Movement Disorders (revue)

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Myoclonus in corticobasal degeneration

Identifieur interne : 003093 ( Istex/Curation ); précédent : 003092; suivant : 003094

Myoclonus in corticobasal degeneration

Auteurs : Carella [Italie] ; Claudia Ciano [Italie] ; Ferruccio Panzica [Italie] ; Vidmer Scaioli [Italie]

Source :

RBID : ISTEX:61DE3D9F716B0F96238AB79337AA7B70F7266890

English descriptors

Abstract

Five patients with unilateral myoclonus and a clinical diagnosis of corticobasal degeneration (CBD) were studied. All patients showed enhanced long‐loop responses in their myoclonic arms without enlarged somatosensory potentials. The cortical relay time of the long‐loop responses was studied in three patients, in two of whom it was <2 ms, even in the nonmyoclonic arm. Myoclonus in CBD is probably related to an enhanced long‐loop reflex whose pathway is unlikely to be the same as that in classic cortical reflex myoclonus.

Url:
DOI: 10.1002/mds.870120419

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ISTEX:61DE3D9F716B0F96238AB79337AA7B70F7266890

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<div type="abstract" xml:lang="en">Five patients with unilateral myoclonus and a clinical diagnosis of corticobasal degeneration (CBD) were studied. All patients showed enhanced long‐loop responses in their myoclonic arms without enlarged somatosensory potentials. The cortical relay time of the long‐loop responses was studied in three patients, in two of whom it was <2 ms, even in the nonmyoclonic arm. Myoclonus in CBD is probably related to an enhanced long‐loop reflex whose pathway is unlikely to be the same as that in classic cortical reflex myoclonus.</div>
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