MovDisordV3, Main, Merge, bibRecord, 001B36

Late-Onset Asymmetric Myoclonus: An Emerging Syndrome

Identifieur interne : 001B36 ( Main/Merge ); précédent : 001B35; suivant : 001B37

Late-Onset Asymmetric Myoclonus: An Emerging Syndrome

Auteurs : Petra Katschnig [Royaume-Uni, Autriche] ; João Massano [Royaume-Uni, Portugal] ; Mark J. Edwards [Royaume-Uni] ; Petra Schwingenschuh [Royaume-Uni, Autriche] ; Carla Cordivari [Royaume-Uni] ; Kailash P. Bhatia [Royaume-Uni]

Source :

Movement disorders [ 0885-3185 ] ; 2011.

RBID : Pascal:11-0380290

Descripteurs français

Pascal (Inist)
- Myoclonie, Pathologie du système nerveux, Sénescence.

English descriptors

KwdEn :
- Myoclonus, Nervous system diseases, Senescence.

Abstract

Background: Asymmetric cortical myoclonus is typically thought to be associated with either contralateral cortical structural lesions or degenerative disorders such as corticobasal degeneration when onset is in middle-aged or aged adults. This view has been challenged after a recent case series brought to light a syndrome of senile-onset, asymmetric cortical myoclonus not associated with any such identifiable disorders, thus, named "primary progressive myoclonus of aging." This is rare and no other reports have been published; hence, further such cases need to be highlighted. Case reports: Here, we describe 3 patients with some similarities, namely, adult-onset, asymmetric myoclonus that is most likely to be cortical, with an unremarkable thorough diagnostic workup, but with younger age at onset and longer follow-up time. Conclusions: This report expands on previous phenotypical descriptions attempting to further develop and refine this possible diagnostic entity.

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Pascal:11-0380290

Le document en format XML

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<sourceDesc><biblStruct><analytic><title xml:lang="en" level="a">Late-Onset Asymmetric Myoclonus: An Emerging Syndrome</title>
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<series><title level="j" type="main">Movement disorders</title>
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<front><div type="abstract" xml:lang="en">Background: Asymmetric cortical myoclonus is typically thought to be associated with either contralateral cortical structural lesions or degenerative disorders such as corticobasal degeneration when onset is in middle-aged or aged adults. This view has been challenged after a recent case series brought to light a syndrome of senile-onset, asymmetric cortical myoclonus not associated with any such identifiable disorders, thus, named "primary progressive myoclonus of aging." This is rare and no other reports have been published; hence, further such cases need to be highlighted. Case reports: Here, we describe 3 patients with some similarities, namely, adult-onset, asymmetric myoclonus that is most likely to be cortical, with an unremarkable thorough diagnostic workup, but with younger age at onset and longer follow-up time. Conclusions: This report expands on previous phenotypical descriptions attempting to further develop and refine this possible diagnostic entity.</div>
</front>
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	Movement Disorders (revue)
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Movement Disorders (revue)

Late-Onset Asymmetric Myoclonus: An Emerging Syndrome

Late-Onset Asymmetric Myoclonus: An Emerging Syndrome

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Links to Exploration step

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri