Unusual nocturnal motor restlessness in a patient with spinocerebellar ataxia 3.
Identifieur interne : 001206 ( Ncbi/Merge ); précédent : 001205; suivant : 001207Unusual nocturnal motor restlessness in a patient with spinocerebellar ataxia 3.
Auteurs : Imad Ghorayeb [France] ; Federica Provini ; Bernard Bioulac ; François TisonSource :
- Movement disorders : official journal of the Movement Disorder Society [ 0885-3185 ] ; 2005.
English descriptors
- KwdEn :
- MESH :
- complications : Machado-Joseph Disease.
- etiology : Nocturnal Myoclonus Syndrome.
- methods : Polysomnography.
- Adult, Female, Humans.
Abstract
Video-polysomnographic monitoring of a female patient with spinocerebellar ataxia 3 (SCA-3) in whom rapid eye movement (REM) sleep behavior disorder was clinically suspected demonstrated recurrent episodes of unusual nocturnal motor restlessness occurring during non-REM sleep and severely disturbing both the patient and her bed partner's sleep. Even if nocturnal manifestations are common features of SCA-3 and increasingly recognized, such a case has never been reported before. We discuss this peculiar movement disorder as a particular manifestation of the wide spectrum of parasomnias occurring in such a rare neurodegenerative disease.
DOI: 10.1002/mds.20415
PubMed: 15799016
Links toward previous steps (curation, corpus...)
- to stream PubMed, to step Corpus: 003095
- to stream PubMed, to step Curation: 003095
- to stream PubMed, to step Checkpoint: 002F15
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pubmed:15799016Le document en format XML
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<front><div type="abstract" xml:lang="en">Video-polysomnographic monitoring of a female patient with spinocerebellar ataxia 3 (SCA-3) in whom rapid eye movement (REM) sleep behavior disorder was clinically suspected demonstrated recurrent episodes of unusual nocturnal motor restlessness occurring during non-REM sleep and severely disturbing both the patient and her bed partner's sleep. Even if nocturnal manifestations are common features of SCA-3 and increasingly recognized, such a case has never been reported before. We discuss this peculiar movement disorder as a particular manifestation of the wide spectrum of parasomnias occurring in such a rare neurodegenerative disease.</div>
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