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Amniotic band syndrom at Bobo Dioulasso university teaching hospital (Burkina-Faso): about two cases.

Identifieur interne : 001096 ( PubMed/Checkpoint ); précédent : 001095; suivant : 001097

Amniotic band syndrom at Bobo Dioulasso university teaching hospital (Burkina-Faso): about two cases.

Auteurs : Cyprien Zaré [Burkina Faso] ; Ibrahim Alain Traoré [Burkina Faso] ; Patrick Wendpuoiré Hamed Dakouré [Burkina Faso] ; Salif Gandéma [Burkina Faso] ; Bakary Gustave Sano [Burkina Faso] ; Lazard Bouma Bénao [Burkina Faso] ; Hermann Belemlilga [Burkina Faso] ; Nassirou Yabré [Burkina Faso]

Source :

RBID : pubmed:26918082

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English descriptors

Abstract

Amniotic band syndrome is a rare congenital disorder. The authors report the first cases documented at Souro Sanou University Hospital in Bobo-Dioulasso (CHUSS) in 2 male new borns. The malformations found at birth, were worn only on limbs and were in the form of skin furrow necking with a major lymphedema downstream. In both cases, the constriction furrow at member pelvic was associated with a club foot and a pseudosyndactyly in one case. Surgical treatment consisted of a section of the constrictor ring and a Z-plasty. The functional outcome was satisfactory with the acquisition of a plantar support for both children. Through these two observations, epidemiological, diagnostic, and particularities of the management of this condition are discussed in the Burkina-Faso.

DOI: 10.11604/pamj.2015.22.187.7863
PubMed: 26918082


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<term>Amniotic Band Syndrome (surgery)</term>
<term>Burkina Faso</term>
<term>Clubfoot (etiology)</term>
<term>Clubfoot (pathology)</term>
<term>Clubfoot (surgery)</term>
<term>Hospitals, University</term>
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<term>Infant, Newborn</term>
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<term>Maladie des brides amniotiques (anatomopathologie)</term>
<term>Maladie des brides amniotiques (diagnostic)</term>
<term>Mâle</term>
<term>Nouveau-né</term>
<term>Pied bot varus équin congénital ()</term>
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<term>Pied bot varus équin congénital (étiologie)</term>
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<div type="abstract" xml:lang="en">Amniotic band syndrome is a rare congenital disorder. The authors report the first cases documented at Souro Sanou University Hospital in Bobo-Dioulasso (CHUSS) in 2 male new borns. The malformations found at birth, were worn only on limbs and were in the form of skin furrow necking with a major lymphedema downstream. In both cases, the constriction furrow at member pelvic was associated with a club foot and a pseudosyndactyly in one case. Surgical treatment consisted of a section of the constrictor ring and a Z-plasty. The functional outcome was satisfactory with the acquisition of a plantar support for both children. Through these two observations, epidemiological, diagnostic, and particularities of the management of this condition are discussed in the Burkina-Faso.</div>
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</MeshHeading>
<MeshHeading>
<DescriptorName UI="D006785" MajorTopicYN="N">Hospitals, University</DescriptorName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D006801" MajorTopicYN="N">Humans</DescriptorName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D007231" MajorTopicYN="N">Infant, Newborn</DescriptorName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D008297" MajorTopicYN="N">Male</DescriptorName>
</MeshHeading>
<MeshHeading>
<DescriptorName UI="D013576" MajorTopicYN="N">Syndactyly</DescriptorName>
<QualifierName UI="Q000209" MajorTopicYN="Y">etiology</QualifierName>
<QualifierName UI="Q000473" MajorTopicYN="N">pathology</QualifierName>
<QualifierName UI="Q000601" MajorTopicYN="N">surgery</QualifierName>
</MeshHeading>
</MeshHeadingList>
<OtherID Source="NLM">PMC4752845</OtherID>
<KeywordList Owner="NOTNLM">
<Keyword MajorTopicYN="N">Amniotic band syndrom</Keyword>
<Keyword MajorTopicYN="N">birth defects</Keyword>
<Keyword MajorTopicYN="N">surgery</Keyword>
</KeywordList>
</MedlineCitation>
<PubmedData>
<History>
<PubMedPubDate PubStatus="received">
<Year>2015</Year>
<Month>08</Month>
<Day>31</Day>
</PubMedPubDate>
<PubMedPubDate PubStatus="accepted">
<Year>2015</Year>
<Month>10</Month>
<Day>08</Day>
</PubMedPubDate>
<PubMedPubDate PubStatus="entrez">
<Year>2016</Year>
<Month>2</Month>
<Day>27</Day>
<Hour>6</Hour>
<Minute>0</Minute>
</PubMedPubDate>
<PubMedPubDate PubStatus="pubmed">
<Year>2016</Year>
<Month>2</Month>
<Day>27</Day>
<Hour>6</Hour>
<Minute>0</Minute>
</PubMedPubDate>
<PubMedPubDate PubStatus="medline">
<Year>2016</Year>
<Month>11</Month>
<Day>1</Day>
<Hour>6</Hour>
<Minute>0</Minute>
</PubMedPubDate>
</History>
<PublicationStatus>epublish</PublicationStatus>
<ArticleIdList>
<ArticleId IdType="pubmed">26918082</ArticleId>
<ArticleId IdType="doi">10.11604/pamj.2015.22.187.7863</ArticleId>
<ArticleId IdType="pii">PAMJ-22-187</ArticleId>
<ArticleId IdType="pmc">PMC4752845</ArticleId>
</ArticleIdList>
</PubmedData>
</pubmed>
<affiliations>
<list>
<country>
<li>Burkina Faso</li>
</country>
</list>
<tree>
<country name="Burkina Faso">
<noRegion>
<name sortKey="Zare, Cyprien" sort="Zare, Cyprien" uniqKey="Zare C" first="Cyprien" last="Zaré">Cyprien Zaré</name>
</noRegion>
<name sortKey="Belemlilga, Hermann" sort="Belemlilga, Hermann" uniqKey="Belemlilga H" first="Hermann" last="Belemlilga">Hermann Belemlilga</name>
<name sortKey="Benao, Lazard Bouma" sort="Benao, Lazard Bouma" uniqKey="Benao L" first="Lazard Bouma" last="Bénao">Lazard Bouma Bénao</name>
<name sortKey="Dakoure, Patrick Wendpuoire Hamed" sort="Dakoure, Patrick Wendpuoire Hamed" uniqKey="Dakoure P" first="Patrick Wendpuoiré Hamed" last="Dakouré">Patrick Wendpuoiré Hamed Dakouré</name>
<name sortKey="Gandema, Salif" sort="Gandema, Salif" uniqKey="Gandema S" first="Salif" last="Gandéma">Salif Gandéma</name>
<name sortKey="Sano, Bakary Gustave" sort="Sano, Bakary Gustave" uniqKey="Sano B" first="Bakary Gustave" last="Sano">Bakary Gustave Sano</name>
<name sortKey="Traore, Ibrahim Alain" sort="Traore, Ibrahim Alain" uniqKey="Traore I" first="Ibrahim Alain" last="Traoré">Ibrahim Alain Traoré</name>
<name sortKey="Yabre, Nassirou" sort="Yabre, Nassirou" uniqKey="Yabre N" first="Nassirou" last="Yabré">Nassirou Yabré</name>
</country>
</tree>
</affiliations>
</record>

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