MovDisordV3, Main, Merge, bibRecord, 004323

Contemporary Encephalitis Lethargica Presenting with Agitated Catatonia, Stereotypy, and Dystonia-Parkinsonism

Identifieur interne : 004323 ( Main/Merge ); précédent : 004322; suivant : 004324

Contemporary Encephalitis Lethargica Presenting with Agitated Catatonia, Stereotypy, and Dystonia-Parkinsonism

Auteurs : Russell C. Dale [Australie] ; Richard Webster [Australie] ; Deepak Gill [Australie]

Source :

Movement disorders [ 0885-3185 ] ; 2007.

RBID : Pascal:08-0071419

Descripteurs français

Pascal (Inist)
- Pathologie du système nerveux, Encéphalite, Agitation, Dystonie, Parkinsonisme, Insomnie, Catatonie, Stéréotypie, Coprolalie, Dopamine.

English descriptors

KwdEn :
- Agitation, Catatonia, Coprolalia, Dopamine, Dystonia, Encephalitis, Insomnia, Nervous system diseases, Parkinsonism, Stereotypy.

Abstract

Encephalitis lethargica (EL) syndrome was classically described by Von Economo and has somnolent-ophthalmoplegic, hyperkinetic, and amyostatic-akinetic forms. We describe 2 recent cases of EL characterized by an acute encephalitis with mixed movement disorders (dystonia-Parkinsonism plus stereotypy) and psychiatric disorders (agitated catatonia, coprolalia, and echo phenomena). Both patients suffered concurrent hyperkinetic and Parkinsonian features resulting in therapeutic challenges. Bradykinetic features responded to dopamine replacement therapy and both patients also had adverse affects to dopamine antagonists (oculogyric crises plus neuroleptic malignant syndrome). Investigation was unremarkable other than the presence of CSF lymphocytosis and oligoclonal bands. Despite prolonged in-patient stays and intensive care management, both patients have made complete recoveries. We believe these cases support the hypothesis that this syndrome is an inflammatory encephalitis that specifically effects dopamine neurotransmission.

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Pascal:08-0071419

Le document en format XML

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<term>Parkinsonisme</term>
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<front><div type="abstract" xml:lang="en">Encephalitis lethargica (EL) syndrome was classically described by Von Economo and has somnolent-ophthalmoplegic, hyperkinetic, and amyostatic-akinetic forms. We describe 2 recent cases of EL characterized by an acute encephalitis with mixed movement disorders (dystonia-Parkinsonism plus stereotypy) and psychiatric disorders (agitated catatonia, coprolalia, and echo phenomena). Both patients suffered concurrent hyperkinetic and Parkinsonian features resulting in therapeutic challenges. Bradykinetic features responded to dopamine replacement therapy and both patients also had adverse affects to dopamine antagonists (oculogyric crises plus neuroleptic malignant syndrome). Investigation was unremarkable other than the presence of CSF lymphocytosis and oligoclonal bands. Despite prolonged in-patient stays and intensive care management, both patients have made complete recoveries. We believe these cases support the hypothesis that this syndrome is an inflammatory encephalitis that specifically effects dopamine neurotransmission.</div>
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	Movement Disorders (revue)
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Movement Disorders (revue)

Contemporary Encephalitis Lethargica Presenting with Agitated Catatonia, Stereotypy, and Dystonia-Parkinsonism

Contemporary Encephalitis Lethargica Presenting with Agitated Catatonia, Stereotypy, and Dystonia-Parkinsonism

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Links to Exploration step

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri