Progressive supranuclear palsy-like phenotype associated with bilateral hypoxic-ischemic striopallidal lesions
Identifieur interne : 000E76 ( PascalFrancis/Curation ); précédent : 000E75; suivant : 000E77Progressive supranuclear palsy-like phenotype associated with bilateral hypoxic-ischemic striopallidal lesions
Auteurs : HEE TAE KIM [Royaume-Uni] ; Simon Shields [Royaume-Uni] ; Kailash P. Bhatia [Royaume-Uni] ; Niall Quinn [Royaume-Uni]Source :
- Movement disorders [ 0885-3185 ] ; 2005.
Descripteurs français
- Pascal (Inist)
English descriptors
- KwdEn :
Abstract
A progressive supranuclear palsy (PSP)-like syndrome due to vascular or anoxic brain insult is rare. We describe a 65-year-old man with a progressive PSP-like phenotype associated with hypoxic-ischemic bilateral striopallidal lesions, secondary to rupture of and subsequent surgery for a thoracic aortic aneurysm. After early extrapyramidal features, 10 months later he started to fall, and developed levator inhibition. A supranuclear gaze palsy for downgaze was documented 5.5 years after the insult.
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