[Congenital intestinal lymphangiectasia].
Identifieur interne : 002650 ( PubMed/Corpus ); précédent : 002649; suivant : 002651[Congenital intestinal lymphangiectasia].
Auteurs : Dugan D J Popovi ; Milan Spuran ; Tamara Alempijevi ; Miodrag Krsti ; Srdjan Djuranovi ; Nada Kovacevi ; Svetozar Damnjanovi ; Marjan MicevSource :
- Vojnosanitetski pregled [ 0042-8450 ] ; 2011.
English descriptors
- KwdEn :
- MESH :
- congenital : Lymphangiectasis, Intestinal.
- diagnosis : Lymphangiectasis, Intestinal.
- therapy : Lymphangiectasis, Intestinal.
- Humans, Male, Young Adult.
Abstract
Congenital intestinal lymphangiectasia is a disease which leads to protein losing enteropathy. Tortuous, dilated lymphatic vessels in the intestinal wall and mesenterium are typical features of the disease. Clinical manifestations include malabsorption, diarrhea, steatorrhea, edema and effusions. Specific diet and medication are required for disease control.
PubMed: 21526555
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pubmed:21526555Le document en format XML
<record><TEI><teiHeader><fileDesc><titleStmt><title xml:lang="en">[Congenital intestinal lymphangiectasia].</title><author><name sortKey="Popovi, Dugan D J" sort="Popovi, Dugan D J" uniqKey="Popovi D" first="Dugan D J" last="Popovi">Dugan D J Popovi</name><affiliation><nlm:affiliation>Klinicki centar Srbije, Sluzba za patohistologiju, Beograd, Srbija. dr.popovic@sezampro.rs</nlm:affiliation></affiliation></author><author><name sortKey="Spuran, Milan" sort="Spuran, Milan" uniqKey="Spuran M" first="Milan" last="Spuran">Milan Spuran</name></author><author><name sortKey="Alempijevi, Tamara" sort="Alempijevi, Tamara" uniqKey="Alempijevi T" first="Tamara" last="Alempijevi">Tamara Alempijevi</name></author><author><name sortKey="Krsti, Miodrag" sort="Krsti, Miodrag" uniqKey="Krsti M" first="Miodrag" last="Krsti">Miodrag Krsti</name></author><author><name sortKey="Djuranovi, Srdjan" sort="Djuranovi, Srdjan" uniqKey="Djuranovi S" first="Srdjan" last="Djuranovi">Srdjan Djuranovi</name></author><author><name sortKey="Kovacevi, Nada" sort="Kovacevi, Nada" uniqKey="Kovacevi N" first="Nada" last="Kovacevi">Nada Kovacevi</name></author><author><name sortKey="Damnjanovi, Svetozar" sort="Damnjanovi, Svetozar" uniqKey="Damnjanovi S" first="Svetozar" last="Damnjanovi">Svetozar Damnjanovi</name></author><author><name sortKey="Micev, Marjan" sort="Micev, Marjan" uniqKey="Micev M" first="Marjan" last="Micev">Marjan Micev</name></author></titleStmt><publicationStmt><idno type="wicri:source">PubMed</idno><date when="2011">2011</date><idno type="RBID">pubmed:21526555</idno><idno type="pmid">21526555</idno><idno type="wicri:Area/PubMed/Corpus">002650</idno><idno type="wicri:explorRef" wicri:stream="PubMed" wicri:step="Corpus" wicri:corpus="PubMed">002650</idno></publicationStmt><sourceDesc><biblStruct><analytic><title xml:lang="en">[Congenital intestinal lymphangiectasia].</title><author><name sortKey="Popovi, Dugan D J" sort="Popovi, Dugan D J" uniqKey="Popovi D" first="Dugan D J" last="Popovi">Dugan D J Popovi</name><affiliation><nlm:affiliation>Klinicki centar Srbije, Sluzba za patohistologiju, Beograd, Srbija. dr.popovic@sezampro.rs</nlm:affiliation></affiliation></author><author><name sortKey="Spuran, Milan" sort="Spuran, Milan" uniqKey="Spuran M" first="Milan" last="Spuran">Milan Spuran</name></author><author><name sortKey="Alempijevi, Tamara" sort="Alempijevi, Tamara" uniqKey="Alempijevi T" first="Tamara" last="Alempijevi">Tamara Alempijevi</name></author><author><name sortKey="Krsti, Miodrag" sort="Krsti, Miodrag" uniqKey="Krsti M" first="Miodrag" last="Krsti">Miodrag Krsti</name></author><author><name sortKey="Djuranovi, Srdjan" sort="Djuranovi, Srdjan" uniqKey="Djuranovi S" first="Srdjan" last="Djuranovi">Srdjan Djuranovi</name></author><author><name sortKey="Kovacevi, Nada" sort="Kovacevi, Nada" uniqKey="Kovacevi N" first="Nada" last="Kovacevi">Nada Kovacevi</name></author><author><name sortKey="Damnjanovi, Svetozar" sort="Damnjanovi, Svetozar" uniqKey="Damnjanovi S" first="Svetozar" last="Damnjanovi">Svetozar Damnjanovi</name></author><author><name sortKey="Micev, Marjan" sort="Micev, Marjan" uniqKey="Micev M" first="Marjan" last="Micev">Marjan Micev</name></author></analytic><series><title level="j">Vojnosanitetski pregled</title><idno type="ISSN">0042-8450</idno><imprint><date when="2011" type="published">2011</date></imprint></series></biblStruct></sourceDesc></fileDesc><profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Humans</term><term>Lymphangiectasis, Intestinal (congenital)</term><term>Lymphangiectasis, Intestinal (diagnosis)</term><term>Lymphangiectasis, Intestinal (therapy)</term><term>Male</term><term>Young Adult</term></keywords><keywords scheme="MESH" qualifier="congenital" xml:lang="en"><term>Lymphangiectasis, Intestinal</term></keywords><keywords scheme="MESH" qualifier="diagnosis" xml:lang="en"><term>Lymphangiectasis, Intestinal</term></keywords><keywords scheme="MESH" qualifier="therapy" xml:lang="en"><term>Lymphangiectasis, Intestinal</term></keywords><keywords scheme="MESH" xml:lang="en"><term>Humans</term><term>Male</term><term>Young Adult</term></keywords></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">Congenital intestinal lymphangiectasia is a disease which leads to protein losing enteropathy. Tortuous, dilated lymphatic vessels in the intestinal wall and mesenterium are typical features of the disease. Clinical manifestations include malabsorption, diarrhea, steatorrhea, edema and effusions. Specific diet and medication are required for disease control.</div></front></TEI><pubmed><MedlineCitation Status="MEDLINE" Owner="NLM"><PMID Version="1">21526555</PMID><DateCreated><Year>2011</Year><Month>04</Month><Day>28</Day></DateCreated><DateCompleted><Year>2011</Year><Month>06</Month><Day>07</Day></DateCompleted><DateRevised><Year>2015</Year><Month>06</Month><Day>12</Day></DateRevised><Article PubModel="Print"><Journal><ISSN IssnType="Print">0042-8450</ISSN><JournalIssue CitedMedium="Print"><Volume>68</Volume><Issue>3</Issue><PubDate><Year>2011</Year><Month>Mar</Month></PubDate></JournalIssue><Title>Vojnosanitetski pregled</Title><ISOAbbreviation>Vojnosanit Pregl</ISOAbbreviation></Journal><ArticleTitle>[Congenital intestinal lymphangiectasia].</ArticleTitle><Pagination><MedlinePgn>270-3</MedlinePgn></Pagination><Abstract><AbstractText Label="BACKGROUND" NlmCategory="BACKGROUND">Congenital intestinal lymphangiectasia is a disease which leads to protein losing enteropathy. Tortuous, dilated lymphatic vessels in the intestinal wall and mesenterium are typical features of the disease. Clinical manifestations include malabsorption, diarrhea, steatorrhea, edema and effusions. Specific diet and medication are required for disease control.</AbstractText><AbstractText Label="CASE REPORT" NlmCategory="METHODS">A 19-year old male patient was hospitalized due to diarrhea, abdominal swelling, weariness and fatigue. Physical examination revealed growth impairment, ascites, and lymphedema of the right hand and forearm. Laboratory assessment indicated iron deficiency anaemia, lymphopenia, malabsorption, inflammatory syndrome, and urinary infection. Enteroscopy and video capsule endoscopy demonstrated dilated lymphatic vessels in the small intestine. The diagnosis was confirmed by intestinal biopsy. The patient was put on high-protein diet containing medium-chain fatty acids, somatotropin and supportive therapy.</AbstractText><AbstractText Label="CONCLUSION" NlmCategory="CONCLUSIONS">Congenital intestinal lymphangiectasia is a rare disease, usually diagnosed in childhood. Early recognition of the disease and adequate treatment can prevent development of various complications.</AbstractText></Abstract><AuthorList CompleteYN="Y"><Author ValidYN="Y"><LastName>Popović</LastName><ForeName>Dugan D j</ForeName><Initials>DD</Initials><AffiliationInfo><Affiliation>Klinicki centar Srbije, Sluzba za patohistologiju, Beograd, Srbija. dr.popovic@sezampro.rs</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Spuran</LastName><ForeName>Milan</ForeName><Initials>M</Initials></Author><Author ValidYN="Y"><LastName>Alempijević</LastName><ForeName>Tamara</ForeName><Initials>T</Initials></Author><Author ValidYN="Y"><LastName>Krstić</LastName><ForeName>Miodrag</ForeName><Initials>M</Initials></Author><Author ValidYN="Y"><LastName>Djuranović</LastName><ForeName>Srdjan</ForeName><Initials>S</Initials></Author><Author ValidYN="Y"><LastName>Kovacević</LastName><ForeName>Nada</ForeName><Initials>N</Initials></Author><Author ValidYN="Y"><LastName>Damnjanović</LastName><ForeName>Svetozar</ForeName><Initials>S</Initials></Author><Author ValidYN="Y"><LastName>Micev</LastName><ForeName>Marjan</ForeName><Initials>M</Initials></Author></AuthorList><Language>srp</Language><PublicationTypeList><PublicationType UI="D002363">Case Reports</PublicationType><PublicationType UI="D004740">English Abstract</PublicationType><PublicationType UI="D016428">Journal Article</PublicationType></PublicationTypeList></Article><MedlineJournalInfo><Country>Serbia</Country><MedlineTA>Vojnosanit Pregl</MedlineTA><NlmUniqueID>21530700R</NlmUniqueID><ISSNLinking>0042-8450</ISSNLinking></MedlineJournalInfo><CitationSubset>IM</CitationSubset><MeshHeadingList><MeshHeading><DescriptorName UI="D006801" MajorTopicYN="N">Humans</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D008201" MajorTopicYN="N">Lymphangiectasis, Intestinal</DescriptorName><QualifierName UI="Q000151" MajorTopicYN="Y">congenital</QualifierName><QualifierName UI="Q000175" MajorTopicYN="N">diagnosis</QualifierName><QualifierName UI="Q000628" MajorTopicYN="N">therapy</QualifierName></MeshHeading><MeshHeading><DescriptorName UI="D008297" MajorTopicYN="N">Male</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D055815" MajorTopicYN="N">Young Adult</DescriptorName></MeshHeading></MeshHeadingList></MedlineCitation><PubmedData><History><PubMedPubDate PubStatus="entrez"><Year>2011</Year><Month>4</Month><Day>30</Day><Hour>6</Hour><Minute>0</Minute></PubMedPubDate><PubMedPubDate PubStatus="pubmed"><Year>2011</Year><Month>4</Month><Day>30</Day><Hour>6</Hour><Minute>0</Minute></PubMedPubDate><PubMedPubDate PubStatus="medline"><Year>2011</Year><Month>6</Month><Day>8</Day><Hour>6</Hour><Minute>0</Minute></PubMedPubDate></History><PublicationStatus>ppublish</PublicationStatus><ArticleIdList><ArticleId IdType="pubmed">21526555</ArticleId></ArticleIdList></PubmedData></pubmed></record>Pour manipuler ce document sous Unix (Dilib)
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