Cortical Myoclonus in Huntington's disease associated with an enlarged somatosensory evoked potential.
Identifieur interne : 004E39 ( Ncbi/Curation ); précédent : 004E38; suivant : 004E40Cortical Myoclonus in Huntington's disease associated with an enlarged somatosensory evoked potential.
Auteurs : J N Caviness [États-Unis] ; M. KurthSource :
- Movement disorders : official journal of the Movement Disorder Society [ 0885-3185 ] ; 1997.
English descriptors
- KwdEn :
- Adult, Brain Tissue Transplantation, Cerebral Cortex (pathology), Corpus Striatum (embryology), Corpus Striatum (transplantation), Electroencephalography, Electromyography, Evoked Potentials, Somatosensory, Humans, Huntington Disease (complications), Huntington Disease (surgery), Male, Myoclonus (complications), Myoclonus (pathology).
- MESH :
- complications : Huntington Disease, Myoclonus.
- embryology : Corpus Striatum.
- pathology : Cerebral Cortex, Myoclonus.
- surgery : Huntington Disease.
- transplantation : Corpus Striatum.
- Adult, Brain Tissue Transplantation, Electroencephalography, Electromyography, Evoked Potentials, Somatosensory, Humans, Male.
Abstract
We report the electrophysiologic findings of myoclonus in a patient with Huntington's disease (HD). This patient was studied postoperatively after a bilateral fetal cell transplant in his striatum. Incomplete transient improvement was seen in the myoclonus, followed by gradual deterioration. The myoclonus itself had a cortical correlate and was associated with an enlarged somatosensory evoked potential (SEP), consistent with the presence of cortical reflex myoclonus. An enlarged SEP has not been previously reported in myoclonus associated with HD. The postulated mechanisms for myoclonus, when it occurs in HD, have differed in the literature. The reason for the transient improvement of the myoclonus following transplantation is unclear, but this case raises the possibility that basal ganglia circuits may modulate cortical myoclonic activity.
DOI: 10.1002/mds.870120633
PubMed: 9399235
Links toward previous steps (curation, corpus...)
- to stream PubMed, to step Corpus: Pour aller vers cette notice dans l'étape Curation :004546
- to stream PubMed, to step Curation: Pour aller vers cette notice dans l'étape Curation :004546
- to stream PubMed, to step Checkpoint: Pour aller vers cette notice dans l'étape Curation :004682
- to stream Ncbi, to step Merge: Pour aller vers cette notice dans l'étape Curation :004E39
Links to Exploration step
pubmed:9399235Le document en format XML
<record><TEI><teiHeader><fileDesc><titleStmt><title xml:lang="en">Cortical Myoclonus in Huntington's disease associated with an enlarged somatosensory evoked potential.</title><author><name sortKey="Caviness, J N" sort="Caviness, J N" uniqKey="Caviness J" first="J N" last="Caviness">J N Caviness</name><affiliation wicri:level="2"><nlm:affiliation>Department of Neurology, Mayo Clinic Scottsdale, AZ 85259, USA.</nlm:affiliation><country xml:lang="fr">États-Unis</country><wicri:regionArea>Department of Neurology, Mayo Clinic Scottsdale, AZ 85259</wicri:regionArea><placeName><region type="state">Arizona</region></placeName></affiliation></author><author><name sortKey="Kurth, M" sort="Kurth, M" uniqKey="Kurth M" first="M" last="Kurth">M. Kurth</name></author></titleStmt><publicationStmt><idno type="wicri:source">PubMed</idno><date when="1997">1997</date><idno type="RBID">pubmed:9399235</idno><idno type="pmid">9399235</idno><idno type="doi">10.1002/mds.870120633</idno><idno type="wicri:Area/PubMed/Corpus">004546</idno><idno type="wicri:Area/PubMed/Curation">004546</idno><idno type="wicri:Area/PubMed/Checkpoint">004682</idno><idno type="wicri:Area/Ncbi/Merge">004E39</idno><idno type="wicri:Area/Ncbi/Curation">004E39</idno></publicationStmt><sourceDesc><biblStruct><analytic><title xml:lang="en">Cortical Myoclonus in Huntington's disease associated with an enlarged somatosensory evoked potential.</title><author><name sortKey="Caviness, J N" sort="Caviness, J N" uniqKey="Caviness J" first="J N" last="Caviness">J N Caviness</name><affiliation wicri:level="2"><nlm:affiliation>Department of Neurology, Mayo Clinic Scottsdale, AZ 85259, USA.</nlm:affiliation><country xml:lang="fr">États-Unis</country><wicri:regionArea>Department of Neurology, Mayo Clinic Scottsdale, AZ 85259</wicri:regionArea><placeName><region type="state">Arizona</region></placeName></affiliation></author><author><name sortKey="Kurth, M" sort="Kurth, M" uniqKey="Kurth M" first="M" last="Kurth">M. Kurth</name></author></analytic><series><title level="j">Movement disorders : official journal of the Movement Disorder Society</title><idno type="ISSN">0885-3185</idno><imprint><date when="1997" type="published">1997</date></imprint></series></biblStruct></sourceDesc></fileDesc><profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Adult</term><term>Brain Tissue Transplantation</term><term>Cerebral Cortex (pathology)</term><term>Corpus Striatum (embryology)</term><term>Corpus Striatum (transplantation)</term><term>Electroencephalography</term><term>Electromyography</term><term>Evoked Potentials, Somatosensory</term><term>Humans</term><term>Huntington Disease (complications)</term><term>Huntington Disease (surgery)</term><term>Male</term><term>Myoclonus (complications)</term><term>Myoclonus (pathology)</term></keywords><keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Huntington Disease</term><term>Myoclonus</term></keywords><keywords scheme="MESH" qualifier="embryology" xml:lang="en"><term>Corpus Striatum</term></keywords><keywords scheme="MESH" qualifier="pathology" xml:lang="en"><term>Cerebral Cortex</term><term>Myoclonus</term></keywords><keywords scheme="MESH" qualifier="surgery" xml:lang="en"><term>Huntington Disease</term></keywords><keywords scheme="MESH" qualifier="transplantation" xml:lang="en"><term>Corpus Striatum</term></keywords><keywords scheme="MESH" xml:lang="en"><term>Adult</term><term>Brain Tissue Transplantation</term><term>Electroencephalography</term><term>Electromyography</term><term>Evoked Potentials, Somatosensory</term><term>Humans</term><term>Male</term></keywords></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">We report the electrophysiologic findings of myoclonus in a patient with Huntington's disease (HD). This patient was studied postoperatively after a bilateral fetal cell transplant in his striatum. Incomplete transient improvement was seen in the myoclonus, followed by gradual deterioration. The myoclonus itself had a cortical correlate and was associated with an enlarged somatosensory evoked potential (SEP), consistent with the presence of cortical reflex myoclonus. An enlarged SEP has not been previously reported in myoclonus associated with HD. The postulated mechanisms for myoclonus, when it occurs in HD, have differed in the literature. The reason for the transient improvement of the myoclonus following transplantation is unclear, but this case raises the possibility that basal ganglia circuits may modulate cortical myoclonic activity.</div></front></TEI></record>Pour manipuler ce document sous Unix (Dilib)
EXPLOR_STEP=$WICRI_ROOT/Wicri/Santé/explor/MovDisordV3/Data/Ncbi/Curation
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 004E39 | SxmlIndent | more
Ou
HfdSelect -h $EXPLOR_AREA/Data/Ncbi/Curation/biblio.hfd -nk 004E39 | SxmlIndent | more
Pour mettre un lien sur cette page dans le réseau Wicri
{{Explor lien
|wiki= Wicri/Santé
|area= MovDisordV3
|flux= Ncbi
|étape= Curation
|type= RBID
|clé= pubmed:9399235
|texte= Cortical Myoclonus in Huntington's disease associated with an enlarged somatosensory evoked potential.
}}
Pour générer des pages wiki
HfdIndexSelect -h $EXPLOR_AREA/Data/Ncbi/Curation/RBID.i -Sk "pubmed:9399235" \
| HfdSelect -Kh $EXPLOR_AREA/Data/Ncbi/Curation/biblio.hfd \
| NlmPubMed2Wicri -a MovDisordV3
| This area was generated with Dilib version V0.6.23. |  |