Plexiform neurofibromatosis: a difficult surgical problem.
Identifieur interne : 005D19 ( PubMed/Corpus ); précédent : 005D18; suivant : 005D20Plexiform neurofibromatosis: a difficult surgical problem.
Auteurs : L A Kuo ; R S KuoSource :
- The Australian and New Zealand journal of surgery [ 0004-8682 ] ; 1990.
English descriptors
- KwdEn :
- Adult, Blood Transfusion, Disarticulation (methods), Elephantiasis (complications), Female, Hemostasis, Surgical, Hip Joint (blood supply), Hip Joint (surgery), Humans, Leg Ulcer (etiology), Leg Ulcer (surgery), Lymphedema (complications), Neurofibromatosis 1 (complications), Neurofibromatosis 1 (diagnostic imaging), Neurofibromatosis 1 (genetics), Pedigree, Radiography.
- MESH :
- blood supply : Hip Joint.
- complications : Elephantiasis, Lymphedema, Neurofibromatosis 1.
- diagnostic imaging : Neurofibromatosis 1.
- etiology : Leg Ulcer.
- genetics : Neurofibromatosis 1.
- methods : Disarticulation.
- surgery : Hip Joint, Leg Ulcer.
- Adult, Blood Transfusion, Female, Hemostasis, Surgical, Humans, Pedigree, Radiography.
Abstract
A severe case of plexiform neurofibromatosis with elephantiasis neuromatosa involving the right lower limb and pelvis, leading to a right hip disarticulation, is reported. Abnormal vasculature can make surgical intervention hazardous.
PubMed: 2118756
Links to Exploration step
pubmed:2118756Le document en format XML
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<author><name sortKey="Kuo, L A" sort="Kuo, L A" uniqKey="Kuo L" first="L A" last="Kuo">L A Kuo</name>
<affiliation><nlm:affiliation>Department of Traumatic and Orthopaedic Surgery, Prince of Wales Hospital, Sydney.</nlm:affiliation>
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<author><name sortKey="Kuo, R S" sort="Kuo, R S" uniqKey="Kuo R" first="R S" last="Kuo">R S Kuo</name>
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<author><name sortKey="Kuo, L A" sort="Kuo, L A" uniqKey="Kuo L" first="L A" last="Kuo">L A Kuo</name>
<affiliation><nlm:affiliation>Department of Traumatic and Orthopaedic Surgery, Prince of Wales Hospital, Sydney.</nlm:affiliation>
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<series><title level="j">The Australian and New Zealand journal of surgery</title>
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<imprint><date when="1990" type="published">1990</date>
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<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Adult</term>
<term>Blood Transfusion</term>
<term>Disarticulation (methods)</term>
<term>Elephantiasis (complications)</term>
<term>Female</term>
<term>Hemostasis, Surgical</term>
<term>Hip Joint (blood supply)</term>
<term>Hip Joint (surgery)</term>
<term>Humans</term>
<term>Leg Ulcer (etiology)</term>
<term>Leg Ulcer (surgery)</term>
<term>Lymphedema (complications)</term>
<term>Neurofibromatosis 1 (complications)</term>
<term>Neurofibromatosis 1 (diagnostic imaging)</term>
<term>Neurofibromatosis 1 (genetics)</term>
<term>Pedigree</term>
<term>Radiography</term>
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<keywords scheme="MESH" qualifier="blood supply" xml:lang="en"><term>Hip Joint</term>
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<keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Elephantiasis</term>
<term>Lymphedema</term>
<term>Neurofibromatosis 1</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnostic imaging" xml:lang="en"><term>Neurofibromatosis 1</term>
</keywords>
<keywords scheme="MESH" qualifier="etiology" xml:lang="en"><term>Leg Ulcer</term>
</keywords>
<keywords scheme="MESH" qualifier="genetics" xml:lang="en"><term>Neurofibromatosis 1</term>
</keywords>
<keywords scheme="MESH" qualifier="methods" xml:lang="en"><term>Disarticulation</term>
</keywords>
<keywords scheme="MESH" qualifier="surgery" xml:lang="en"><term>Hip Joint</term>
<term>Leg Ulcer</term>
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<keywords scheme="MESH" xml:lang="en"><term>Adult</term>
<term>Blood Transfusion</term>
<term>Female</term>
<term>Hemostasis, Surgical</term>
<term>Humans</term>
<term>Pedigree</term>
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<front><div type="abstract" xml:lang="en">A severe case of plexiform neurofibromatosis with elephantiasis neuromatosa involving the right lower limb and pelvis, leading to a right hip disarticulation, is reported. Abnormal vasculature can make surgical intervention hazardous.</div>
</front>
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<Title>The Australian and New Zealand journal of surgery</Title>
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<Abstract><AbstractText>A severe case of plexiform neurofibromatosis with elephantiasis neuromatosa involving the right lower limb and pelvis, leading to a right hip disarticulation, is reported. Abnormal vasculature can make surgical intervention hazardous.</AbstractText>
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