Hereditary Lymphedema of the Leg - A Case Report.
Identifieur interne : 000059 ( PubMed/Curation ); précédent : 000058; suivant : 000060Hereditary Lymphedema of the Leg - A Case Report.
Auteurs : Birgit Heinig [Allemagne] ; Torello Lotti [Pays-Bas] ; Georgi Tchernev [Bulgarie] ; Uwe Wollina [Allemagne]Source :
- Open access Macedonian journal of medical sciences [ 1857-9655 ] ; 2017.
Abstract
Primary of hereditary lymphedema is a rare but progressive disease. It is yet not curable. We present a 48-year-old male patient with hereditary lymphedema of his left leg, that was realised by minor trauma (able twist) when he was seven years old. He had never been treated for lymphedema but experienced multiple erysipelas during his life. After diagnostic procedures to exclude other causes of leg swelling, the diagnosis of hereditary lymphedema of the leg, stage III was confirmed. We initialized complex decongestive therapy. During two weeks of intensive treatment, the circumference of the left leg could be reduced by 10 cm. This case illustrates the "natural course" hereditary lymphedema. But it raises the hope that even after decades of ignorance, the patients benefits from complex decongestive treatment. Therapeutic nihilism is unnecessary and poses lymphedema patients to risks of infection and secondary malignancies like Stewart-Trewes syndrome.
DOI: 10.3889/oamjms.2017.082
PubMed: 28785330
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Marconi", Rome, Italy; Department of Biotechnology, Delft University of Technology, 2628 BC, Delft</wicri:regionArea></affiliation></author><author><name sortKey="Tchernev, Georgi" sort="Tchernev, Georgi" uniqKey="Tchernev G" first="Georgi" last="Tchernev">Georgi Tchernev</name><affiliation wicri:level="1"><nlm:affiliation>Department of Dermatology, Venereology and Dermatologic Surgery, Medical Institute of Ministry of Interior, and Onkoderma Policlinic for Dermatology and Dermatologic Surgery, Sofia, Bulgaria.</nlm:affiliation><country xml:lang="fr">Bulgarie</country><wicri:regionArea>Department of Dermatology, Venereology and Dermatologic Surgery, Medical Institute of Ministry of Interior, and Onkoderma Policlinic for Dermatology and Dermatologic Surgery, Sofia</wicri:regionArea></affiliation></author><author><name sortKey="Wollina, Uwe" sort="Wollina, Uwe" uniqKey="Wollina U" first="Uwe" last="Wollina">Uwe Wollina</name><affiliation wicri:level="1"><nlm:affiliation>Department of Dermatology and Allergology, Academic Teaching Hospital Dresden-Friedrichstadt, Friedrichstrasse 41, 01067, Dresden, Germany.</nlm:affiliation><country xml:lang="fr">Allemagne</country><wicri:regionArea>Department of Dermatology and Allergology, Academic Teaching Hospital Dresden-Friedrichstadt, Friedrichstrasse 41, 01067, Dresden</wicri:regionArea></affiliation></author></analytic><series><title level="j">Open access Macedonian journal of medical sciences</title><idno type="ISSN">1857-9655</idno><imprint><date when="2017" type="published">2017</date></imprint></series></biblStruct></sourceDesc></fileDesc><profileDesc><textClass></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">Primary of hereditary lymphedema is a rare but progressive disease. It is yet not curable. We present a 48-year-old male patient with hereditary lymphedema of his left leg, that was realised by minor trauma (able twist) when he was seven years old. He had never been treated for lymphedema but experienced multiple erysipelas during his life. After diagnostic procedures to exclude other causes of leg swelling, the diagnosis of hereditary lymphedema of the leg, stage III was confirmed. We initialized complex decongestive therapy. During two weeks of intensive treatment, the circumference of the left leg could be reduced by 10 cm. This case illustrates the "natural course" hereditary lymphedema. But it raises the hope that even after decades of ignorance, the patients benefits from complex decongestive treatment. Therapeutic nihilism is unnecessary and poses lymphedema patients to risks of infection and secondary malignancies like Stewart-Trewes syndrome.</div></front></TEI><pubmed><MedlineCitation Status="PubMed-not-MEDLINE" Owner="NLM"><PMID Version="1">28785330</PMID><DateCreated><Year>2017</Year><Month>08</Month><Day>08</Day></DateCreated><DateRevised><Year>2017</Year><Month>08</Month><Day>11</Day></DateRevised><Article PubModel="Electronic-eCollection"><Journal><ISSN IssnType="Print">1857-9655</ISSN><JournalIssue CitedMedium="Print"><Volume>5</Volume><Issue>4</Issue><PubDate><Year>2017</Year><Month>Jul</Month><Day>25</Day></PubDate></JournalIssue><Title>Open access Macedonian journal of medical sciences</Title><ISOAbbreviation>Open Access Maced J Med Sci</ISOAbbreviation></Journal><ArticleTitle>Hereditary Lymphedema of the Leg - A Case Report.</ArticleTitle><Pagination><MedlinePgn>451-453</MedlinePgn></Pagination><ELocationID EIdType="doi" ValidYN="Y">10.3889/oamjms.2017.082</ELocationID><Abstract><AbstractText>Primary of hereditary lymphedema is a rare but progressive disease. It is yet not curable. We present a 48-year-old male patient with hereditary lymphedema of his left leg, that was realised by minor trauma (able twist) when he was seven years old. He had never been treated for lymphedema but experienced multiple erysipelas during his life. After diagnostic procedures to exclude other causes of leg swelling, the diagnosis of hereditary lymphedema of the leg, stage III was confirmed. We initialized complex decongestive therapy. During two weeks of intensive treatment, the circumference of the left leg could be reduced by 10 cm. This case illustrates the "natural course" hereditary lymphedema. But it raises the hope that even after decades of ignorance, the patients benefits from complex decongestive treatment. Therapeutic nihilism is unnecessary and poses lymphedema patients to risks of infection and secondary malignancies like Stewart-Trewes syndrome.</AbstractText></Abstract><AuthorList CompleteYN="Y"><Author ValidYN="Y"><LastName>Heinig</LastName><ForeName>Birgit</ForeName><Initials>B</Initials><AffiliationInfo><Affiliation>Center of Physical and Rehabilitative Medicine, Academic Teaching Hospital Dresden-Friedrichstadt, Friedrichstrasse 41, 01067, Dresden, Germany.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Lotti</LastName><ForeName>Torello</ForeName><Initials>T</Initials><AffiliationInfo><Affiliation>Department of Dermatology, University of Rome "G. Marconi", Rome, Italy; Department of Biotechnology, Delft University of Technology, 2628 BC, Delft, The Netherlands.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Tchernev</LastName><ForeName>Georgi</ForeName><Initials>G</Initials><AffiliationInfo><Affiliation>Department of Dermatology, Venereology and Dermatologic Surgery, Medical Institute of Ministry of Interior, and Onkoderma Policlinic for Dermatology and Dermatologic Surgery, Sofia, Bulgaria.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Wollina</LastName><ForeName>Uwe</ForeName><Initials>U</Initials><AffiliationInfo><Affiliation>Department of Dermatology and Allergology, Academic Teaching Hospital Dresden-Friedrichstadt, Friedrichstrasse 41, 01067, Dresden, Germany.</Affiliation></AffiliationInfo></Author></AuthorList><Language>eng</Language><PublicationTypeList><PublicationType UI="D016428">Journal Article</PublicationType></PublicationTypeList><ArticleDate DateType="Electronic"><Year>2017</Year><Month>07</Month><Day>19</Day></ArticleDate></Article><MedlineJournalInfo><Country>Macedonia</Country><MedlineTA>Open Access Maced J Med Sci</MedlineTA><NlmUniqueID>101662294</NlmUniqueID><ISSNLinking>1857-9655</ISSNLinking></MedlineJournalInfo><CommentsCorrectionsList><CommentsCorrections RefType="Cites"><RefSource>Lymphat Res Biol. 2014 Dec;12(4):289-94</RefSource><PMID Version="1">25495384</PMID></CommentsCorrections><CommentsCorrections RefType="Cites"><RefSource>J Clin Invest. 2014 Mar;124(3):898-904</RefSource><PMID Version="1">24590274</PMID></CommentsCorrections><CommentsCorrections RefType="Cites"><RefSource>J Reconstr Microsurg. 2017 Jul;33(6):412-425</RefSource><PMID Version="1">28235214</PMID></CommentsCorrections><CommentsCorrections RefType="Cites"><RefSource>Phys Ther. 2011 Nov;91(11):1618-26</RefSource><PMID Version="1">21868611</PMID></CommentsCorrections><CommentsCorrections RefType="Cites"><RefSource>Hautarzt. 2015 Nov;66(11):810-8</RefSource><PMID Version="1">26315101</PMID></CommentsCorrections><CommentsCorrections RefType="Cites"><RefSource>Eur J Obstet Gynecol Reprod Biol. 2017 Apr;211:112-121</RefSource><PMID Version="1">28242470</PMID></CommentsCorrections><CommentsCorrections RefType="Cites"><RefSource>Int J Dermatol. 2007 Jun;46(6):662</RefSource><PMID Version="1">17550576</PMID></CommentsCorrections><CommentsCorrections RefType="Cites"><RefSource>Plast Reconstr Surg. 2011 Jun;127(6):2419-31</RefSource><PMID Version="1">21617474</PMID></CommentsCorrections><CommentsCorrections RefType="Cites"><RefSource>Eplasty. 2014 Feb 28;14:e11</RefSource><PMID Version="1">24741382</PMID></CommentsCorrections></CommentsCorrectionsList><KeywordList Owner="NOTNLM"><Keyword MajorTopicYN="N">Complex decongestive therapy</Keyword><Keyword MajorTopicYN="N">Elephantiasis nostra</Keyword><Keyword MajorTopicYN="N">Erysipelas</Keyword><Keyword MajorTopicYN="N">Fibrosis</Keyword><Keyword MajorTopicYN="N">Immunocompromised district</Keyword><Keyword MajorTopicYN="N">Primary lymphedema</Keyword><Keyword MajorTopicYN="N">Secondary lymphedema</Keyword></KeywordList></MedlineCitation><PubmedData><History><PubMedPubDate PubStatus="received"><Year>2017</Year><Month>05</Month><Day>25</Day></PubMedPubDate><PubMedPubDate PubStatus="revised"><Year>2017</Year><Month>04</Month><Day>21</Day></PubMedPubDate><PubMedPubDate PubStatus="accepted"><Year>2017</Year><Month>04</Month><Day>26</Day></PubMedPubDate><PubMedPubDate PubStatus="entrez"><Year>2017</Year><Month>8</Month><Day>9</Day><Hour>6</Hour><Minute>0</Minute></PubMedPubDate><PubMedPubDate PubStatus="pubmed"><Year>2017</Year><Month>8</Month><Day>9</Day><Hour>6</Hour><Minute>0</Minute></PubMedPubDate><PubMedPubDate PubStatus="medline"><Year>2017</Year><Month>8</Month><Day>9</Day><Hour>6</Hour><Minute>1</Minute></PubMedPubDate></History><PublicationStatus>epublish</PublicationStatus><ArticleIdList><ArticleId IdType="pubmed">28785330</ArticleId><ArticleId IdType="doi">10.3889/oamjms.2017.082</ArticleId><ArticleId IdType="pii">OAMJMS-5-451</ArticleId><ArticleId IdType="pmc">PMC5535655</ArticleId></ArticleIdList></PubmedData></pubmed></record>Pour manipuler ce document sous Unix (Dilib)
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