Myoclonus in corticobasal degeneration
Identifieur interne : 003093 ( Istex/Curation ); précédent : 003092; suivant : 003094Myoclonus in corticobasal degeneration
Auteurs : Carella [Italie] ; Claudia Ciano [Italie] ; Ferruccio Panzica [Italie] ; Vidmer Scaioli [Italie]Source :
- Movement Disorders [ 0885-3185 ] ; 1997-07.
English descriptors
Abstract
Five patients with unilateral myoclonus and a clinical diagnosis of corticobasal degeneration (CBD) were studied. All patients showed enhanced long‐loop responses in their myoclonic arms without enlarged somatosensory potentials. The cortical relay time of the long‐loop responses was studied in three patients, in two of whom it was <2 ms, even in the nonmyoclonic arm. Myoclonus in CBD is probably related to an enhanced long‐loop reflex whose pathway is unlikely to be the same as that in classic cortical reflex myoclonus.
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DOI: 10.1002/mds.870120419
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<front><div type="abstract" xml:lang="en">Five patients with unilateral myoclonus and a clinical diagnosis of corticobasal degeneration (CBD) were studied. All patients showed enhanced long‐loop responses in their myoclonic arms without enlarged somatosensory potentials. The cortical relay time of the long‐loop responses was studied in three patients, in two of whom it was <2 ms, even in the nonmyoclonic arm. Myoclonus in CBD is probably related to an enhanced long‐loop reflex whose pathway is unlikely to be the same as that in classic cortical reflex myoclonus.</div>
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