HHV6-related mild encephalopathy with reversible splenial lesion (MERS) presenting with urinary and fecal retention in an Italian adolescent.
Identifieur interne : 000555 ( Main/Merge ); précédent : 000554; suivant : 000556HHV6-related mild encephalopathy with reversible splenial lesion (MERS) presenting with urinary and fecal retention in an Italian adolescent.
Auteurs : Laura Cursi [Italie] ; Elena Boccuzzi [Italie] ; Laura Lancella [Italie] ; Daniela Longo [Italie] ; Lorenzo Figá Talamanca [Italie] ; Elena Bozzola [Italie] ; Alberto Villani [Italie]Source :
- Le infezioni in medicina [ 1124-9390 ] ; 2019.
Descripteurs français
- KwdFr :
- Adolescent, Constipation (étiologie), Corps calleux (imagerie diagnostique), Encéphalopathies (imagerie diagnostique), Encéphalopathies (virologie), Femelle, Herpèsvirus humain de type 6, Humains, Hyponatrémie (étiologie), Imagerie par résonance magnétique de diffusion, Infections à roséolovirus (), Rétention d'urine (étiologie), Symptômes prodromiques.
- MESH :
- imagerie diagnostique : Corps calleux, Encéphalopathies.
- virologie : Encéphalopathies.
- étiologie : Constipation, Hyponatrémie, Rétention d'urine.
- Adolescent, Femelle, Herpèsvirus humain de type 6, Humains, Imagerie par résonance magnétique de diffusion, Infections à roséolovirus, Symptômes prodromiques.
English descriptors
- KwdEn :
- Adolescent, Brain Diseases (diagnostic imaging), Brain Diseases (virology), Constipation (etiology), Corpus Callosum (diagnostic imaging), Diffusion Magnetic Resonance Imaging, Female, Herpesvirus 6, Human, Humans, Hyponatremia (etiology), Prodromal Symptoms, Roseolovirus Infections (complications), Urinary Retention (etiology).
- MESH :
- complications : Roseolovirus Infections.
- diagnostic imaging : Brain Diseases, Corpus Callosum.
- etiology : Constipation, Hyponatremia, Urinary Retention.
- virology : Brain Diseases.
- Adolescent, Diffusion Magnetic Resonance Imaging, Female, Herpesvirus 6, Human, Humans, Prodromal Symptoms.
Abstract
Mild encephalopathy with a reversible splenial lesion (MERS) is an uncommon clinico-radiological entity characterized by magnetic resonance imaging (MRI) findings of a reversible lesion in the splenium of corpus callosum associated with a significant neurological manifestation of encephalopathy. The majority of reported cases involve the Asiatic population and are closely associated with infection. We report the case of an adolescent with an HHV6-related MERS presenting with hyponatremia and urinary and fecal retention. To our knowledge, urinary retention is not a constant aspect of the disease and has rarely been described, while fecal retention has never been reported before. Despite the self-limiting nature of the disease, it is mandatory to suspect it for a faster diagnosis and it might be useful to know its rare occurrences in order to better understand its etiopathogenetic mechanisms.
PubMed: 30882387
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pubmed:30882387Le document en format XML
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<front><div type="abstract" xml:lang="en">Mild encephalopathy with a reversible splenial lesion (MERS) is an uncommon clinico-radiological entity characterized by magnetic resonance imaging (MRI) findings of a reversible lesion in the splenium of corpus callosum associated with a significant neurological manifestation of encephalopathy. The majority of reported cases involve the Asiatic population and are closely associated with infection. We report the case of an adolescent with an HHV6-related MERS presenting with hyponatremia and urinary and fecal retention. To our knowledge, urinary retention is not a constant aspect of the disease and has rarely been described, while fecal retention has never been reported before. Despite the self-limiting nature of the disease, it is mandatory to suspect it for a faster diagnosis and it might be useful to know its rare occurrences in order to better understand its etiopathogenetic mechanisms.</div>
</front>
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