Serveur d'exploration MERS

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Mild encephalitis/encephalopathy with reversible splenial lesion (MERS) in adults-a case report and literature review

Identifieur interne : 000C76 ( Main/Exploration ); précédent : 000C75; suivant : 000C77

Mild encephalitis/encephalopathy with reversible splenial lesion (MERS) in adults-a case report and literature review

Auteurs : Junliang Yuan [République populaire de Chine] ; Shuna Yang [République populaire de Chine] ; Shuangkun Wang [République populaire de Chine] ; Wei Qin [République populaire de Chine] ; Lei Yang [République populaire de Chine] ; Wenli Hu [République populaire de Chine]

Source :

RBID : PMC:5445341

Descripteurs français

English descriptors

Abstract

Background

Mild encephalitis/encephalopathy with reversible splenial lesion (MERS) is a rare clinico-radiological entity characterized by the magnetic resonance imaging (MRI) finding of a reversible lesion in the corpus callosum, sometimes involved the symmetrical white matters. Many cases of child-onset MERS with various causes have been reported. However, adult-onset MERS is relatively rare. The clinical characteristics and pathophysiologiccal mechanisms of adult-onset MERS are not well understood. We reviewed the literature on adult-onset MERS in order to describe the characteristics of MERS in adults and to provide experiences for clinician.

Methods

We reported a case of adult-onset MERS with acute urinary retension and performed literature search from PubMed and web of science databases to identify other adult-onset MERS reports from Januarary 2004 to March 2016. Preferred Reporting Items for Systematic Reviews and Meta-Analyses (PRISMA) guideline was followed on selection process. And then we summarized the clinico-radiological features of adult-onset MERS.

Results

Twenty-nine adult-onset MERS cases were reviewed from available literature including the case we have. 86.2% of the cases (25/29) were reported in Asia, especially in Japan. Ages varied between 18 and 59 years old with a 12:17 female-to-male ratio. The major cause was infection by virus or bacteria. Fever and headache were the most common clinical manifestation, and acute urinary retention was observed in 6 patients. All patients recovered completely within a month.

Conclusion

Adult-onset MERS is an entity with a broad clinico-radiological spectrum because of the various diseases and conditions. There are similar characteristics between MERS in adults and children, also some differences.


Url:
DOI: 10.1186/s12883-017-0875-5
PubMed: 28545419
PubMed Central: 5445341


Affiliations:


Links toward previous steps (curation, corpus...)


Le document en format XML

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<term>Adult</term>
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<term>Brain Diseases (diagnostic imaging)</term>
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<term>Encephalitis</term>
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<term>Encephalitis</term>
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<term>Encephalitis</term>
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<title>Background</title>
<p>Mild encephalitis/encephalopathy with reversible splenial lesion (MERS) is a rare clinico-radiological entity characterized by the magnetic resonance imaging (MRI) finding of a reversible lesion in the corpus callosum, sometimes involved the symmetrical white matters. Many cases of child-onset MERS with various causes have been reported. However, adult-onset MERS is relatively rare. The clinical characteristics and pathophysiologiccal mechanisms of adult-onset MERS are not well understood. We reviewed the literature on adult-onset MERS in order to describe the characteristics of MERS in adults and to provide experiences for clinician.</p>
</sec>
<sec>
<title>Methods</title>
<p>We reported a case of adult-onset MERS with acute urinary retension and performed literature search from PubMed and web of science databases to identify other adult-onset MERS reports from Januarary 2004 to March 2016. Preferred Reporting Items for Systematic Reviews and Meta-Analyses (PRISMA) guideline was followed on selection process. And then we summarized the clinico-radiological features of adult-onset MERS.</p>
</sec>
<sec>
<title>Results</title>
<p>Twenty-nine adult-onset MERS cases were reviewed from available literature including the case we have. 86.2% of the cases (25/29) were reported in Asia, especially in Japan. Ages varied between 18 and 59 years old with a 12:17 female-to-male ratio. The major cause was infection by virus or bacteria. Fever and headache were the most common clinical manifestation, and acute urinary retention was observed in 6 patients. All patients recovered completely within a month.</p>
</sec>
<sec>
<title>Conclusion</title>
<p>Adult-onset MERS is an entity with a broad clinico-radiological spectrum because of the various diseases and conditions. There are similar characteristics between MERS in adults and children, also some differences.</p>
</sec>
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<affiliations>
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<li>République populaire de Chine</li>
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<li>Pékin</li>
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</record>

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