Serveur d'exploration sur le lymphœdème

Attention, ce site est en cours de développement !
Attention, site généré par des moyens informatiques à partir de corpus bruts.
Les informations ne sont donc pas validées.

[Generalized lymphatic dysplasia in a 6-month-old nursing infant].

Identifieur interne : 008069 ( PubMed/Checkpoint ); précédent : 008068; suivant : 008070

[Generalized lymphatic dysplasia in a 6-month-old nursing infant].

Auteurs : L. Massimo [Italie] ; G. Di Iorio ; A. Martone ; R. Sottile ; A. Retolatto ; F. Loiodice ; A. Campa ; S. Angelone

Source :

RBID : pubmed:2052465

Descripteurs français

English descriptors

Abstract

G.L.D. is a rare syndrome characterized by chylothorax, chylous ascites and lymphedema associated to minor symptoms following from lymphangiectasis or to lymphangiomatosis. This syndrome is caused by congenital dysplasia of lymphatic vessels and has, generally, an extremely severe prognosis. In the present papers the authors describe one case of G.L.D. in a six months old infant with chylous ascites, chylothorax, lymphedema, hemangioma and a history of fetal ascites. The preservative (dietetic and evacuative) therapy was not resolutive, therefore an exploratory laparotomy was necessary, but no surgical solution was possible because of the absence of chylous vessels in the anatomical region of the principal lymphatic route. However, laparatomy led to a progressive recovery of ascites and chylothorax, probably due to thrombosis of dysplasic lymph vessels and to neoformation of collateral circulation.

PubMed: 2052465


Affiliations:


Links toward previous steps (curation, corpus...)


Links to Exploration step

pubmed:2052465

Le document en format XML

<record>
<TEI>
<teiHeader>
<fileDesc>
<titleStmt>
<title xml:lang="en">[Generalized lymphatic dysplasia in a 6-month-old nursing infant].</title>
<author>
<name sortKey="Massimo, L" sort="Massimo, L" uniqKey="Massimo L" first="L" last="Massimo">L. Massimo</name>
<affiliation wicri:level="1">
<nlm:affiliation>I Divisione di Pediatria, Ospedale Santobono, USL 40 Napoli, Italia.</nlm:affiliation>
<country xml:lang="fr">Italie</country>
<wicri:regionArea>I Divisione di Pediatria, Ospedale Santobono, USL 40 Napoli</wicri:regionArea>
<wicri:noRegion>USL 40 Napoli</wicri:noRegion>
</affiliation>
</author>
<author>
<name sortKey="Di Iorio, G" sort="Di Iorio, G" uniqKey="Di Iorio G" first="G" last="Di Iorio">G. Di Iorio</name>
</author>
<author>
<name sortKey="Martone, A" sort="Martone, A" uniqKey="Martone A" first="A" last="Martone">A. Martone</name>
</author>
<author>
<name sortKey="Sottile, R" sort="Sottile, R" uniqKey="Sottile R" first="R" last="Sottile">R. Sottile</name>
</author>
<author>
<name sortKey="Retolatto, A" sort="Retolatto, A" uniqKey="Retolatto A" first="A" last="Retolatto">A. Retolatto</name>
</author>
<author>
<name sortKey="Loiodice, F" sort="Loiodice, F" uniqKey="Loiodice F" first="F" last="Loiodice">F. Loiodice</name>
</author>
<author>
<name sortKey="Campa, A" sort="Campa, A" uniqKey="Campa A" first="A" last="Campa">A. Campa</name>
</author>
<author>
<name sortKey="Angelone, S" sort="Angelone, S" uniqKey="Angelone S" first="S" last="Angelone">S. Angelone</name>
</author>
</titleStmt>
<publicationStmt>
<idno type="wicri:source">PubMed</idno>
<date when="????">
<PubDate>
<MedlineDate>1991 Jan-Feb</MedlineDate>
</PubDate>
</date>
<idno type="RBID">pubmed:2052465</idno>
<idno type="pmid">2052465</idno>
<idno type="wicri:Area/PubMed/Corpus">005C12</idno>
<idno type="wicri:explorRef" wicri:stream="PubMed" wicri:step="Corpus" wicri:corpus="PubMed">005C12</idno>
<idno type="wicri:Area/PubMed/Curation">005C12</idno>
<idno type="wicri:explorRef" wicri:stream="PubMed" wicri:step="Curation">005C12</idno>
<idno type="wicri:Area/PubMed/Checkpoint">005C12</idno>
<idno type="wicri:explorRef" wicri:stream="Checkpoint" wicri:step="PubMed">005C12</idno>
</publicationStmt>
<sourceDesc>
<biblStruct>
<analytic>
<title xml:lang="en">[Generalized lymphatic dysplasia in a 6-month-old nursing infant].</title>
<author>
<name sortKey="Massimo, L" sort="Massimo, L" uniqKey="Massimo L" first="L" last="Massimo">L. Massimo</name>
<affiliation wicri:level="1">
<nlm:affiliation>I Divisione di Pediatria, Ospedale Santobono, USL 40 Napoli, Italia.</nlm:affiliation>
<country xml:lang="fr">Italie</country>
<wicri:regionArea>I Divisione di Pediatria, Ospedale Santobono, USL 40 Napoli</wicri:regionArea>
<wicri:noRegion>USL 40 Napoli</wicri:noRegion>
</affiliation>
</author>
<author>
<name sortKey="Di Iorio, G" sort="Di Iorio, G" uniqKey="Di Iorio G" first="G" last="Di Iorio">G. Di Iorio</name>
</author>
<author>
<name sortKey="Martone, A" sort="Martone, A" uniqKey="Martone A" first="A" last="Martone">A. Martone</name>
</author>
<author>
<name sortKey="Sottile, R" sort="Sottile, R" uniqKey="Sottile R" first="R" last="Sottile">R. Sottile</name>
</author>
<author>
<name sortKey="Retolatto, A" sort="Retolatto, A" uniqKey="Retolatto A" first="A" last="Retolatto">A. Retolatto</name>
</author>
<author>
<name sortKey="Loiodice, F" sort="Loiodice, F" uniqKey="Loiodice F" first="F" last="Loiodice">F. Loiodice</name>
</author>
<author>
<name sortKey="Campa, A" sort="Campa, A" uniqKey="Campa A" first="A" last="Campa">A. Campa</name>
</author>
<author>
<name sortKey="Angelone, S" sort="Angelone, S" uniqKey="Angelone S" first="S" last="Angelone">S. Angelone</name>
</author>
</analytic>
<series>
<title level="j">La Pediatria medica e chirurgica : Medical and surgical pediatrics</title>
<idno type="ISSN">0391-5387</idno>
</series>
</biblStruct>
</sourceDesc>
</fileDesc>
<profileDesc>
<textClass>
<keywords scheme="KwdEn" xml:lang="en">
<term>Chylothorax (diagnosis)</term>
<term>Chylothorax (therapy)</term>
<term>Chylous Ascites (diagnosis)</term>
<term>Chylous Ascites (therapy)</term>
<term>Combined Modality Therapy (methods)</term>
<term>Humans</term>
<term>Infant</term>
<term>Lymphatic Diseases (diagnosis)</term>
<term>Lymphatic Diseases (therapy)</term>
<term>Lymphedema (diagnosis)</term>
<term>Lymphedema (therapy)</term>
<term>Male</term>
<term>Syndrome</term>
</keywords>
<keywords scheme="KwdFr" xml:lang="fr">
<term>Ascite chyleuse ()</term>
<term>Ascite chyleuse (diagnostic)</term>
<term>Association thérapeutique ()</term>
<term>Chylothorax ()</term>
<term>Chylothorax (diagnostic)</term>
<term>Humains</term>
<term>Lymphoedème ()</term>
<term>Lymphoedème (diagnostic)</term>
<term>Maladies lymphatiques ()</term>
<term>Maladies lymphatiques (diagnostic)</term>
<term>Mâle</term>
<term>Nourrisson</term>
<term>Syndrome</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en">
<term>Chylothorax</term>
<term>Chylous Ascites</term>
<term>Lymphatic Diseases</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnostic" xml:lang="fr">
<term>Ascite chyleuse</term>
<term>Chylothorax</term>
<term>Lymphoedème</term>
<term>Maladies lymphatiques</term>
</keywords>
<keywords scheme="MESH" qualifier="methods" xml:lang="en">
<term>Combined Modality Therapy</term>
</keywords>
<keywords scheme="MESH" qualifier="therapy" xml:lang="en">
<term>Chylothorax</term>
<term>Chylous Ascites</term>
<term>Lymphatic Diseases</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" xml:lang="en">
<term>Humans</term>
<term>Infant</term>
<term>Male</term>
<term>Syndrome</term>
</keywords>
<keywords scheme="MESH" xml:lang="fr">
<term>Ascite chyleuse</term>
<term>Association thérapeutique</term>
<term>Chylothorax</term>
<term>Humains</term>
<term>Lymphoedème</term>
<term>Maladies lymphatiques</term>
<term>Mâle</term>
<term>Nourrisson</term>
<term>Syndrome</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front>
<div type="abstract" xml:lang="en">G.L.D. is a rare syndrome characterized by chylothorax, chylous ascites and lymphedema associated to minor symptoms following from lymphangiectasis or to lymphangiomatosis. This syndrome is caused by congenital dysplasia of lymphatic vessels and has, generally, an extremely severe prognosis. In the present papers the authors describe one case of G.L.D. in a six months old infant with chylous ascites, chylothorax, lymphedema, hemangioma and a history of fetal ascites. The preservative (dietetic and evacuative) therapy was not resolutive, therefore an exploratory laparotomy was necessary, but no surgical solution was possible because of the absence of chylous vessels in the anatomical region of the principal lymphatic route. However, laparatomy led to a progressive recovery of ascites and chylothorax, probably due to thrombosis of dysplasic lymph vessels and to neoformation of collateral circulation.</div>
</front>
</TEI>
<pubmed>
<MedlineCitation Status="MEDLINE" Owner="NLM">
<PMID Version="1">2052465</PMID>
<DateCreated>
<Year>1991</Year>
<Month>07</Month>
<Day>24</Day>
</DateCreated>
<DateCompleted>
<Year>1991</Year>
<Month>07</Month>
<Day>24</Day>
</DateCompleted>
<DateRevised>
<Year>2006</Year>
<Month>11</Month>
<Day>15</Day>
</DateRevised>
<Article PubModel="Print">
<Journal>
<ISSN IssnType="Print">0391-5387</ISSN>
<JournalIssue CitedMedium="Print">
<Volume>13</Volume>
<Issue>1</Issue>
<PubDate>
<MedlineDate>1991 Jan-Feb</MedlineDate>
</PubDate>
</JournalIssue>
<Title>La Pediatria medica e chirurgica : Medical and surgical pediatrics</Title>
<ISOAbbreviation>Pediatr Med Chir</ISOAbbreviation>
</Journal>
<ArticleTitle>[Generalized lymphatic dysplasia in a 6-month-old nursing infant].</ArticleTitle>
<Pagination>
<MedlinePgn>99-103</MedlinePgn>
</Pagination>
<Abstract>
<AbstractText>G.L.D. is a rare syndrome characterized by chylothorax, chylous ascites and lymphedema associated to minor symptoms following from lymphangiectasis or to lymphangiomatosis. This syndrome is caused by congenital dysplasia of lymphatic vessels and has, generally, an extremely severe prognosis. In the present papers the authors describe one case of G.L.D. in a six months old infant with chylous ascites, chylothorax, lymphedema, hemangioma and a history of fetal ascites. The preservative (dietetic and evacuative) therapy was not resolutive, therefore an exploratory laparotomy was necessary, but no surgical solution was possible because of the absence of chylous vessels in the anatomical region of the principal lymphatic route. However, laparatomy led to a progressive recovery of ascites and chylothorax, probably due to thrombosis of dysplasic lymph vessels and to neoformation of collateral circulation.</AbstractText>
</Abstract>
<AuthorList CompleteYN="Y">
<Author ValidYN="Y">
<LastName>Massimo</LastName>
<ForeName>L</ForeName>
<Initials>L</Initials>
<AffiliationInfo>
<Affiliation>I Divisione di Pediatria, Ospedale Santobono, USL 40 Napoli, Italia.</Affiliation>
</AffiliationInfo>
</Author>
<Author ValidYN="Y">
<LastName>Di Iorio</LastName>
<ForeName>G</ForeName>
<Initials>G</Initials>
</Author>
<Author ValidYN="Y">
<LastName>Martone</LastName>
<ForeName>A</ForeName>
<Initials>A</Initials>
</Author>
<Author ValidYN="Y">
<LastName>Sottile</LastName>
<ForeName>R</ForeName>
<Initials>R</Initials>
</Author>
<Author ValidYN="Y">
<LastName>Retolatto</LastName>
<ForeName>A</ForeName>
<Initials>A</Initials>
</Author>
<Author ValidYN="Y">
<LastName>Loiodice</LastName>
<ForeName>F</ForeName>
<Initials>F</Initials>
</Author>
<Author ValidYN="Y">
<LastName>Campa</LastName>
<ForeName>A</ForeName>
<Initials>A</Initials>
</Author>
<Author ValidYN="Y">
<LastName>Angelone</LastName>
<ForeName>S</ForeName>
<Initials>S</Initials>
</Author>
</AuthorList>
<Language>ita</Language>
<PublicationTypeList>
<PublicationType UI="D002363">Case Reports</PublicationType>
<PublicationType UI="D004740">English Abstract</PublicationType>
<PublicationType UI="D016428">Journal Article</PublicationType>
</PublicationTypeList>
<VernacularTitle>Displasia linfatica generalizzata in un lattante di sei mesi.</VernacularTitle>
</Article>
<MedlineJournalInfo>
<Country>Italy</Country>
<MedlineTA>Pediatr Med Chir</MedlineTA>
<NlmUniqueID>8100625</NlmUniqueID>
<ISSNLinking>0391-5387</ISSNLinking>
</MedlineJournalInfo>
<CitationSubset>IM</CitationSubset>
<MeshHeadingList>
<MeshHeading>
<DescriptorName UI="D002916" MajorTopicYN="N">Chylothorax</DescriptorName>
<QualifierName UI="Q000175" MajorTopicYN="N">diagnosis</QualifierName>
<QualifierName UI="Q000628" MajorTopicYN="N">therapy</QualifierName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D002915" MajorTopicYN="N">Chylous Ascites</DescriptorName>
<QualifierName UI="Q000175" MajorTopicYN="N">diagnosis</QualifierName>
<QualifierName UI="Q000628" MajorTopicYN="N">therapy</QualifierName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D003131" MajorTopicYN="N">Combined Modality Therapy</DescriptorName>
<QualifierName UI="Q000379" MajorTopicYN="N">methods</QualifierName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D006801" MajorTopicYN="N">Humans</DescriptorName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D007223" MajorTopicYN="N">Infant</DescriptorName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D008206" MajorTopicYN="N">Lymphatic Diseases</DescriptorName>
<QualifierName UI="Q000175" MajorTopicYN="Y">diagnosis</QualifierName>
<QualifierName UI="Q000628" MajorTopicYN="N">therapy</QualifierName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D008209" MajorTopicYN="N">Lymphedema</DescriptorName>
<QualifierName UI="Q000175" MajorTopicYN="N">diagnosis</QualifierName>
<QualifierName UI="Q000628" MajorTopicYN="N">therapy</QualifierName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D008297" MajorTopicYN="N">Male</DescriptorName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D013577" MajorTopicYN="N">Syndrome</DescriptorName>
</MeshHeading>
</MeshHeadingList>
</MedlineCitation>
<PubmedData>
<History>
<PubMedPubDate PubStatus="pubmed">
<Year>1991</Year>
<Month>1</Month>
<Day>1</Day>
</PubMedPubDate>
<PubMedPubDate PubStatus="medline">
<Year>1991</Year>
<Month>1</Month>
<Day>1</Day>
<Hour>0</Hour>
<Minute>1</Minute>
</PubMedPubDate>
<PubMedPubDate PubStatus="entrez">
<Year>1991</Year>
<Month>1</Month>
<Day>1</Day>
<Hour>0</Hour>
<Minute>0</Minute>
</PubMedPubDate>
</History>
<PublicationStatus>ppublish</PublicationStatus>
<ArticleIdList>
<ArticleId IdType="pubmed">2052465</ArticleId>
</ArticleIdList>
</PubmedData>
</pubmed>
<affiliations>
<list>
<country>
<li>Italie</li>
</country>
</list>
<tree>
<noCountry>
<name sortKey="Angelone, S" sort="Angelone, S" uniqKey="Angelone S" first="S" last="Angelone">S. Angelone</name>
<name sortKey="Campa, A" sort="Campa, A" uniqKey="Campa A" first="A" last="Campa">A. Campa</name>
<name sortKey="Di Iorio, G" sort="Di Iorio, G" uniqKey="Di Iorio G" first="G" last="Di Iorio">G. Di Iorio</name>
<name sortKey="Loiodice, F" sort="Loiodice, F" uniqKey="Loiodice F" first="F" last="Loiodice">F. Loiodice</name>
<name sortKey="Martone, A" sort="Martone, A" uniqKey="Martone A" first="A" last="Martone">A. Martone</name>
<name sortKey="Retolatto, A" sort="Retolatto, A" uniqKey="Retolatto A" first="A" last="Retolatto">A. Retolatto</name>
<name sortKey="Sottile, R" sort="Sottile, R" uniqKey="Sottile R" first="R" last="Sottile">R. Sottile</name>
</noCountry>
<country name="Italie">
<noRegion>
<name sortKey="Massimo, L" sort="Massimo, L" uniqKey="Massimo L" first="L" last="Massimo">L. Massimo</name>
</noRegion>
</country>
</tree>
</affiliations>
</record>

Pour manipuler ce document sous Unix (Dilib)

EXPLOR_STEP=$WICRI_ROOT/Wicri/Sante/explor/LymphedemaV1/Data/PubMed/Checkpoint
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 008069 | SxmlIndent | more

Ou

HfdSelect -h $EXPLOR_AREA/Data/PubMed/Checkpoint/biblio.hfd -nk 008069 | SxmlIndent | more

Pour mettre un lien sur cette page dans le réseau Wicri

{{Explor lien
   |wiki=    Wicri/Sante
   |area=    LymphedemaV1
   |flux=    PubMed
   |étape=   Checkpoint
   |type=    RBID
   |clé=     pubmed:2052465
   |texte=   [Generalized lymphatic dysplasia in a 6-month-old nursing infant].
}}

Pour générer des pages wiki

HfdIndexSelect -h $EXPLOR_AREA/Data/PubMed/Checkpoint/RBID.i   -Sk "pubmed:2052465" \
       | HfdSelect -Kh $EXPLOR_AREA/Data/PubMed/Checkpoint/biblio.hfd   \
       | NlmPubMed2Wicri -a LymphedemaV1 

Wicri

This area was generated with Dilib version V0.6.31.
Data generation: Sat Nov 4 17:40:35 2017. Site generation: Tue Feb 13 16:42:16 2024