Elephantiasis nostras verrucosa or "mossy foot lesions" in lymphedema praecox: report of a case.
Identifieur interne : 003411 ( PubMed/Curation ); précédent : 003410; suivant : 003412Elephantiasis nostras verrucosa or "mossy foot lesions" in lymphedema praecox: report of a case.
Auteurs : Amy L. Duckworth [États-Unis] ; Jugnoo Husain ; Patrick DeheerSource :
- Journal of the American Podiatric Medical Association [ 8750-7315 ]
Descripteurs français
- KwdFr :
- MESH :
- anatomopathologie : Dermatoses du pied, Derme, Éléphantiasis.
- métabolisme : Dermatoses du pied, Éléphantiasis.
- Adulte, Biopsie, Femelle, Fibrose, Humains, Odorisants.
English descriptors
- KwdEn :
- MESH :
- metabolism : Elephantiasis, Foot Dermatoses.
- pathology : Dermis, Elephantiasis, Foot Dermatoses.
- Adult, Biopsy, Female, Fibrosis, Humans, Odorants.
Abstract
Elephantiasis nostras verrucosa is a rare disorder that results from chronic obstructive lymphedema. It is characterized clinically by deforming, nonpitting edema; malodorous hyperkeratosis with generalized lichenification; cobblestoned papules; and verrucous changes, that often result in extreme enlargement of the involved body part. Although elephantiasis nostras verrucosa is striking in clinical appearance, biopsy reveals only moderately abnormal findings: pseudoepitheliomatous hyperplasia with dilated lymphatic spaces in the dermis, accompanied by chronic inflammation and fibroblast proliferation. The term elephantiasis nostras (nostras means "from our region") has traditionally been used to differentiate temperate zone disease from the classic disease process, elephantiasis tropica, which is defined by chronic filarial lymphatic obstruction caused by Wuchereria bancrofti, Wuchereria malayi, or Wuchereria pacifica. We present a case report of elephantiasis nostras verrucosa arising as a result of lymphedema praecox.
PubMed: 18202337
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pubmed:18202337Le document en format XML
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<front><div type="abstract" xml:lang="en">Elephantiasis nostras verrucosa is a rare disorder that results from chronic obstructive lymphedema. It is characterized clinically by deforming, nonpitting edema; malodorous hyperkeratosis with generalized lichenification; cobblestoned papules; and verrucous changes, that often result in extreme enlargement of the involved body part. Although elephantiasis nostras verrucosa is striking in clinical appearance, biopsy reveals only moderately abnormal findings: pseudoepitheliomatous hyperplasia with dilated lymphatic spaces in the dermis, accompanied by chronic inflammation and fibroblast proliferation. The term elephantiasis nostras (nostras means "from our region") has traditionally been used to differentiate temperate zone disease from the classic disease process, elephantiasis tropica, which is defined by chronic filarial lymphatic obstruction caused by Wuchereria bancrofti, Wuchereria malayi, or Wuchereria pacifica. We present a case report of elephantiasis nostras verrucosa arising as a result of lymphedema praecox.</div>
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<Abstract><AbstractText>Elephantiasis nostras verrucosa is a rare disorder that results from chronic obstructive lymphedema. It is characterized clinically by deforming, nonpitting edema; malodorous hyperkeratosis with generalized lichenification; cobblestoned papules; and verrucous changes, that often result in extreme enlargement of the involved body part. Although elephantiasis nostras verrucosa is striking in clinical appearance, biopsy reveals only moderately abnormal findings: pseudoepitheliomatous hyperplasia with dilated lymphatic spaces in the dermis, accompanied by chronic inflammation and fibroblast proliferation. The term elephantiasis nostras (nostras means "from our region") has traditionally been used to differentiate temperate zone disease from the classic disease process, elephantiasis tropica, which is defined by chronic filarial lymphatic obstruction caused by Wuchereria bancrofti, Wuchereria malayi, or Wuchereria pacifica. We present a case report of elephantiasis nostras verrucosa arising as a result of lymphedema praecox.</AbstractText>
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