Movement Disorders (revue)

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Essential tremor in childhood: A series of nineteen cases

Identifieur interne : 000408 ( PascalFrancis/Curation ); précédent : 000407; suivant : 000409

Essential tremor in childhood: A series of nineteen cases

Auteurs : Elan D. Louis [États-Unis] ; Leon S. Iv Dure [États-Unis] ; Seth Pullman [États-Unis]

Source :

RBID : Pascal:02-0050705

Descripteurs français

English descriptors

Abstract

One in 20 essential tremor (ET) cases arises during childhood. We report 19 pediatric ET cases (mean age = 12.7 years). The majority (68.4%) were male, and only one had head tremor. Childhood and adult forms of ET may differ in several important respects, providing information about the underlying biology of ET. A possible male preponderance in childhood ET cases could reflect a modification of disease expression by gender, such that males manifest the disease at an earlier age than females. A paucity of childhood cases with head tremor suggests that the neuropathological changes in ET may evolve somatotopically. Head tremor may require midline or more extensive bilateral pathology which may only occur later in the disease.
pA  
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A08 01  1  ENG  @1 Essential tremor in childhood: A series of nineteen cases
A11 01  1    @1 LOUIS (Elan D.)
A11 02  1    @1 DURE (Leon S. IV)
A11 03  1    @1 PULLMAN (Seth)
A14 01      @1 Gertrude H. Sergievsky Center, College of Physicians and Surgeons, Columbia University @2 New York, New York @3 USA @Z 1 aut.
A14 02      @1 Department of Neurology, College of Physicians and Surgeons, Columbia University @2 New York, New York @3 USA @Z 1 aut. @Z 3 aut.
A14 03      @1 University of Alabama at Birmingham @2 Birmingham, Alabama @3 USA @Z 2 aut.
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A21       @1 2001
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A44       @0 0000 @1 © 2002 INIST-CNRS. All rights reserved.
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A60       @1 P
A61       @0 A
A64 01  1    @0 Movement disorders
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C01 01    ENG  @0 One in 20 essential tremor (ET) cases arises during childhood. We report 19 pediatric ET cases (mean age = 12.7 years). The majority (68.4%) were male, and only one had head tremor. Childhood and adult forms of ET may differ in several important respects, providing information about the underlying biology of ET. A possible male preponderance in childhood ET cases could reflect a modification of disease expression by gender, such that males manifest the disease at an earlier age than females. A paucity of childhood cases with head tremor suggests that the neuropathological changes in ET may evolve somatotopically. Head tremor may require midline or more extensive bilateral pathology which may only occur later in the disease.
C02 01  X    @0 002B17A01
C03 01  X  FRE  @0 Tremblement @5 01
C03 01  X  ENG  @0 Tremor @5 01
C03 01  X  SPA  @0 Temblor @5 01
C03 02  X  FRE  @0 Essentiel @5 02
C03 02  X  ENG  @0 Essential @5 02
C03 02  X  SPA  @0 Esencial @5 02
C03 03  X  FRE  @0 Symptomatologie @5 04
C03 03  X  ENG  @0 Symptomatology @5 04
C03 03  X  SPA  @0 Sintomatología @5 04
C03 04  X  FRE  @0 Localisation @5 05
C03 04  X  ENG  @0 Localization @5 05
C03 04  X  SPA  @0 Localización @5 05
C03 05  X  FRE  @0 Diagnostic @5 17
C03 05  X  ENG  @0 Diagnosis @5 17
C03 05  X  SPA  @0 Diagnóstico @5 17
C03 06  X  FRE  @0 Etude comparative @5 18
C03 06  X  ENG  @0 Comparative study @5 18
C03 06  X  SPA  @0 Estudio comparativo @5 18
C03 07  X  FRE  @0 Enfant @5 20
C03 07  X  ENG  @0 Child @5 20
C03 07  X  SPA  @0 Niño @5 20
C03 08  X  FRE  @0 Adulte @5 21
C03 08  X  ENG  @0 Adult @5 21
C03 08  X  SPA  @0 Adulto @5 21
C07 01  X  FRE  @0 Homme
C07 01  X  ENG  @0 Human
C07 01  X  SPA  @0 Hombre
C07 02  X  FRE  @0 Système nerveux pathologie @5 37
C07 02  X  ENG  @0 Nervous system diseases @5 37
C07 02  X  SPA  @0 Sistema nervioso patología @5 37
C07 03  X  FRE  @0 Trouble neurologique @5 38
C07 03  X  ENG  @0 Neurological disorder @5 38
C07 03  X  SPA  @0 Trastorno neurológico @5 38
C07 04  X  FRE  @0 Mouvement involontaire @5 39
C07 04  X  ENG  @0 Involuntary movement @5 39
C07 04  X  SPA  @0 Movimiento involuntario @5 39
N21       @1 021

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