Secondary hypogammaglobulinemia in Waldmann's disease treated with subcutaneous immunoglobulins.
Identifieur interne : 000972 ( PubMed/Corpus ); précédent : 000971; suivant : 000973Secondary hypogammaglobulinemia in Waldmann's disease treated with subcutaneous immunoglobulins.
Auteurs : G. Patuzzo ; E. Tinazzi ; M. Micheletti ; A. Puccetti ; C. LunardiSource :
- European annals of allergy and clinical immunology [ 1764-1489 ] ; 2016.
English descriptors
- KwdEn :
- Adult, Agammaglobulinemia (diagnosis), Agammaglobulinemia (immunology), Agammaglobulinemia (therapy), Diet, Fat-Restricted, Humans, Immunoglobulin G (administration & dosage), Immunoglobulin G (blood), Immunologic Factors (administration & dosage), Immunologic Factors (blood), Infusions, Subcutaneous, Lymphangiectasis, Intestinal (complications), Lymphangiectasis, Intestinal (diagnosis), Lymphangiectasis, Intestinal (immunology), Lymphangiectasis, Intestinal (therapy), Lymphedema (complications), Lymphedema (diagnosis), Lymphedema (immunology), Lymphedema (therapy), Male, Severity of Illness Index, Treatment Outcome, Triglycerides (administration & dosage).
- MESH :
- chemical , administration & dosage : Immunoglobulin G, Immunologic Factors, Triglycerides.
- chemical , blood : Immunoglobulin G, Immunologic Factors.
- complications : Lymphangiectasis, Intestinal, Lymphedema.
- diagnosis : Agammaglobulinemia, Lymphangiectasis, Intestinal, Lymphedema.
- immunology : Agammaglobulinemia, Lymphangiectasis, Intestinal, Lymphedema.
- therapy : Agammaglobulinemia, Lymphangiectasis, Intestinal, Lymphedema.
- Adult, Diet, Fat-Restricted, Humans, Infusions, Subcutaneous, Male, Severity of Illness Index, Treatment Outcome.
Abstract
Primary intestinal lymphangiectasia (PIL) is rare disorder characterized by congenital malformation or obstruction of intestinal lymphatic drainage; it is responsible for protein losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia. A low-fat diet associated with medium-chain triglyceride supplementation is the cornerstone of PIL management. The administration of intravenous immunoglobulins does not always lead to satisfactory plasma levels and therefore the replacement therapy with immunoglobulins is controversial. We describe here the case of a patient with PIL and severe hypogammaglobulinemia treated with immunoglobulins. The striking aspect of this case is the clinical and serological benefit obtained with the subcutaneous compared to the intravenous immunoglobulins administration.
PubMed: 26934740
Links to Exploration step
pubmed:26934740Le document en format XML
<record><TEI><teiHeader><fileDesc><titleStmt><title xml:lang="en">Secondary hypogammaglobulinemia in Waldmann's disease treated with subcutaneous immunoglobulins.</title><author><name sortKey="Patuzzo, G" sort="Patuzzo, G" uniqKey="Patuzzo G" first="G" last="Patuzzo">G. Patuzzo</name><affiliation><nlm:affiliation>Clinical Immunology and Allergy Unit Department of Medicine University of Verona 37134 Verona, Italy. E-mail: jeps.pz@gmail.com Phone: +39 045 812 4401 Fax: +39 045 802 7473.</nlm:affiliation></affiliation></author><author><name sortKey="Tinazzi, E" sort="Tinazzi, E" uniqKey="Tinazzi E" first="E" last="Tinazzi">E. Tinazzi</name><affiliation><nlm:affiliation>Department of Medicine, University of Verona, Verona, Italy.</nlm:affiliation></affiliation></author><author><name sortKey="Micheletti, M" sort="Micheletti, M" uniqKey="Micheletti M" first="M" last="Micheletti">M. Micheletti</name><affiliation><nlm:affiliation>Department of Medicine, University of Verona, Verona, Italy.</nlm:affiliation></affiliation></author><author><name sortKey="Puccetti, A" sort="Puccetti, A" uniqKey="Puccetti A" first="A" last="Puccetti">A. Puccetti</name><affiliation><nlm:affiliation>Immunology Area, Pediatric Hospital Bambino Gesù, Rome, Italy.</nlm:affiliation></affiliation></author><author><name sortKey="Lunardi, C" sort="Lunardi, C" uniqKey="Lunardi C" first="C" last="Lunardi">C. Lunardi</name><affiliation><nlm:affiliation>Department of Medicine, University of Verona, Verona, Italy.</nlm:affiliation></affiliation></author></titleStmt><publicationStmt><idno type="wicri:source">PubMed</idno><date when="2016">2016</date><idno type="RBID">pubmed:26934740</idno><idno type="pmid">26934740</idno><idno type="wicri:Area/PubMed/Corpus">000972</idno><idno type="wicri:explorRef" wicri:stream="PubMed" wicri:step="Corpus" wicri:corpus="PubMed">000972</idno></publicationStmt><sourceDesc><biblStruct><analytic><title xml:lang="en">Secondary hypogammaglobulinemia in Waldmann's disease treated with subcutaneous immunoglobulins.</title><author><name sortKey="Patuzzo, G" sort="Patuzzo, G" uniqKey="Patuzzo G" first="G" last="Patuzzo">G. Patuzzo</name><affiliation><nlm:affiliation>Clinical Immunology and Allergy Unit Department of Medicine University of Verona 37134 Verona, Italy. E-mail: jeps.pz@gmail.com Phone: +39 045 812 4401 Fax: +39 045 802 7473.</nlm:affiliation></affiliation></author><author><name sortKey="Tinazzi, E" sort="Tinazzi, E" uniqKey="Tinazzi E" first="E" last="Tinazzi">E. Tinazzi</name><affiliation><nlm:affiliation>Department of Medicine, University of Verona, Verona, Italy.</nlm:affiliation></affiliation></author><author><name sortKey="Micheletti, M" sort="Micheletti, M" uniqKey="Micheletti M" first="M" last="Micheletti">M. Micheletti</name><affiliation><nlm:affiliation>Department of Medicine, University of Verona, Verona, Italy.</nlm:affiliation></affiliation></author><author><name sortKey="Puccetti, A" sort="Puccetti, A" uniqKey="Puccetti A" first="A" last="Puccetti">A. Puccetti</name><affiliation><nlm:affiliation>Immunology Area, Pediatric Hospital Bambino Gesù, Rome, Italy.</nlm:affiliation></affiliation></author><author><name sortKey="Lunardi, C" sort="Lunardi, C" uniqKey="Lunardi C" first="C" last="Lunardi">C. Lunardi</name><affiliation><nlm:affiliation>Department of Medicine, University of Verona, Verona, Italy.</nlm:affiliation></affiliation></author></analytic><series><title level="j">European annals of allergy and clinical immunology</title><idno type="ISSN">1764-1489</idno><imprint><date when="2016" type="published">2016</date></imprint></series></biblStruct></sourceDesc></fileDesc><profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Adult</term><term>Agammaglobulinemia (diagnosis)</term><term>Agammaglobulinemia (immunology)</term><term>Agammaglobulinemia (therapy)</term><term>Diet, Fat-Restricted</term><term>Humans</term><term>Immunoglobulin G (administration & dosage)</term><term>Immunoglobulin G (blood)</term><term>Immunologic Factors (administration & dosage)</term><term>Immunologic Factors (blood)</term><term>Infusions, Subcutaneous</term><term>Lymphangiectasis, Intestinal (complications)</term><term>Lymphangiectasis, Intestinal (diagnosis)</term><term>Lymphangiectasis, Intestinal (immunology)</term><term>Lymphangiectasis, Intestinal (therapy)</term><term>Lymphedema (complications)</term><term>Lymphedema (diagnosis)</term><term>Lymphedema (immunology)</term><term>Lymphedema (therapy)</term><term>Male</term><term>Severity of Illness Index</term><term>Treatment Outcome</term><term>Triglycerides (administration & dosage)</term></keywords><keywords scheme="MESH" type="chemical" qualifier="administration & dosage" xml:lang="en"><term>Immunoglobulin G</term><term>Immunologic Factors</term><term>Triglycerides</term></keywords><keywords scheme="MESH" type="chemical" qualifier="blood" xml:lang="en"><term>Immunoglobulin G</term><term>Immunologic Factors</term></keywords><keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Lymphangiectasis, Intestinal</term><term>Lymphedema</term></keywords><keywords scheme="MESH" qualifier="diagnosis" xml:lang="en"><term>Agammaglobulinemia</term><term>Lymphangiectasis, Intestinal</term><term>Lymphedema</term></keywords><keywords scheme="MESH" qualifier="immunology" xml:lang="en"><term>Agammaglobulinemia</term><term>Lymphangiectasis, Intestinal</term><term>Lymphedema</term></keywords><keywords scheme="MESH" qualifier="therapy" xml:lang="en"><term>Agammaglobulinemia</term><term>Lymphangiectasis, Intestinal</term><term>Lymphedema</term></keywords><keywords scheme="MESH" xml:lang="en"><term>Adult</term><term>Diet, Fat-Restricted</term><term>Humans</term><term>Infusions, Subcutaneous</term><term>Male</term><term>Severity of Illness Index</term><term>Treatment Outcome</term></keywords></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">Primary intestinal lymphangiectasia (PIL) is rare disorder characterized by congenital malformation or obstruction of intestinal lymphatic drainage; it is responsible for protein losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia. A low-fat diet associated with medium-chain triglyceride supplementation is the cornerstone of PIL management. The administration of intravenous immunoglobulins does not always lead to satisfactory plasma levels and therefore the replacement therapy with immunoglobulins is controversial. We describe here the case of a patient with PIL and severe hypogammaglobulinemia treated with immunoglobulins. The striking aspect of this case is the clinical and serological benefit obtained with the subcutaneous compared to the intravenous immunoglobulins administration.</div></front></TEI><pubmed><MedlineCitation Status="MEDLINE" Owner="NLM"><PMID Version="1">26934740</PMID><DateCreated><Year>2016</Year><Month>03</Month><Day>03</Day></DateCreated><DateCompleted><Year>2016</Year><Month>06</Month><Day>29</Day></DateCompleted><DateRevised><Year>2016</Year><Month>03</Month><Day>03</Day></DateRevised><Article PubModel="Print"><Journal><ISSN IssnType="Print">1764-1489</ISSN><JournalIssue CitedMedium="Print"><Volume>48</Volume><Issue>2</Issue><PubDate><Year>2016</Year><Month>Mar</Month></PubDate></JournalIssue><Title>European annals of allergy and clinical immunology</Title><ISOAbbreviation>Eur Ann Allergy Clin Immunol</ISOAbbreviation></Journal><ArticleTitle>Secondary hypogammaglobulinemia in Waldmann's disease treated with subcutaneous immunoglobulins.</ArticleTitle><Pagination><MedlinePgn>55-7</MedlinePgn></Pagination><Abstract><AbstractText>Primary intestinal lymphangiectasia (PIL) is rare disorder characterized by congenital malformation or obstruction of intestinal lymphatic drainage; it is responsible for protein losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia. A low-fat diet associated with medium-chain triglyceride supplementation is the cornerstone of PIL management. The administration of intravenous immunoglobulins does not always lead to satisfactory plasma levels and therefore the replacement therapy with immunoglobulins is controversial. We describe here the case of a patient with PIL and severe hypogammaglobulinemia treated with immunoglobulins. The striking aspect of this case is the clinical and serological benefit obtained with the subcutaneous compared to the intravenous immunoglobulins administration.</AbstractText></Abstract><AuthorList CompleteYN="Y"><Author ValidYN="Y"><LastName>Patuzzo</LastName><ForeName>G</ForeName><Initials>G</Initials><AffiliationInfo><Affiliation>Clinical Immunology and Allergy Unit Department of Medicine University of Verona 37134 Verona, Italy. E-mail: jeps.pz@gmail.com Phone: +39 045 812 4401 Fax: +39 045 802 7473.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Tinazzi</LastName><ForeName>E</ForeName><Initials>E</Initials><AffiliationInfo><Affiliation>Department of Medicine, University of Verona, Verona, Italy.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Micheletti</LastName><ForeName>M</ForeName><Initials>M</Initials><AffiliationInfo><Affiliation>Department of Medicine, University of Verona, Verona, Italy.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Puccetti</LastName><ForeName>A</ForeName><Initials>A</Initials><AffiliationInfo><Affiliation>Immunology Area, Pediatric Hospital Bambino Gesù, Rome, Italy.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Lunardi</LastName><ForeName>C</ForeName><Initials>C</Initials><AffiliationInfo><Affiliation>Department of Medicine, University of Verona, Verona, Italy.</Affiliation></AffiliationInfo></Author></AuthorList><Language>eng</Language><PublicationTypeList><PublicationType UI="D002363">Case Reports</PublicationType><PublicationType UI="D016428">Journal Article</PublicationType></PublicationTypeList></Article><MedlineJournalInfo><Country>Italy</Country><MedlineTA>Eur Ann Allergy Clin Immunol</MedlineTA><NlmUniqueID>101466614</NlmUniqueID><ISSNLinking>1764-1489</ISSNLinking></MedlineJournalInfo><ChemicalList><Chemical><RegistryNumber>0</RegistryNumber><NameOfSubstance UI="C558471">Hizentra</NameOfSubstance></Chemical><Chemical><RegistryNumber>0</RegistryNumber><NameOfSubstance UI="D007074">Immunoglobulin G</NameOfSubstance></Chemical><Chemical><RegistryNumber>0</RegistryNumber><NameOfSubstance UI="D007155">Immunologic Factors</NameOfSubstance></Chemical><Chemical><RegistryNumber>0</RegistryNumber><NameOfSubstance UI="D014280">Triglycerides</NameOfSubstance></Chemical></ChemicalList><SupplMeshList><SupplMeshName Type="Disease" UI="C536567">Waldmann disease</SupplMeshName></SupplMeshList><CitationSubset>IM</CitationSubset><MeshHeadingList><MeshHeading><DescriptorName UI="D000328" MajorTopicYN="N">Adult</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D000361" MajorTopicYN="N">Agammaglobulinemia</DescriptorName><QualifierName UI="Q000175" MajorTopicYN="N">diagnosis</QualifierName><QualifierName UI="Q000276" MajorTopicYN="N">immunology</QualifierName><QualifierName UI="Q000628" MajorTopicYN="Y">therapy</QualifierName></MeshHeading><MeshHeading><DescriptorName UI="D018752" MajorTopicYN="N">Diet, Fat-Restricted</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D006801" MajorTopicYN="N">Humans</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D007074" MajorTopicYN="N">Immunoglobulin G</DescriptorName><QualifierName UI="Q000008" MajorTopicYN="Y">administration & dosage</QualifierName><QualifierName UI="Q000097" MajorTopicYN="N">blood</QualifierName></MeshHeading><MeshHeading><DescriptorName UI="D007155" MajorTopicYN="N">Immunologic Factors</DescriptorName><QualifierName UI="Q000008" MajorTopicYN="Y">administration & dosage</QualifierName><QualifierName UI="Q000097" MajorTopicYN="N">blood</QualifierName></MeshHeading><MeshHeading><DescriptorName UI="D055104" MajorTopicYN="N">Infusions, Subcutaneous</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D008201" MajorTopicYN="N">Lymphangiectasis, Intestinal</DescriptorName><QualifierName UI="Q000150" MajorTopicYN="N">complications</QualifierName><QualifierName UI="Q000175" MajorTopicYN="N">diagnosis</QualifierName><QualifierName UI="Q000276" MajorTopicYN="N">immunology</QualifierName><QualifierName UI="Q000628" MajorTopicYN="Y">therapy</QualifierName></MeshHeading><MeshHeading><DescriptorName UI="D008209" MajorTopicYN="N">Lymphedema</DescriptorName><QualifierName UI="Q000150" MajorTopicYN="N">complications</QualifierName><QualifierName UI="Q000175" MajorTopicYN="N">diagnosis</QualifierName><QualifierName UI="Q000276" MajorTopicYN="N">immunology</QualifierName><QualifierName UI="Q000628" MajorTopicYN="Y">therapy</QualifierName></MeshHeading><MeshHeading><DescriptorName UI="D008297" MajorTopicYN="N">Male</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D012720" MajorTopicYN="N">Severity of Illness Index</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D016896" MajorTopicYN="N">Treatment Outcome</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D014280" MajorTopicYN="N">Triglycerides</DescriptorName><QualifierName UI="Q000008" MajorTopicYN="N">administration & dosage</QualifierName></MeshHeading></MeshHeadingList><KeywordList Owner="NOTNLM"><Keyword MajorTopicYN="N">Waldmann‘s disease</Keyword><Keyword MajorTopicYN="N">primary intestinal lymphangectasia</Keyword><Keyword MajorTopicYN="N">protein-losing enteropathy</Keyword><Keyword MajorTopicYN="N">secondary immunodeficiencies</Keyword><Keyword MajorTopicYN="N">subcutaneous immunoglobulins</Keyword></KeywordList></MedlineCitation><PubmedData><History><PubMedPubDate PubStatus="entrez"><Year>2016</Year><Month>3</Month><Day>3</Day><Hour>6</Hour><Minute>0</Minute></PubMedPubDate><PubMedPubDate PubStatus="pubmed"><Year>2016</Year><Month>3</Month><Day>5</Day><Hour>6</Hour><Minute>0</Minute></PubMedPubDate><PubMedPubDate PubStatus="medline"><Year>2016</Year><Month>6</Month><Day>30</Day><Hour>6</Hour><Minute>0</Minute></PubMedPubDate></History><PublicationStatus>ppublish</PublicationStatus><ArticleIdList><ArticleId IdType="pubmed">26934740</ArticleId></ArticleIdList></PubmedData></pubmed></record>Pour manipuler ce document sous Unix (Dilib)
EXPLOR_STEP=$WICRI_ROOT/Wicri/Sante/explor/LymphedemaV1/Data/PubMed/Corpus
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 000972 | SxmlIndent | more
Ou
HfdSelect -h $EXPLOR_AREA/Data/PubMed/Corpus/biblio.hfd -nk 000972 | SxmlIndent | more
Pour mettre un lien sur cette page dans le réseau Wicri
{{Explor lien
|wiki= Wicri/Sante
|area= LymphedemaV1
|flux= PubMed
|étape= Corpus
|type= RBID
|clé= pubmed:26934740
|texte= Secondary hypogammaglobulinemia in Waldmann's disease treated with subcutaneous immunoglobulins.
}}
Pour générer des pages wiki
HfdIndexSelect -h $EXPLOR_AREA/Data/PubMed/Corpus/RBID.i -Sk "pubmed:26934740" \
| HfdSelect -Kh $EXPLOR_AREA/Data/PubMed/Corpus/biblio.hfd \
| NlmPubMed2Wicri -a LymphedemaV1
| This area was generated with Dilib version V0.6.31. |  |