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Transient renal dysfunction with reversible splenial lesion

Identifieur interne : 001D78 ( Main/Exploration ); précédent : 001D77; suivant : 001D79

Transient renal dysfunction with reversible splenial lesion

Auteurs : Toru Watanabe [Japon] ; Tomoka Matsuda [Japon] ; Ryoichi Kitagata [Japon] ; Iwao Tajima [Japon] ; Hiroyuki Ono [Japon] ; Keiko Hirano [Japon] ; Masami Shirai [Japon] ; Akira Endoh [Japon] ; Teruaki Hongo [Japon]

Source :

RBID : ISTEX:1B05E2E5E9F2B40D4FDBB90B5FAEB8897A088139

Abstract

We report the case of a 6‐month‐old boy with transient renal dysfunction who had an intensified signal in the splenium of the corpus callosum on magnetic resonance imaging. He presented to hospital with fever and sudden disturbance of consciousness. Cerebrospinal fluid analysis did not show pleocytosis. The mild consciousness disturbance disappeared after 30 min, but the splenial signal persisted even after 8 days. Further, renal glucosuria, increased excretion of select amino acids, and abnormal fractional excretion of electrolytes were observed, indicating renal tubular dysfunction. The abnormal urinary findings spontaneously resolved by day 9 of hospitalization. The splenial lesion took 21 days to normalize. There were no signs of neurological complications 2 months later. This case suggests the possibility of renal involvement in splenial lesions.

Url:
DOI: 10.1111/ped.12412


Affiliations:


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Le document en format XML

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<div type="abstract">We report the case of a 6‐month‐old boy with transient renal dysfunction who had an intensified signal in the splenium of the corpus callosum on magnetic resonance imaging. He presented to hospital with fever and sudden disturbance of consciousness. Cerebrospinal fluid analysis did not show pleocytosis. The mild consciousness disturbance disappeared after 30 min, but the splenial signal persisted even after 8 days. Further, renal glucosuria, increased excretion of select amino acids, and abnormal fractional excretion of electrolytes were observed, indicating renal tubular dysfunction. The abnormal urinary findings spontaneously resolved by day 9 of hospitalization. The splenial lesion took 21 days to normalize. There were no signs of neurological complications 2 months later. This case suggests the possibility of renal involvement in splenial lesions.</div>
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