Movement Disorders (revue)

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Sporadic rapid‐onset dystonia–parkinsonism syndrome: Failure of bilateral pallidal stimulation

Identifieur interne : 003145 ( Istex/Curation ); précédent : 003144; suivant : 003146

Sporadic rapid‐onset dystonia–parkinsonism syndrome: Failure of bilateral pallidal stimulation

Auteurs : Angela Deutschl Nder [Allemagne] ; Friedrich Asmus [Allemagne] ; Thomas Gasser [Allemagne] ; Ulrich Steude [Allemagne] ; Kai Bötzel [Allemagne]

Source :

RBID : ISTEX:B7EDBBEC7F2E46B7DE148C4F2695C5B6A0CD1E72

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Abstract

We report on a woman who had a severe sporadic nonprogressive dystonia–parkinsonism syndrome with rapid onset of symptoms at age 21. Secondary causes for dystonia were ruled out. No response to levodopa/carbidopa was seen. The patient fulfilled all diagnostic criteria of rapid‐onset dystonia–parkinsonism, except for autosomal‐dominant inheritance. Bilateral deep brain stimulation of the globus pallidus failed to alleviate her symptoms. © 2004 Movement Disorder Society

Url:
DOI: 10.1002/mds.20296

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ISTEX:B7EDBBEC7F2E46B7DE148C4F2695C5B6A0CD1E72

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