Movement Disorders (revue)

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Corticobasal degeneration syndrome with basal ganglia calcification: Fahr's disease as a corticobasal look-alike?

Identifieur interne : 000580 ( PascalFrancis/Curation ); précédent : 000579; suivant : 000581

Corticobasal degeneration syndrome with basal ganglia calcification: Fahr's disease as a corticobasal look-alike?

Auteurs : Jason D. Warren [Royaume-Uni] ; Catherine J. Mummery [Royaume-Uni] ; Amir S. Al-Din [Royaume-Uni] ; Peter Brown [Royaume-Uni] ; Nicholas W. Wood [Royaume-Uni]

Source :

RBID : Pascal:02-0368569

Descripteurs français

English descriptors

Abstract

A 57-year-old man with a 5-year history of progressive left-sided rigidity and apraxia had extensive bilateral calcification of basal ganglia, centrum semiovale, dentate nuclei, and cerebellar white matter on brain imaging. The case is an example of radiological Fahr's disease accompanying a clinical syndrome of corticobasal degeneration. Possible pathogenetic and nosological implications of this association are discussed.
pA  
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A05       @2 17
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A08 01  1  ENG  @1 Corticobasal degeneration syndrome with basal ganglia calcification: Fahr's disease as a corticobasal look-alike?
A11 01  1    @1 WARREN (Jason D.)
A11 02  1    @1 MUMMERY (Catherine J.)
A11 03  1    @1 AL-DIN (Amir S.)
A11 04  1    @1 BROWN (Peter)
A11 05  1    @1 WOOD (Nicholas W.)
A14 01      @1 The National Hospital for Neurology and Neurosurgery, Queen Square @2 London @3 GBR @Z 1 aut. @Z 2 aut. @Z 4 aut. @Z 5 aut.
A14 02      @1 Pinderfields General Hospital @2 Wakefield @3 GBR @Z 3 aut.
A14 03      @1 Sobell Department of Neurophysiology, Institute of Neurology, Queen Square @2 London @3 GBR @Z 4 aut.
A14 04      @1 Neurogenetics Unit, Institute of Neurology, Queen Square @2 London @3 GBR @Z 5 aut.
A20       @1 563-567
A21       @1 2002
A23 01      @0 ENG
A43 01      @1 INIST @2 20953 @5 354000108224770210
A44       @0 0000 @1 © 2002 INIST-CNRS. All rights reserved.
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A47 01  1    @0 02-0368569
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C01 01    ENG  @0 A 57-year-old man with a 5-year history of progressive left-sided rigidity and apraxia had extensive bilateral calcification of basal ganglia, centrum semiovale, dentate nuclei, and cerebellar white matter on brain imaging. The case is an example of radiological Fahr's disease accompanying a clinical syndrome of corticobasal degeneration. Possible pathogenetic and nosological implications of this association are discussed.
C02 01  X    @0 002B17G
C03 01  X  FRE  @0 Dégénérescence @5 01
C03 01  X  ENG  @0 Degeneration @5 01
C03 01  X  SPA  @0 Degeneración @5 01
C03 02  X  FRE  @0 Cortex cérébral @5 02
C03 02  X  ENG  @0 Cerebral cortex @5 02
C03 02  X  SPA  @0 Corteza cerebral @5 02
C03 03  X  FRE  @0 Noyau gris central @5 03
C03 03  X  ENG  @0 Basal ganglion @5 03
C03 03  X  SPA  @0 Núcleo basal @5 03
C03 04  X  FRE  @0 Calcification @5 04
C03 04  X  ENG  @0 Calcification @5 04
C03 04  X  SPA  @0 Calcificación @5 04
C03 05  X  FRE  @0 Imagerie RMN @5 07
C03 05  X  ENG  @0 Nuclear magnetic resonance imaging @5 07
C03 05  X  SPA  @0 Imaginería RMN @5 07
C03 06  X  FRE  @0 Etude cas @5 17
C03 06  X  ENG  @0 Case study @5 17
C03 06  X  SPA  @0 Estudio caso @5 17
C03 07  X  FRE  @0 Diagnostic différentiel @5 18
C03 07  X  ENG  @0 Differential diagnostic @5 18
C03 07  X  SPA  @0 Diagnóstico diferencial @5 18
C03 08  X  FRE  @0 Pathogénie @5 19
C03 08  X  ENG  @0 Pathogenesis @5 19
C03 08  X  SPA  @0 Patogenia @5 19
C03 09  X  FRE  @0 Adulte @5 20
C03 09  X  ENG  @0 Adult @5 20
C03 09  X  SPA  @0 Adulto @5 20
C03 10  X  FRE  @0 Mâle @5 21
C03 10  X  ENG  @0 Male @5 21
C03 10  X  SPA  @0 Macho @5 21
C03 11  X  FRE  @0 Fahr maladie @4 INC @5 86
C07 01  X  FRE  @0 Homme
C07 01  X  ENG  @0 Human
C07 01  X  SPA  @0 Hombre
C07 02  X  FRE  @0 Système nerveux pathologie @5 37
C07 02  X  ENG  @0 Nervous system diseases @5 37
C07 02  X  SPA  @0 Sistema nervioso patología @5 37
C07 03  X  FRE  @0 Système nerveux central pathologie @5 38
C07 03  X  ENG  @0 Central nervous system disease @5 38
C07 03  X  SPA  @0 Sistema nervosio central patología @5 38
C07 04  X  FRE  @0 Encéphale pathologie @5 39
C07 04  X  ENG  @0 Cerebral disorder @5 39
C07 04  X  SPA  @0 Encéfalo patología @5 39
C07 05  X  FRE  @0 Maladie dégénérative @5 40
C07 05  X  ENG  @0 Degenerative disease @5 40
C07 05  X  SPA  @0 Enfermedad degenerativa @5 40
C07 06  X  FRE  @0 Imagerie médicale @5 53
C07 06  X  ENG  @0 Medical imagery @5 53
C07 06  X  SPA  @0 Imaginería médica @5 53
N21       @1 203
N82       @1 PSI

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Pascal:02-0368569

Le document en format XML

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<div type="abstract" xml:lang="en">A 57-year-old man with a 5-year history of progressive left-sided rigidity and apraxia had extensive bilateral calcification of basal ganglia, centrum semiovale, dentate nuclei, and cerebellar white matter on brain imaging. The case is an example of radiological Fahr's disease accompanying a clinical syndrome of corticobasal degeneration. Possible pathogenetic and nosological implications of this association are discussed.</div>
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<fC03 i1="09" i2="X" l="ENG">
<s0>Adult</s0>
<s5>20</s5>
</fC03>
<fC03 i1="09" i2="X" l="SPA">
<s0>Adulto</s0>
<s5>20</s5>
</fC03>
<fC03 i1="10" i2="X" l="FRE">
<s0>Mâle</s0>
<s5>21</s5>
</fC03>
<fC03 i1="10" i2="X" l="ENG">
<s0>Male</s0>
<s5>21</s5>
</fC03>
<fC03 i1="10" i2="X" l="SPA">
<s0>Macho</s0>
<s5>21</s5>
</fC03>
<fC03 i1="11" i2="X" l="FRE">
<s0>Fahr maladie</s0>
<s4>INC</s4>
<s5>86</s5>
</fC03>
<fC07 i1="01" i2="X" l="FRE">
<s0>Homme</s0>
</fC07>
<fC07 i1="01" i2="X" l="ENG">
<s0>Human</s0>
</fC07>
<fC07 i1="01" i2="X" l="SPA">
<s0>Hombre</s0>
</fC07>
<fC07 i1="02" i2="X" l="FRE">
<s0>Système nerveux pathologie</s0>
<s5>37</s5>
</fC07>
<fC07 i1="02" i2="X" l="ENG">
<s0>Nervous system diseases</s0>
<s5>37</s5>
</fC07>
<fC07 i1="02" i2="X" l="SPA">
<s0>Sistema nervioso patología</s0>
<s5>37</s5>
</fC07>
<fC07 i1="03" i2="X" l="FRE">
<s0>Système nerveux central pathologie</s0>
<s5>38</s5>
</fC07>
<fC07 i1="03" i2="X" l="ENG">
<s0>Central nervous system disease</s0>
<s5>38</s5>
</fC07>
<fC07 i1="03" i2="X" l="SPA">
<s0>Sistema nervosio central patología</s0>
<s5>38</s5>
</fC07>
<fC07 i1="04" i2="X" l="FRE">
<s0>Encéphale pathologie</s0>
<s5>39</s5>
</fC07>
<fC07 i1="04" i2="X" l="ENG">
<s0>Cerebral disorder</s0>
<s5>39</s5>
</fC07>
<fC07 i1="04" i2="X" l="SPA">
<s0>Encéfalo patología</s0>
<s5>39</s5>
</fC07>
<fC07 i1="05" i2="X" l="FRE">
<s0>Maladie dégénérative</s0>
<s5>40</s5>
</fC07>
<fC07 i1="05" i2="X" l="ENG">
<s0>Degenerative disease</s0>
<s5>40</s5>
</fC07>
<fC07 i1="05" i2="X" l="SPA">
<s0>Enfermedad degenerativa</s0>
<s5>40</s5>
</fC07>
<fC07 i1="06" i2="X" l="FRE">
<s0>Imagerie médicale</s0>
<s5>53</s5>
</fC07>
<fC07 i1="06" i2="X" l="ENG">
<s0>Medical imagery</s0>
<s5>53</s5>
</fC07>
<fC07 i1="06" i2="X" l="SPA">
<s0>Imaginería médica</s0>
<s5>53</s5>
</fC07>
<fN21>
<s1>203</s1>
</fN21>
<fN82>
<s1>PSI</s1>
</fN82>
</pA>
</standard>
</inist>
</record>

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