Mild encephalitis/encephalopathy with reversible splenial lesion (MERS) in adults-a case report and literature review
Identifieur interne : 000C76 ( Main/Exploration ); précédent : 000C75; suivant : 000C77Mild encephalitis/encephalopathy with reversible splenial lesion (MERS) in adults-a case report and literature review
Auteurs : Junliang Yuan [République populaire de Chine] ; Shuna Yang [République populaire de Chine] ; Shuangkun Wang [République populaire de Chine] ; Wei Qin [République populaire de Chine] ; Lei Yang [République populaire de Chine] ; Wenli Hu [République populaire de Chine]Source :
- BMC Neurology [ 1471-2377 ] ; 2017.
Descripteurs français
- KwdFr :
- Adulte, Corps calleux (anatomopathologie), Encéphalite (), Encéphalite (anatomopathologie), Encéphalite (diagnostic), Encéphalite (imagerie diagnostique), Encéphalopathies (), Encéphalopathies (anatomopathologie), Encéphalopathies (diagnostic), Encéphalopathies (imagerie diagnostique), Femelle, Humains, Imagerie par résonance magnétique, Jeune adulte, Mâle, Pronostic.
- MESH :
- anatomopathologie : Corps calleux, Encéphalite, Encéphalopathies.
- diagnostic : Encéphalite, Encéphalopathies.
- imagerie diagnostique : Encéphalite, Encéphalopathies.
- Adulte, Encéphalite, Encéphalopathies, Femelle, Humains, Imagerie par résonance magnétique, Jeune adulte, Mâle, Pronostic.
English descriptors
- KwdEn :
- Adult, Brain Diseases (complications), Brain Diseases (diagnosis), Brain Diseases (diagnostic imaging), Brain Diseases (pathology), Corpus Callosum (pathology), Encephalitis (complications), Encephalitis (diagnosis), Encephalitis (diagnostic imaging), Encephalitis (pathology), Female, Humans, Magnetic Resonance Imaging, Male, Prognosis, Young Adult.
- MESH :
- complications : Brain Diseases, Encephalitis.
- diagnosis : Brain Diseases, Encephalitis.
- diagnostic imaging : Brain Diseases, Encephalitis.
- pathology : Brain Diseases, Corpus Callosum, Encephalitis.
- Adult, Female, Humans, Magnetic Resonance Imaging, Male, Prognosis, Young Adult.
Abstract
Mild encephalitis/encephalopathy with reversible splenial lesion (MERS) is a rare clinico-radiological entity characterized by the magnetic resonance imaging (MRI) finding of a reversible lesion in the corpus callosum, sometimes involved the symmetrical white matters. Many cases of child-onset MERS with various causes have been reported. However, adult-onset MERS is relatively rare. The clinical characteristics and pathophysiologiccal mechanisms of adult-onset MERS are not well understood. We reviewed the literature on adult-onset MERS in order to describe the characteristics of MERS in adults and to provide experiences for clinician.
We reported a case of adult-onset MERS with acute urinary retension and performed literature search from PubMed and web of science databases to identify other adult-onset MERS reports from Januarary 2004 to March 2016. Preferred Reporting Items for Systematic Reviews and Meta-Analyses (PRISMA) guideline was followed on selection process. And then we summarized the clinico-radiological features of adult-onset MERS.
Twenty-nine adult-onset MERS cases were reviewed from available literature including the case we have. 86.2% of the cases (25/29) were reported in Asia, especially in Japan. Ages varied between 18 and 59 years old with a 12:17 female-to-male ratio. The major cause was infection by virus or bacteria. Fever and headache were the most common clinical manifestation, and acute urinary retention was observed in 6 patients. All patients recovered completely within a month.
Adult-onset MERS is an entity with a broad clinico-radiological spectrum because of the various diseases and conditions. There are similar characteristics between MERS in adults and children, also some differences.
Url:
DOI: 10.1186/s12883-017-0875-5
PubMed: 28545419
PubMed Central: 5445341
Affiliations:
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Le document en format XML
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<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Adult</term>
<term>Brain Diseases (complications)</term>
<term>Brain Diseases (diagnosis)</term>
<term>Brain Diseases (diagnostic imaging)</term>
<term>Brain Diseases (pathology)</term>
<term>Corpus Callosum (pathology)</term>
<term>Encephalitis (complications)</term>
<term>Encephalitis (diagnosis)</term>
<term>Encephalitis (diagnostic imaging)</term>
<term>Encephalitis (pathology)</term>
<term>Female</term>
<term>Humans</term>
<term>Magnetic Resonance Imaging</term>
<term>Male</term>
<term>Prognosis</term>
<term>Young Adult</term>
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<keywords scheme="KwdFr" xml:lang="fr"><term>Adulte</term>
<term>Corps calleux (anatomopathologie)</term>
<term>Encéphalite ()</term>
<term>Encéphalite (anatomopathologie)</term>
<term>Encéphalite (diagnostic)</term>
<term>Encéphalite (imagerie diagnostique)</term>
<term>Encéphalopathies ()</term>
<term>Encéphalopathies (anatomopathologie)</term>
<term>Encéphalopathies (diagnostic)</term>
<term>Encéphalopathies (imagerie diagnostique)</term>
<term>Femelle</term>
<term>Humains</term>
<term>Imagerie par résonance magnétique</term>
<term>Jeune adulte</term>
<term>Mâle</term>
<term>Pronostic</term>
</keywords>
<keywords scheme="MESH" qualifier="anatomopathologie" xml:lang="fr"><term>Corps calleux</term>
<term>Encéphalite</term>
<term>Encéphalopathies</term>
</keywords>
<keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Brain Diseases</term>
<term>Encephalitis</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en"><term>Brain Diseases</term>
<term>Encephalitis</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnostic" xml:lang="fr"><term>Encéphalite</term>
<term>Encéphalopathies</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnostic imaging" xml:lang="en"><term>Brain Diseases</term>
<term>Encephalitis</term>
</keywords>
<keywords scheme="MESH" qualifier="imagerie diagnostique" xml:lang="fr"><term>Encéphalite</term>
<term>Encéphalopathies</term>
</keywords>
<keywords scheme="MESH" qualifier="pathology" xml:lang="en"><term>Brain Diseases</term>
<term>Corpus Callosum</term>
<term>Encephalitis</term>
</keywords>
<keywords scheme="MESH" xml:lang="en"><term>Adult</term>
<term>Female</term>
<term>Humans</term>
<term>Magnetic Resonance Imaging</term>
<term>Male</term>
<term>Prognosis</term>
<term>Young Adult</term>
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<keywords scheme="MESH" xml:lang="fr"><term>Adulte</term>
<term>Encéphalite</term>
<term>Encéphalopathies</term>
<term>Femelle</term>
<term>Humains</term>
<term>Imagerie par résonance magnétique</term>
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<front><div type="abstract" xml:lang="en"><sec><title>Background</title>
<p>Mild encephalitis/encephalopathy with reversible splenial lesion (MERS) is a rare clinico-radiological entity characterized by the magnetic resonance imaging (MRI) finding of a reversible lesion in the corpus callosum, sometimes involved the symmetrical white matters. Many cases of child-onset MERS with various causes have been reported. However, adult-onset MERS is relatively rare. The clinical characteristics and pathophysiologiccal mechanisms of adult-onset MERS are not well understood. We reviewed the literature on adult-onset MERS in order to describe the characteristics of MERS in adults and to provide experiences for clinician.</p>
</sec>
<sec><title>Methods</title>
<p>We reported a case of adult-onset MERS with acute urinary retension and performed literature search from PubMed and web of science databases to identify other adult-onset MERS reports from Januarary 2004 to March 2016. Preferred Reporting Items for Systematic Reviews and Meta-Analyses (PRISMA) guideline was followed on selection process. And then we summarized the clinico-radiological features of adult-onset MERS.</p>
</sec>
<sec><title>Results</title>
<p>Twenty-nine adult-onset MERS cases were reviewed from available literature including the case we have. 86.2% of the cases (25/29) were reported in Asia, especially in Japan. Ages varied between 18 and 59 years old with a 12:17 female-to-male ratio. The major cause was infection by virus or bacteria. Fever and headache were the most common clinical manifestation, and acute urinary retention was observed in 6 patients. All patients recovered completely within a month.</p>
</sec>
<sec><title>Conclusion</title>
<p>Adult-onset MERS is an entity with a broad clinico-radiological spectrum because of the various diseases and conditions. There are similar characteristics between MERS in adults and children, also some differences.</p>
</sec>
</div>
</front>
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</div1>
</back>
</TEI>
<affiliations><list><country><li>République populaire de Chine</li>
</country>
<settlement><li>Pékin</li>
</settlement>
</list>
<tree><country name="République populaire de Chine"><noRegion><name sortKey="Yuan, Junliang" sort="Yuan, Junliang" uniqKey="Yuan J" first="Junliang" last="Yuan">Junliang Yuan</name>
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<name sortKey="Hu, Wenli" sort="Hu, Wenli" uniqKey="Hu W" first="Wenli" last="Hu">Wenli Hu</name>
<name sortKey="Qin, Wei" sort="Qin, Wei" uniqKey="Qin W" first="Wei" last="Qin">Wei Qin</name>
<name sortKey="Wang, Shuangkun" sort="Wang, Shuangkun" uniqKey="Wang S" first="Shuangkun" last="Wang">Shuangkun Wang</name>
<name sortKey="Yang, Lei" sort="Yang, Lei" uniqKey="Yang L" first="Lei" last="Yang">Lei Yang</name>
<name sortKey="Yang, Shuna" sort="Yang, Shuna" uniqKey="Yang S" first="Shuna" last="Yang">Shuna Yang</name>
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</tree>
</affiliations>
</record>
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