Case of symptomatic propriospinal myoclonus evolving toward acute “myoclonic status”
Identifieur interne : 002401 ( Istex/Checkpoint ); précédent : 002400; suivant : 002402Case of symptomatic propriospinal myoclonus evolving toward acute “myoclonic status”
Auteurs : Mauro Manconi [Italie] ; Barbara Sferrazza [Italie] ; Sandro Iannaccone [Italie] ; Antonio Massimo [Italie] ; Marco Zucconi [Italie] ; Luigi Ferini-Strambi [Italie]Source :
- Movement Disorders [ 0885-3185 ] ; 2005-12.
English descriptors
Abstract
Propriospinal myoclonus is a rare motor disorder consisting of involuntary spinal‐generated muscular jerks. Here, we report a severe and uncommon case of propriospinal myoclonus that appeared after a vertebral fracture of T11. In this patient, the polysomnographic investigation showed continuing focal myoclonic activity in axial muscles during stable sleep and an acute progression into a myoclonic “status” associated with respiratory failure and loss of consciousness. It is necessary to consider this severe progression and support it with prompt emergency maneuvers and adequate pharmacotherapy. © 2005 Movement Disorder Society
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DOI: 10.1002/mds.20645
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<front><div type="abstract" xml:lang="en">Propriospinal myoclonus is a rare motor disorder consisting of involuntary spinal‐generated muscular jerks. Here, we report a severe and uncommon case of propriospinal myoclonus that appeared after a vertebral fracture of T11. In this patient, the polysomnographic investigation showed continuing focal myoclonic activity in axial muscles during stable sleep and an acute progression into a myoclonic “status” associated with respiratory failure and loss of consciousness. It is necessary to consider this severe progression and support it with prompt emergency maneuvers and adequate pharmacotherapy. © 2005 Movement Disorder Society</div>
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