
</fC03>
<fC03 i1="02" i2="X" l="ENG"><s0>Dystonia</s0>
<s5>02</s5>
</fC03>
<fC03 i1="02" i2="X" l="SPA"><s0>Distonía</s0>
<s5>02</s5>
</fC03>
<fC03 i1="03" i2="X" l="FRE"><s0>Conduite à tenir</s0>
<s5>09</s5>
</fC03>
<fC03 i1="03" i2="X" l="ENG"><s0>Clinical management</s0>
<s5>09</s5>
</fC03>
<fC03 i1="03" i2="X" l="SPA"><s0>Actitud médica</s0>
<s5>09</s5>
</fC03>
<fC03 i1="04" i2="X" l="FRE"><s0>Expérience</s0>
<s5>10</s5>
</fC03>
<fC03 i1="04" i2="X" l="ENG"><s0>Experience</s0>
<s5>10</s5>
</fC03>
<fC03 i1="04" i2="X" l="SPA"><s0>Experiencia</s0>
<s5>10</s5>
</fC03>
<fC03 i1="05" i2="X" l="FRE"><s0>Midazolam</s0>
<s2>NK</s2>
<s2>FR</s2>
<s5>11</s5>
</fC03>
<fC03 i1="05" i2="X" l="ENG"><s0>Midazolam</s0>
<s2>NK</s2>
<s2>FR</s2>
<s5>11</s5>
</fC03>
<fC03 i1="05" i2="X" l="SPA"><s0>Midazolam</s0>
<s2>NK</s2>
<s2>FR</s2>
<s5>11</s5>
</fC03>
<fC03 i1="06" i2="X" l="FRE"><s0>Pantothenate kinase</s0>
<s2>FE</s2>
<s5>12</s5>
</fC03>
<fC03 i1="06" i2="X" l="ENG"><s0>Pantothenate kinase</s0>
<s2>FE</s2>
<s5>12</s5>
</fC03>
<fC03 i1="06" i2="X" l="SPA"><s0>Pantothenate kinase</s0>
<s2>FE</s2>
<s5>12</s5>
</fC03>
<fC07 i1="01" i2="X" l="FRE"><s0>Transferases</s0>
<s2>FE</s2>
</fC07>
<fC07 i1="01" i2="X" l="ENG"><s0>Transferases</s0>
<s2>FE</s2>
</fC07>
<fC07 i1="01" i2="X" l="SPA"><s0>Transferases</s0>
<s2>FE</s2>
</fC07>
<fC07 i1="02" i2="X" l="FRE"><s0>Enzyme</s0>
<s2>FE</s2>
</fC07>
<fC07 i1="02" i2="X" l="ENG"><s0>Enzyme</s0>
<s2>FE</s2>
</fC07>
<fC07 i1="02" i2="X" l="SPA"><s0>Enzima</s0>
<s2>FE</s2>
</fC07>
<fC07 i1="03" i2="X" l="FRE"><s0>Extrapyramidal syndrome</s0>
<s5>37</s5>
</fC07>
<fC07 i1="03" i2="X" l="ENG"><s0>Extrapyramidal syndrome</s0>
<s5>37</s5>
</fC07>
<fC07 i1="03" i2="X" l="SPA"><s0>Extrapiramidal síndrome</s0>
<s5>37</s5>
</fC07>
<fC07 i1="04" i2="X" l="FRE"><s0>Mouvement involontaire</s0>
<s5>38</s5>
</fC07>
<fC07 i1="04" i2="X" l="ENG"><s0>Involuntary movement</s0>
<s5>38</s5>
</fC07>
<fC07 i1="04" i2="X" l="SPA"><s0>Movimiento involuntario</s0>
<s5>38</s5>
</fC07>
<fC07 i1="05" i2="X" l="FRE"><s0>Muscle strié pathologie</s0>
<s5>39</s5>
</fC07>
<fC07 i1="05" i2="X" l="ENG"><s0>Striated muscle disease</s0>
<s5>39</s5>
</fC07>
<fC07 i1="05" i2="X" l="SPA"><s0>Músculo estriado patología</s0>
<s5>39</s5>
</fC07>
<fC07 i1="06" i2="X" l="FRE"><s0>Trouble neurologique</s0>
<s5>40</s5>
</fC07>
<fC07 i1="06" i2="X" l="ENG"><s0>Neurological disorder</s0>
<s5>40</s5>
</fC07>
<fC07 i1="06" i2="X" l="SPA"><s0>Trastorno neurológico</s0>
<s5>40</s5>
</fC07>
<fC07 i1="07" i2="X" l="FRE"><s0>Encéphale pathologie</s0>
<s5>41</s5>
</fC07>
<fC07 i1="07" i2="X" l="ENG"><s0>Cerebral disorder</s0>
<s5>41</s5>
</fC07>
<fC07 i1="07" i2="X" l="SPA"><s0>Encéfalo patología</s0>
<s5>41</s5>
</fC07>
<fC07 i1="08" i2="X" l="FRE"><s0>Système nerveux central pathologie</s0>
<s5>42</s5>
</fC07>
<fC07 i1="08" i2="X" l="ENG"><s0>Central nervous system disease</s0>
<s5>42</s5>
</fC07>
<fC07 i1="08" i2="X" l="SPA"><s0>Sistema nervosio central patología</s0>
<s5>42</s5>
</fC07>
<fN21><s1>204</s1>
</fN21>
<fN44 i1="01"><s1>OTO</s1>
</fN44>
<fN82><s1>OTO</s1>
</fN82>
</pA>
</standard>
</inist>
</record>

Pour manipuler ce document sous Unix (Dilib)

EXPLOR_STEP=$WICRI_ROOT/Wicri/Santé/explor/MovDisordV3/Data/PascalFrancis/Curation

HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 001649 | SxmlIndent | more

HfdSelect -h $EXPLOR_AREA/Data/PascalFrancis/Curation/biblio.hfd -nk 001649 | SxmlIndent | more

Pour mettre un lien sur cette page dans le réseau Wicri

{{Explor lien
   |wiki=    Wicri/Santé
   |area=    MovDisordV3
   |flux=    PascalFrancis
   |étape=   Curation
   |type=    RBID
   |clé=     Pascal:07-0314951
   |texte=   Management of Status dystonicus: Our experience and review of the literature
}}

This area was generated with Dilib version V0.6.23.
Data generation: Sun Jul 3 12:29:32 2016. Site generation: Wed Feb 14 10:52:30 2024

	Movement Disorders (revue)
	Attention, ce site est en cours de développement ! Attention, site généré par des moyens informatiques à partir de corpus bruts. Les informations ne sont donc pas validées.

Movement Disorders (revue)

Management of Status dystonicus: Our experience and review of the literature

Management of Status dystonicus: Our experience and review of the literature

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Links to Exploration step

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri