Successful management of late-onset primary lymphatic hypoplasia.
Identifieur interne : 006788 ( PubMed/Corpus ); précédent : 006787; suivant : 006789Successful management of late-onset primary lymphatic hypoplasia.
Auteurs : A K Rustgi ; F S Rotolo ; W P Peete ; R T Vollmer ; W C MeyersSource :
- Surgery [ 0039-6060 ] ; 1985.
English descriptors
- KwdEn :
- MESH :
- abnormalities : Lymphatic System.
- diagnosis : Lymphedema.
- etiology : Chylothorax, Chylous Ascites, Lymphedema.
- pathology : Lymphedema.
- therapy : Chylothorax, Chylous Ascites, Lymphedema.
- Humans, Male, Middle Aged, Time Factors.
Abstract
Primary lymphedema of the extremities, abdomen, or chest is an unusual and difficult clinical problem with few guidelines for management. A case is reported of lymphedema acquired at the age of 61 years, with associated massive chylous ascites and chylothorax. No underlying condition was discovered and the patient was found to have hypoplastic lymphatics by lymphangiography. Initial management consisted of extremity elevation, diuresis, and repeated paracenteses and thoracenteses. A peritoneojugular shunt provided temporary relief. Surgical pleurodesis combined with intensive diuresis has given prolonged relief of his symptoms allowing him to return to a functional life. Diagnostic and therapeutic guidelines for the management of this unusual condition are suggested.
PubMed: 4002118
Links to Exploration step
pubmed:4002118Le document en format XML
<record><TEI><teiHeader><fileDesc><titleStmt><title xml:lang="en">Successful management of late-onset primary lymphatic hypoplasia.</title>
<author><name sortKey="Rustgi, A K" sort="Rustgi, A K" uniqKey="Rustgi A" first="A K" last="Rustgi">A K Rustgi</name>
</author>
<author><name sortKey="Rotolo, F S" sort="Rotolo, F S" uniqKey="Rotolo F" first="F S" last="Rotolo">F S Rotolo</name>
</author>
<author><name sortKey="Peete, W P" sort="Peete, W P" uniqKey="Peete W" first="W P" last="Peete">W P Peete</name>
</author>
<author><name sortKey="Vollmer, R T" sort="Vollmer, R T" uniqKey="Vollmer R" first="R T" last="Vollmer">R T Vollmer</name>
</author>
<author><name sortKey="Meyers, W C" sort="Meyers, W C" uniqKey="Meyers W" first="W C" last="Meyers">W C Meyers</name>
</author>
</titleStmt>
<publicationStmt><idno type="wicri:source">PubMed</idno>
<date when="1985">1985</date>
<idno type="RBID">pubmed:4002118</idno>
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<sourceDesc><biblStruct><analytic><title xml:lang="en">Successful management of late-onset primary lymphatic hypoplasia.</title>
<author><name sortKey="Rustgi, A K" sort="Rustgi, A K" uniqKey="Rustgi A" first="A K" last="Rustgi">A K Rustgi</name>
</author>
<author><name sortKey="Rotolo, F S" sort="Rotolo, F S" uniqKey="Rotolo F" first="F S" last="Rotolo">F S Rotolo</name>
</author>
<author><name sortKey="Peete, W P" sort="Peete, W P" uniqKey="Peete W" first="W P" last="Peete">W P Peete</name>
</author>
<author><name sortKey="Vollmer, R T" sort="Vollmer, R T" uniqKey="Vollmer R" first="R T" last="Vollmer">R T Vollmer</name>
</author>
<author><name sortKey="Meyers, W C" sort="Meyers, W C" uniqKey="Meyers W" first="W C" last="Meyers">W C Meyers</name>
</author>
</analytic>
<series><title level="j">Surgery</title>
<idno type="ISSN">0039-6060</idno>
<imprint><date when="1985" type="published">1985</date>
</imprint>
</series>
</biblStruct>
</sourceDesc>
</fileDesc>
<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Chylothorax (etiology)</term>
<term>Chylothorax (therapy)</term>
<term>Chylous Ascites (etiology)</term>
<term>Chylous Ascites (therapy)</term>
<term>Humans</term>
<term>Lymphatic System (abnormalities)</term>
<term>Lymphedema (diagnosis)</term>
<term>Lymphedema (etiology)</term>
<term>Lymphedema (pathology)</term>
<term>Lymphedema (therapy)</term>
<term>Male</term>
<term>Middle Aged</term>
<term>Time Factors</term>
</keywords>
<keywords scheme="MESH" qualifier="abnormalities" xml:lang="en"><term>Lymphatic System</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en"><term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" qualifier="etiology" xml:lang="en"><term>Chylothorax</term>
<term>Chylous Ascites</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" qualifier="pathology" xml:lang="en"><term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" qualifier="therapy" xml:lang="en"><term>Chylothorax</term>
<term>Chylous Ascites</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" xml:lang="en"><term>Humans</term>
<term>Male</term>
<term>Middle Aged</term>
<term>Time Factors</term>
</keywords>
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<front><div type="abstract" xml:lang="en">Primary lymphedema of the extremities, abdomen, or chest is an unusual and difficult clinical problem with few guidelines for management. A case is reported of lymphedema acquired at the age of 61 years, with associated massive chylous ascites and chylothorax. No underlying condition was discovered and the patient was found to have hypoplastic lymphatics by lymphangiography. Initial management consisted of extremity elevation, diuresis, and repeated paracenteses and thoracenteses. A peritoneojugular shunt provided temporary relief. Surgical pleurodesis combined with intensive diuresis has given prolonged relief of his symptoms allowing him to return to a functional life. Diagnostic and therapeutic guidelines for the management of this unusual condition are suggested.</div>
</front>
</TEI>
<pubmed><MedlineCitation Status="MEDLINE" Owner="NLM"><PMID Version="1">4002118</PMID>
<DateCreated><Year>1985</Year>
<Month>07</Month>
<Day>22</Day>
</DateCreated>
<DateCompleted><Year>1985</Year>
<Month>07</Month>
<Day>22</Day>
</DateCompleted>
<DateRevised><Year>2004</Year>
<Month>11</Month>
<Day>17</Day>
</DateRevised>
<Article PubModel="Print"><Journal><ISSN IssnType="Print">0039-6060</ISSN>
<JournalIssue CitedMedium="Print"><Volume>97</Volume>
<Issue>6</Issue>
<PubDate><Year>1985</Year>
<Month>Jun</Month>
</PubDate>
</JournalIssue>
<Title>Surgery</Title>
<ISOAbbreviation>Surgery</ISOAbbreviation>
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<ArticleTitle>Successful management of late-onset primary lymphatic hypoplasia.</ArticleTitle>
<Pagination><MedlinePgn>714-20</MedlinePgn>
</Pagination>
<Abstract><AbstractText>Primary lymphedema of the extremities, abdomen, or chest is an unusual and difficult clinical problem with few guidelines for management. A case is reported of lymphedema acquired at the age of 61 years, with associated massive chylous ascites and chylothorax. No underlying condition was discovered and the patient was found to have hypoplastic lymphatics by lymphangiography. Initial management consisted of extremity elevation, diuresis, and repeated paracenteses and thoracenteses. A peritoneojugular shunt provided temporary relief. Surgical pleurodesis combined with intensive diuresis has given prolonged relief of his symptoms allowing him to return to a functional life. Diagnostic and therapeutic guidelines for the management of this unusual condition are suggested.</AbstractText>
</Abstract>
<AuthorList CompleteYN="Y"><Author ValidYN="Y"><LastName>Rustgi</LastName>
<ForeName>A K</ForeName>
<Initials>AK</Initials>
</Author>
<Author ValidYN="Y"><LastName>Rotolo</LastName>
<ForeName>F S</ForeName>
<Initials>FS</Initials>
</Author>
<Author ValidYN="Y"><LastName>Peete</LastName>
<ForeName>W P</ForeName>
<Initials>WP</Initials>
</Author>
<Author ValidYN="Y"><LastName>Vollmer</LastName>
<ForeName>R T</ForeName>
<Initials>RT</Initials>
</Author>
<Author ValidYN="Y"><LastName>Meyers</LastName>
<ForeName>W C</ForeName>
<Initials>WC</Initials>
</Author>
</AuthorList>
<Language>eng</Language>
<PublicationTypeList><PublicationType UI="D002363">Case Reports</PublicationType>
<PublicationType UI="D016428">Journal Article</PublicationType>
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<MedlineJournalInfo><Country>United States</Country>
<MedlineTA>Surgery</MedlineTA>
<NlmUniqueID>0417347</NlmUniqueID>
<ISSNLinking>0039-6060</ISSNLinking>
</MedlineJournalInfo>
<CitationSubset>AIM</CitationSubset>
<CitationSubset>IM</CitationSubset>
<MeshHeadingList><MeshHeading><DescriptorName UI="D002916" MajorTopicYN="N">Chylothorax</DescriptorName>
<QualifierName UI="Q000209" MajorTopicYN="N">etiology</QualifierName>
<QualifierName UI="Q000628" MajorTopicYN="N">therapy</QualifierName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D002915" MajorTopicYN="N">Chylous Ascites</DescriptorName>
<QualifierName UI="Q000209" MajorTopicYN="N">etiology</QualifierName>
<QualifierName UI="Q000628" MajorTopicYN="N">therapy</QualifierName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D006801" MajorTopicYN="N">Humans</DescriptorName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D008208" MajorTopicYN="N">Lymphatic System</DescriptorName>
<QualifierName UI="Q000002" MajorTopicYN="Y">abnormalities</QualifierName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D008209" MajorTopicYN="N">Lymphedema</DescriptorName>
<QualifierName UI="Q000175" MajorTopicYN="N">diagnosis</QualifierName>
<QualifierName UI="Q000209" MajorTopicYN="N">etiology</QualifierName>
<QualifierName UI="Q000473" MajorTopicYN="N">pathology</QualifierName>
<QualifierName UI="Q000628" MajorTopicYN="Y">therapy</QualifierName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D008297" MajorTopicYN="N">Male</DescriptorName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D008875" MajorTopicYN="N">Middle Aged</DescriptorName>
</MeshHeading>
<MeshHeading><DescriptorName UI="D013997" MajorTopicYN="N">Time Factors</DescriptorName>
</MeshHeading>
</MeshHeadingList>
</MedlineCitation>
<PubmedData><History><PubMedPubDate PubStatus="pubmed"><Year>1985</Year>
<Month>6</Month>
<Day>1</Day>
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<PubMedPubDate PubStatus="medline"><Year>1985</Year>
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<PublicationStatus>ppublish</PublicationStatus>
<ArticleIdList><ArticleId IdType="pubmed">4002118</ArticleId>
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